Recent insights into the molecular pathogenesis of Huntington disease

Seminars in Neurology

Volumn 19, Issue 4, 1999, Pages 385-395

  Leavitt, Blair R ^a   Wellington, Cheryl L ^a   Hayden, Michael R ^a  

^a Centre for Molecular Medicine and Therapeutics   (Canada)

Author keywords

Apoptosis; Caspase; Genetic instability; Huntington disease; Neurodegeneration; Polyglutamine repeats; Yeast artificial chromosomes

Indexed keywords

CASPASE; CYSTEINE PROTEINASE; GENE PRODUCT; HUNTINGTIN; MUTANT PROTEIN; POLYGLUTAMINE; TRINUCLEOTIDE;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; APOPTOSIS; CONTROLLED STUDY; ENZYME DEGRADATION; GENE MUTATION; HUMAN; HUMAN CELL; HUNTINGTON CHOREA; MOUSE; NERVE DEGENERATION; NEUROPATHOLOGY; NONHUMAN; ONSET AGE; PHENOTYPE; PRIORITY JOURNAL; REVIEW; TRANSGENIC MOUSE; TRINUCLEOTIDE REPEAT; YEAST ARTIFICIAL CHROMOSOME;

EID: 0033380140     PISSN: 02718235     EISSN: None     Source Type: Journal    
DOI: 10.1055/s-2008-1040853     Document Type: Review

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