Modern pathology: Protein mis-folding and mis-processing in complex disease

Current Protein and Peptide Science

Volumn 8, Issue 1, 2007, Pages 29-37

  Fadiel, Ahmed ^a   Eichenbaum, Kenneth D ^b   Hamza, Adel ^c,e   Tan, Orkon ^d   Lee, Hae H ^a   Naftolin, Frederick ^a  

^a NEW YORK UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b MOUNT SINAI SCHOOL OF MEDICINE   (United States)

^c PASTEUR INSTITUTE OF TUNIS   (Tunisia)

^d YALE UNIVERSITY SCHOOL OF MEDICINE   (United States)

^e University of Kentucky   (United States)

Author keywords

Disease etiology; Drug targeting; Endoplasmic reticulum; Protein folding; Protein mis folding; Proteomics

Indexed keywords

AMINO ACID; AMYLOID BETA PROTEIN; PRION PROTEIN; PROTEASOME; PROTEINASE K; TRANSCRIPTION FACTOR SP1; TRANSMEMBRANE CONDUCTANCE REGULATOR;

ALPHA 1 ANTITRYPSIN DEFICIENCY; ALPHA HELIX; ALZHEIMER DISEASE; AMINO ACID SEQUENCE; BIOCHEMISTRY; CONFORMATIONAL TRANSITION; CREUTZFELDT JAKOB DISEASE; CYSTIC FIBROSIS; DEGENERATIVE DISEASE; GENE MUTATION; GENETIC TRANSCRIPTION; GENOMICS; HISTOPATHOLOGY; HUMAN; MACROMOLECULE; MUTATIONAL ANALYSIS; PROMOTER REGION; PROTEIN FOLDING; PROTEIN PROCESSING; PROTEIN STRUCTURE; PROTEOMICS; RETINA DISEASE; REVIEW;

ALZHEIMER DISEASE; AMINO ACID SEQUENCE; ANIMALS; CREUTZFELDT-JAKOB SYNDROME; CYSTIC FIBROSIS; ELECTROCHEMISTRY; ELECTROSTATICS; EVOLUTION, MOLECULAR; HUMANS; MODELS, MOLECULAR; MOLECULAR SEQUENCE DATA; MULTIPROTEIN COMPLEXES; PRIONS; PROTEIN FOLDING; PROTEIN PROCESSING, POST-TRANSLATIONAL; PROTEINS; PROTEOMICS; SEQUENCE HOMOLOGY, AMINO ACID; SYNDROME;

EID: 33847337335     PISSN: 13892037     EISSN: None     Source Type: Journal    
DOI: 10.2174/138920307779941532     Document Type: Review

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