-
1
-
-
0025887093
-
Human dystrophin expression in mdx mice after intramuscular injection of DNA constructs
-
Acsadi, G., Dickson, G., Love, D.R., Jani, A., Walsh, F.S., Gurusinghe, A., Wolff, J.A., and Davies, K.E., 1991, Human dystrophin expression in mdx mice after intramuscular injection of DNA constructs, Nature, 352, pp 815-818.
-
(1991)
Nature
, vol.352
, pp. 815-818
-
-
Acsadi, G.1
Dickson, G.2
Love, D.R.3
Jani, A.4
Walsh, F.S.5
Gurusinghe, A.6
Wolff, J.A.7
Davies, K.E.8
-
2
-
-
0034468908
-
How calcium influx through calcium leak channels is responsible for the elevated levels of calcium-dependent proteolysis in dystrophic myotubes
-
Alderton, J.M., and Steinhardt, R.A., 2000a, How calcium influx through calcium leak channels is responsible for the elevated levels of calcium-dependent proteolysis in dystrophic myotubes, Trends Cardiovasc Med, 10, pp 268-272.
-
(2000)
Trends Cardiovasc Med
, vol.10
, pp. 268-272
-
-
Alderton, J.M.1
Steinhardt, R.A.2
-
3
-
-
0034737602
-
Calcium influx through calcium leak channels is responsible for the elevated levels of calcium-dependent proteolysis in dystrophic myotubes
-
Alderton, J.M., and Steinhardt, R.A., 2000b, Calcium influx through calcium leak channels is responsible for the elevated levels of calcium-dependent proteolysis in dystrophic myotubes, J Biol Chem, 275, pp 9452-9460.
-
(2000)
J Biol Chem
, vol.275
, pp. 9452-9460
-
-
Alderton, J.M.1
Steinhardt, R.A.2
-
4
-
-
0033758449
-
Animal models for muscular dystrophy: Valuable tools for the development of therapies
-
Allamand, V., and Campbell, K.P., 2000, Animal models for muscular dystrophy: valuable tools for the development of therapies, Hum Mol Genet, 9, pp 2459-2467.
-
(2000)
Hum Mol Genet
, vol.9
, pp. 2459-2467
-
-
Allamand, V.1
Campbell, K.P.2
-
5
-
-
25844469934
-
Mechanisms of stretch-induced muscle damage in normal and dystrophic muscle: Role of ionic changes
-
Allen, D.G., Whitehead, N.P., and Yeung, E.W., 2005, Mechanisms of stretch-induced muscle damage in normal and dystrophic muscle: role of ionic changes, J Physiol, 567, pp 723-735.
-
(2005)
J Physiol
, vol.567
, pp. 723-735
-
-
Allen, D.G.1
Whitehead, N.P.2
Yeung, E.W.3
-
6
-
-
0002138867
-
Structure and mutation of the dystrophin gene
-
(S. Brown and J.A. Lucy, eds) Cambridge University Press, Cambridge, UK
-
Amalfitano, A., Rafael, J.A., and Chamberlain, J.S., 1997, Structure and mutation of the dystrophin gene. In: Dystrophin: Gene, Protein and Cell Biology (S. Brown and J.A. Lucy, eds) Cambridge University Press, Cambridge, UK, pp 1-26.
-
(1997)
Dystrophin: Gene, Protein and Cell Biology
, pp. 1-26
-
-
Amalfitano, A.1
Rafael, J.A.2
Chamberlain, J.S.3
-
7
-
-
0029664392
-
2+-calmodulin binds to the carboxyl-terminal domain of dystrophin
-
2+-calmodulin binds to the carboxyl-terminal domain of dystrophin, J Biol Chem, 271, pp 6605-6610.
-
(1996)
J Biol Chem
, vol.271
, pp. 6605-6610
-
-
Anderson, J.T.1
Rogers, R.P.2
Jarrett, H.W.3
-
8
-
-
0033982278
-
Delay of muscle degeneration and necrosis in mdx mice by calpain inhibition
-
Badalamente, M.A., and Stracher, A., 2000, Delay of muscle degeneration and necrosis in mdx mice by calpain inhibition, Muscle Nerve, 23, pp 106-111.
-
(2000)
Muscle Nerve
, vol.23
, pp. 106-111
-
-
Badalamente, M.A.1
Stracher, A.2
-
10
-
-
0037738510
-
Defective membrane repair in dysferlin-deficient muscular dystrophy
-
Bansal, D., Miyake, K., Vogel, S.S., Groh, S., Chen, C.C., Williamson, R., McNeil, P.L., and Campbell, K.P., 2003, Defective membrane repair in dysferlin-deficient muscular dystrophy, Nature, 423, pp 168-172.
-
(2003)
Nature
, vol.423
, pp. 168-172
-
-
Bansal, D.1
Miyake, K.2
Vogel, S.S.3
Groh, S.4
Chen, C.C.5
Williamson, R.6
McNeil, P.L.7
Campbell, K.P.8
-
11
-
-
0025641035
-
Specificity of expression of the muscle and brain dystrophin gene promoters in muscle and brain cells
-
Barnea, E., Zuk, D., Simantov, R., Nudel, U., and Yaffe, D., 1990, Specificity of expression of the muscle and brain dystrophin gene promoters in muscle and brain cells, Neuron, 5, pp 881-888.
-
(1990)
Neuron
, vol.5
, pp. 881-888
-
-
Barnea, E.1
Zuk, D.2
Simantov, R.3
Nudel, U.4
Yaffe, D.5
-
12
-
-
33645756318
-
Bcl-2 overexpression prevents calcium overload and subsequent apoptosis in dystrophic myotubes
-
Basset, O., Boittin, F.X., Cognard, C., Constantin, B., and Ruegg, U.T., 2006, Bcl-2 overexpression prevents calcium overload and subsequent apoptosis in dystrophic myotubes, Biochem J, 395, pp 267-276.
-
(2006)
Biochem J
, vol.395
, pp. 267-276
-
-
Basset, O.1
Boittin, F.X.2
Cognard, C.3
Constantin, B.4
Ruegg, U.T.5
-
13
-
-
8744299928
-
Involvement of inositol 1,4,5-trisphosphate in nicotinic calcium responses in dystrophic myotubes assessed by near-plasma membrane calcium measurement
-
Basset, O., Boittin, F.X., Dorchies, O.M., Chatton, J.Y., van Breemen, C., and Ruegg, U.T., 2004, Involvement of inositol 1,4,5-trisphosphate in nicotinic calcium responses in dystrophic myotubes assessed by near-plasma membrane calcium measurement, J Biol Chem, 279, pp 47092-47100.
-
(2004)
J Biol Chem
, vol.279
, pp. 47092-47100
-
-
Basset, O.1
Boittin, F.X.2
Dorchies, O.M.3
Chatton, J.Y.4
van Breemen, C.5
Ruegg, U.T.6
-
14
-
-
0024580404
-
Molecular and clinical correlations of deletions leading to Duchenne and Becker muscular dystrophies
-
Baumbach, L.L., Chamberlain, J.S., Ward, P.A., Farwell, N.J., and Caskey, C.T., 1989, Molecular and clinical correlations of deletions leading to Duchenne and Becker muscular dystrophies, Neurology, 39, pp 465-474.
-
(1989)
Neurology
, vol.39
, pp. 465-474
-
-
Baumbach, L.L.1
Chamberlain, J.S.2
Ward, P.A.3
Farwell, N.J.4
Caskey, C.T.5
-
15
-
-
0025244924
-
Detection of 98% of DMD/BMD gene deletions by polymerase chain reaction
-
Beggs, A.H., Koenig, M., Boyce, F.M., and Kunkel, L.M., 1990, Detection of 98% of DMD/BMD gene deletions by polymerase chain reaction, Hum Genet, 86, pp 45-48.
-
(1990)
Hum Genet
, vol.86
, pp. 45-48
-
-
Beggs, A.H.1
Koenig, M.2
Boyce, F.M.3
Kunkel, L.M.4
-
16
-
-
0025250185
-
Improved diagnosis of Duchenne/Becker muscular dystrophy
-
Beggs, A.H., and Kunkel, L.M., 1990, Improved diagnosis of Duchenne/Becker muscular dystrophy, J Clin Invest, 85, pp 613-619.
-
(1990)
J Clin Invest
, vol.85
, pp. 613-619
-
-
Beggs, A.H.1
Kunkel, L.M.2
-
17
-
-
0014353260
-
Histopathological changes in Duchenne muscular dystrophy
-
Bell, C.D., and Conen, P.E., 1968, Histopathological changes in Duchenne muscular dystrophy, J Neurol Sci, 7, pp 529-544.
-
(1968)
J Neurol Sci
, vol.7
, pp. 529-544
-
-
Bell, C.D.1
Conen, P.E.2
-
18
-
-
0032432922
-
Mutations in the Caenorhabditis elegans dystrophin-like gene dys-1 lead to hyperactivity and suggest a link with cholinergic transmission
-
Bessou, C., Giugia, J.B., Franks, C.J., Holden-Dye, L., and Segalat, L., 1998, Mutations in the Caenorhabditis elegans dystrophin-like gene dys-1 lead to hyperactivity and suggest a link with cholinergic transmission, Neurogenetics, 2, pp 61-72.
-
(1998)
Neurogenetics
, vol.2
, pp. 61-72
-
-
Bessou, C.1
Giugia, J.B.2
Franks, C.J.3
Holden-Dye, L.4
Segalat, L.5
-
19
-
-
0026674204
-
An intact cysteine-rich domain is required for dystrophin function
-
Bies, R.D., Caskey, C.T., and Fenwick, R., 1992a, An intact cysteine-rich domain is required for dystrophin function, J Clin Invest, 90, pp 666-672.
-
(1992)
J Clin Invest
, vol.90
, pp. 666-672
-
-
Bies, R.D.1
Caskey, C.T.2
Fenwick, R.3
-
20
-
-
0026519484
-
Human and murine dystrophin mRNA transcripts are differentially expressed during skeletal muscle, heart, and brain development
-
Bies, R.D., Phelps, S.F., Cortez, M.D., Roberts, R., Caskey, C.T., and Chamberlain, J.S., 1992b, Human and murine dystrophin mRNA transcripts are differentially expressed during skeletal muscle, heart, and brain development, Nucleic Acids Res, 20, pp 1725-1731.
-
(1992)
Nucleic Acids Res
, vol.20
, pp. 1725-1731
-
-
Bies, R.D.1
Phelps, S.F.2
Cortez, M.D.3
Roberts, R.4
Caskey, C.T.5
Chamberlain, J.S.6
-
21
-
-
0026864614
-
Characterization of a 4.8kb transcript from the Duchenne muscular dystrophy locus expressed in Schwannoma cells
-
Blake, D.J., Love, D.R., Tinsley, J., Morris, G.E., Turley, H., Gatter, K., Dickson, G., Edwards, Y.H., and Davies, K.E., 1992, Characterization of a 4.8kb transcript from the Duchenne muscular dystrophy locus expressed in Schwannoma cells, Hum Mol Genet, 1, pp 103-109.
-
(1992)
Hum Mol Genet
, vol.1
, pp. 103-109
-
-
Blake, D.J.1
Love, D.R.2
Tinsley, J.3
Morris, G.E.4
Turley, H.5
Gatter, K.6
Dickson, G.7
Edwards, Y.H.8
Davies, K.E.9
-
22
-
-
0028987269
-
Coiled-coil regions in the carboxy-terminal domains of dystrophin and related proteins: Potentials for protein-protein interactions
-
Blake, D.J., Tinsley, J.M., Davies, K.E., Knight, A.E., Winder, S.J., and Kendrick-Jones, J., 1995, Coiled-coil regions in the carboxy-terminal domains of dystrophin and related proteins: potentials for protein-protein interactions, Trends Biochem Sci, 20, pp 133-135.
-
(1995)
Trends Biochem Sci
, vol.20
, pp. 133-135
-
-
Blake, D.J.1
Tinsley, J.M.2
Davies, K.E.3
Knight, A.E.4
Winder, S.J.5
Kendrick-Jones, J.6
-
23
-
-
0141760313
-
Proteasome inhibitor (MG-132) treatment of mdx mice rescues the expression and membrane localization of dystrophin and dystrophin-associated proteins
-
Bonuccelli, G., Sotgia, F., Schubert, W., Park, D.S., Frank, P.G., Woodman, S.E., Insabato, L., Cammer, M., Minetti, C., and Lisanti, M.P., 2003, Proteasome inhibitor (MG-132) treatment of mdx mice rescues the expression and membrane localization of dystrophin and dystrophin-associated proteins, Am J Pathol, 163, pp 1663-1675.
-
(2003)
Am J Pathol
, vol.163
, pp. 1663-1675
-
-
Bonuccelli, G.1
Sotgia, F.2
Schubert, W.3
Park, D.S.4
Frank, P.G.5
Woodman, S.E.6
Insabato, L.7
Cammer, M.8
Minetti, C.9
Lisanti, M.P.10
-
24
-
-
0027988814
-
The WW domain: A signalling site in dystrophin?
-
Bork, P., and Sudol, M., 1994, The WW domain: a signalling site in dystrophin?, Trends Biochem Sci, 19, pp 531-533.
-
(1994)
Trends Biochem Sci
, vol.19
, pp. 531-533
-
-
Bork, P.1
Sudol, M.2
-
25
-
-
0026013330
-
Dystrophin is transcribed in brain from a distant upstream promoter
-
Boyce, F.M., Beggs, A.H., Feener, C., and Kunkel, L.M., 1991, Dystrophin is transcribed in brain from a distant upstream promoter, Proc Natl Acad Sci U S A, 88, pp 1276-1280.
-
(1991)
Proc Natl Acad Sci U S A
, vol.88
, pp. 1276-1280
-
-
Boyce, F.M.1
Beggs, A.H.2
Feener, C.3
Kunkel, L.M.4
-
26
-
-
0022610195
-
Cytogenetic heterogeneity of translocations associated with Duchenne muscular dystrophy
-
Boyd, Y., and Buckle, V.J., 1986, Cytogenetic heterogeneity of translocations associated with Duchenne muscular dystrophy, Clin Genet, 29, pp 108-115.
-
(1986)
Clin Genet
, vol.29
, pp. 108-115
-
-
Boyd, Y.1
Buckle, V.J.2
-
27
-
-
0345731966
-
X chromosome-linked muscular dystrophy (mdx) in the mouse
-
Bulfield, G., Siller, W.G., Wight, P.A., and Moore, K.J., 1984, X chromosome-linked muscular dystrophy (mdx) in the mouse, Proc Natl Acad Sci U S A, 81, pp 1189-1192.
-
(1984)
Proc Natl Acad Sci U S A
, vol.81
, pp. 1189-1192
-
-
Bulfield, G.1
Siller, W.G.2
Wight, P.A.3
Moore, K.J.4
-
28
-
-
0035252931
-
Coiled coils: A highly versatile protein folding motif
-
Burkhard, P., Stetefeld, J., and Strelkov, S.V., 2001, Coiled coils: a highly versatile protein folding motif, Trends Cell Biol, 11, pp 82-88.
-
(2001)
Trends Cell Biol
, vol.11
, pp. 82-88
-
-
Burkhard, P.1
Stetefeld, J.2
Strelkov, S.V.3
-
29
-
-
0027214837
-
An alternative dystrophin transcript specific to peripheral nerve
-
Byers, T.J., Lidov, H.G., and Kunkel, L.M., 1993, An alternative dystrophin transcript specific to peripheral nerve, Nat Genet, 4, pp 77-81.
-
(1993)
Nat Genet
, vol.4
, pp. 77-81
-
-
Byers, T.J.1
Lidov, H.G.2
Kunkel, L.M.3
-
30
-
-
0142250850
-
2+ influx is not increased in a severely dystrophic expiratory muscle (triangularis sterni) of the mdx mouse
-
2+ influx is not increased in a severely dystrophic expiratory muscle (triangularis sterni) of the mdx mouse, Neurobiol Dis, 14, pp 229-239.
-
(2003)
Neurobiol Dis
, vol.14
, pp. 229-239
-
-
Carlson, C.G.1
Gueorguiev, A.2
Roshek, D.M.3
Ashmore, R.4
Chu, J.S.5
Anderson, J.E.6
-
31
-
-
0025301397
-
A noninvasive procedure to detect muscle weakness in the mdx mouse
-
Carlson, C.G., and Makiejus, R.V., 1990, A noninvasive procedure to detect muscle weakness in the mdx mouse, Muscle Nerve, 13, pp 480-484.
-
(1990)
Muscle Nerve
, vol.13
, pp. 480-484
-
-
Carlson, C.G.1
Makiejus, R.V.2
-
32
-
-
27744563126
-
Chronic treatment with agents that stabilize cytosolic IkappaB-alpha enhances survival and improves resting membrane potential in MDX muscle fibers subjected to chronic passive stretch
-
Carlson, C.G., Samadi, A., and Siegel, A., 2005, Chronic treatment with agents that stabilize cytosolic IkappaB-alpha enhances survival and improves resting membrane potential in MDX muscle fibers subjected to chronic passive stretch, Neurobiol Dis, 20, pp 719-730.
-
(2005)
Neurobiol Dis
, vol.20
, pp. 719-730
-
-
Carlson, C.G.1
Samadi, A.2
Siegel, A.3
-
33
-
-
0018351620
-
Duchenne muscular dystrophy: Plasma membrane loss initiates muscle cell necrosis unless it is repaired
-
Carpenter, S., and Karpati, G., 1979, Duchenne muscular dystrophy: plasma membrane loss initiates muscle cell necrosis unless it is repaired, Brain, 102, pp 147-161.
-
(1979)
Brain
, vol.102
, pp. 147-161
-
-
Carpenter, S.1
Karpati, G.2
-
34
-
-
0026737790
-
X-linked dystrophies: From gene localization to gene therapy
-
Chamberlain, J.S., 1992, X-linked dystrophies: from gene localization to gene therapy, Curr Opin Neurol Neurosurg, 5, pp 610-614.
-
(1992)
Curr Opin Neurol Neurosurg
, vol.5
, pp. 610-614
-
-
Chamberlain, J.S.1
-
35
-
-
0024580709
-
Recovery of induced mutations for X chromosome-linked muscular dystrophy in mice
-
Chapman, V.M., Miller, D.R., Armstrong, D., and Caskey, C.T., 1989, Recovery of induced mutations for X chromosome-linked muscular dystrophy in mice, Proc Natl Acad Sci U S A, 86, pp 1292-1296.
-
(1989)
Proc Natl Acad Sci U S A
, vol.86
, pp. 1292-1296
-
-
Chapman, V.M.1
Miller, D.R.2
Armstrong, D.3
Caskey, C.T.4
-
36
-
-
0025021669
-
Dystrophin gene transcribed from different promoters in neuronal and glial cells
-
Chelly, J., Hamard, G., Koulakoff, A., Kaplan, J.C., Kahn, A., and Berwald-Netter, Y., 1990, Dystrophin gene transcribed from different promoters in neuronal and glial cells, Nature, 344, pp 64-65.
-
(1990)
Nature
, vol.344
, pp. 64-65
-
-
Chelly, J.1
Hamard, G.2
Koulakoff, A.3
Kaplan, J.C.4
Kahn, A.5
Berwald-Netter, Y.6
-
37
-
-
0027430098
-
Loss of cytoplasmic basic fibroblast growth factor from physiologically wounded myofibers of normal and dystrophic muscle
-
Clarke, M.S., Khakee, R., and McNeil, P.L., 1993, Loss of cytoplasmic basic fibroblast growth factor from physiologically wounded myofibers of normal and dystrophic muscle, J Cell Sci, 106 (Pt 1), pp 121-133.
-
(1993)
J Cell Sci
, vol.106
, pp. 121-133
-
-
Clarke, M.S.1
Khakee, R.2
McNeil, P.L.3
-
38
-
-
0026608273
-
Construction of a 2.6-Mb contig in yeast artificial chromosomes spanning the human dystrophin gene using an STS-based approach
-
Coffey, A.J., Roberts, R.G., Green, E.D., Cole, C.G., Butler, R., Anand, R., Giannelli, F., and Bentley, D.R., 1992, Construction of a 2.6-Mb contig in yeast artificial chromosomes spanning the human dystrophin gene using an STS-based approach, Genomics, 12, pp 474-484.
-
(1992)
Genomics
, vol.12
, pp. 474-484
-
-
Coffey, A.J.1
Roberts, R.G.2
Green, E.D.3
Cole, C.G.4
Butler, R.5
Anand, R.6
Giannelli, F.7
Bentley, D.R.8
-
39
-
-
0033569656
-
Intracellular calcium signals measured with indo-1 in isolated skeletal muscle fibres from control and mdx mice
-
Collet, C., Allard, B., Tourneur, Y., and Jacquemond, V., 1999, Intracellular calcium signals measured with indo-1 in isolated skeletal muscle fibres from control and mdx mice, J Physiol, 520 Pt 2, pp 417-429.
-
(1999)
J Physiol
, vol.520
, pp. 417-429
-
-
Collet, C.1
Allard, B.2
Tourneur, Y.3
Jacquemond, V.4
-
40
-
-
0030590441
-
No alteration in gene expression of components of the ubiquitin-proteasome proteolytic pathway in dystrophin-deficient muscles
-
Combaret, L., Taillandier, D., Voisin, L., Samuels, S.E., Boespflug-Tanguy, O., and Attaix, D., 1996, No alteration in gene expression of components of the ubiquitin-proteasome proteolytic pathway in dystrophin-deficient muscles, FEBS Lett, 393, pp 292-296.
-
(1996)
FEBS Lett
, vol.393
, pp. 292-296
-
-
Combaret, L.1
Taillandier, D.2
Voisin, L.3
Samuels, S.E.4
Boespflug-Tanguy, O.5
Attaix, D.6
-
41
-
-
0024460536
-
Barium- and calcium-permeable channels open at negative membrane potentials in rat ventricular myocytes
-
Coulombe, A., Lefevre, I.A., Baro, I., and Coraboeuf, E., 1989, Barium- and calcium-permeable channels open at negative membrane potentials in rat ventricular myocytes, J Membr Biol, 111, pp 57-67.
-
(1989)
J Membr Biol
, vol.111
, pp. 57-67
-
-
Coulombe, A.1
Lefevre, I.A.2
Baro, I.3
Coraboeuf, E.4
-
42
-
-
0023910734
-
The mdx mouse skeletal muscle myopathy: I. A histological, morphometric and biochemical investigation
-
Coulton, G.R., Morgan, J.E., Partridge, T.A., and Sloper, J.C., 1988, The mdx mouse skeletal muscle myopathy: I. A histological, morphometric and biochemical investigation, Neuropathol Appl Neurobiol, 14, pp 53-70.
-
(1988)
Neuropathol Appl Neurobiol
, vol.14
, pp. 53-70
-
-
Coulton, G.R.1
Morgan, J.E.2
Partridge, T.A.3
Sloper, J.C.4
-
43
-
-
0027273835
-
New mdx mutation disrupts expression of muscle and nonmuscle isoforms of dystrophin
-
Cox, G.A., Phelps, S.F., Chapman, V.M., and Chamberlain, J.S., 1993, New mdx mutation disrupts expression of muscle and nonmuscle isoforms of dystrophin, Nat Genet, 4, pp 87-93.
-
(1993)
Nat Genet
, vol.4
, pp. 87-93
-
-
Cox, G.A.1
Phelps, S.F.2
Chapman, V.M.3
Chamberlain, J.S.4
-
44
-
-
0028134623
-
Dp71 can restore the dystrophinassociated glycoprotein complex in muscle but fails to prevent dystrophy
-
Cox, G.A., Sunada, Y., Campbell, K.P., and Chamberlain, J.S., 1994, Dp71 can restore the dystrophinassociated glycoprotein complex in muscle but fails to prevent dystrophy, Nat Genet, 8, pp 333-339.
-
(1994)
Nat Genet
, vol.8
, pp. 333-339
-
-
Cox, G.A.1
Sunada, Y.2
Campbell, K.P.3
Chamberlain, J.S.4
-
45
-
-
0034683567
-
Assembly of the dystrophin-associated protein complex does not require the dystrophin COOHterminal domain
-
Crawford, G.E., Faulkner, J.A., Crosbie, R.H., Campbell, K.P., Froehner, S.C., and Chamberlain, J.S., 2000, Assembly of the dystrophin-associated protein complex does not require the dystrophin COOHterminal domain, J Cell Biol, 150, pp 1399-1410.
-
(2000)
J Cell Biol
, vol.150
, pp. 1399-1410
-
-
Crawford, G.E.1
Faulkner, J.A.2
Crosbie, R.H.3
Campbell, K.P.4
Froehner, S.C.5
Chamberlain, J.S.6
-
46
-
-
0036092560
-
Drastic reduction of calsequestrin-like proteins and impaired calcium binding in dystrophic mdx muscle
-
Culligan, K., Banville, N., Dowling, P., and Ohlendieck, K., 2002, Drastic reduction of calsequestrin-like proteins and impaired calcium binding in dystrophic mdx muscle, J Appl Physiol, 92, pp 435-445.
-
(2002)
J Appl Physiol
, vol.92
, pp. 435-445
-
-
Culligan, K.1
Banville, N.2
Dowling, P.3
Ohlendieck, K.4
-
47
-
-
0021713536
-
Muscle development in mdx mutant mice
-
Dangain, J., and Vrbova, G., 1984, Muscle development in mdx mutant mice, Muscle Nerve, 7, pp 700-704.
-
(1984)
Muscle Nerve
, vol.7
, pp. 700-704
-
-
Dangain, J.1
Vrbova, G.2
-
48
-
-
0021111901
-
Linkage analysis of two cloned DNA sequences flanking the Duchenne muscular dystrophy locus on the short arm of the human X chromosome
-
Davies, K.E., Pearson, P.L., Harper, P.S., Murray, J.M., O'Brien, T., Sarfarazi, M., and Williamson, R., 1983, Linkage analysis of two cloned DNA sequences flanking the Duchenne muscular dystrophy locus on the short arm of the human X chromosome, Nucleic Acids Res, 11, pp 2303-2312.
-
(1983)
Nucleic Acids Res
, vol.11
, pp. 2303-2312
-
-
Davies, K.E.1
Pearson, P.L.2
Harper, P.S.3
Murray, J.M.4
O'Brien, T.5
Sarfarazi, M.6
Williamson, R.7
-
49
-
-
0036686713
-
Long-term study of Ca(2+) homeostasis and of survival in collagenase-isolated muscle fibres from normal and mdx mice
-
De Backer, F., Vandebrouck, C., Gailly, P., and Gillis, J.M., 2002, Long-term study of Ca(2+) homeostasis and of survival in collagenase-isolated muscle fibres from normal and mdx mice, J Physiol, 542, pp 855-865.
-
(2002)
J Physiol
, vol.542
, pp. 855-865
-
-
De Backer, F.1
Vandebrouck, C.2
Gailly, P.3
Gillis, J.M.4
-
50
-
-
0037215644
-
Enhanced dystrophic progression in mdx mice by exercise and beneficial effects of taurine and insulin-like growth factor-1
-
De Luca, A., Pierno, S., Liantonio, A., Cetrone, M., Camerino, C., Fraysse, B., Mirabella, M., Servidei, S., Ruegg, U.T., and Conte Camerino, D., 2003, Enhanced dystrophic progression in mdx mice by exercise and beneficial effects of taurine and insulin-like growth factor-1, J Pharmacol Exp Ther, 304, pp 453-463.
-
(2003)
J Pharmacol Exp Ther
, vol.304
, pp. 453-463
-
-
De Luca, A.1
Pierno, S.2
Liantonio, A.3
Cetrone, M.4
Camerino, C.5
Fraysse, B.6
Mirabella, M.7
Servidei, S.8
Ruegg, U.T.9
Conte Camerino, D.10
-
51
-
-
0029918603
-
Functional protection of dystrophic mouse (mdx) muscles after adenovirus-mediated transfer of a dystrophin minigene
-
Deconinck, N., Ragot, T., Marechal, G., Perricaudet, M., and Gillis, J.M., 1996, Functional protection of dystrophic mouse (mdx) muscles after adenovirus-mediated transfer of a dystrophin minigene, Proc Natl Acad Sci U S A, 93, pp 3570-3574.
-
(1996)
Proc Natl Acad Sci U S A
, vol.93
, pp. 3570-3574
-
-
Deconinck, N.1
Ragot, T.2
Marechal, G.3
Perricaudet, M.4
Gillis, J.M.5
-
52
-
-
0022930821
-
2+ channels in normal human skeletal muscle and in muscle from Duchenne muscular dystrophy patients
-
2+ channels in normal human skeletal muscle and in muscle from Duchenne muscular dystrophy patients, Muscle Nerve, 9, pp 148-151.
-
(1986)
Muscle Nerve
, vol.9
, pp. 148-151
-
-
Desnuelle, C.1
Renaud, J.F.2
Delpont, E.3
Serratrice, G.4
Lazdunski, M.5
-
53
-
-
0026038987
-
Fiber regeneration is not persistent in dystrophic (MDX) mouse skeletal muscle
-
DiMario, J.X., Uzman, A., and Strohman, R.C., 1991, Fiber regeneration is not persistent in dystrophic (MDX) mouse skeletal muscle, Dev Biol, 148, pp 314-321.
-
(1991)
Dev Biol
, vol.148
, pp. 314-321
-
-
DiMario, J.X.1
Uzman, A.2
Strohman, R.C.3
-
54
-
-
0036452835
-
Sarcoplasmic reticulum function in slow- and fast-twitch skeletal muscles from mdx mice
-
Divet, A., and Huchet-Cadiou, C., 2002, Sarcoplasmic reticulum function in slow- and fast-twitch skeletal muscles from mdx mice, Pflugers Arch, 444, pp 634-643.
-
(2002)
Pflugers Arch
, vol.444
, pp. 634-643
-
-
Divet, A.1
Huchet-Cadiou, C.2
-
55
-
-
21244467179
-
Effect of cyclopiazonic acid, an inhibitor of the sarcoplasmic reticulum Ca-ATPase, on skeletal muscles from normal and mdx mice
-
Divet, A., Lompre, A.M., and Huchet-Cadiou, C., 2005, Effect of cyclopiazonic acid, an inhibitor of the sarcoplasmic reticulum Ca-ATPase, on skeletal muscles from normal and mdx mice, Acta Physiol Scand, 184, pp 173-186.
-
(2005)
Acta Physiol Scand
, vol.184
, pp. 173-186
-
-
Divet, A.1
Lompre, A.M.2
Huchet-Cadiou, C.3
-
56
-
-
0042427273
-
Repairing the tears: Dysferlin in muscle membrane repair
-
Doherty, K.R., and McNally, E.M., 2003, Repairing the tears: dysferlin in muscle membrane repair, Trends Mol Med, 9, pp 327-330.
-
(2003)
Trends Mol Med
, vol.9
, pp. 327-330
-
-
Doherty, K.R.1
McNally, E.M.2
-
57
-
-
33646102225
-
Reduced expression of regucalcin in young and aged mdx diaphragm indicates abnormal cytosolic calcium handling in dystrophin-deficient muscle
-
Doran, P., Dowling, P., Donoghue, P., Buffini, M., and Ohlendieck, K., 2006, Reduced expression of regucalcin in young and aged mdx diaphragm indicates abnormal cytosolic calcium handling in dystrophin-deficient muscle, Biochim Biophys Acta, 1764, pp 773-785.
-
(2006)
Biochim Biophys Acta
, vol.1764
, pp. 773-785
-
-
Doran, P.1
Dowling, P.2
Donoghue, P.3
Buffini, M.4
Ohlendieck, K.5
-
58
-
-
4944230808
-
+-binding proteins demonstrates decreased calsequestrin expression in dystrophic mouse skeletal muscle
-
+-binding proteins demonstrates decreased calsequestrin expression in dystrophic mouse skeletal muscle, Eur J Biochem, 271, pp 3943-3952.
-
(2004)
Eur J Biochem
, vol.271
, pp. 3943-3952
-
-
Doran, P.1
Dowling, P.2
Lohan, J.3
McDonnell, K.4
Poetsch, S.5
Ohlendieck, K.6
-
59
-
-
2342614190
-
Drastic reduction of sarcalumenin in Dp427 (dystrophin of 427 kDa)-deficient fibres indicates that abnormal calcium handling plays a key role in muscular dystrophy
-
Dowling, P., Doran, P., and Ohlendieck, K., 2004, Drastic reduction of sarcalumenin in Dp427 (dystrophin of 427 kDa)-deficient fibres indicates that abnormal calcium handling plays a key role in muscular dystrophy, Biochem J, 379, pp 479-488.
-
(2004)
Biochem J
, vol.379
, pp. 479-488
-
-
Dowling, P.1
Doran, P.2
Ohlendieck, K.3
-
60
-
-
0027174251
-
Direct retroviral-mediated transfer of a dystrophin minigene into mdx mouse muscle in vivo
-
Dunckley, M.G., Wells, D.J., Walsh, F.S., and Dickson, G., 1993, Direct retroviral-mediated transfer of a dystrophin minigene into mdx mouse muscle in vivo, Hum Mol Genet, 2, pp 717-723.
-
(1993)
Hum Mol Genet
, vol.2
, pp. 717-723
-
-
Dunckley, M.G.1
Wells, D.J.2
Walsh, F.S.3
Dickson, G.4
-
61
-
-
0027389932
-
Sodium is elevated in mdx muscles: Ionic interactions in dystrophic cells
-
Dunn, J.F., Bannister, N., Kemp, G.J., and Publicover, S.J., 1993, Sodium is elevated in mdx muscles: ionic interactions in dystrophic cells, J Neurol Sci, 114, pp 76-80.
-
(1993)
J Neurol Sci
, vol.114
, pp. 76-80
-
-
Dunn, J.F.1
Bannister, N.2
Kemp, G.J.3
Publicover, S.J.4
-
62
-
-
0025159208
-
Very mild muscular dystrophy associated with the deletion of 46% of dystrophin
-
England, S.B., Nicholson, L.V., Johnson, M.A., Forrest, S.M., Love, D.R., Zubrzycka-Gaarn, E.E., Bulman, D.E., Harris, J.B., and Davies, K.E., 1990, Very mild muscular dystrophy associated with the deletion of 46% of dystrophin, Nature, 343, pp 180-182.
-
(1990)
Nature
, vol.343
, pp. 180-182
-
-
England, S.B.1
Nicholson, L.V.2
Johnson, M.A.3
Forrest, S.M.4
Love, D.R.5
Zubrzycka-Gaarn, E.E.6
Bulman, D.E.7
Harris, J.B.8
Davies, K.E.9
-
63
-
-
0024582731
-
Alternative splicing of human dystrophin mRNA generates isoforms at the carboxy terminus
-
Feener, C.A., Koenig, M., and Kunkel, L.M., 1989, Alternative splicing of human dystrophin mRNA generates isoforms at the carboxy terminus, Nature, 338, pp 509-511.
-
(1989)
Nature
, vol.338
, pp. 509-511
-
-
Feener, C.A.1
Koenig, M.2
Kunkel, L.M.3
-
64
-
-
0032966762
-
X-linked dilated cardiomyopathy and the dystrophin gene
-
Ferlini, A., Sewry, C., Melis, M.A., Mateddu, A., and Muntoni, F., 1999, X-linked dilated cardiomyopathy and the dystrophin gene, Neuromuscul Disord, 9, pp 339-346.
-
(1999)
Neuromuscul Disord
, vol.9
, pp. 339-346
-
-
Ferlini, A.1
Sewry, C.2
Melis, M.A.3
Mateddu, A.4
Muntoni, F.5
-
65
-
-
0025222219
-
Increased activity of calcium leak channels in myotubes of Duchenne human and mdx mouse origin
-
Fong, P.Y., Turner, P.R., Denetclaw, W.F., and Steinhardt, R.A., 1990, Increased activity of calcium leak channels in myotubes of Duchenne human and mdx mouse origin, Science, 250, pp 673-676.
-
(1990)
Science
, vol.250
, pp. 673-676
-
-
Fong, P.Y.1
Turner, P.R.2
Denetclaw, W.F.3
Steinhardt, R.A.4
-
66
-
-
0028564748
-
Mechanosensitive ion channels in skeletal muscle from normal and dystrophic mice
-
Franco-Obregon, A., Jr., and Lansman, J.B., 1994, Mechanosensitive ion channels in skeletal muscle from normal and dystrophic mice, J Physiol, 481 (Pt 2), pp 299-309.
-
(1994)
J Physiol
, vol.481
, pp. 299-309
-
-
Franco-Obregon, A.1
Lansman, J.B.2
-
67
-
-
0036522015
-
Changes in mechanosensitive channel gating following mechanical stimulation in skeletal muscle myotubes from the mdx mouse
-
Franco-Obregon, A., and Lansman, J.B., 2002, Changes in mechanosensitive channel gating following mechanical stimulation in skeletal muscle myotubes from the mdx mouse, J Physiol, 539, pp 391-407.
-
(2002)
J Physiol
, vol.539
, pp. 391-407
-
-
Franco-Obregon, A.1
Lansman, J.B.2
-
68
-
-
0025317892
-
Calcium entry through stretch-inactivated ion channels in mdx myotubes
-
Franco, A., Jr., and Lansman, J.B., 1990, Calcium entry through stretch-inactivated ion channels in mdx myotubes, Nature, 344, pp 670-673.
-
(1990)
Nature
, vol.344
, pp. 670-673
-
-
Franco, A.1
Lansman, J.B.2
-
69
-
-
5144232790
-
The alteration of calcium homeostasis in adult dystrophic mdx muscle fibers is worsened by a chronic exercise in vivo
-
Fraysse, B., Liantonio, A., Cetrone, M., Burdi, R., Pierno, S., Frigeri, A., Pisoni, M., Camerino, C., and De Luca, A., 2004, The alteration of calcium homeostasis in adult dystrophic mdx muscle fibers is worsened by a chronic exercise in vivo, Neurobiol Dis, 17, pp 144-154.
-
(2004)
Neurobiol Dis
, vol.17
, pp. 144-154
-
-
Fraysse, B.1
Liantonio, A.2
Cetrone, M.3
Burdi, R.4
Pierno, S.5
Frigeri, A.6
Pisoni, M.7
Camerino, C.8
De Luca, A.9
-
70
-
-
1542299755
-
Mini-dystrophin restores L-type calcium currents in skeletal muscle of transgenic mdx mice
-
Friedrich, O., Both, M., Gillis, J.M., Chamberlain, J.S., and Fink, R.H., 2004, Mini-dystrophin restores L-type calcium currents in skeletal muscle of transgenic mdx mice, J Physiol, 555, pp 251-265.
-
(2004)
J Physiol
, vol.555
, pp. 251-265
-
-
Friedrich, O.1
Both, M.2
Gillis, J.M.3
Chamberlain, J.S.4
Fink, R.H.5
-
71
-
-
0022466140
-
2+ or muscle injury does not involve a lysosomal mechanism
-
2+ or muscle injury does not involve a lysosomal mechanism, Biochem J, 237, pp 859-864.
-
(1986)
Biochem J
, vol.237
, pp. 859-864
-
-
Furuno, K.1
Goldberg, A.L.2
-
72
-
-
0037020667
-
New aspects of calcium signaling in skeletal muscle cells: Implications in Duchenne muscular dystrophy
-
Gailly, P., 2002, New aspects of calcium signaling in skeletal muscle cells: implications in Duchenne muscular dystrophy, Biochim Biophys Acta, 1600, pp 38-44.
-
(2002)
Biochim Biophys Acta
, vol.1600
, pp. 38-44
-
-
Gailly, P.1
-
73
-
-
0027234619
-
Critical evaluation of cytosolic calcium determination in resting muscle fibres from normal and dystrophic (mdx) mice
-
Gailly, P., Boland, B., Himpens, B., Casteels, R., and Gillis, J.M., 1993, Critical evaluation of cytosolic calcium determination in resting muscle fibres from normal and dystrophic (mdx) mice, Cell Calcium, 14, pp 473-483.
-
(1993)
Cell Calcium
, vol.14
, pp. 473-483
-
-
Gailly, P.1
Boland, B.2
Himpens, B.3
Casteels, R.4
Gillis, J.M.5
-
74
-
-
0029020724
-
The identification of point mutations in Duchenne muscular dystrophy patients by using reverse-transcription PCR and the protein truncation test
-
Gardner, R.J., Bobrow, M., and Roberts, R.G., 1995, The identification of point mutations in Duchenne muscular dystrophy patients by using reverse-transcription PCR and the protein truncation test, Am J Hum Genet, 57, pp 311-320.
-
(1995)
Am J Hum Genet
, vol.57
, pp. 311-320
-
-
Gardner, R.J.1
Bobrow, M.2
Roberts, R.G.3
-
75
-
-
4444267191
-
Differential expression of the skeletal muscle proteome in mdx mice at different ages
-
Ge, Y., Molloy, M.P., Chamberlain, J.S., and Andrews, P.C., 2004, Differential expression of the skeletal muscle proteome in mdx mice at different ages, Electrophoresis, 25, pp 2576-2585.
-
(2004)
Electrophoresis
, vol.25
, pp. 2576-2585
-
-
Ge, Y.1
Molloy, M.P.2
Chamberlain, J.S.3
Andrews, P.C.4
-
76
-
-
0033382340
-
Understanding dystrophinopathies: An inventory of the structural and functional consequences of the absence of dystrophin in muscles of the mdx mouse
-
Gillis, J.M., 1999, Understanding dystrophinopathies: an inventory of the structural and functional consequences of the absence of dystrophin in muscles of the mdx mouse, J Muscle Res Cell Motil, 20, pp 605-625.
-
(1999)
J Muscle Res Cell Motil
, vol.20
, pp. 605-625
-
-
Gillis, J.M.1
-
77
-
-
0031736870
-
A dystrophin missense mutation showing persistence of dystrophin and dystrophin-associated proteins yet a severe phenotype
-
Goldberg, L.R., Hausmanowa-Petrusewicz, I., Fidzianska, A., Duggan, D.J., Steinberg, L.S., and Hoffman, E.P., 1998, A dystrophin missense mutation showing persistence of dystrophin and dystrophin-associated proteins yet a severe phenotype, Ann Neurol, 44, pp 971-976.
-
(1998)
Ann Neurol
, vol.44
, pp. 971-976
-
-
Goldberg, L.R.1
Hausmanowa-Petrusewicz, I.2
Fidzianska, A.3
Duggan, D.J.4
Steinberg, L.S.5
Hoffman, E.P.6
-
78
-
-
0026937998
-
Expression of four alternative dystrophin transcripts in brain regions regulated by different promoters
-
Gorecki, D.C., Monaco, A.P., Derry, J.M., Walker, A.P., Barnard, E.A., and Barnard, P.J., 1992, Expression of four alternative dystrophin transcripts in brain regions regulated by different promoters, Hum Mol Genet, 1, pp 505-510.
-
(1992)
Hum Mol Genet
, vol.1
, pp. 505-510
-
-
Gorecki, D.C.1
Monaco, A.P.2
Derry, J.M.3
Walker, A.P.4
Barnard, E.A.5
Barnard, P.J.6
-
79
-
-
0002978451
-
Pathophysiology of dystrophin deficiency: A clinical and biological enigma
-
Dystrophin: Gene, (S. Brown and J.A. Lucy, eds) Cambridge University Press, Cambridge, UK
-
Gorospe, J.R.M., Nishikawa, B.K., and Hoffman, E.P., Pathophysiology of dystrophin deficiency: a clinical and biological enigma. In: Dystrophin: Gene, Protein and Cell Biology (S. Brown and J.A. Lucy, eds) Cambridge University Press, Cambridge, UK, pp 201-232.
-
Protein and Cell Biology
, pp. 201-232
-
-
Gorospe, J.R.M.1
Nishikawa, B.K.2
Hoffman, E.P.3
-
80
-
-
0034214278
-
Pre-clinical screening of drugs using the mdx mouse
-
Granchelli, J.A., Pollina, C., and Hudecki, M.S., 2000, Pre-clinical screening of drugs using the mdx mouse, Neuromuscul Disord, 10, pp 235-239.
-
(2000)
Neuromuscul Disord
, vol.10
, pp. 235-239
-
-
Granchelli, J.A.1
Pollina, C.2
Hudecki, M.S.3
-
81
-
-
0028051872
-
Exogenous Dp71 restores the levels of dystrophin associated proteins but does not alleviate muscle damage in mdx mice
-
Greenberg, D.S., Sunada, Y., Campbell, K.P., Yaffe, D., and Nudel, U., 1994, Exogenous Dp71 restores the levels of dystrophin associated proteins but does not alleviate muscle damage in mdx mice, Nat Genet, 8, pp 340-344.
-
(1994)
Nat Genet
, vol.8
, pp. 340-344
-
-
Greenberg, D.S.1
Sunada, Y.2
Campbell, K.P.3
Yaffe, D.4
Nudel, U.5
-
82
-
-
0042266913
-
A conserved domain in axonal targeting of Kv1 (Shaker) voltage-gated potassium channels
-
Gu, C., Jan, Y.N., and Jan, L.Y., 2003, A conserved domain in axonal targeting of Kv1 (Shaker) voltage-gated potassium channels, Science, 301, pp 646-649.
-
(2003)
Science
, vol.301
, pp. 646-649
-
-
Gu, C.1
Jan, Y.N.2
Jan, L.Y.3
-
83
-
-
0034995804
-
Stretch-activation and stretch-inactivation of Shaker-IR, a voltage-gated K+ channel
-
Gu, C.X., Juranka, P.F., and Morris, C.E., 2001, Stretch-activation and stretch-inactivation of Shaker-IR, a voltage-gated K+ channel, Biophys J, 80, pp 2678-2693.
-
(2001)
Biophys J
, vol.80
, pp. 2678-2693
-
-
Gu, C.X.1
Juranka, P.F.2
Morris, C.E.3
-
84
-
-
0016427755
-
Histochemical changes in innervated and denervated skeletal muscle fibers following treatment with bupivacaine (marcain)
-
Hall-Craggs, E.C., and Seyan, H.S., 1975, Histochemical changes in innervated and denervated skeletal muscle fibers following treatment with bupivacaine (marcain), Exp Neurol, 46, pp 345-354.
-
(1975)
Exp Neurol
, vol.46
, pp. 345-354
-
-
Hall-Craggs, E.C.1
Seyan, H.S.2
-
85
-
-
32544448060
-
The association of caveolae, actin, and the dystrophinglycoprotein complex: A role in smooth muscle phenotype and function?
-
Halayko, A.J., and Stelmack, G.L., 2005, The association of caveolae, actin, and the dystrophinglycoprotein complex: a role in smooth muscle phenotype and function?, Can J Physiol Pharmacol, 83, pp 877-891.
-
(2005)
Can J Physiol Pharmacol
, vol.83
, pp. 877-891
-
-
Halayko, A.J.1
Stelmack, G.L.2
-
86
-
-
0033065198
-
Undetectable dystrophin can still result in a relatively benign phenotype of dystrophinopathy
-
Hattori, N., Kaido, M., Nishigaki, T., Inui, K., Fujimura, H., Nishimura, T., Naka, T., and Hazama, T., 1999, Undetectable dystrophin can still result in a relatively benign phenotype of dystrophinopathy, Neuromuscul Disord, 9, pp 220-226.
-
(1999)
Neuromuscul Disord
, vol.9
, pp. 220-226
-
-
Hattori, N.1
Kaido, M.2
Nishigaki, T.3
Inui, K.4
Fujimura, H.5
Nishimura, T.6
Naka, T.7
Hazama, T.8
-
87
-
-
0026587401
-
A truncated dystrophin lacking the C-terminal domains is localized at the muscle membrane
-
Helliwell, T.R., Ellis, J.M., Mountford, R.C., Appleton, R.E., and Morris, G.E., 1992, A truncated dystrophin lacking the C-terminal domains is localized at the muscle membrane, Am J Hum Genet, 50, pp 508-514.
-
(1992)
Am J Hum Genet
, vol.50
, pp. 508-514
-
-
Helliwell, T.R.1
Ellis, J.M.2
Mountford, R.C.3
Appleton, R.E.4
Morris, G.E.5
-
88
-
-
0032442182
-
Muscle fibre atrophy in critically ill patients is associated with the loss of myosin filaments and the presence of lysosomal enzymes and ubiquitin
-
Helliwell, T.R., Wilkinson, A., Griffiths, R.D., McClelland, P., Palmer, T.E., and Bone, J.M., 1998, Muscle fibre atrophy in critically ill patients is associated with the loss of myosin filaments and the presence of lysosomal enzymes and ubiquitin, Neuropathol Appl Neurobiol, 24, pp 507-517.
-
(1998)
Neuropathol Appl Neurobiol
, vol.24
, pp. 507-517
-
-
Helliwell, T.R.1
Wilkinson, A.2
Griffiths, R.D.3
McClelland, P.4
Palmer, T.E.5
Bone, J.M.6
-
89
-
-
0026746706
-
Dystrophin: The protein product of the Duchene muscular dystrophy locus. 1987
-
Hoffman, E.P., Brown, R.H., and Kunkel, L.M., 1992, Dystrophin: the protein product of the Duchene muscular dystrophy locus. 1987, Biotechnology, 24, pp 457-466.
-
(1992)
Biotechnology
, vol.24
, pp. 457-466
-
-
Hoffman, E.P.1
Brown, R.H.2
Kunkel, L.M.3
-
90
-
-
0026049619
-
Is the carboxyl-terminus of dystrophin required for membrane association? A novel, severe case of Duchenne muscular dystrophy
-
Hoffman, E.P., Garcia, C.A., Chamberlain, J.S., Angelini, C., Lupski, J.R., and Fenwick, R., 1991, Is the carboxyl-terminus of dystrophin required for membrane association? A novel, severe case of Duchenne muscular dystrophy, Ann Neurol, 30, pp 605-610.
-
(1991)
Ann Neurol
, vol.30
, pp. 605-610
-
-
Hoffman, E.P.1
Garcia, C.A.2
Chamberlain, J.S.3
Angelini, C.4
Lupski, J.R.5
Fenwick, R.6
-
91
-
-
0030025402
-
Expression and regulation of the dystrophin Purkinje promoter in human skeletal muscle, heart, and brain
-
Holder, E., Maeda, M., and Bies, R.D., 1996, Expression and regulation of the dystrophin Purkinje promoter in human skeletal muscle, heart, and brain, Hum Genet, 97, pp 232-239.
-
(1996)
Hum Genet
, vol.97
, pp. 232-239
-
-
Holder, E.1
Maeda, M.2
Bies, R.D.3
-
92
-
-
0029788097
-
A capacitative calcium current in cultured skeletal muscle cells is mediated by the calcium-specific leak channel and inhibited by dihydropyridine compounds
-
Hopf, F.W., Reddy, P., Hong, J., and Steinhardt, R.A., 1996a, A capacitative calcium current in cultured skeletal muscle cells is mediated by the calcium-specific leak channel and inhibited by dihydropyridine compounds, J Biol Chem, 271, pp 22358-22367.
-
(1996)
J Biol Chem
, vol.271
, pp. 22358-22367
-
-
Hopf, F.W.1
Reddy, P.2
Hong, J.3
Steinhardt, R.A.4
-
93
-
-
0029964897
-
A critical evaluation of resting intracellular free calcium regulation in dystrophic mdx muscle
-
Hopf, F.W., Turner, P.R., Denetclaw, W.F., Jr., Reddy, P., and Steinhardt, R.A., 1996b, A critical evaluation of resting intracellular free calcium regulation in dystrophic mdx muscle, Am J Physiol, 271, pp C1325-1339.
-
(1996)
Am J Physiol
, vol.271
, pp. C1325-C1339
-
-
Hopf, F.W.1
Turner, P.R.2
Denetclaw, W.F.3
Reddy, P.4
Steinhardt, R.A.5
-
94
-
-
0032889265
-
Dystrophin isoforms DP71 and DP427 have distinct roles in myogenic cells
-
Howard, P.L., Dally, G.Y., Ditta, S.D., Austin, R.C., Worton, R.G., Klamut, H.J., and Ray, P.N., 1999, Dystrophin isoforms DP71 and DP427 have distinct roles in myogenic cells, Muscle Nerve, 22, pp 16-27.
-
(1999)
Muscle Nerve
, vol.22
, pp. 16-27
-
-
Howard, P.L.1
Dally, G.Y.2
Ditta, S.D.3
Austin, R.C.4
Worton, R.G.5
Klamut, H.J.6
Ray, P.N.7
-
95
-
-
0031683687
-
Localization of dystrophin isoform Dp71 to the inner limiting membrane of the retina suggests a unique functional contribution of Dp71 in the retina
-
Howard, P.L., Dally, G.Y., Wong, M.H., Ho, A., Weleber, R.G., Pillers, D.A., and Ray, P.N., 1998, Localization of dystrophin isoform Dp71 to the inner limiting membrane of the retina suggests a unique functional contribution of Dp71 in the retina, Hum Mol Genet, 7, pp 1385-1391.
-
(1998)
Hum Mol Genet
, vol.7
, pp. 1385-1391
-
-
Howard, P.L.1
Dally, G.Y.2
Wong, M.H.3
Ho, A.4
Weleber, R.G.5
Pillers, D.A.6
Ray, P.N.7
-
96
-
-
0343081091
-
Structure of a WW domain containing fragment of dystrophin in complex with beta-dystroglycan
-
Huang, X., Poy, F., Zhang, R., Joachimiak, A., Sudol, M., and Eck, M.J., 2000, Structure of a WW domain containing fragment of dystrophin in complex with beta-dystroglycan, Nat Struct Biol, 7, pp 634-638.
-
(2000)
Nat Struct Biol
, vol.7
, pp. 634-638
-
-
Huang, X.1
Poy, F.2
Zhang, R.3
Joachimiak, A.4
Sudol, M.5
Eck, M.J.6
-
97
-
-
0026732709
-
Distal transcript of the dystrophin gene initiated from an alternative first exon and encoding a 75-kDa protein widely distributed in nonmuscle tissues
-
Hugnot, J.P., Gilgenkrantz, H., Vincent, N., Chafey, P., Morris, G.E., Monaco, A.P., Berwald-Netter, Y., Koulakoff, A., Kaplan, J.C., Kahn, A., and et al., 1992, Distal transcript of the dystrophin gene initiated from an alternative first exon and encoding a 75-kDa protein widely distributed in nonmuscle tissues, Proc Natl Acad Sci U S A, 89, pp 7506-7510.
-
(1992)
Proc Natl Acad Sci U S A
, vol.89
, pp. 7506-7510
-
-
Hugnot, J.P.1
Gilgenkrantz, H.2
Vincent, N.3
Chafey, P.4
Morris, G.E.5
Monaco, A.P.6
Berwald-Netter, Y.7
Koulakoff, A.8
Kaplan, J.C.9
Kahn, A.10
-
98
-
-
0026543686
-
Primary structure of dystrophin-associated glycoproteins linking dystrophin to the extracellular matrix
-
Ibraghimov-Beskrovnaya, O., Ervasti, J.M., Leveille, C.J., Slaughter, C.A., Sernett, S.W., and Campbell, K.P., 1992, Primary structure of dystrophin-associated glycoproteins linking dystrophin to the extracellular matrix, Nature, 355, pp 696-702.
-
(1992)
Nature
, vol.355
, pp. 696-702
-
-
Ibraghimov-Beskrovnaya, O.1
Ervasti, J.M.2
Leveille, C.J.3
Slaughter, C.A.4
Sernett, S.W.5
Campbell, K.P.6
-
99
-
-
0027377154
-
Human dystroglycan: Skeletal muscle cDNA, genomic structure, origin of tissue specific isoforms and chromosomal localization
-
Ibraghimov-Beskrovnaya, O., Milatovich, A., Ozcelik, T., Yang, B., Koepnick, K., Francke, U., and Campbell, K.P., 1993, Human dystroglycan: skeletal muscle cDNA, genomic structure, origin of tissue specific isoforms and chromosomal localization, Hum Mol Genet, 2, pp 1651-1657.
-
(1993)
Hum Mol Genet
, vol.2
, pp. 1651-1657
-
-
Ibraghimov-Beskrovnaya, O.1
Milatovich, A.2
Ozcelik, T.3
Yang, B.4
Koepnick, K.5
Francke, U.6
Campbell, K.P.7
-
100
-
-
0029820310
-
Differential expression of dystrophin isoforms in strains of mdx mice with different mutations
-
Im, W.B., Phelps, S.F., Copen, E.H., Adams, E.G., Slightom, J.L., and Chamberlain, J.S., 1996, Differential expression of dystrophin isoforms in strains of mdx mice with different mutations, Hum Mol Genet, 5, pp 1149-1153.
-
(1996)
Hum Mol Genet
, vol.5
, pp. 1149-1153
-
-
Im, W.B.1
Phelps, S.F.2
Copen, E.H.3
Adams, E.G.4
Slightom, J.L.5
Chamberlain, J.S.6
-
101
-
-
0029609424
-
Abnormal calcium homeostasis in Duchenne muscular dystrophy myotubes contracting in vitro
-
Imbert, N., Cognard, C., Duport, G., Guillou, C., and Raymond, G., 1995, Abnormal calcium homeostasis in Duchenne muscular dystrophy myotubes contracting in vitro, Cell Calcium, 18, pp 177-186.
-
(1995)
Cell Calcium
, vol.18
, pp. 177-186
-
-
Imbert, N.1
Cognard, C.2
Duport, G.3
Guillou, C.4
Raymond, G.5
-
102
-
-
0030273325
-
Hypoosmotic shocks induce elevation of resting calcium level in Duchenne muscular dystrophy myotubes contracting in vitro
-
Imbert, N., Vandebrouck, C., Constantin, B., Duport, G., Guillou, C., Cognard, C., and Raymond, G., 1996, Hypoosmotic shocks induce elevation of resting calcium level in Duchenne muscular dystrophy myotubes contracting in vitro, Neuromuscul Disord, 6, pp 351-360.
-
(1996)
Neuromuscul Disord
, vol.6
, pp. 351-360
-
-
Imbert, N.1
Vandebrouck, C.2
Constantin, B.3
Duport, G.4
Guillou, C.5
Cognard, C.6
Raymond, G.7
-
103
-
-
0035878751
-
Calcium currents and transients in co-cultured contracting normal and Duchenne muscular dystrophy human myotubes
-
Imbert, N., Vandebrouck, C., Duport, G., Raymond, G., Hassoni, A.A., Constantin, B., Cullen, M.J., and Cognard, C., 2001, Calcium currents and transients in co-cultured contracting normal and Duchenne muscular dystrophy human myotubes, J Physiol, 534, pp 343-355.
-
(2001)
J Physiol
, vol.534
, pp. 343-355
-
-
Imbert, N.1
Vandebrouck, C.2
Duport, G.3
Raymond, G.4
Hassoni, A.A.5
Constantin, B.6
Cullen, M.J.7
Cognard, C.8
-
104
-
-
0038457838
-
2+-permeable growth factor-regulated channel
-
2+-permeable growth factor-regulated channel, J Cell Biol, 161, pp 957-967.
-
(2003)
J Cell Biol
, vol.161
, pp. 957-967
-
-
Iwata, Y.1
Katanosaka, Y.2
Arai, Y.3
Komamura, K.4
Miyatake, K.5
Shigekawa, M.6
-
105
-
-
0021130954
-
Experimental skeletal muscle damage: The nature of the calcium-activated degenerative processes
-
Jackson, M.J., Jones, D.A., and Edwards, R.H., 1984, Experimental skeletal muscle damage: the nature of the calcium-activated degenerative processes, Eur J Clin Invest, 14, pp 369-374.
-
(1984)
Eur J Clin Invest
, vol.14
, pp. 369-374
-
-
Jackson, M.J.1
Jones, D.A.2
Edwards, R.H.3
-
106
-
-
0034027602
-
Adhesion-dependent tyrosine phosphorylation of (beta)-dystroglycan regulates its interaction with utrophin
-
James, M., Nuttall, A., Ilsley, J.L., Ottersbach, K., Tinsley, J.M., Sudol, M., and Winder, S.J., 2000, Adhesion-dependent tyrosine phosphorylation of (beta)-dystroglycan regulates its interaction with utrophin, J Cell Sci, 113 (Pt 10), pp 1717-1726.
-
(2000)
J Cell Sci
, vol.113
, pp. 1717-1726
-
-
James, M.1
Nuttall, A.2
Ilsley, J.L.3
Ottersbach, K.4
Tinsley, J.M.5
Sudol, M.6
Winder, S.J.7
-
107
-
-
0034024776
-
Expression of MyoD and myogenin in dystrophic mice, mdx and dy, during regeneration
-
Jin, Y., Murakami, N., Saito, Y., Goto, Y., Koishi, K., and Nonaka, I., 2000, Expression of MyoD and myogenin in dystrophic mice, mdx and dy, during regeneration, Acta Neuropathol (Berl), 99, pp 619-627.
-
(2000)
Acta Neuropathol (Berl)
, vol.99
, pp. 619-627
-
-
Jin, Y.1
Murakami, N.2
Saito, Y.3
Goto, Y.4
Koishi, K.5
Nonaka, I.6
-
108
-
-
0028805790
-
Identification and characterization of the dystrophin anchoring site on beta-dystroglycan
-
Jung, D., Yang, B., Meyer, J., Chamberlain, J.S., and Campbell, K.P., 1995, Identification and characterization of the dystrophin anchoring site on beta-dystroglycan, J Biol Chem, 270, pp 27305-27310.
-
(1995)
J Biol Chem
, vol.270
, pp. 27305-27310
-
-
Jung, D.1
Yang, B.2
Meyer, J.3
Chamberlain, J.S.4
Campbell, K.P.5
-
109
-
-
0018083852
-
Muscular dystrophy and activation of proteinases
-
Kar, N.C., and Pearson, C.M., 1978, Muscular dystrophy and activation of proteinases, Muscle Nerve, 1, pp 308-313.
-
(1978)
Muscle Nerve
, vol.1
, pp. 308-313
-
-
Kar, N.C.1
Pearson, C.M.2
-
110
-
-
0030003967
-
The sarcoplasmic reticulum calcium pump is functionally altered in dystrophic muscle
-
Kargacin, M.E., and Kargacin, G.J., 1996, The sarcoplasmic reticulum calcium pump is functionally altered in dystrophic muscle, Biochim Biophys Acta, 1290, pp 4-8.
-
(1996)
Biochim Biophys Acta
, vol.1290
, pp. 4-8
-
-
Kargacin, M.E.1
Kargacin, G.J.2
-
111
-
-
0021108172
-
Localisation of gene for Becker muscular dystrophy
-
Kingston, H.M., Harper, P.S., Pearson, P.L., Davies, K.E., Williamson, R., and Page, D., 1983, Localisation of gene for Becker muscular dystrophy, Lancet, 2, pp 1200.
-
(1983)
Lancet
, vol.2
, pp. 1200
-
-
Kingston, H.M.1
Harper, P.S.2
Pearson, P.L.3
Davies, K.E.4
Williamson, R.5
Page, D.6
-
112
-
-
0032480821
-
Functional interaction between InsP3 receptors and store-operated Htrp3 channels
-
Kiselyov, K., Xu, X., Mozhayeva, G., Kuo, T., Pessah, I., Mignery, G., Zhu, X., Birnbaumer, L., and Muallem, S., 1998, Functional interaction between InsP3 receptors and store-operated Htrp3 channels, Nature, 396, pp 478-482.
-
(1998)
Nature
, vol.396
, pp. 478-482
-
-
Kiselyov, K.1
Xu, X.2
Mozhayeva, G.3
Kuo, T.4
Pessah, I.5
Mignery, G.6
Zhu, X.7
Birnbaumer, L.8
Muallem, S.9
-
113
-
-
0025181885
-
Molecular and functional analysis of the muscle-specific promoter region of the Duchenne muscular dystrophy gene
-
Klamut, H.J., Gangopadhyay, S.B., Worton, R.G., and Ray, P.N., 1990, Molecular and functional analysis of the muscle-specific promoter region of the Duchenne muscular dystrophy gene, Mol Cell Biol, 10, pp 193-205.
-
(1990)
Mol Cell Biol
, vol.10
, pp. 193-205
-
-
Klamut, H.J.1
Gangopadhyay, S.B.2
Worton, R.G.3
Ray, P.N.4
-
114
-
-
0024466501
-
The molecular basis for Duchenne versus Becker muscular dystrophy: Correlation of severity with type of deletion
-
Koenig, M., Beggs, A.H., Moyer, M., Scherpf, S., Heindrich, K., Bettecken, T., Meng, G., Muller, C.R., Lindlof, M., Kaariainen, H., and et al., 1989, The molecular basis for Duchenne versus Becker muscular dystrophy: correlation of severity with type of deletion, Am J Hum Genet, 45, pp 498-506.
-
(1989)
Am J Hum Genet
, vol.45
, pp. 498-506
-
-
Koenig, M.1
Beggs, A.H.2
Moyer, M.3
Scherpf, S.4
Heindrich, K.5
Bettecken, T.6
Meng, G.7
Muller, C.R.8
Lindlof, M.9
Kaariainen, H.10
-
115
-
-
0023614271
-
Complete cloning of the Duchenne muscular dystrophy (DMD) cDNA and preliminary genomic organization of the DMD gene in normal and affected individuals
-
Koenig, M., Hoffman, E.P., Bertelson, C.J., Monaco, A.P., Feener, C., and Kunkel, L.M., 1987, Complete cloning of the Duchenne muscular dystrophy (DMD) cDNA and preliminary genomic organization of the DMD gene in normal and affected individuals, Cell, 50, pp 509-517.
-
(1987)
Cell
, vol.50
, pp. 509-517
-
-
Koenig, M.1
Hoffman, E.P.2
Bertelson, C.J.3
Monaco, A.P.4
Feener, C.5
Kunkel, L.M.6
-
116
-
-
0025217703
-
Detailed analysis of the repeat domain of dystrophin reveals four potential hinge segments that may confer flexibility
-
Koenig, M., and Kunkel, L.M., 1990, Detailed analysis of the repeat domain of dystrophin reveals four potential hinge segments that may confer flexibility, J Biol Chem, 265, pp 4560-4566.
-
(1990)
J Biol Chem
, vol.265
, pp. 4560-4566
-
-
Koenig, M.1
Kunkel, L.M.2
-
117
-
-
0023904860
-
The complete sequence of dystrophin predicts a rod-shaped cytoskeletal protein
-
Koenig, M., Monaco, A.P., and Kunkel, L.M., 1988, The complete sequence of dystrophin predicts a rod-shaped cytoskeletal protein, Cell, 53, pp 219-226.
-
(1988)
Cell
, vol.53
, pp. 219-226
-
-
Koenig, M.1
Monaco, A.P.2
Kunkel, L.M.3
-
118
-
-
0033770344
-
Proteasome expression in the skeletal muscles of patients with muscular dystrophy
-
Kumamoto, T., Fujimoto, S., Ito, T., Horinouchi, H., Ueyama, H., and Tsuda, T., 2000, Proteasome expression in the skeletal muscles of patients with muscular dystrophy, Acta Neuropathol (Berl), 100, pp 595-602.
-
(2000)
Acta Neuropathol (Berl)
, vol.100
, pp. 595-602
-
-
Kumamoto, T.1
Fujimoto, S.2
Ito, T.3
Horinouchi, H.4
Ueyama, H.5
Tsuda, T.6
-
119
-
-
0030939046
-
Calpain and cathepsins in the skeletal muscle of inflammatory myopathies
-
Kumamoto, T., Ueyama, H., Sugihara, R., Kominami, E., Goll, D.E., and Tsuda, T., 1997, Calpain and cathepsins in the skeletal muscle of inflammatory myopathies, Eur Neurol, 37, pp 176-181.
-
(1997)
Eur Neurol
, vol.37
, pp. 176-181
-
-
Kumamoto, T.1
Ueyama, H.2
Sugihara, R.3
Kominami, E.4
Goll, D.E.5
Tsuda, T.6
-
120
-
-
0347915657
-
Loss of dystrophin causes aberrant mechanotransduction in skeletal muscle fibers
-
Kumar, A., Khandelwal, N., Malya, R., Reid, M.B., and Boriek, A.M., 2004, Loss of dystrophin causes aberrant mechanotransduction in skeletal muscle fibers, Faseb J, 18, pp 102-113.
-
(2004)
Faseb J
, vol.18
, pp. 102-113
-
-
Kumar, A.1
Khandelwal, N.2
Malya, R.3
Reid, M.B.4
Boriek, A.M.5
-
121
-
-
0035867041
-
2+ entry into mouse skeletal muscle fibres
-
2+ entry into mouse skeletal muscle fibres, J Physiol, 533, pp 185-199.
-
(2001)
J Physiol
, vol.533
, pp. 185-199
-
-
Kurebayashi, N.1
Ogawa, Y.2
-
122
-
-
0026653859
-
A 71-kilodalton protein is a major product of the Duchenne muscular dystrophy gene in brain and other nonmuscle tissues
-
Lederfein, D., Levy, Z., Augier, N., Mornet, D., Morris, G., Fuchs, O., Yaffe, D., and Nudel, U., 1992, A 71-kilodalton protein is a major product of the Duchenne muscular dystrophy gene in brain and other nonmuscle tissues, Proc Natl Acad Sci U S A, 89, pp 5346-5350.
-
(1992)
Proc Natl Acad Sci U S A
, vol.89
, pp. 5346-5350
-
-
Lederfein, D.1
Levy, Z.2
Augier, N.3
Mornet, D.4
Morris, G.5
Fuchs, O.6
Yaffe, D.7
Nudel, U.8
-
123
-
-
0029973085
-
Regulation of cytosolic calcium in skeletal muscle cells of the mdx mouse under conditions of stress
-
Leijendekker, W.J., Passaquin, A.C., Metzinger, L., and Ruegg, U.T., 1996, Regulation of cytosolic calcium in skeletal muscle cells of the mdx mouse under conditions of stress, Br J Pharmacol, 118, pp 611-616.
-
(1996)
Br J Pharmacol
, vol.118
, pp. 611-616
-
-
Leijendekker, W.J.1
Passaquin, A.C.2
Metzinger, L.3
Ruegg, U.T.4
-
124
-
-
0027484533
-
Point mutations at the carboxy terminus of the human dystrophin gene: Implications for an association with mental retardation in DMD patients
-
Lenk, U., Hanke, R., Thiele, H., and Speer, A., 1993, Point mutations at the carboxy terminus of the human dystrophin gene: implications for an association with mental retardation in DMD patients, Hum Mol Genet, 2, pp 1877-1881.
-
(1993)
Hum Mol Genet
, vol.2
, pp. 1877-1881
-
-
Lenk, U.1
Hanke, R.2
Thiele, H.3
Speer, A.4
-
125
-
-
0030016360
-
A cysteine 3340 substitution in the dystroglycan-binding domain of dystrophin associated with Duchenne muscular dystrophy, mental retardation and absence of the ERG b-wave
-
Lenk, U., Oexle, K., Voit, T., Ancker, U., Hellner, K.A., Speer, A., and Hubner, C., 1996, A cysteine 3340 substitution in the dystroglycan-binding domain of dystrophin associated with Duchenne muscular dystrophy, mental retardation and absence of the ERG b-wave, Hum Mol Genet, 5, pp 973-975.
-
(1996)
Hum Mol Genet
, vol.5
, pp. 973-975
-
-
Lenk, U.1
Oexle, K.2
Voit, T.3
Ancker, U.4
Hellner, K.A.5
Speer, A.6
Hubner, C.7
-
126
-
-
0031744741
-
Differences in both inositol 1,4,5-trisphosphate mass and inositol 1,4,5-trisphosphate receptors between normal and dystrophic skeletal muscle cell lines
-
Liberona, J.L., Powell, J.A., Shenoi, S., Petherbridge, L., Caviedes, R., and Jaimovich, E., 1998, Differences in both inositol 1,4,5-trisphosphate mass and inositol 1,4,5-trisphosphate receptors between normal and dystrophic skeletal muscle cell lines, Muscle Nerve, 21, pp 902-909.
-
(1998)
Muscle Nerve
, vol.21
, pp. 902-909
-
-
Liberona, J.L.1
Powell, J.A.2
Shenoi, S.3
Petherbridge, L.4
Caviedes, R.5
Jaimovich, E.6
-
127
-
-
0028937525
-
Dp140: A novel 140 kDa CNS transcript from the dystrophin locus
-
Lidov, H.G., Selig, S., and Kunkel, L.M., 1995, Dp140: a novel 140 kDa CNS transcript from the dystrophin locus, Hum Mol Genet, 4, pp 329-335.
-
(1995)
Hum Mol Genet
, vol.4
, pp. 329-335
-
-
Lidov, H.G.1
Selig, S.2
Kunkel, L.M.3
-
128
-
-
0024598162
-
Molecular deletion patterns in Duchenne and Becker type muscular dystrophy
-
Liechti-Gallati, S., Koenig, M., Kunkel, L.M., Frey, D., Boltshauser, E., Schneider, V., Braga, S., and Moser, H., 1989, Molecular deletion patterns in Duchenne and Becker type muscular dystrophy, Hum Genet, 81, pp 343-348.
-
(1989)
Hum Genet
, vol.81
, pp. 343-348
-
-
Liechti-Gallati, S.1
Koenig, M.2
Kunkel, L.M.3
Frey, D.4
Boltshauser, E.5
Schneider, V.6
Braga, S.7
Moser, H.8
-
129
-
-
0030271515
-
Coiled coils: New structures and new functions
-
Lupas, A., 1996, Coiled coils: new structures and new functions, Trends Biochem Sci, 21, pp 375-382.
-
(1996)
Trends Biochem Sci
, vol.21
, pp. 375-382
-
-
Lupas, A.1
-
130
-
-
0035449110
-
Force and power output of fast and slow skeletal muscles from mdx mice 6-28 months old
-
Lynch, G.S., Hinkle, R.T., Chamberlain, J.S., Brooks, S.V., and Faulkner, J.A., 2001, Force and power output of fast and slow skeletal muscles from mdx mice 6-28 months old, J Physiol, 535, pp 591-600.
-
(2001)
J Physiol
, vol.535
, pp. 591-600
-
-
Lynch, G.S.1
Hinkle, R.T.2
Chamberlain, J.S.3
Brooks, S.V.4
Faulkner, J.A.5
-
131
-
-
0033695935
-
Contraction-induced injury to single permeabilized muscle fibers from mdx, transgenic mdx, and control mice
-
Lynch, G.S., Rafael, J.A., Chamberlain, J.S., and Faulkner, J.A., 2000, Contraction-induced injury to single permeabilized muscle fibers from mdx, transgenic mdx, and control mice, Am J Physiol Cell Physiol, 279, pp C1290-1294.
-
(2000)
Am J Physiol Cell Physiol
, vol.279
, pp. C1290-C1294
-
-
Lynch, G.S.1
Rafael, J.A.2
Chamberlain, J.S.3
Faulkner, J.A.4
-
132
-
-
0029775570
-
Structure of the WW domain of a kinase-associated protein complexed with a proline-rich peptide
-
Macias, M.J., Hyvonen, M., Baraldi, E., Schultz, J., Sudol, M., Saraste, M., and Oschkinat, H., 1996, Structure of the WW domain of a kinase-associated protein complexed with a proline-rich peptide, Nature, 382, pp 646-649.
-
(1996)
Nature
, vol.382
, pp. 646-649
-
-
Macias, M.J.1
Hyvonen, M.2
Baraldi, E.3
Schultz, J.4
Sudol, M.5
Saraste, M.6
Oschkinat, H.7
-
133
-
-
0025933660
-
Brain-type and muscle-type promoters of the dystrophin gene differ greatly in structure
-
Makover, A., Zuk, D., Breakstone, J., Yaffe, D., and Nudel, U., 1991, Brain-type and muscle-type promoters of the dystrophin gene differ greatly in structure, Neuromuscul Disord, 1, pp 39-45.
-
(1991)
Neuromuscul Disord
, vol.1
, pp. 39-45
-
-
Makover, A.1
Zuk, D.2
Breakstone, J.3
Yaffe, D.4
Nudel, U.5
-
134
-
-
0023812570
-
Frame-shift deletions in patients with Duchenne and Becker muscular dystrophy
-
Malhotra, S.B., Hart, K.A., Klamut, H.J., Thomas, N.S., Bodrug, S.E., Burghes, A.H., Bobrow, M., Harper, P.S., Thompson, M.W., Ray, P.N., and et al., 1988, Frame-shift deletions in patients with Duchenne and Becker muscular dystrophy, Science, 242, pp 755-759.
-
(1988)
Science
, vol.242
, pp. 755-759
-
-
Malhotra, S.B.1
Hart, K.A.2
Klamut, H.J.3
Thomas, N.S.4
Bodrug, S.E.5
Burghes, A.H.6
Bobrow, M.7
Harper, P.S.8
Thompson, M.W.9
Ray, P.N.10
-
136
-
-
0035975968
-
Muscular degeneration in the absence of dystrophin is a calciumdependent process
-
Mariol, M.C., and Segalat, L., 2001, Muscular degeneration in the absence of dystrophin is a calciumdependent process, Curr Biol, 11, pp 1691-1694.
-
(2001)
Curr Biol
, vol.11
, pp. 1691-1694
-
-
Mariol, M.C.1
Segalat, L.2
-
137
-
-
13944263659
-
TRPC1 forms the stretch-activated cation channel in vertebrate cells
-
Maroto, R., Raso, A., Wood, T.G., Kurosky, A., Martinac, B., and Hamill, O.P., 2005, TRPC1 forms the stretch-activated cation channel in vertebrate cells, Nat Cell Biol, 7, pp 179-185.
-
(2005)
Nat Cell Biol
, vol.7
, pp. 179-185
-
-
Maroto, R.1
Raso, A.2
Wood, T.G.3
Kurosky, A.4
Martinac, B.5
Hamill, O.P.6
-
138
-
-
0028817970
-
Visualization of dystrophic muscle fibers in mdx mouse by vital staining with Evans blue: Evidence of apoptosis in dystrophin-deficient muscle
-
Matsuda, R., Nishikawa, A., and Tanaka, H., 1995, Visualization of dystrophic muscle fibers in mdx mouse by vital staining with Evans blue: evidence of apoptosis in dystrophin-deficient muscle, J Biochem (Tokyo), 118, pp 959-964.
-
(1995)
J Biochem (Tokyo)
, vol.118
, pp. 959-964
-
-
Matsuda, R.1
Nishikawa, A.2
Tanaka, H.3
-
139
-
-
0026782356
-
Pressure-clamp: A method for rapid step perturbation of mechanosensitive channels
-
McBride, D.W., Jr., and Hamill, O.P., 1992, Pressure-clamp: a method for rapid step perturbation of mechanosensitive channels, Pflugers Arch, 421, pp 606-612.
-
(1992)
Pflugers Arch
, vol.421
, pp. 606-612
-
-
McBride, D.W.1
Hamill, O.P.2
-
140
-
-
0033984029
-
Stretch-activated ion channels contribute to membrane depolarization after eccentric contractions
-
McBride, T.A., Stockert, B.W., Gorin, F.A., and Carlsen, R.C., 2000, Stretch-activated ion channels contribute to membrane depolarization after eccentric contractions, J Appl Physiol, 88, pp 91-101.
-
(2000)
J Appl Physiol
, vol.88
, pp. 91-101
-
-
McBride, T.A.1
Stockert, B.W.2
Gorin, F.A.3
Carlsen, R.C.4
-
141
-
-
0033863129
-
Increased activity of calcium leak channels caused by proteolysis near sarcolemmal ruptures
-
McCarter, G.C., and Steinhardt, R.A., 2000, Increased activity of calcium leak channels caused by proteolysis near sarcolemmal ruptures, J Membr Biol, 176, pp 169-174.
-
(2000)
J Membr Biol
, vol.176
, pp. 169-174
-
-
McCarter, G.C.1
Steinhardt, R.A.2
-
142
-
-
0344824647
-
Plasma membrane disruption: Repair, prevention, adaptation
-
McNeil, P.L., and Steinhardt, R.A., 2003, Plasma membrane disruption: repair, prevention, adaptation, Annu Rev Cell Dev Biol, 19, pp 697-731.
-
(2003)
Annu Rev Cell Dev Biol
, vol.19
, pp. 697-731
-
-
McNeil, P.L.1
Steinhardt, R.A.2
-
143
-
-
0026032731
-
Decreased osmotic stability of dystrophin-less muscle cells from the mdx mouse
-
Menke, A., and Jockusch, H., 1991, Decreased osmotic stability of dystrophin-less muscle cells from the mdx mouse, Nature, 349, pp 69-71.
-
(1991)
Nature
, vol.349
, pp. 69-71
-
-
Menke, A.1
Jockusch, H.2
-
144
-
-
0023134993
-
Localization and cloning of Xp21 deletion breakpoints involved in muscular dystrophy
-
Monaco, A.P., Bertelson, C.J., Colletti-Feener, C., and Kunkel, L.M., 1987, Localization and cloning of Xp21 deletion breakpoints involved in muscular dystrophy, Hum Genet, 75, pp 221-227.
-
(1987)
Hum Genet
, vol.75
, pp. 221-227
-
-
Monaco, A.P.1
Bertelson, C.J.2
Colletti-Feener, C.3
Kunkel, L.M.4
-
145
-
-
0023718118
-
An explanation for the phenotypic differences between patients bearing partial deletions of the DMD locus
-
Monaco, A.P., Bertelson, C.J., Liechti-Gallati, S., Moser, H., and Kunkel, L.M., 1988, An explanation for the phenotypic differences between patients bearing partial deletions of the DMD locus, Genomics, 2, pp 90-95.
-
(1988)
Genomics
, vol.2
, pp. 90-95
-
-
Monaco, A.P.1
Bertelson, C.J.2
Liechti-Gallati, S.3
Moser, H.4
Kunkel, L.M.5
-
146
-
-
0021863554
-
Detection of deletions spanning the Duchenne muscular dystrophy locus using a tightly linked DNA segment
-
Monaco, A.P., Bertelson, C.J., Middlesworth, W., Colletti, C.A., Aldridge, J., Fischbeck, K.H., Bartlett, R., Pericak-Vance, M.A., Roses, A.D., and Kunkel, L.M., 1985, Detection of deletions spanning the Duchenne muscular dystrophy locus using a tightly linked DNA segment, Nature, 316, pp 842-845.
-
(1985)
Nature
, vol.316
, pp. 842-845
-
-
Monaco, A.P.1
Bertelson, C.J.2
Middlesworth, W.3
Colletti, C.A.4
Aldridge, J.5
Fischbeck, K.H.6
Bartlett, R.7
Pericak-Vance, M.A.8
Roses, A.D.9
Kunkel, L.M.10
-
147
-
-
0022496289
-
Isolation of candidate cDNAs for portions of the Duchenne muscular dystrophy gene
-
Monaco, A.P., Neve, R.L., Colletti-Feener, C., Bertelson, C.J., Kurnit, D.M., and Kunkel, L.M., 1986, Isolation of candidate cDNAs for portions of the Duchenne muscular dystrophy gene, Nature, 323, pp 646-650.
-
(1986)
Nature
, vol.323
, pp. 646-650
-
-
Monaco, A.P.1
Neve, R.L.2
Colletti-Feener, C.3
Bertelson, C.J.4
Kurnit, D.M.5
Kunkel, L.M.6
-
148
-
-
0026535028
-
A yeast artificial chromosome contig containing the complete Duchenne muscular dystrophy gene
-
Monaco, A.P., Walker, A.P., Millwood, I., Larin, Z., and Lehrach, H., 1992, A yeast artificial chromosome contig containing the complete Duchenne muscular dystrophy gene, Genomics, 12, pp 465-473.
-
(1992)
Genomics
, vol.12
, pp. 465-473
-
-
Monaco, A.P.1
Walker, A.P.2
Millwood, I.3
Larin, Z.4
Lehrach, H.5
-
149
-
-
0142042349
-
Cardiomyopathy in muscular dystrophies
-
Muntoni, F., 2003, Cardiomyopathy in muscular dystrophies, Curr Opin Neurol, 16, pp 577-583.
-
(2003)
Curr Opin Neurol
, vol.16
, pp. 577-583
-
-
Muntoni, F.1
-
150
-
-
0034841007
-
Mdx myotubes have normal excitability but show reduced contraction-relaxation dynamics
-
Nicolas-Metral, V., Raddatz, E., Kucera, P., and Ruegg, U.T., 2001, Mdx myotubes have normal excitability but show reduced contraction-relaxation dynamics, J Muscle Res Cell Motil, 22, pp 69-75.
-
(2001)
J Muscle Res Cell Motil
, vol.22
, pp. 69-75
-
-
Nicolas-Metral, V.1
Raddatz, E.2
Kucera, P.3
Ruegg, U.T.4
-
151
-
-
0024595610
-
Duchenne muscular dystrophy gene product is not identical in muscle and brain
-
Nudel, U., Zuk, D., Einat, P., Zeelon, E., Levy, Z., Neuman, S., and Yaffe, D., 1989, Duchenne muscular dystrophy gene product is not identical in muscle and brain, Nature, 337, pp 76-78.
-
(1989)
Nature
, vol.337
, pp. 76-78
-
-
Nudel, U.1
Zuk, D.2
Einat, P.3
Zeelon, E.4
Levy, Z.5
Neuman, S.6
Yaffe, D.7
-
152
-
-
0033120705
-
Covert persistence of mdx mouse myopathy is revealed by acute and chronic effects of irradiation
-
Pagel, C.N., and Partridge, T.A., 1999, Covert persistence of mdx mouse myopathy is revealed by acute and chronic effects of irradiation, J Neurol Sci, 164, pp 103-116.
-
(1999)
J Neurol Sci
, vol.164
, pp. 103-116
-
-
Pagel, C.N.1
Partridge, T.A.2
-
153
-
-
0030810066
-
Store depletion and calcium influx
-
Parekh, A.B., and Penner, R., 1997, Store depletion and calcium influx, Physiol Rev, 77, pp 901-930.
-
(1997)
Physiol Rev
, vol.77
, pp. 901-930
-
-
Parekh, A.B.1
Penner, R.2
-
154
-
-
0028906307
-
mdx mice show progressive weakness and muscle deterioration with age
-
Pastoret, C., and Sebille, A., 1995, mdx mice show progressive weakness and muscle deterioration with age, J Neurol Sci, 129, pp 97-105.
-
(1995)
J Neurol Sci
, vol.129
, pp. 97-105
-
-
Pastoret, C.1
Sebille, A.2
-
155
-
-
0018336256
-
Muscle breakdown and lysosomal activation (biochemistry)
-
Pearson, C.M., and Kar, N.C., 1979, Muscle breakdown and lysosomal activation (biochemistry), Ann N Y Acad Sci, 317, pp 465-477.
-
(1979)
Ann N Y Acad Sci
, vol.317
, pp. 465-477
-
-
Pearson, C.M.1
Kar, N.C.2
-
156
-
-
33745759762
-
Amplification of CRAC current by STIM1 and CRACM1 (Orai1)
-
Peinelt, C., Vig, M., Koomoa, D.L., Beck, A., Nadler, M.J., Koblan-Huberson, M., Lis, A., Fleig, A., Penner, R., and Kinet, J.P., 2006, Amplification of CRAC current by STIM1 and CRACM1 (Orai1), Nat Cell Biol, 8, pp 771-773.
-
(2006)
Nat Cell Biol
, vol.8
, pp. 771-773
-
-
Peinelt, C.1
Vig, M.2
Koomoa, D.L.3
Beck, A.4
Nadler, M.J.5
Koblan-Huberson, M.6
Lis, A.7
Fleig, A.8
Penner, R.9
Kinet, J.P.10
-
157
-
-
0031593173
-
Dihydropyridine receptor gene expression in skeletal muscle from mdx and control mice
-
Pereon, Y., Dettbarn, C., Navarro, J., Noireaud, J., and Palade, P.T., 1997, Dihydropyridine receptor gene expression in skeletal muscle from mdx and control mice, Biochim Biophys Acta, 1362, pp 201-207.
-
(1997)
Biochim Biophys Acta
, vol.1362
, pp. 201-207
-
-
Pereon, Y.1
Dettbarn, C.2
Navarro, J.3
Noireaud, J.4
Palade, P.T.5
-
158
-
-
0027460658
-
Dystrophin protects the sarcolemma from stresses developed during muscle contraction
-
Petrof, B.J., Shrager, J.B., Stedman, H.H., Kelly, A.M., and Sweeney, H.L., 1993, Dystrophin protects the sarcolemma from stresses developed during muscle contraction, Proc Natl Acad Sci U S A, 90, pp 3710-3714.
-
(1993)
Proc Natl Acad Sci U S A
, vol.90
, pp. 3710-3714
-
-
Petrof, B.J.1
Shrager, J.B.2
Stedman, H.H.3
Kelly, A.M.4
Sweeney, H.L.5
-
159
-
-
0029122523
-
Expression of full-length and truncated dystrophin mini-genes in transgenic mdx mice
-
Phelps, S.F., Hauser, M.A., Cole, N.M., Rafael, J.A., Hinkle, R.T., Faulkner, J.A., and Chamberlain, J.S., 1995, Expression of full-length and truncated dystrophin mini-genes in transgenic mdx mice, Hum Mol Genet, 4, pp 1251-1258.
-
(1995)
Hum Mol Genet
, vol.4
, pp. 1251-1258
-
-
Phelps, S.F.1
Hauser, M.A.2
Cole, N.M.3
Rafael, J.A.4
Hinkle, R.T.5
Faulkner, J.A.6
Chamberlain, J.S.7
-
160
-
-
0030034593
-
ZZ and TAZ: New putative zinc fingers in dystrophin and other proteins
-
Ponting, C.P., Blake, D.J., Davies, K.E., Kendrick-Jones, J., and Winder, S.J., 1996, ZZ and TAZ: new putative zinc fingers in dystrophin and other proteins, Trends Biochem Sci, 21, pp 11-13.
-
(1996)
Trends Biochem Sci
, vol.21
, pp. 11-13
-
-
Ponting, C.P.1
Blake, D.J.2
Davies, K.E.3
Kendrick-Jones, J.4
Winder, S.J.5
-
161
-
-
0028414945
-
2+ concentrations are not elevated in resting cultured muscle from Duchenne (DMD) patients and in MDX mouse muscle fibres
-
2+ concentrations are not elevated in resting cultured muscle from Duchenne (DMD) patients and in MDX mouse muscle fibres, Pflugers Arch, 426, pp 499-505.
-
(1994)
Pflugers Arch
, vol.426
, pp. 499-505
-
-
Pressmar, J.1
Brinkmeier, H.2
Seewald, M.J.3
Naumann, T.4
Rudel, R.5
-
162
-
-
0029073192
-
Spectrum of small mutations in the dystrophin coding region
-
Prior, T.W., Bartolo, C., Pearl, D.K., Papp, A.C., Snyder, P.J., Sedra, M.S., Burghes, A.H., and Mendell, J.R., 1995, Spectrum of small mutations in the dystrophin coding region, Am J Hum Genet, 57, pp 22-33.
-
(1995)
Am J Hum Genet
, vol.57
, pp. 22-33
-
-
Prior, T.W.1
Bartolo, C.2
Pearl, D.K.3
Papp, A.C.4
Snyder, P.J.5
Sedra, M.S.6
Burghes, A.H.7
Mendell, J.R.8
-
163
-
-
0029959354
-
Forced expression of dystrophin deletion constructs reveals structure-function correlations
-
Rafael, J.A., Cox, G.A., Corrado, K., Jung, D., Campbell, K.P., and Chamberlain, J.S., 1996, Forced expression of dystrophin deletion constructs reveals structure-function correlations, J Cell Biol, 134, pp 93-102.
-
(1996)
J Cell Biol
, vol.134
, pp. 93-102
-
-
Rafael, J.A.1
Cox, G.A.2
Corrado, K.3
Jung, D.4
Campbell, K.P.5
Chamberlain, J.S.6
-
164
-
-
0033852660
-
Testing of SHIRPA, a mouse phenotypic assessment protocol, on Dmd(mdx) and Dmd(mdx3cv) dystrophin-deficient mice
-
Rafael, J.A., Nitta, Y., Peters, J., and Davies, K.E., 2000, Testing of SHIRPA, a mouse phenotypic assessment protocol, on Dmd(mdx) and Dmd(mdx3cv) dystrophin-deficient mice, Mamm Genome, 11, pp 725-728.
-
(2000)
Mamm Genome
, vol.11
, pp. 725-728
-
-
Rafael, J.A.1
Nitta, Y.2
Peters, J.3
Davies, K.E.4
-
165
-
-
0027408847
-
Efficient adenovirus-mediated transfer of a human minidystrophin gene to skeletal muscle of mdx mice
-
Ragot, T., Vincent, N., Chafey, P., Vigne, E., Gilgenkrantz, H., Couton, D., Cartaud, J., Briand, P., Kaplan, J.C., Perricaudet, M., and et al., 1993, Efficient adenovirus-mediated transfer of a human minidystrophin gene to skeletal muscle of mdx mice, Nature, 361, pp 647-650.
-
(1993)
Nature
, vol.361
, pp. 647-650
-
-
Ragot, T.1
Vincent, N.2
Chafey, P.3
Vigne, E.4
Gilgenkrantz, H.5
Couton, D.6
Cartaud, J.7
Briand, P.8
Kaplan, J.C.9
Perricaudet, M.10
-
166
-
-
0035190381
-
The dystrophin-glycoprotein complex, cellular signaling, and the regulation of cell survival in the muscular dystrophies
-
Rando, T.A., 2001, The dystrophin-glycoprotein complex, cellular signaling, and the regulation of cell survival in the muscular dystrophies, Muscle Nerve, 24, pp 1575-1594.
-
(2001)
Muscle Nerve
, vol.24
, pp. 1575-1594
-
-
Rando, T.A.1
-
167
-
-
0023038510
-
Calcium activated neutral proteases (milliand micro-CANP) and endogenous CANP inhibitor of muscle in Duchenne muscular dystrophy (DMD)
-
Reddy, P.A., Anandavalli, T.E., and Anandaraj, M.P., 1986, Calcium activated neutral proteases (milliand micro-CANP) and endogenous CANP inhibitor of muscle in Duchenne muscular dystrophy (DMD), Clin Chim Acta, 160, pp 281-288.
-
(1986)
Clin Chim Acta
, vol.160
, pp. 281-288
-
-
Reddy, P.A.1
Anandavalli, T.E.2
Anandaraj, M.P.3
-
168
-
-
0032915455
-
The WW domain of dystrophin requires EF-hands region to interact with beta-dystroglycan
-
Rentschler, S., Linn, H., Deininger, K., Bedford, M.T., Espanel, X., and Sudol, M., 1999, The WW domain of dystrophin requires EF-hands region to interact with beta-dystroglycan, Biol Chem, 380, pp 431-442.
-
(1999)
Biol Chem
, vol.380
, pp. 431-442
-
-
Rentschler, S.1
Linn, H.2
Deininger, K.3
Bedford, M.T.4
Espanel, X.5
Sudol, M.6
-
169
-
-
0033546753
-
Increased number of caveolae and caveolin-3 overexpression in Duchenne muscular dystrophy
-
Repetto, S., Bado, M., Broda, P., Lucania, G., Masetti, E., Sotgia, F., Carbone, I., Pavan, A., Bonilla, E., Cordone, G., Lisanti, M.P., and Minetti, C., 1999, Increased number of caveolae and caveolin-3 overexpression in Duchenne muscular dystrophy, Biochem Biophys Res Commun, 261, pp 547-550.
-
(1999)
Biochem Biophys Res Commun
, vol.261
, pp. 547-550
-
-
Repetto, S.1
Bado, M.2
Broda, P.3
Lucania, G.4
Masetti, E.5
Sotgia, F.6
Carbone, I.7
Pavan, A.8
Bonilla, E.9
Cordone, G.10
Lisanti, M.P.11
Minetti, C.12
-
170
-
-
0035895903
-
Alteration in calcium handling at the subcellular level in mdx myotubes
-
Robert, V., Massimino, M.L., Tosello, V., Marsault, R., Cantini, M., Sorrentino, V., and Pozzan, T., 2001, Alteration in calcium handling at the subcellular level in mdx myotubes, J Biol Chem, 276, pp 4647-4651.
-
(2001)
J Biol Chem
, vol.276
, pp. 4647-4651
-
-
Robert, V.1
Massimino, M.L.2
Tosello, V.3
Marsault, R.4
Cantini, M.5
Sorrentino, V.6
Pozzan, T.7
-
171
-
-
0027232968
-
Exon structure of the human dystrophin gene
-
Roberts, R.G., Coffey, A.J., Bobrow, M., and Bentley, D.R., 1993, Exon structure of the human dystrophin gene, Genomics, 16, pp 536-538.
-
(1993)
Genomics
, vol.16
, pp. 536-538
-
-
Roberts, R.G.1
Coffey, A.J.2
Bobrow, M.3
Bentley, D.R.4
-
172
-
-
0028303798
-
Searching for the 1 in 2,400,000: A review of dystrophin gene point mutations
-
Roberts, R.G., Gardner, R.J., and Bobrow, M., 1994, Searching for the 1 in 2,400,000: a review of dystrophin gene point mutations, Hum Mutat, 4, pp 1-11.
-
(1994)
Hum Mutat
, vol.4
, pp. 1-11
-
-
Roberts, R.G.1
Gardner, R.J.2
Bobrow, M.3
-
173
-
-
0141514416
-
Decreased mAKAP, ryanodine receptor, and SERCA2a gene expression in mdx hearts
-
Rohman, M.S., Emoto, N., Takeshima, Y., Yokoyama, M., and Matsuo, M., 2003, Decreased mAKAP, ryanodine receptor, and SERCA2a gene expression in mdx hearts, Biochem Biophys Res Commun, 310, pp 228-235.
-
(2003)
Biochem Biophys Res Commun
, vol.310
, pp. 228-235
-
-
Rohman, M.S.1
Emoto, N.2
Takeshima, Y.3
Yokoyama, M.4
Matsuo, M.5
-
174
-
-
0030583157
-
Localization of the dystrophin binding site at the carboxyl terminus of beta-dystroglycan
-
Rosa, G., Ceccarini, M., Cavaldesi, M., Zini, M., and Petrucci, T.C., 1996, Localization of the dystrophin binding site at the carboxyl terminus of beta-dystroglycan, Biochem Biophys Res Commun, 223, pp 272-277.
-
(1996)
Biochem Biophys Res Commun
, vol.223
, pp. 272-277
-
-
Rosa, G.1
Ceccarini, M.2
Cavaldesi, M.3
Zini, M.4
Petrucci, T.C.5
-
175
-
-
0029804981
-
A new model for the interaction of dystrophin with F-actin
-
Rybakova, I.N., Amann, K.J., and Ervasti, J.M., 1996, A new model for the interaction of dystrophin with F-actin, J Cell Biol, 135, pp 661-672.
-
(1996)
J Cell Biol
, vol.135
, pp. 661-672
-
-
Rybakova, I.N.1
Amann, K.J.2
Ervasti, J.M.3
-
176
-
-
0030695947
-
Dystrophin-glycoprotein complex is monomeric and stabilizes actin filaments in vitro through a lateral association
-
Rybakova, I.N., and Ervasti, J.M., 1997, Dystrophin-glycoprotein complex is monomeric and stabilizes actin filaments in vitro through a lateral association, J Biol Chem, 272, pp 28771-28778.
-
(1997)
J Biol Chem
, vol.272
, pp. 28771-28778
-
-
Rybakova, I.N.1
Ervasti, J.M.2
-
177
-
-
0026546263
-
Contractile properties and susceptibility to exercise-induced damage of normal and mdx mouse tibialis anterior muscle
-
Sacco, P., Jones, D.A., Dick, J.R., and Vrbova, G., 1992, Contractile properties and susceptibility to exercise-induced damage of normal and mdx mouse tibialis anterior muscle, Clin Sci (Lond), 82, pp 227-236.
-
(1992)
Clin Sci (Lond)
, vol.82
, pp. 227-236
-
-
Sacco, P.1
Jones, D.A.2
Dick, J.R.3
Vrbova, G.4
-
179
-
-
0030775377
-
Dystrobrevin and dystrophin: An interaction through coiled-coil motifs
-
Sadoulet-Puccio, H.M., Rajala, M., and Kunkel, L.M., 1997, Dystrobrevin and dystrophin: an interaction through coiled-coil motifs, Proc Natl Acad Sci U S A, 94, pp 12413-12418.
-
(1997)
Proc Natl Acad Sci U S A
, vol.94
, pp. 12413-12418
-
-
Sadoulet-Puccio, H.M.1
Rajala, M.2
Kunkel, L.M.3
-
180
-
-
0032952705
-
Targeted inactivation of Dp71, the major non-muscle product of the DMD gene: Differential activity of the Dp71 promoter during development
-
Sarig, R., Mezger-Lallemand, V., Gitelman, I., Davis, C., Fuchs, O., Yaffe, D., and Nudel, U., 1999, Targeted inactivation of Dp71, the major non-muscle product of the DMD gene: differential activity of the Dp71 promoter during development, Hum Mol Genet, 8, pp 1-10.
-
(1999)
Hum Mol Genet
, vol.8
, pp. 1-10
-
-
Sarig, R.1
Mezger-Lallemand, V.2
Gitelman, I.3
Davis, C.4
Fuchs, O.5
Yaffe, D.6
Nudel, U.7
-
181
-
-
0028133595
-
Apo-dystrophin-1 and apo-dystrophin-2, products of the Duchenne muscular dystrophy locus: Expression during mouse embryogenesis and in cultured cell lines
-
Schofield, J.N., Blake, D.J., Simmons, C., Morris, G.E., Tinsley, J.M., Davies, K.E., and Edwards, Y.H., 1994, Apo-dystrophin-1 and apo-dystrophin-2, products of the Duchenne muscular dystrophy locus: expression during mouse embryogenesis and in cultured cell lines, Hum Mol Genet, 3, pp 1309-1316.
-
(1994)
Hum Mol Genet
, vol.3
, pp. 1309-1316
-
-
Schofield, J.N.1
Blake, D.J.2
Simmons, C.3
Morris, G.E.4
Tinsley, J.M.5
Davies, K.E.6
Edwards, Y.H.7
-
182
-
-
0035044102
-
Altered electrical activity in colonic smooth muscle cells from dystrophic (mdx) mice
-
Serio, R., Bonvissuto, F., and Mule, F., 2001, Altered electrical activity in colonic smooth muscle cells from dystrophic (mdx) mice, Neurogastroenterol Motil, 13, pp 169-175.
-
(2001)
Neurogastroenterol Motil
, vol.13
, pp. 169-175
-
-
Serio, R.1
Bonvissuto, F.2
Mule, F.3
-
183
-
-
0024353559
-
The molecular basis of muscular dystrophy in the mdx mouse: A point mutation
-
Sicinski, P., Geng, Y., Ryder-Cook, A.S., Barnard, E.A., Darlison, M.G., and Barnard, P.J., 1989, The molecular basis of muscular dystrophy in the mdx mouse: a point mutation, Science, 244, pp 1578-1580.
-
(1989)
Science
, vol.244
, pp. 1578-1580
-
-
Sicinski, P.1
Geng, Y.2
Ryder-Cook, A.S.3
Barnard, E.A.4
Darlison, M.G.5
Barnard, P.J.6
-
184
-
-
0029072703
-
Purification of cranin, a laminin binding membrane protein. Identity with dystroglycan and reassessment of its carbohydrate moieties
-
Smalheiser, N.R., and Kim, E., 1995, Purification of cranin, a laminin binding membrane protein. Identity with dystroglycan and reassessment of its carbohydrate moieties, J Biol Chem, 270, pp 15425-15433.
-
(1995)
J Biol Chem
, vol.270
, pp. 15425-15433
-
-
Smalheiser, N.R.1
Kim, E.2
-
185
-
-
0023410821
-
Cranin: A laminin-binding protein of cell membranes
-
Smalheiser, N.R., and Schwartz, N.B., 1987, Cranin: a laminin-binding protein of cell membranes, Proc Natl Acad Sci U S A, 84, pp 6457-6461.
-
(1987)
Proc Natl Acad Sci U S A
, vol.84
, pp. 6457-6461
-
-
Smalheiser, N.R.1
Schwartz, N.B.2
-
186
-
-
0024369426
-
Molecular cloning of a novel mammalian calcium-dependent protease distinct from both m- and mu-types. Specific expression of the mRNA in skeletal muscle
-
Sorimachi, H., Imajoh-Ohmi, S., Emori, Y., Kawasaki, H., Ohno, S., Minami, Y., and Suzuki, K., 1989, Molecular cloning of a novel mammalian calcium-dependent protease distinct from both m- and mu-types. Specific expression of the mRNA in skeletal muscle, J Biol Chem, 264, pp 20106-20111.
-
(1989)
J Biol Chem
, vol.264
, pp. 20106-20111
-
-
Sorimachi, H.1
Imajoh-Ohmi, S.2
Emori, Y.3
Kawasaki, H.4
Ohno, S.5
Minami, Y.6
Suzuki, K.7
-
187
-
-
0034992155
-
The structure of calpain
-
Sorimachi, H., and Suzuki, K., 2001, The structure of calpain, J Biochem (Tokyo), 129, pp 653-664.
-
(2001)
J Biochem (Tokyo)
, vol.129
, pp. 653-664
-
-
Sorimachi, H.1
Suzuki, K.2
-
188
-
-
0036798005
-
Overexpression of a calpastatin transgene in mdx muscle reduces dystrophic pathology
-
Spencer, M.J., and Mellgren, R.L., 2002, Overexpression of a calpastatin transgene in mdx muscle reduces dystrophic pathology, Hum Mol Genet, 11, pp 2645-2655.
-
(2002)
Hum Mol Genet
, vol.11
, pp. 2645-2655
-
-
Spencer, M.J.1
Mellgren, R.L.2
-
189
-
-
0030218963
-
Calpain translocation during muscle fiber necrosis and regeneration in dystrophin-deficient mice
-
Spencer, M.J., and Tidball, J.G., 1996, Calpain translocation during muscle fiber necrosis and regeneration in dystrophin-deficient mice, Exp Cell Res, 226, pp 264-272.
-
(1996)
Exp Cell Res
, vol.226
, pp. 264-272
-
-
Spencer, M.J.1
Tidball, J.G.2
-
190
-
-
12244272395
-
Prevention of pathology in mdx mice by expression of utrophin: Analysis using an inducible transgenic expression system
-
Squire, S., Raymackers, J.M., Vandebrouck, C., Potter, A., Tinsley, J., Fisher, R., Gillis, J.M., and Davies, K.E., 2002, Prevention of pathology in mdx mice by expression of utrophin: analysis using an inducible transgenic expression system, Hum Mol Genet, 11, pp 3333-3344.
-
(2002)
Hum Mol Genet
, vol.11
, pp. 3333-3344
-
-
Squire, S.1
Raymackers, J.M.2
Vandebrouck, C.3
Potter, A.4
Tinsley, J.5
Fisher, R.6
Gillis, J.M.7
Davies, K.E.8
-
191
-
-
0035139227
-
Physiology of nitric oxide in skeletal muscle
-
Stamler, J.S., and Meissner, G., 2001, Physiology of nitric oxide in skeletal muscle, Physiol Rev, 81, pp 209-237.
-
(2001)
Physiol Rev
, vol.81
, pp. 209-237
-
-
Stamler, J.S.1
Meissner, G.2
-
192
-
-
0026419948
-
The mdx mouse diaphragm reproduces the degenerative changes of Duchenne muscular dystrophy
-
Stedman, H.H., Sweeney, H.L., Shrager, J.B., Maguire, H.C., Panettieri, R.A., Petrof, B., Narusawa, M., Leferovich, J.M., Sladky, J.T., and Kelly, A.M., 1991, The mdx mouse diaphragm reproduces the degenerative changes of Duchenne muscular dystrophy, Nature, 352, pp 536-539.
-
(1991)
Nature
, vol.352
, pp. 536-539
-
-
Stedman, H.H.1
Sweeney, H.L.2
Shrager, J.B.3
Maguire, H.C.4
Panettieri, R.A.5
Petrof, B.6
Narusawa, M.7
Leferovich, J.M.8
Sladky, J.T.9
Kelly, A.M.10
-
193
-
-
0028206868
-
Molecular organization at the glycoprotein-complex-binding site of dystrophin. Three dystrophin-associated proteins bind directly to the carboxy-terminal portion of dystrophin
-
Suzuki, A., Yoshida, M., Hayashi, K., Mizuno, Y., Hagiwara, Y., and Ozawa, E., 1994, Molecular organization at the glycoprotein-complex-binding site of dystrophin. Three dystrophin-associated proteins bind directly to the carboxy-terminal portion of dystrophin, Eur J Biochem, 220, pp 283-292.
-
(1994)
Eur J Biochem
, vol.220
, pp. 283-292
-
-
Suzuki, A.1
Yoshida, M.2
Hayashi, K.3
Mizuno, Y.4
Hagiwara, Y.5
Ozawa, E.6
-
194
-
-
0026695175
-
Glycoprotein-binding site of dystrophin is confined to the cysteine-rich domain and the first half of the carboxy-terminal domain
-
Suzuki, A., Yoshida, M., Yamamoto, H., and Ozawa, E., 1992, Glycoprotein-binding site of dystrophin is confined to the cysteine-rich domain and the first half of the carboxy-terminal domain, FEBS Lett, 308, pp 154-160.
-
(1992)
FEBS Lett
, vol.308
, pp. 154-160
-
-
Suzuki, A.1
Yoshida, M.2
Yamamoto, H.3
Ozawa, E.4
-
195
-
-
0022638233
-
Skeletal muscle pathology in X chromosome-linked muscular dystrophy (mdx) mouse
-
Tanabe, Y., Esaki, K., and Nomura, T., 1986, Skeletal muscle pathology in X chromosome-linked muscular dystrophy (mdx) mouse, Acta Neuropathol (Berl), 69, pp 91-95.
-
(1986)
Acta Neuropathol (Berl)
, vol.69
, pp. 91-95
-
-
Tanabe, Y.1
Esaki, K.2
Nomura, T.3
-
196
-
-
0022570670
-
Voltage-dependent channels of human muscle cultures
-
Trautmann, A., Delaporte, C., and Marty, A., 1986, Voltage-dependent channels of human muscle cultures, Pflugers Arch, 406, pp 163-172.
-
(1986)
Pflugers Arch
, vol.406
, pp. 163-172
-
-
Trautmann, A.1
Delaporte, C.2
Marty, A.3
-
197
-
-
0026347187
-
Increased calcium influx in dystrophic muscle
-
Turner, P.R., Fong, P.Y., Denetclaw, W.F., and Steinhardt, R.A., 1991, Increased calcium influx in dystrophic muscle, J Cell Biol, 115, pp 1701-1712.
-
(1991)
J Cell Biol
, vol.115
, pp. 1701-1712
-
-
Turner, P.R.1
Fong, P.Y.2
Denetclaw, W.F.3
Steinhardt, R.A.4
-
198
-
-
0027281140
-
Proteolysis results in altered leak channel kinetics and elevated free calcium in mdx muscle
-
Turner, P.R., Schultz, R., Ganguly, B., and Steinhardt, R.A., 1993, Proteolysis results in altered leak channel kinetics and elevated free calcium in mdx muscle, J Membr Biol, 133, pp 243-251.
-
(1993)
J Membr Biol
, vol.133
, pp. 243-251
-
-
Turner, P.R.1
Schultz, R.2
Ganguly, B.3
Steinhardt, R.A.4
-
199
-
-
0023739851
-
Increased protein degradation results from elevated free calcium levels found in muscle from mdx mice
-
Turner, P.R., Westwood, T., Regen, C.M., and Steinhardt, R.A., 1988, Increased protein degradation results from elevated free calcium levels found in muscle from mdx mice, Nature, 335, pp 735-738.
-
(1988)
Nature
, vol.335
, pp. 735-738
-
-
Turner, P.R.1
Westwood, T.2
Regen, C.M.3
Steinhardt, R.A.4
-
200
-
-
0033559330
-
Increased calcium entry into dystrophindeficient muscle fibres of MDX and ADR-MDX mice is reduced by ion channel blockers
-
Tutdibi, O., Brinkmeier, H., Rudel, R., and Fohr, K.J., 1999, Increased calcium entry into dystrophindeficient muscle fibres of MDX and ADR-MDX mice is reduced by ion channel blockers, J Physiol, 515 (Pt 3), pp 859-868.
-
(1999)
J Physiol
, vol.515
, pp. 859-868
-
-
Tutdibi, O.1
Brinkmeier, H.2
Rudel, R.3
Fohr, K.J.4
-
201
-
-
0027401081
-
Is the maintainance of the C-terminus domain of dystrophin enough to ensure a milder Becker muscular dystrophy phenotype?
-
Vainzof, M., Takata, R.I., Passos-Bueno, M.R., Pavanello, R.C., and Zatz, M., 1993, Is the maintainance of the C-terminus domain of dystrophin enough to ensure a milder Becker muscular dystrophy phenotype?, Hum Mol Genet, 2, pp 39-42.
-
(1993)
Hum Mol Genet
, vol.2
, pp. 39-42
-
-
Vainzof, M.1
Takata, R.I.2
Passos-Bueno, M.R.3
Pavanello, R.C.4
Zatz, M.5
-
202
-
-
30744439614
-
Regulation of store-operated calcium entries and mitochondrial uptake by minidystrophin expression in cultured myotubes
-
Vandebrouck, A., Ducret, T., Basset, O., Sebille, S., Raymond, G., Ruegg, U., Gailly, P., Cognard, C., and Constantin, B., 2006, Regulation of store-operated calcium entries and mitochondrial uptake by minidystrophin expression in cultured myotubes, Faseb J, 20, pp 136-138.
-
(2006)
Faseb J
, vol.20
, pp. 136-138
-
-
Vandebrouck, A.1
Ducret, T.2
Basset, O.3
Sebille, S.4
Raymond, G.5
Ruegg, U.6
Gailly, P.7
Cognard, C.8
Constantin, B.9
-
203
-
-
0035143117
-
Cationic channels in normal and dystrophic human myotubes
-
Vandebrouck, C., Duport, G., Cognard, C., and Raymond, G., 2001, Cationic channels in normal and dystrophic human myotubes, Neuromuscul Disord, 11, pp 72-79.
-
(2001)
Neuromuscul Disord
, vol.11
, pp. 72-79
-
-
Vandebrouck, C.1
Duport, G.2
Cognard, C.3
Raymond, G.4
-
204
-
-
0037012784
-
Hypotonic medium increases calcium permeant channels activity in human normal and dystrophic myotubes
-
Vandebrouck, C., Duport, G., Raymond, G., and Cognard, C., 2002a, Hypotonic medium increases calcium permeant channels activity in human normal and dystrophic myotubes, Neurosci Lett, 323, pp 239-243.
-
(2002)
Neurosci Lett
, vol.323
, pp. 239-243
-
-
Vandebrouck, C.1
Duport, G.2
Raymond, G.3
Cognard, C.4
-
205
-
-
0037119993
-
Involvement of TRPC in the abnormal calcium influx observed in dystrophic (mdx) mouse skeletal muscle fibers
-
Vandebrouck, C., Martin, D., Colson-Van Schoor, M., Debaix, H., and Gailly, P., 2002b, Involvement of TRPC in the abnormal calcium influx observed in dystrophic (mdx) mouse skeletal muscle fibers, J Cell Biol, 158, pp 1089-1096.
-
(2002)
J Cell Biol
, vol.158
, pp. 1089-1096
-
-
Vandebrouck, C.1
Martin, D.2
Colson-Van Schoor, M.3
Debaix, H.4
Gailly, P.5
-
206
-
-
0029883726
-
2+-activated, and ubiquitin-proteasome proteolytic pathways
-
2+-activated, and ubiquitin-proteasome proteolytic pathways, J Clin Invest, 97, pp 1610-1617.
-
(1996)
J Clin Invest
, vol.97
, pp. 1610-1617
-
-
Voisin, L.1
Breuille, D.2
Combaret, L.3
Pouyet, C.4
Taillandier, D.5
Aurousseau, E.6
Obled, C.7
Attaix, D.8
-
207
-
-
0141429991
-
Modulation of myoblast fusion by caveolin-3 in dystrophic skeletal muscle cells: Implications for Duchenne muscular dystrophy and limb-girdle muscular dystrophy-1C
-
Volonte, D., Peoples, A.J., and Galbiati, F., 2003, Modulation of myoblast fusion by caveolin-3 in dystrophic skeletal muscle cells: implications for Duchenne muscular dystrophy and limb-girdle muscular dystrophy-1C, Mol Biol Cell, 14, pp 4075-4088.
-
(2003)
Mol Biol Cell
, vol.14
, pp. 4075-4088
-
-
Volonte, D.1
Peoples, A.J.2
Galbiati, F.3
-
208
-
-
21044446378
-
Uncontrolled calcium sparks act as a dystrophic signal for mammalian skeletal muscle
-
Wang, X., Weisleder, N., Collet, C., Zhou, J., Chu, Y., Hirata, Y., Zhao, X., Pan, Z., Brotto, M., Cheng, H., and Ma, J., 2005, Uncontrolled calcium sparks act as a dystrophic signal for mammalian skeletal muscle, Nat Cell Biol, 7, pp 525-530.
-
(2005)
Nat Cell Biol
, vol.7
, pp. 525-530
-
-
Wang, X.1
Weisleder, N.2
Collet, C.3
Zhou, J.4
Chu, Y.5
Hirata, Y.6
Zhao, X.7
Pan, Z.8
Brotto, M.9
Cheng, H.10
Ma, J.11
-
209
-
-
0025662048
-
Dystrophin-deficient mdx muscle fibers are preferentially vulnerable to necrosis induced by experimental lengthening contractions
-
Weller, B., Karpati, G., and Carpenter, S., 1990, Dystrophin-deficient mdx muscle fibers are preferentially vulnerable to necrosis induced by experimental lengthening contractions, J Neurol Sci, 100, pp 9-13.
-
(1990)
J Neurol Sci
, vol.100
, pp. 9-13
-
-
Weller, B.1
Karpati, G.2
Carpenter, S.3
-
210
-
-
0029122522
-
Expression of human full-length and minidystrophin in transgenic mdx mice: Implications for gene therapy of Duchenne muscular dystrophy
-
Wells, D.J., Wells, K.E., Asante, E.A., Turner, G., Sunada, Y., Campbell, K.P., Walsh, F.S., and Dickson, G., 1995, Expression of human full-length and minidystrophin in transgenic mdx mice: implications for gene therapy of Duchenne muscular dystrophy, Hum Mol Genet, 4, pp 1245-1250.
-
(1995)
Hum Mol Genet
, vol.4
, pp. 1245-1250
-
-
Wells, D.J.1
Wells, K.E.2
Asante, E.A.3
Turner, G.4
Sunada, Y.5
Campbell, K.P.6
Walsh, F.S.7
Dickson, G.8
-
211
-
-
0031748456
-
Dmd(mdx-beta geo): A new allele for the mouse dystrophin gene
-
Wertz, K., and Fuchtbauer, E.M., 1998, Dmd(mdx-beta geo): a new allele for the mouse dystrophin gene, Dev Dyn, 212, pp 229-241.
-
(1998)
Dev Dyn
, vol.212
, pp. 229-241
-
-
Wertz, K.1
Fuchtbauer, E.M.2
-
212
-
-
11144354850
-
The caveolin proteins
-
Williams, T.M., and Lisanti, M.P., 2004, The caveolin proteins, Genome Biol, 5, pp 214.
-
(2004)
Genome Biol
, vol.5
, pp. 214
-
-
Williams, T.M.1
Lisanti, M.P.2
-
213
-
-
0029117231
-
Dystrophin and utrophin: The missing links!
-
Winder, S.J., Gibson, T.J., and Kendrick-Jones, J., 1995, Dystrophin and utrophin: the missing links!, FEBS Lett, 369, pp 27-33.
-
(1995)
FEBS Lett
, vol.369
, pp. 27-33
-
-
Winder, S.J.1
Gibson, T.J.2
Kendrick-Jones, J.3
-
214
-
-
0027207248
-
Characterization of translational frame exception patients in Duchenne/Becker muscular dystrophy
-
Winnard, A.V., Klein, C.J., Coovert, D.D., Prior, T., Papp, A., Snyder, P., Bulman, D.E., Ray, P.N., McAndrew, P., King, W., and et al., 1993, Characterization of translational frame exception patients in Duchenne/Becker muscular dystrophy, Hum Mol Genet, 2, pp 737-744.
-
(1993)
Hum Mol Genet
, vol.2
, pp. 737-744
-
-
Winnard, A.V.1
Klein, C.J.2
Coovert, D.D.3
Prior, T.4
Papp, A.5
Snyder, P.6
Bulman, D.E.7
Ray, P.N.8
McAndrew, P.9
King, W.10
-
215
-
-
27844464496
-
Propagation in the transverse tubular system and voltage dependence of calcium release in normal and mdx mouse muscle fibres
-
Woods, C.E., Novo, D., DiFranco, M., Capote, J., and Vergara, J.L., 2005, Propagation in the transverse tubular system and voltage dependence of calcium release in normal and mdx mouse muscle fibres, J Physiol, 568, pp 867-880.
-
(2005)
J Physiol
, vol.568
, pp. 867-880
-
-
Woods, C.E.1
Novo, D.2
DiFranco, M.3
Capote, J.4
Vergara, J.L.5
-
216
-
-
33744929843
-
Alterations in dihydropyridine receptors in dystrophin-deficient cardiac muscle
-
Woolf, P.J., Lu, S., Cornford-Nairn, R., Watson, M., Xiao, X.H., Holroyd, S.M., Brown, L., and Hoey, A.J., 2006, Alterations in dihydropyridine receptors in dystrophin-deficient cardiac muscle, Am J Physiol Heart Circ Physiol, 290, pp H2439-2445.
-
(2006)
Am J Physiol Heart Circ Physiol
, vol.290
, pp. H2439-H2445
-
-
Woolf, P.J.1
Lu, S.2
Cornford-Nairn, R.3
Watson, M.4
Xiao, X.H.5
Holroyd, S.M.6
Brown, L.7
Hoey, A.J.8
-
217
-
-
0029013870
-
SH3 domain-mediated interaction of dystroglycan and Grb2
-
Yang, B., Jung, D., Motto, D., Meyer, J., Koretzky, G., and Campbell, K.P., 1995, SH3 domain-mediated interaction of dystroglycan and Grb2, J Biol Chem, 270, pp 11711-11714.
-
(1995)
J Biol Chem
, vol.270
, pp. 11711-11714
-
-
Yang, B.1
Jung, D.2
Motto, D.3
Meyer, J.4
Koretzky, G.5
Campbell, K.P.6
-
218
-
-
23944459786
-
Dystrophic heart failure blocked by membrane sealant poloxamer
-
Yasuda, S., Townsend, D., Michele, D.E., Favre, E.G., Day, S.M., and Metzger, J.M., 2005, Dystrophic heart failure blocked by membrane sealant poloxamer, Nature, 436, pp 1025-1029.
-
(2005)
Nature
, vol.436
, pp. 1025-1029
-
-
Yasuda, S.1
Townsend, D.2
Michele, D.E.3
Favre, E.G.4
Day, S.M.5
Metzger, J.M.6
-
219
-
-
0142181051
-
Gadolinium reduces short-term stretch-induced muscle damage in isolated mdx mouse muscle fibres
-
Yeung, E.W., Head, S.I., and Allen, D.G., 2003, Gadolinium reduces short-term stretch-induced muscle damage in isolated mdx mouse muscle fibres, J Physiol, 552, pp 449-458.
-
(2003)
J Physiol
, vol.552
, pp. 449-458
-
-
Yeung, E.W.1
Head, S.I.2
Allen, D.G.3
-
220
-
-
12744268414
-
2+]i and muscle damage in the mdx mouse
-
2+]i and muscle damage in the mdx mouse, J Physiol, 562, pp 367-380.
-
(2005)
J Physiol
, vol.562
, pp. 367-380
-
-
Yeung, E.W.1
Whitehead, N.P.2
Suchyna, T.M.3
Gottlieb, P.A.4
Sachs, F.5
Allen, D.G.6
-
221
-
-
0028302369
-
Dissociation of the complex of dystrophin and its associated proteins into several unique groups by n-octyl beta- D-glucoside
-
Yoshida, M., Suzuki, A., Yamamoto, H., Noguchi, S., Mizuno, Y., and Ozawa, E., 1994, Dissociation of the complex of dystrophin and its associated proteins into several unique groups by n-octyl beta- D-glucoside, Eur J Biochem, 222, pp 1055-1061.
-
(1994)
Eur J Biochem
, vol.222
, pp. 1055-1061
-
-
Yoshida, M.1
Suzuki, A.2
Yamamoto, H.3
Noguchi, S.4
Mizuno, Y.5
Ozawa, E.6
-
222
-
-
0022402473
-
Regulation of protein degradation in muscle by calcium. Evidence for enhanced nonlysosomal proteolysis associated with elevated cytosolic calcium
-
Zeman, R.J., Kameyama, T., Matsumoto, K., Bernstein, P., and Etlinger, J.D., 1985, Regulation of protein degradation in muscle by calcium. Evidence for enhanced nonlysosomal proteolysis associated with elevated cytosolic calcium, J Biol Chem, 260, pp 13619-13624.
-
(1985)
J Biol Chem
, vol.260
, pp. 13619-13624
-
-
Zeman, R.J.1
Kameyama, T.2
Matsumoto, K.3
Bernstein, P.4
Etlinger, J.D.5
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