-
1
-
-
0025732188
-
Identification of mitochondrial and non-mitochondrial glutaminase within select neurons and glia of rat forebrain by electron microscopic immunocytochemistry
-
Aoki C., Kaneko T., Starr A., and Pickel V. (1991) Identification of mitochondrial and non-mitochondrial glutaminase within select neurons and glia of rat forebrain by electron microscopic immunocytochemistry. J. Neurosci. Res. 28, 531-548.
-
(1991)
J. Neurosci. Res.
, vol.28
, pp. 531-548
-
-
Aoki, C.1
Kaneko, T.2
Starr, A.3
Pickel, V.4
-
2
-
-
0023874590
-
Glutamine and ketone-body metabolism in the gut of streptozotocin-diabetic rats
-
Ardawi M. S. (1988) Glutamine and ketone-body metabolism in the gut of streptozotocin-diabetic rats. Biochem. J. 249, 565-572.
-
(1988)
Biochem. J.
, vol.249
, pp. 565-572
-
-
Ardawi, M.S.1
-
3
-
-
0031892603
-
Functional evaluation techniques in mitochondrial disorders
-
Argov Z. (1998) Functional evaluation techniques in mitochondrial disorders. Eur. Neurol. 39, 65-71.
-
(1998)
Eur. Neurol.
, vol.39
, pp. 65-71
-
-
Argov, Z.1
-
4
-
-
0031950826
-
Frontal lobe volume in patients with Huntington's disease
-
Aylward E. H., Anderson N. B., Bylsma F. W., Wagster M. V., Barta P. E., Sherr M., Feeney J., Davis A., Rosenblatt A., Pearlson G. D., and Ross C. A. (1998) Frontal lobe volume in patients with Huntington's disease. Neurology 50, 252-258.
-
(1998)
Neurology
, vol.50
, pp. 252-258
-
-
Aylward, E.H.1
Anderson, N.B.2
Bylsma, F.W.3
Wagster, M.V.4
Barta, P.E.5
Sherr, M.6
Feeney, J.7
Davis, A.8
Rosenblatt, A.9
Pearlson, G.D.10
Ross, C.A.11
-
5
-
-
2642666489
-
Cognitive deficits in Huntington's disease are predicted by dopaminergic PET markers and brain volumes
-
Backman L., Robins-Wahlin T. B., Lundin A., Ginovart N., and Farde L. (1997) Cognitive deficits in Huntington's disease are predicted by dopaminergic PET markers and brain volumes. Brain 120, 2207-2217.
-
(1997)
Brain
, vol.120
, pp. 2207-2217
-
-
Backman, L.1
Robins-Wahlin, T.B.2
Lundin, A.3
Ginovart, N.4
Farde, L.5
-
6
-
-
0027228506
-
Mitochondrial disorders: Analysis of their clinical and imaging characteristics
-
Barkovich A. J., Good W. V., Koch T. K., and Berg B. O. (1993) Mitochondrial disorders: analysis of their clinical and imaging characteristics. AJNR Am. J. Neuroradiol. 14, 1119-1137.
-
(1993)
AJNR Am. J. Neuroradiol.
, vol.14
, pp. 1119-1137
-
-
Barkovich, A.J.1
Good, W.V.2
Koch, T.K.3
Berg, B.O.4
-
7
-
-
0030712094
-
Transgenic mouse models of neurodegenerative disease caused by CAG/polyglutamine expansions
-
Bates G. P. and Davies S. W. (1997) Transgenic mouse models of neurodegenerative disease caused by CAG/polyglutamine expansions. Mol. Med. Today 3, 508-515.
-
(1997)
Mol. Med. Today
, vol.3
, pp. 508-515
-
-
Bates, G.P.A.1
Davies, S.W.2
-
8
-
-
0030866538
-
Transgenic models of Huntington's disease
-
Bates G. P., Mangiarini L., Mahal A., and Davies S. W. (1997) Transgenic models of Huntington's disease. Hum. Mol. Genet. 6, 1633-1637.
-
(1997)
Hum. Mol. Genet.
, vol.6
, pp. 1633-1637
-
-
Bates, G.P.1
Mangiarini, L.2
Mahal, A.3
Davies, S.W.4
-
10
-
-
0025925019
-
1H spectrum of rat brain by two-dimensional shift correlated and J-resolved NMR spectroscopy
-
1H spectrum of rat brain by two-dimensional shift correlated and J-resolved NMR spectroscopy. Magn. Reson. Med. 17, 285-303.
-
(1991)
Magn. Reson. Med.
, vol.17
, pp. 285-303
-
-
Behar, K.L.1
Ogino, T.2
-
11
-
-
0023636904
-
Spatial localization in NMR spectroscopy in vivo
-
Bottomley P. (1987) Spatial localization in NMR spectroscopy in vivo. Ann. NY Acad. Sci. 508, 333-348.
-
(1987)
Ann. NY Acad. Sci.
, vol.508
, pp. 333-348
-
-
Bottomley, P.1
-
12
-
-
0027448161
-
Age-dependent vulnerability of the striatum to the mitochondrial toxin 3-nitropropionic acid
-
Brouillet E., Jenkins B. G., Hyman B. T., Ferrante R. J., Kowall N. W., Srivastava R., Roy D. S., Rosen B. R., and Beal M. F. (1993) Age-dependent vulnerability of the striatum to the mitochondrial toxin 3-nitropropionic acid. J. Neurochem. 60, 356-359.
-
(1993)
J. Neurochem.
, vol.60
, pp. 356-359
-
-
Brouillet, E.1
Jenkins, B.G.2
Hyman, B.T.3
Ferrante, R.J.4
Kowall, N.W.5
Srivastava, R.6
Roy, D.S.7
Rosen, B.R.8
Beal, M.F.9
-
13
-
-
0021011613
-
The composition of animal cells: Solutes contributing to osmotic pressure and charge balance
-
Burton R. F. (1983) The composition of animal cells: solutes contributing to osmotic pressure and charge balance. Comp. Biochem. Physiol. B Biochem. Mol. Biol. 76, 663-671.
-
(1983)
Comp. Biochem. Physiol. B Biochem. Mol. Biol.
, vol.76
, pp. 663-671
-
-
Burton, R.F.1
-
14
-
-
0021917344
-
Distribution of phosphate-activated glutaminase, succinic dehydrogenase, pyruvate dehydrogenase and gamma-glutamyl transpeptidase in postmortem brain from Huntington's disease and agonal cases
-
Butterworth J., Yates C. M., and Reynolds G. P. (1985) Distribution of phosphate-activated glutaminase, succinic dehydrogenase, pyruvate dehydrogenase and gamma-glutamyl transpeptidase in postmortem brain from Huntington's disease and agonal cases. J. Neurol. Sci. 67, 161-171.
-
(1985)
J. Neurol. Sci.
, vol.67
, pp. 161-171
-
-
Butterworth, J.1
Yates, C.M.2
Reynolds, G.P.3
-
15
-
-
0017870540
-
Effect of alloxan diabetes on cerebellar amino acids
-
Butterworth R. F., Hamel E., Landreville F., and Barbeau A. (1978) Effect of alloxan diabetes on cerebellar amino acids. Can. J. Neurol. Sci. 5, 135-137.
-
(1978)
Can. J. Neurol. Sci.
, vol.5
, pp. 135-137
-
-
Butterworth, R.F.1
Hamel, E.2
Landreville, F.3
Barbeau, A.4
-
16
-
-
0031468302
-
Normalization of neuronal metabolic dysfunction after surgery for temporal lobe epilepsy. Evidence from proton MR spectroscopic imaging
-
Cendes F., Andermann F., Dubeau F., Matthews P. M., and Arnold D. L. (1997) Normalization of neuronal metabolic dysfunction after surgery for temporal lobe epilepsy. Evidence from proton MR spectroscopic imaging. Neurology 49, 1525-1533.
-
(1997)
Neurology
, vol.49
, pp. 1525-1533
-
-
Cendes, F.1
Andermann, F.2
Dubeau, F.3
Matthews, P.M.4
Arnold, D.L.5
-
17
-
-
0032568517
-
Altered brain neurotransmitter receptors in transgenic mice expressing a portion of an abnormal human huntington disease gene
-
Cha J. H., Kosinski C. M., Kerner J. A., Alsdorf S. A., Mangiarini L., Davies S. W., Penney J. B., Bates G. P., and Young A. B. (1998) Altered brain neurotransmitter receptors in transgenic mice expressing a portion of an abnormal human huntington disease gene. Proc. Natl. Acad. Sci. USA 95, 6480-6485.
-
(1998)
Proc. Natl. Acad. Sci. USA
, vol.95
, pp. 6480-6485
-
-
Cha, J.H.1
Kosinski, C.M.2
Kerner, J.A.3
Alsdorf, S.A.4
Mangiarini, L.5
Davies, S.W.6
Penney, J.B.7
Bates, G.P.8
Young, A.B.9
-
18
-
-
84919592151
-
Proton MRS in Huntington's disease
-
Davie C. A., Barker G. J., Quinn N., Tofts P. S., and Miller D. H. (1994a) Proton MRS in Huntington's disease. Lancet 343, 1580.
-
(1994)
Lancet
, vol.343
, pp. 1580
-
-
Davie, C.A.1
Barker, G.J.2
Quinn, N.3
Tofts, P.S.4
Miller, D.H.5
-
19
-
-
0028265609
-
Serial proton magnetic resonance spectroscopy in acute multiple sclerosis lesions
-
Davie C. A., Hawkins C. P., Barker G. J., Brennan A., Tofts P. S., Miller D. H., and McDonald W. I. (1994b) Serial proton magnetic resonance spectroscopy in acute multiple sclerosis lesions. Brain 117, 49-58.
-
(1994)
Brain
, vol.117
, pp. 49-58
-
-
Davie, C.A.1
Hawkins, C.P.2
Barker, G.J.3
Brennan, A.4
Tofts, P.S.5
Miller, D.H.6
McDonald, W.I.7
-
20
-
-
18544410106
-
Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation
-
Davies S. W., Turmaine M., Cozens B. A., DiFiglia M., Sharp A. H., Ross C. A., Scherzinger E., Wanker E. E., Mangiarini L., and Bates G. P. (1997) Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation. Cell 90, 537-548.
-
(1997)
Cell
, vol.90
, pp. 537-548
-
-
Davies, S.W.1
Turmaine, M.2
Cozens, B.A.3
DiFiglia, M.4
Sharp, A.H.5
Ross, C.A.6
Scherzinger, E.7
Wanker, E.E.8
Mangiarini, L.9
Bates, G.P.10
-
21
-
-
0032501740
-
Are neuronal intranuclear inclusions the common neuropathology of triplet-repeat disorders with polyglutamine-repeat expansions?
-
Davies S. W., Beardsall K., Turmaine M., DiFiglia M., Aronin N., and Bates G. P. (1998) Are neuronal intranuclear inclusions the common neuropathology of triplet-repeat disorders with polyglutamine-repeat expansions? Lancet 351, 131-133.
-
(1998)
Lancet
, vol.351
, pp. 131-133
-
-
Davies, S.W.1
Beardsall, K.2
Turmaine, M.3
DiFiglia, M.4
Aronin, N.5
Bates, G.P.6
-
22
-
-
0028792005
-
Reversible decreases in N-acetylaspartate after acute brain injury
-
De Stefano N., Matthews P. M., and Arnold D. L. (1995) Reversible decreases in N-acetylaspartate after acute brain injury. Magn. Reson. Med. 34, 721-727.
-
(1995)
Magn. Reson. Med.
, vol.34
, pp. 721-727
-
-
De Stefano, N.1
Matthews, P.M.2
Arnold, D.L.3
-
23
-
-
0030752709
-
Aggregation of huntingtin in neuronal intranuclear inclusions and dystrophic neurites in brain
-
DiFiglia M., Sapp E., Chase K. O., Davies S. W., Bates G. P., Vonsattel J. P., and Aronin N. (1997) Aggregation of huntingtin in neuronal intranuclear inclusions and dystrophic neurites in brain. Science 277, 1990-1993.
-
(1997)
Science
, vol.277
, pp. 1990-1993
-
-
DiFiglia, M.1
Sapp, E.2
Chase, K.O.3
Davies, S.W.4
Bates, G.P.5
Vonsattel, J.P.6
Aronin, N.7
-
24
-
-
0026694238
-
Decreased brain N-acetylaspartate in Huntington's disease
-
Dunlop D. S., McHale D. M., and Lajtha A. (1992) Decreased brain N-acetylaspartate in Huntington's disease. Brain Res. 580, 44-48.
-
(1992)
Brain Res.
, vol.580
, pp. 44-48
-
-
Dunlop, D.S.1
McHale, D.M.2
Lajtha, A.3
-
25
-
-
0021927818
-
Diabetes mellitus in Huntington disease
-
Farrer L. A. (1985) Diabetes mellitus in Huntington disease. Clin. Genet. 27, 62-67.
-
(1985)
Clin. Genet.
, vol.27
, pp. 62-67
-
-
Farrer, L.A.1
-
26
-
-
0030767498
-
Increased 3-nitrotyrosine and oxidative damage in mice with a human Cu,Zn superoxide dismutase mutation
-
Ferrante R. J., Shinobu L. A., Schulz J. B., Matthews R. T., Thomas C. E., Kowall N. W., Gurney M. E., and Beal M. F. (1997) Increased 3-nitrotyrosine and oxidative damage in mice with a human Cu,Zn Superoxide dismutase mutation. Ann. Neurol. 42, 326-334.
-
(1997)
Ann. Neurol.
, vol.42
, pp. 326-334
-
-
Ferrante, R.J.1
Shinobu, L.A.2
Schulz, J.B.3
Matthews, R.T.4
Thomas, C.E.5
Kowall, N.W.6
Gurney, M.E.7
Beal, M.F.8
-
27
-
-
0014574467
-
Glucose metabolism in brains of diabetic rats
-
Flock E. V., Tyce G. M., and Owen C. A., Jr. (1969) Glucose metabolism in brains of diabetic rats. Endocrinology 85, 428-437.
-
(1969)
Endocrinology
, vol.85
, pp. 428-437
-
-
Flock, E.V.1
Tyce, G.M.2
Owen C.A., Jr.3
-
29
-
-
0032209255
-
1H NMR spectra with increased magnetic field strength
-
1H NMR spectra with increased magnetic field strength. J. Magn. Reson. 135, 260-264.
-
(1998)
J. Magn. Reson.
, vol.135
, pp. 260-264
-
-
Gruetter, R.1
Weisdorf, S.A.2
Rajanayagan, V.3
Terpstra, M.4
Merkle, H.5
Truwit, C.L.6
Garwood, M.7
Nyberg, S.L.8
Ugurbil, K.9
-
30
-
-
0028971456
-
1H nuclear magnetic resonance spectroscopic imaging of neuronal loss in rat brain
-
1H nuclear magnetic resonance spectroscopic imaging of neuronal loss in rat brain. Neuroscience 69, 1095-1101.
-
(1995)
Neuroscience
, vol.69
, pp. 1095-1101
-
-
Guimaraes, A.R.1
Schwartz, P.2
Prakash, M.R.3
Carr, C.A.4
Berger, U.V.5
Jenkins, B.G.6
Coyle, J.T.7
Gonzalez, R.G.8
-
31
-
-
0032103078
-
Huntingtin: A single bait hooks many species
-
Gusella J. F. and MacDonald M. E. (1998) Huntingtin: a single bait hooks many species. Curr. Opin. Neurobiol. 8, 425-430.
-
(1998)
Curr. Opin. Neurobiol.
, vol.8
, pp. 425-430
-
-
Gusella, J.F.1
MacDonald, M.E.2
-
32
-
-
0029098594
-
Selective inhibition of the tricarboxylic acid cycle of GABAergic neurons with 3-nitropropionic acid in vivo
-
Hassel B. and Sonnewald U. (1995) Selective inhibition of the tricarboxylic acid cycle of GABAergic neurons with 3-nitropropionic acid in vivo. J. Neurochem. 65, 1184-1191.
-
(1995)
J. Neurochem.
, vol.65
, pp. 1184-1191
-
-
Hassel, B.1
Sonnewald, U.2
-
33
-
-
0033009587
-
Mice transgenic for an expanded CAG repeat in the Huntington's disease gene develop diabetes
-
Hurlbert M. S., Zhou W., Wasmeier C., Kaddis F. G., Hullon J. C., and Freed C. R. (1999) Mice transgenic for an expanded CAG repeat in the Huntington's disease gene develop diabetes. Diabetes 48, 649-651.
-
(1999)
Diabetes
, vol.48
, pp. 649-651
-
-
Hurlbert, M.S.1
Zhou, W.2
Wasmeier, C.3
Kaddis, F.G.4
Hullon, J.C.5
Freed, C.R.6
-
34
-
-
0017797718
-
Metabolic disorders in Huntington's chorea
-
Insarova N. G., Korshunova T. S., Mzhel'skaia T. I., and Borisova T. V. (1978) Metabolic disorders in Huntington's chorea [in Russian]. Zh. Nevropatot. Psikhiatr. Im S. S. Korsakova 78, 489-495.
-
(1978)
Zh. Nevropatot. Psikhiatr. Im S. S. Korsakova
, vol.78
, pp. 489-495
-
-
Insarova, N.G.1
Korshunova, T.S.2
Mzhel'skaia, T.I.3
Borisova, T.V.4
-
36
-
-
0029866972
-
Non-invasive neurochemical analysis of focal excitotoxic lesions in models of neurodegenerative illness using spectroscopic imaging
-
Jenkins B. G., Brouillet E., Chen Y. C., Storey E., Schulz J. B., Kirschner P., Beal M. F., and Rosen B. R. (1996) Non-invasive neurochemical analysis of focal excitotoxic lesions in models of neurodegenerative illness using spectroscopic imaging. J. Cereb. Blood Flow Metab. 16, 450-461.
-
(1996)
J. Cereb. Blood Flow Metab.
, vol.16
, pp. 450-461
-
-
Jenkins, B.G.1
Brouillet, E.2
Chen, Y.C.3
Storey, E.4
Schulz, J.B.5
Kirschner, P.6
Beal, M.F.7
Rosen, B.R.8
-
37
-
-
0002514027
-
-
Beal M. F., Howell N., and Bodis-Wollner I., eds, Wiley-Liss, New York
-
Jenkins B., Chen Y., and Rosen B. (1997) Investigating the neurochemistry and etiology of neurodegenerative disorders using magnetic resonance spectroscopy, in Mitochondria and Free Radicals in Neurodegenerative Diseases, (Beal M. F., Howell N., and Bodis-Wollner I., eds), pp. 423-470. Wiley-Liss, New York.
-
(1997)
Investigating the Neurochemistry and Etiology of Neurodegenerative Disorders using Magnetic Resonance Spectroscopy, in Mitochondria and Free Radicals in Neurodegenerative Diseases
, pp. 423-470
-
-
Jenkins, B.1
Chen, Y.2
Rosen, B.3
-
38
-
-
0031596998
-
1H NMR spectroscopy studies of Huntington's disease: Correlations with CAG repeat numbers
-
1H NMR spectroscopy studies of Huntington's disease: correlations with CAG repeat numbers. Neurology 50, 1357-1365.
-
(1998)
Neurology
, vol.50
, pp. 1357-1365
-
-
Jenkins, B.G.1
Rosas, H.D.2
Chen, Y.C.3
Makabe, T.4
Myers, R.5
MacDonald, M.6
Rosen, B.R.7
Beal, M.F.8
Koroshetz, W.J.9
-
39
-
-
0032102114
-
Recovery of N-acetylaspartate in corticomotor neurons of patients with ALS after riluzole therapy
-
Kalra S., Cashman N. R., Genge A., and Arnold D. L. (1998) Recovery of N-acetylaspartate in corticomotor neurons of patients with ALS after riluzole therapy. Neuroreport 9, 1757-1761.
-
(1998)
Neuroreport
, vol.9
, pp. 1757-1761
-
-
Kalra, S.1
Cashman, N.R.2
Genge, A.3
Arnold, D.L.4
-
40
-
-
0032475941
-
Ataxin-1 nuclear localization and aggregation: Role in polyglutamine-induced disease in SCA1 transgenic mice
-
Klement I. A., Skinner P. J., Kaytor M. D., Yi H., Hersch S. M., Clark H. B., Zoghbi H. Y., and Orr H. T. (1998) Ataxin-1 nuclear localization and aggregation: role in polyglutamine-induced disease in SCA1 transgenic mice. Cell 95, 41-53.
-
(1998)
Cell
, vol.95
, pp. 41-53
-
-
Klement, I.A.1
Skinner, P.J.2
Kaytor, M.D.3
Yi, H.4
Hersch, S.M.5
Clark, H.B.6
Zoghbi, H.Y.7
Orr, H.T.8
-
41
-
-
0026726198
-
N-acetyl-L-aspartate and other amino acid metabolites in Alzheimer's disease brain: A preliminary proton nuclear magnetic resonance study
-
Klunk W. E., Panchalingam K., Moossy J., McClure R. J., and Pettegrew J. W. (1992) N-Acetyl-L-aspartate and other amino acid metabolites in Alzheimer's disease brain: a preliminary proton nuclear magnetic resonance study. Neurology 42, 1578-1585.
-
(1992)
Neurology
, vol.42
, pp. 1578-1585
-
-
Klunk, W.E.1
Panchalingam, K.2
Moossy, J.3
McClure, R.J.4
Pettegrew, J.W.5
-
42
-
-
0026773392
-
Cerebral metabolic disturbances in patients with subacute and chronic diabetes mellitus: Detection with proton MR spectroscopy
-
Kreis R. and Ross B. D. (1992) Cerebral metabolic disturbances in patients with subacute and chronic diabetes mellitus: detection with proton MR spectroscopy. Radiology 184, 123-130.
-
(1992)
Radiology
, vol.184
, pp. 123-130
-
-
Kreis, R.1
Ross, B.D.2
-
43
-
-
0024510676
-
Endocrine functions in Huntington's disease. A two-and-a-half years follow-up study
-
Kremer H. P., Roos R. A., Frolich M., Radder J. K., Nieuwenhuijzen Kruseman A. C., Van der Velde A., and Buruma O. J. (1989) Endocrine functions in Huntington's disease. A two-and-a-half years follow-up study. J. Neurol. Sci. 90, 335-344.
-
(1989)
J. Neurol. Sci.
, vol.90
, pp. 335-344
-
-
Kremer, H.P.1
Roos, R.A.2
Frolich, M.3
Radder, J.K.4
Nieuwenhuijzen Kruseman, A.C.5
Van Der Velde, A.6
Buruma, O.J.7
-
44
-
-
0025153344
-
Cortical and subcortical glucose consumption measured by PET in patients with Huntington's disease
-
Kuwert T., Lange H. W., Langen K. J., Herzog H., Aulich A., and Feinendegen L. E. (1990) Cortical and subcortical glucose consumption measured by PET in patients with Huntington's disease. Brain 113, 1405-1423.
-
(1990)
Brain
, vol.113
, pp. 1405-1423
-
-
Kuwert, T.1
Lange, H.W.2
Langen, K.J.3
Herzog, H.4
Aulich, A.5
Feinendegen, L.E.6
-
45
-
-
0027388933
-
Comparison of somatosensory evoked potentials with striatal glucose consumption measured by positron emission tomography in the early diagnosis of Huntington's disease
-
Kuwert T., Noth J., Scholz D., Schwarz M., Lange H. W., Topper R., Herzog H., Aulich A., and Feinendegen L. E. (1993) Comparison of somatosensory evoked potentials with striatal glucose consumption measured by positron emission tomography in the early diagnosis of Huntington's disease. Mov. Disord. 8, 98-106.
-
(1993)
Mov. Disord.
, vol.8
, pp. 98-106
-
-
Kuwert, T.1
Noth, J.2
Scholz, D.3
Schwarz, M.4
Lange, H.W.5
Topper, R.6
Herzog, H.7
Aulich, A.8
Feinendegen, L.E.9
-
46
-
-
0028371970
-
Regulation of mammalian brain cell volume
-
Law R. O. (1994) Regulation of mammalian brain cell volume. J. Exp. Zool. 268, 90-96.
-
(1994)
J. Exp. Zool.
, vol.268
, pp. 90-96
-
-
Law, R.O.1
-
47
-
-
0031945025
-
Aggregation of N-terminal huntingtin is dependent on the length of its glutamine repeats
-
Li S.-H. and Li X.-J. (1998) Aggregation of N-terminal huntingtin is dependent on the length of its glutamine repeats. Hum. Mol. Genet. 7, 777-782.
-
(1998)
Hum. Mol. Genet.
, vol.7
, pp. 777-782
-
-
Li, S.-H.1
Li, X.-J.2
-
49
-
-
0028897760
-
Lipid metabolism and membrane composition are altered in the brains of type II diabetic mice
-
Makar T. K., Hungund B. L., Cook G. A., Kashfi K., and Cooper A. J. L. (1995) Lipid metabolism and membrane composition are altered in the brains of type II diabetic mice. J. Neurochem. 64, 2159-2168.
-
(1995)
J. Neurochem.
, vol.64
, pp. 2159-2168
-
-
Makar, T.K.1
Hungund, B.L.2
Cook, G.A.3
Kashfi, K.4
Cooper, A.J.L.5
-
50
-
-
16044373842
-
Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice
-
Mangiarini L., Sathasivam K., Seller M., Cozens B., Harper A., Hetherington C., Lawton M., Trottier Y., Lehrach H., Davies S. W., and Bates G. P. (1996) Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice. Cell 87, 493-506.
-
(1996)
Cell
, vol.87
, pp. 493-506
-
-
Mangiarini, L.1
Sathasivam, K.2
Seller, M.3
Cozens, B.4
Harper, A.5
Hetherington, C.6
Lawton, M.7
Trottier, Y.8
Lehrach, H.9
Davies, S.W.10
Bates, G.P.11
-
51
-
-
0031056685
-
Instability of highly expanded CAG repeats in mice transgenic for the Huntington's disease mutation
-
Mangiarini L., Sathasivam K., Mahal A., Mott R., Seller M., and Bates G. P. (1997) Instability of highly expanded CAG repeats in mice transgenic for the Huntington's disease mutation. Nat. Genet. 15, 197-200.
-
(1997)
Nat. Genet.
, vol.15
, pp. 197-200
-
-
Mangiarini, L.1
Sathasivam, K.2
Mahal, A.3
Mott, R.4
Seller, M.5
Bates, G.P.6
-
52
-
-
0027722281
-
Proton MR spectroscopic characterization of differences in regional brain metabolic abnormalities in mitochondrial encephalomyopathies
-
Mathews P. M., Andermann F., Silver K., Karpati G., and Arnold D. L. (1993) Proton MR spectroscopic characterization of differences in regional brain metabolic abnormalities in mitochondrial encephalomyopathies. Neurology 43, 2484-2490.
-
(1993)
Neurology
, vol.43
, pp. 2484-2490
-
-
Mathews, P.M.1
Andermann, F.2
Silver, K.3
Karpati, G.4
Arnold, D.L.5
-
53
-
-
0031964359
-
Neuroprotective effects of creatine and cyclocreatine in animal models of Huntington's disease
-
Matthews R. T., Yang L., Jenkins B. G., Ferrante R. J., Rosen B. R., Kaddurah-Daouk R., and Beal M. F. (1998) Neuroprotective effects of creatine and cyclocreatine in animal models of Huntington's disease. J. Neurosci. 18, 156-163.
-
(1998)
J. Neurosci.
, vol.18
, pp. 156-163
-
-
Matthews, R.T.1
Yang, L.2
Jenkins, B.G.3
Ferrante, R.J.4
Rosen, B.R.5
Kaddurah-Daouk, R.6
Beal, M.F.7
-
54
-
-
0026452013
-
Brain pH and lactic acidosis: Quantitative analysis of taurine effect
-
Nakada T., Hida K., and Kwee I. L. (1992) Brain pH and lactic acidosis: quantitative analysis of taurine effect. Neurosci. Res. 15, 115-123.
-
(1992)
Neurosci. Res.
, vol.15
, pp. 115-123
-
-
Nakada, T.1
Hida, K.2
Kwee, I.L.3
-
55
-
-
0000263890
-
Extraneural metabolism in early Huntington's disease
-
O'Brien C. F., Miller C., Goldblatt D., Welle S., Forbes G., Lipinski B., Panzik J., Peck R., Plumb S., Oakes D., Kurlan R., and Shoulson I. (1990) Extraneural metabolism in early Huntington's disease. Ann. Neurol. 28, 300-301.
-
(1990)
Ann. Neurol.
, vol.28
, pp. 300-301
-
-
O'Brien, C.F.1
Miller, C.2
Goldblatt, D.3
Welle, S.4
Forbes, G.5
Lipinski, B.6
Panzik, J.7
Peck, R.8
Plumb, S.9
Oakes, D.10
Kurlan, R.11
Shoulson, I.12
-
56
-
-
0031469707
-
Ectopically expressed CAG repeats cause intranuclear inclusions and a progressive late onset neurological phenotype in the mouse
-
Ordway J. M., Tallaksen-Greene S., Gutekunst C-A., Bernstein E. M., Cearley J. A., Wiener H. W., Dure L. S., Lindsey R., Hersch S. M., Jope R. S., Albin R. L., and Detloff P. J. (1997) Ectopically expressed CAG repeats cause intranuclear inclusions and a progressive late onset neurological phenotype in the mouse. Cell 91, 753-763.
-
(1997)
Cell
, vol.91
, pp. 753-763
-
-
Ordway, J.M.1
Tallaksen-Greene, S.2
Gutekunst, C.-A.3
Bernstein, E.M.4
Cearley, J.A.5
Wiener, H.W.6
Dure, L.S.7
Lindsey, R.8
Hersch, S.M.9
Jope, R.S.10
Albin, R.L.11
Detloff, P.J.12
-
57
-
-
0018622817
-
Synthesis of N-acetyl-L-aspartate by rat brain mitochondria and its involvement in mitochondrial/cytosolic carbon transport
-
Patel T. B. and Clark J. B. (1979) Synthesis of N-acetyl-L-aspartate by rat brain mitochondria and its involvement in mitochondrial/cytosolic carbon transport. Biochem. J. 184, 539-546.
-
(1979)
Biochem. J.
, vol.184
, pp. 539-546
-
-
Patel, T.B.1
Clark, J.B.2
-
58
-
-
0031731776
-
Evidence supporting the existence of an activity-dependent astrocyte-neuron lactate shuttle
-
Pellerin L., Pellegri G., Bittar P. G., Charnay Y., Bouras C., Martin J. L., Stella N., and Magistretti P. J. (1998) Evidence supporting the existence of an activity-dependent astrocyte-neuron lactate shuttle. Dev. Neurosci. 20, 291-299.
-
(1998)
Dev. Neurosci.
, vol.20
, pp. 291-299
-
-
Pellerin, L.1
Pellegri, G.2
Bittar, P.G.3
Charnay, Y.4
Bouras, C.5
Martin, J.L.6
Stella, N.7
Magistretti, P.J.8
-
59
-
-
0017369458
-
Abnormal glucose tolerance and arginine tolerance tests in Huntington's disease
-
Podolsky S. and Leopold N. A. (1977) Abnormal glucose tolerance and arginine tolerance tests in Huntington's disease. Gerontology 23, 55-63.
-
(1977)
Gerontology
, vol.23
, pp. 55-63
-
-
Podolsky, S.1
Leopold, N.A.2
-
60
-
-
0015521813
-
Increased frequency of diabetes mellitus in patients with Huntington's chorea
-
Podolsky S., Leopold N. A., and Sax D. S. (1972) Increased frequency of diabetes mellitus in patients with Huntington's chorea. Lancet 1, 1356-1358.
-
(1972)
Lancet
, vol.1
, pp. 1356-1358
-
-
Podolsky, S.1
Leopold, N.A.2
Sax, D.S.3
-
61
-
-
0032491494
-
Genetic neurodegenerative diseases: The human illness and transgenic models
-
Price D. L., Sisodia S. S., and Borchelt D. R. (1998) Genetic neurodegenerative diseases: the human illness and transgenic models. Science 282, 1079-1083.
-
(1998)
Science
, vol.282
, pp. 1079-1083
-
-
Price, D.L.1
Sisodia, S.S.2
Borchelt, D.R.3
-
62
-
-
0033066942
-
Brain neurotransmitter deficits in mice transgenic for the Huntington's disease mutation
-
Reynolds G. P., Dalton C. F., Tillery C. L., Mangiarini L., Davies S. W., and Bates G. P. (1999) Brain neurotransmitter deficits in mice transgenic for the Huntington's disease mutation. J. Neurochem. 72, 1773-1776.
-
(1999)
J. Neurochem.
, vol.72
, pp. 1773-1776
-
-
Reynolds, G.P.1
Dalton, C.F.2
Tillery, C.L.3
Mangiarini, L.4
Davies, S.W.5
Bates, G.P.6
-
63
-
-
0021775960
-
Pharmacological evidence for taurine as an inhibitory neurotransmitter in the cerebellum
-
Sakai Y., Okamoto K., and Kimura H. (1985) Pharmacological evidence for taurine as an inhibitory neurotransmitter in the cerebellum. Prog. Clin. Biol. Res. 179, 313-319.
-
(1985)
Prog. Clin. Biol. Res.
, vol.179
, pp. 313-319
-
-
Sakai, Y.1
Okamoto, K.2
Kimura, H.3
-
64
-
-
0032475931
-
Huntingtin acts in the nucleus to induce apoptosis but death does not correlate with the formation of intranuclear inclusions
-
Saudou F., Finkbeiner S., Devys D., and Greenberg M. E. (1998) Huntingtin acts in the nucleus to induce apoptosis but death does not correlate with the formation of intranuclear inclusions. Cell 95, 55-66.
-
(1998)
Cell
, vol.95
, pp. 55-66
-
-
Saudou, F.1
Finkbeiner, S.2
Devys, D.3
Greenberg, M.E.4
-
65
-
-
0031982340
-
Alzheimer disease: Quantitative H-1 MR spectroscopic imaging of frontoparietal brain
-
Schuff N., Amend D. L., Meyerhoff D. J., Tanabe J. L., Norman D., Fein G., and Weiner M. W. (1998) Alzheimer disease: quantitative H-1 MR spectroscopic imaging of frontoparietal brain. Radiology 207, 91-102.
-
(1998)
Radiology
, vol.207
, pp. 91-102
-
-
Schuff, N.1
Amend, D.L.2
Meyerhoff, D.J.3
Tanabe, J.L.4
Norman, D.5
Fein, G.6
Weiner, M.W.7
-
66
-
-
0027408521
-
Proton magnetic resonance spectroscopy with dementia
-
Shiino A., Matsuda M., Morikawa S., Inubushi T., Akiguchi I., and Handa J. (1993) Proton magnetic resonance spectroscopy with dementia. Surg. Neurol. 39, 143-147.
-
(1993)
Surg. Neurol.
, vol.39
, pp. 143-147
-
-
Shiino, A.1
Matsuda, M.2
Morikawa, S.3
Inubushi, T.4
Akiguchi, I.5
Handa, J.6
-
67
-
-
0028932753
-
Probable Alzheimer disease: Diagnosis with proton MR spectroscopy
-
Shonk T. K., Moats R. A., Gifford P., Michaelis T., Mandigo J. C., Izumi J., and Ross B. D. (1995) Probable Alzheimer disease: diagnosis with proton MR spectroscopy. Radiology 195, 65-72.
-
(1995)
Radiology
, vol.195
, pp. 65-72
-
-
Shonk, T.K.1
Moats, R.A.2
Gifford, P.3
Michaelis, T.4
Mandigo, J.C.5
Izumi, J.6
Ross, B.D.7
-
68
-
-
0031914762
-
Stoichiometric coupling of brain glucose metabolism and glutamatergic neuronal activity
-
Sibson N. R., Dhankhar A., Mason G. F., Rothman D. L., Behar K. L., and Shulman R. G. (1998) Stoichiometric coupling of brain glucose metabolism and glutamatergic neuronal activity. Proc. Natl. Acad. Sci. USA 95, 316-321.
-
(1998)
Proc. Natl. Acad. Sci. USA
, vol.95
, pp. 316-321
-
-
Sibson, N.R.1
Dhankhar, A.2
Mason, G.F.3
Rothman, D.L.4
Behar, K.L.5
Shulman, R.G.6
-
69
-
-
0022920117
-
Classification of inhibitory amino acid receptors in the mammalian nervous system
-
Simmonds M. A. (1986) Classification of inhibitory amino acid receptors in the mammalian nervous system. Med. Biol. 64, 301-311.
-
(1986)
Med. Biol.
, vol.64
, pp. 301-311
-
-
Simmonds, M.A.1
-
70
-
-
0026000851
-
Immunocytochemical localization of N-acetyl-aspartate with monoclonal antibodies
-
Simmons M., Frandoza C., and Coyle J. (1991) Immunocytochemical localization of N-acetyl-aspartate with monoclonal antibodies. Neuroscience 45, 37-45.
-
(1991)
Neuroscience
, vol.45
, pp. 37-45
-
-
Simmons, M.1
Frandoza, C.2
Coyle, J.3
-
71
-
-
0001876029
-
Computer simulations in magnetic resonance. An object oriented programming approach
-
Smith S. A., Levante T. O., Meier B. H., and Ernst R. R. (1994) Computer simulations in magnetic resonance. An object oriented programming approach. J. Magn. Reson. 106, 75-105.
-
(1994)
J. Magn. Reson.
, vol.106
, pp. 75-105
-
-
Smith, S.A.1
Levante, T.O.2
Meier, B.H.3
Ernst, R.R.4
-
73
-
-
0001980452
-
Mitochondrial biochemical features of the R6/2 transgenic mice model of Huntington's disease
-
Tabrizi S. J., Mangiarini L., Workman J., Mahal A., Bates G., Cooper J. M., and Schapira A. H. V. (1998) Mitochondrial biochemical features of the R6/2 transgenic mice model of Huntington's disease. Mov. Disord. 13, 153.
-
(1998)
Mov. Disord.
, vol.13
, pp. 153
-
-
Tabrizi, S.J.1
Mangiarini, L.2
Workman, J.3
Mahal, A.4
Bates, G.5
Cooper, J.M.6
Schapira, A.H.V.7
-
74
-
-
0022196667
-
N-acetylation of L-aspartate in the nervous system: Differential distribution of a specific enzyme
-
Truckenmiller M. E., Namboodiri M. A. A., Brownstein M. J., and Neale J. H. (1985) N-Acetylation of L-aspartate in the nervous system: differential distribution of a specific enzyme. J. Neurochem. 45, 1658-1662.
-
(1985)
J. Neurochem.
, vol.45
, pp. 1658-1662
-
-
Truckenmiller, M.E.1
Namboodiri, M.A.A.2
Brownstein, M.J.3
Neale, J.H.4
-
75
-
-
0027450301
-
Proton nuclear magnetic resonance spectroscopy unambiguously identifies different neural cell types
-
Urenjak J., Williams S. R., Gadian D. G., and Noble M. (1993) Proton nuclear magnetic resonance spectroscopy unambiguously identifies different neural cell types. J. Neurosci. 13, 981-989.
-
(1993)
J. Neurosci.
, vol.13
, pp. 981-989
-
-
Urenjak, J.1
Williams, S.R.2
Gadian, D.G.3
Noble, M.4
-
76
-
-
0031785348
-
Glutamine, exercise and immune function. Links and possible mechanisms
-
Walsh N. P., Blannin A. K., Robson P. J., and Gleeson M. (1998) Glutamine, exercise and immune function. Links and possible mechanisms. Sports Med. 26, 177-191.
-
(1998)
Sports Med.
, vol.26
, pp. 177-191
-
-
Walsh, N.P.1
Blannin, A.K.2
Robson, P.J.3
Gleeson, M.4
-
77
-
-
0023113123
-
The regulation of glutamine and ketone-body metabolism in the small intestine of the long-term (40-day) streptozotocin-diabetic rat
-
Watford M., Erbelding E. J., and Smith E. M. (1987) The regulation of glutamine and ketone-body metabolism in the small intestine of the long-term (40-day) streptozotocin-diabetic rat. Biochem. J. 242, 61-68.
-
(1987)
Biochem. J.
, vol.242
, pp. 61-68
-
-
Watford, M.1
Erbelding, E.J.2
Smith, E.M.3
-
78
-
-
0014118812
-
Concentrations of free glucogenic amino acids in livers of rats subjected to various metabolic stresses
-
Williamson D. H., Lopes-Vieira O., and Walker B. (1967) Concentrations of free glucogenic amino acids in livers of rats subjected to various metabolic stresses. Biochem. J. 104, 497-502.
-
(1967)
Biochem. J.
, vol.104
, pp. 497-502
-
-
Williamson, D.H.1
Lopes-Vieira, O.2
Walker, B.3
-
79
-
-
0022553413
-
PET scan investigations of Huntington's disease: Cerebral metabolic correlates of neurological features and functional decline
-
Young A. B., Penney J. B., Starosta-Rubinstein S., Markel D. S., Berent S., Giordani B., Ehrenkaufer R., Jewett D., and Hichwa R. (1986) PET scan investigations of Huntington's disease: cerebral metabolic correlates of neurological features and functional decline. Ann. Neurol. 20, 296-303.
-
(1986)
Ann. Neurol.
, vol.20
, pp. 296-303
-
-
Young, A.B.1
Penney, J.B.2
Starosta-Rubinstein, S.3
Markel, D.S.4
Berent, S.5
Giordani, B.6
Ehrenkaufer, R.7
Jewett, D.8
Hichwa, R.9
-
80
-
-
0027080877
-
Nitrogen metabolism: Neuronal-astroglial relationships
-
Yudkoff M., Nissim I., Hertz L., Pleasure D., and Erecińska M. (1992) Nitrogen metabolism: neuronal-astroglial relationships. Prog. Brain Res. 94, 213-224.
-
(1992)
Prog. Brain Res.
, vol.94
, pp. 213-224
-
-
Yudkoff, M.1
Nissim, I.2
Hertz, L.3
Pleasure, D.4
Erecińska, M.5
-
81
-
-
0027760001
-
Brain glutamate metabolism: Neuronal-astroglial relationships
-
Yudkoff M., Nissim I., Daikhin Y., Lin Z. P., Nelson D., Pleasure D., and Erecińska M. (1993) Brain glutamate metabolism: neuronal-astroglial relationships. Dev. Neurosci. 15, 343-350.
-
(1993)
Dev. Neurosci.
, vol.15
, pp. 343-350
-
-
Yudkoff, M.1
Nissim, I.2
Daikhin, Y.3
Lin, Z.P.4
Nelson, D.5
Pleasure, D.6
Erecińska, M.7
-
82
-
-
0021366190
-
Glutamine: A major energy source for cultured mammalian cells
-
Zielke H. R., Zielke C. L., and Ozand P. T. (1984) Glutamine: a major energy source for cultured mammalian cells. Fed. Proc. 43, 121-125.
-
(1984)
Fed. Proc.
, vol.43
, pp. 121-125
-
-
Zielke, H.R.1
Zielke, C.L.2
Ozand, P.T.3
|