Cholesterol balance and metabolism in mice with loss of function of Niemann-Pick C protein

American Journal of Physiology - Endocrinology and Metabolism

Volumn 276, Issue 2 39-2, 1999, Pages

  Xie, Chonglun ^a   Turley, Stephen D ^a   Pentchev, Peter G ^b   Dietschy, John M ^a,c  

^a UNIVERSITY OF TEXAS SOUTHWESTERN MEDICAL CENTER   (United States)

^b NATIONAL INSTITUTE OF NEUROLOGICAL DISORDERS AND STROKE   (United States)

^c UNIVERSITY OF TEXAS SOUTHWESTERN MEDICAL CENTER   (United States)

Author keywords

Cholesterol synthesis; Endoplasmic reticulum; Low density lipoprotein receptor; Lysosome; Neurodegeneration

Indexed keywords

CELL PROTEIN; CHOLESTEROL; LOW DENSITY LIPOPROTEIN CHOLESTEROL; LOW DENSITY LIPOPROTEIN RECEPTOR; NIEMANN PICK C PROTEIN; UNCLASSIFIED DRUG;

ANIMAL MODEL; ARTICLE; BODY WEIGHT; CHOLESTEROL BLOOD LEVEL; CHOLESTEROL ESTERIFICATION; CHOLESTEROL METABOLISM; CHOLESTEROL SYNTHESIS; CHOLESTEROL TRANSPORT; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; GENE MUTATION; HETEROZYGOSITY; HOMOZYGOSITY; MOUSE; NERVE CELL DEGENERATION; NIEMANN PICK DISEASE; NONHUMAN; PRIORITY JOURNAL;

EID: 0033049909     PISSN: 01931849     EISSN: None     Source Type: Journal    
DOI: 10.1152/ajpendo.1999.276.2.e336     Document Type: Article

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