Human Complex I Defects Can Be Resolved by Monoclonal Antibody Analysis into Distinct Subunit Assembly Patterns

Journal of Biological Chemistry

Volumn 276, Issue 12, 2001, Pages 8892-8897

  Triepels, Ralf H ^a   Hanson, Bonnie J ^b   Van den Heuvel, Lambert P ^a   Sundell, Linda ^b   Marusich, Michael F ^b   Smeitink, Jan A ^a   Capaldi, Roderick A ^b  

^a RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

^b UNIVERSITY OF OREGON   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ANTIBODIES; COMPLEXATION; ENZYME KINETICS; GENES; MUTAGENESIS;

RESPIRATORY CHAIN DISORDER;

BIOCHEMISTRY;

MONOCLONAL ANTIBODY; PROTEIN SUBUNIT; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); OXIDOREDUCTASE; PRIMER DNA;

ANTIGEN ANTIBODY REACTION; ARTICLE; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; DIAGNOSTIC VALUE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME ACTIVE SITE; ENZYME ACTIVITY; ENZYME ANALYSIS; ENZYME ASSAY; ENZYME DEFECT; ENZYME DEFICIENCY; GENE IDENTIFICATION; GENE MUTATION; GENOTYPE PHENOTYPE CORRELATION; HUMAN; HUMAN CELL; MEASUREMENT; MOLECULAR WEIGHT; MUTATIONAL ANALYSIS; NONHUMAN; PRIORITY JOURNAL; PROTEIN ASSEMBLY; SUCROSE GRADIENT; TECHNIQUE; WESTERN BLOTTING; ANIMAL; CATTLE; CELL CULTURE; GENETICS; IMMUNOLOGY; MUTATION; NUCLEOTIDE SEQUENCE;

ANIMALS; BASE SEQUENCE; CATTLE; CELLS, CULTURED; DNA PRIMERS; ELECTRON TRANSPORT COMPLEX I; HUMANS; MUTATION; NADH, NADPH OXIDOREDUCTASES;

EID: 0035937748     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M009903200     Document Type: Article

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