Sites and temporal changes of gangliosides GM1/GM2 storage in the Niemann-Pick disease type C mouse brain

Brain and Development

Volumn 23, Issue 6, 2001, Pages 414-421

  Taniguchi, Miyako ^a   Shinoda, Yoko ^a   Ninomiya, Haruaki ^a   Vanier, Marie T ^b   Ohno, Kousaku ^a  

^a TOTTORI UNIVERSITY   (Japan)

^b INSERM   (France)

Author keywords

Ganglioside; Niemann Pick disease type C; Purkinje cells

Indexed keywords

ANTIBODY; GANGLIOSIDE GM1; GANGLIOSIDE GM2; GLIAL FIBRILLARY ACIDIC PROTEIN; LYSOZYME; MONOSIALOGANGLIOSIDE;

AGE; ANIMAL CELL; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; ASTROCYTE; BRAIN NERVE CELL; BRAIN REGION; CELL TYPE; CELLULAR DISTRIBUTION; CONTROLLED STUDY; CYTOPLASM; CYTOPLASM VESICLE; DENDRITE; DISEASE COURSE; GM1 GANGLIOSIDOSIS; GM2 GANGLIOSIDOSIS; IMMUNOCYTOCHEMISTRY; LIPID STORAGE; MACROPHAGE; MOUSE; MOUSE STRAIN; NERVE CELL CULTURE; NEWBORN; NIEMANN PICK DISEASE; NONHUMAN; PURKINJE CELL; STAINING; TEMPORAL LOBE; TISSUE DISTRIBUTION;

AGING; ANIMALS; ANIMALS, NEWBORN; BRAIN; BRAIN CHEMISTRY; CELLS, CULTURED; CEREBELLUM; FLUORESCENT ANTIBODY TECHNIQUE; G(M1) GANGLIOSIDE; G(M2) GANGLIOSIDE; GLIAL FIBRILLARY ACIDIC PROTEIN; IMMUNOHISTOCHEMISTRY; MICE; MICE, INBRED BALB C; NIEMANN-PICK DISEASES; PURKINJE CELLS;

EID: 0034801896     PISSN: 03877604     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0387-7604(01)00252-2     Document Type: Article

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