Drastic reduction of sarcalumenin in Dp427 (dystrophin of 427 kDa)-deficient fibres indicates that abnormal calcium handling plays a key role in muscular dystrophy

Biochemical Journal

Volumn 379, Issue 2, 2004, Pages 479-488

  Dowling, Paul ^a   Doran, Philip ^a   Ohlendieck, Kay ^a  

^a NATIONAL UNIVERSITY OF IRELAND   (Ireland)

Author keywords

Calcium handling; Dp427 (dystrophin of 427 kDa); Dystrophin; Muscular dystrophy; Sarcalumenin

Indexed keywords

CHROMOSOMES; CROSSLINKING; EXPERIMENTS; FIBERS; FLUORESCENCE; MEMBRANES; MICROSCOPIC EXAMINATION; PROTEINS; REDUCTION;

CYTOSOLIC; IMMUNOFLUORESCENCE MICROSCOPY; MYONEROSIS; PATHOPHYSIOLOGICAL MECHANISM;

MUSCLE;

ADENOSINE TRIPHOSPHATASE (CALCIUM); CALCIUM BINDING PROTEIN; CALCIUM ION; CALSEQUESTRIN; DYSTROPHIN; ISOENZYME; SARCALUMENIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CALCIUM BINDING; CALCIUM TRANSPORT; CONTROLLED STUDY; CROSS LINKING; IMMUNOBLOTTING; IMMUNOFLUORESCENCE MICROSCOPY; IMMUNOPRECIPITATION; MALE; MOUSE; MUSCLE CELL; MUSCLE NECROSIS; MUSCULAR DYSTROPHY; NONHUMAN; PRIORITY JOURNAL; PROTEIN DEFICIENCY; PROTEIN DEGRADATION; PROTEIN DOMAIN; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN SYNTHESIS; SARCOPLASMIC RETICULUM; SKELETAL MUSCLE;

ANIMALS; CALCIUM; CALCIUM-TRANSPORTING ATPASES; DYSTROPHIN; MALE; MEMBRANE PROTEINS; MICE; MICE, INBRED MDX; MODELS, BIOLOGICAL; MUSCLE FIBERS; MUSCLE, SKELETAL; MUSCULAR DYSTROPHY, ANIMAL; POINT MUTATION; SARCOPLASMIC RETICULUM;

ANIMALIA;

EID: 2342614190     PISSN: 02646021     EISSN: None     Source Type: Journal    
DOI: 10.1042/BJ20031311     Document Type: Article

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