Trafficking defects in endogenously synthesized cholesterol in fibroblasts, macrophages, hepatocytes, and glial cells from Niemann-Pick type C1 mice

Journal of Lipid Research

Volumn 44, Issue 5, 2003, Pages 1010-1019

  Reid, Patrick C ^a   Sugii, Shigeki ^a   Chang, Ta Yuan ^a  

^a DARTMOUTH MEDICAL SCHOOL   (United States)

Author keywords

Acyl CoA:cholesterol acyltransferase; Cholesterol biosynthesis; Intracellular cholesterol trafficking; Membrane recycling; NPC disease

Indexed keywords

CHOLESTEROL; GLYCOLIPID; LOW DENSITY LIPOPROTEIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CELL MEMBRANE; CELL ORGANELLE; CELL TYPE; CHO CELL; CHOLESTEROL SYNTHESIS; CHOLESTEROL TRANSPORT; EMBRYO; ENDOSOME; ESTERIFICATION; FIBROBLAST; GLIA CELL; HETEROZYGOSITY; HOMOZYGOSITY; LIVER CELL; MACROPHAGE; MOUSE; MOUSE STRAIN; NIEMANN PICK DISEASE; NONHUMAN; PRIORITY JOURNAL; WILD TYPE;

ANIMALS; BIOLOGICAL TRANSPORT; CHO CELLS; CHOLESTEROL; CHOLESTEROL, LDL; CRICETINAE; CYCLODEXTRINS; ENDOPLASMIC RETICULUM; FEMALE; FIBROBLASTS; HEPATOCYTES; HUMANS; MACROPHAGES, PERITONEAL; MALE; MEMBRANE GLYCOPROTEINS; MICE; MICE, INBRED BALB C; MICE, MUTANT STRAINS; MUTATION; NEUROGLIA; NIEMANN-PICK DISEASES; PREGNANCY; TIME FACTORS;

EID: 0042163785     PISSN: 00222275     EISSN: None     Source Type: Journal    
DOI: 10.1194/jlr.M300009-JLR200     Document Type: Article

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