-
1
-
-
0025770657
-
Early bacteriologic, immunologic, and clinical courses of young infants with cystic fibrosis identified by neonatal screening
-
ABMAN, S. H., J. W. OGLE, R. J. HARBECK, N. BUTLER-SIMON, K. B. HAMMOND, AND F. J. ACCURSO. Early bacteriologic, immunologic, and clinical courses of young infants with cystic fibrosis identified by neonatal screening. J. Pediatr. 119: 211-217, 1991.
-
(1991)
J. Pediatr.
, vol.119
, pp. 211-217
-
-
Abman, S.H.1
Ogle, J.W.2
Harbeck, R.J.3
Butler-Simon, N.4
Hammond, K.B.5
Accurso, F.J.6
-
2
-
-
0020609685
-
Adherence of Streptococcus pyogenes, Eschericia coli, and Pseudomonas aeruginosa to fibronectin-coated and uncoated epithelial cells
-
ABRAHAM, S. N., E. H. BEACHEY, AND W. A. SIMPSON. Adherence of Streptococcus pyogenes, Eschericia coli, and Pseudomonas aeruginosa to fibronectin-coated and uncoated epithelial cells. Infect. Immun. 41: 1261-1268, 1983.
-
(1983)
Infect. Immun.
, vol.41
, pp. 1261-1268
-
-
Abraham, S.N.1
Beachey, E.H.2
Simpson, W.A.3
-
3
-
-
0001668367
-
Immotile-cilia syndrome (primary ciliary dyskinesia), including Kartagener's syndrome
-
edited by C. R. Scriver, J. B. Stanbury, J. B. Wyngaarden, and D. S. Frederickson. New York: McGraw-Hill
-
AFZELIUS, B. A., AND B. MOSSBERG. Immotile-cilia syndrome (primary ciliary dyskinesia), including Kartagener's syndrome. In: Metabolic Basis of Inherited Disease, edited by C. R. Scriver, J. B. Stanbury, J. B. Wyngaarden, and D. S. Frederickson. New York: McGraw-Hill, 1995, p. 3943-3954.
-
(1995)
Metabolic Basis of Inherited Disease
, pp. 3943-3954
-
-
Afzelius, B.A.1
Mossberg, B.2
-
4
-
-
0031445462
-
Molecular physiology of water transport: Aquaporin nomenclature workshop. Mammalian aquaporins
-
AGRE, P. Molecular physiology of water transport: aquaporin nomenclature workshop. Mammalian aquaporins. Biol. Cell 89: 255-257, 1997.
-
(1997)
Biol. Cell
, vol.89
, pp. 255-257
-
-
Agre, P.1
-
5
-
-
0026602608
-
Recombinant human DNase inhalation in normal subjects and patients with cystic fibrosis. A phase 1 study
-
AITKEN, M. L., W. BURKE, G. McDONALD, S. SHAK, A. B. MONTGOMERY, AND A SMITH. Recombinant human DNase inhalation in normal subjects and patients with cystic fibrosis. A phase 1 study. JAMA 267: 1947-1951, 1992.
-
(1992)
JAMA
, vol.267
, pp. 1947-1951
-
-
Aitken, M.L.1
Burke, W.2
McDonald, G.3
Shak, S.4
Montgomery, A.B.5
Smith, A.6
-
6
-
-
8244219690
-
Pseudohypoaldosteronism and cholelithiasis: Coincidence or pathogenetic correlation
-
AKKURT, I., U. KUHNLE, AND C. RINGENBERG. Pseudohypoaldosteronism and cholelithiasis: coincidence or pathogenetic correlation. Eur. J. Pediatr. 156: 363-366, 1997.
-
(1997)
Eur. J. Pediatr.
, vol.156
, pp. 363-366
-
-
Akkurt, I.1
Kuhnle, U.2
Ringenberg, C.3
-
7
-
-
0016806225
-
Epithelial surfaces of the trachea and principal bronchi in the rat
-
ALEXANDER, I., B. C. RITCHIE, J. E. MALONEY, AND C. R. HUNTER. Epithelial surfaces of the trachea and principal bronchi in the rat. Thorax 30: 171-177, 1975.
-
(1975)
Thorax
, vol.30
, pp. 171-177
-
-
Alexander, I.1
Ritchie, B.C.2
Maloney, J.E.3
Hunter, C.R.4
-
8
-
-
0000031146
-
Influence of surfactant on mucociliary transport
-
ALLEGRA, L., R. BOSSI, AND P. C. BRAGA. Influence of surfactant on mucociliary transport. Prog. Respir. Dis. 19: 441-460, 1985.
-
(1985)
Prog. Respir. Dis.
, vol.19
, pp. 441-460
-
-
Allegra, L.1
Bossi, R.2
Braga, P.C.3
-
9
-
-
0028902685
-
A unique subset of rat and human intestinal villus cells express the cystic fibrosis transmembrane conductance regulator
-
AMEEN, N. A., T. ARDITO, M. KASHGARIAN, AND C. R. MARINO. A unique subset of rat and human intestinal villus cells express the cystic fibrosis transmembrane conductance regulator. Gastroenterology 108: 1016-1023, 1995.
-
(1995)
Gastroenterology
, vol.108
, pp. 1016-1023
-
-
Ameen, N.A.1
Ardito, T.2
Kashgarian, M.3
Marino, C.R.4
-
10
-
-
0026651508
-
Cl channels in the apical membrane of normal and cystic fibrosis airway and intestinal epithelia
-
ANDERSON, M. P., D. N. SHEPPARD, H. A. BERGER, AND M. J. WELSH. Cl channels in the apical membrane of normal and cystic fibrosis airway and intestinal epithelia. Am. J. Physiol. 263 (Lung Cell. Mol. Physiol. 7): L1-L14, 1992.
-
(1992)
Am. J. Physiol. 263 (Lung Cell. Mol. Physiol. 7)
, vol.263
-
-
Anderson, M.P.1
Sheppard, D.N.2
Berger, H.A.3
Welsh, M.J.4
-
11
-
-
0031040853
-
Genotype-phenotype relationship in 12 patients carrying cystic fibrosis mutation R334W
-
ANTINOLO, G., S. BORREGO, M. GILI, J. DAPENA, I. ALFAGEME, AND F. REINA. Genotype-phenotype relationship in 12 patients carrying cystic fibrosis mutation R334W. J. Med. Genet. 34: 89-91, 1997.
-
(1997)
J. Med. Genet.
, vol.34
, pp. 89-91
-
-
Antinolo, G.1
Borrego, S.2
Gili, M.3
Dapena, J.4
Alfageme, I.5
Reina, F.6
-
12
-
-
0029010510
-
Lower respiratory infection and inflammation in infants with newly diagnosed cystic fibrosis
-
ARMSTRONG, D. S., K. GRIMWOOD, R. CARZINO, J. B. CARLIN, A. OLlNSKY, AND P. D. PHELAN. Lower respiratory infection and inflammation in infants with newly diagnosed cystic fibrosis. Br. Med. J. 310: 1571-1572, 1995.
-
(1995)
Br. Med. J.
, vol.310
, pp. 1571-1572
-
-
Armstrong, D.S.1
Grimwood, K.2
Carzino, R.3
Carlin, J.B.4
Ollnsky, A.5
Phelan, P.D.6
-
13
-
-
0030768159
-
Lower airway inflammation in infants and young children with cystic fibrosis
-
ARMSTRONG, D. S., K. GRIMWOOD, J. B. CARLIN, R. CARZINO, J. P. GUTIERREZ, J. HULL, A. OLINSKY, E. M. PHELAN, C. F. ROBERTSON, AND P. D. PHELAN. Lower airway inflammation in infants and young children with cystic fibrosis. Am. J. Respir. Crit. Care Med. 156: 1197-204, 1997.
-
(1997)
Am. J. Respir. Crit. Care Med.
, vol.156
, pp. 1197-1204
-
-
Armstrong, D.S.1
Grimwood, K.2
Carlin, J.B.3
Carzino, R.4
Gutierrez, J.P.5
Hull, J.6
Olinsky, A.7
Phelan, E.M.8
Robertson, C.F.9
Phelan, P.D.10
-
14
-
-
0014846907
-
Mucociliary clearance rates at various levels in dog lungs
-
ASMUNDSSON, T., AND K. H. KILBURN. Mucociliary clearance rates at various levels in dog lungs. Am. Rev. Respir. Dis. 102: 388-398, 1970.
-
(1970)
Am. Rev. Respir. Dis.
, vol.102
, pp. 388-398
-
-
Asmundsson, T.1
Kilburn, K.H.2
-
15
-
-
0023239485
-
Relations among alveolar surface tension, surface area, volume, and recoil pressure
-
BACHOFEN, H., S. SCHUERCH, M. URBINELLI, AND E. R. WEIBEL. Relations among alveolar surface tension, surface area, volume, and recoil pressure. J. Appl. Physiol. 62: 1878-1887, 1987.
-
(1987)
J. Appl. Physiol.
, vol.62
, pp. 1878-1887
-
-
Bachofen, H.1
Schuerch, S.2
Urbinelli, M.3
Weibel, E.R.4
-
16
-
-
0025604331
-
Protein kinase A regulates Cl conductance in endocytic vesicles from the proximal tubule
-
BAE, H.-R., AND A. S. VERKMAN. Protein kinase A regulates Cl conductance in endocytic vesicles from the proximal tubule. Nature 348: 637-639, 1990.
-
(1990)
Nature
, vol.348
, pp. 637-639
-
-
Bae, H.-R.1
Verkman, A.S.2
-
17
-
-
0028958573
-
Cl secretion across distal airway epithelium: Relationship to submucosal gland distribution
-
BALLARD, S. T., J. D. FOUNTAIN, S. K. INGLIS, M. R. CORBOZ, AND A. E. TAYLOR. Cl secretion across distal airway epithelium: relationship to submucosal gland distribution. Am. J. Physiol. 268 (Lung Cell. Mol. Physiol. 12): L526-L531, 1995.
-
(1995)
Am. J. Physiol. 268 (Lung Cell. Mol. Physiol. 12)
, vol.268
-
-
S, T.1
Fountain, J.D.2
Inglis, S.K.3
Corboz, M.R.4
Taylor, A.E.5
-
18
-
-
0024835905
-
Immunohistopathologic localization of Pseudomonas aentginosa in lungs from patients with cystic fibrosis. Implications for the pathogenesis of progressive lung deterioration
-
BALTIMORE, R. S., C. D. CHRISTIE, AND G. J. SMITH. Immunohistopathologic localization of Pseudomonas aentginosa in lungs from patients with cystic fibrosis. Implications for the pathogenesis of progressive lung deterioration. Am. Rev. Respir. Dis. 140: 1650-1661, 1989.
-
(1989)
Am. Rev. Respir. Dis.
, vol.140
, pp. 1650-1661
-
-
Baltimore, R.S.1
Christie, C.D.2
Smith, G.J.3
-
19
-
-
0027763241
-
Defective acidification of the biosynthetic pathway in cystic fibrosis
-
BARASCH, J., AND Q. AL-AWQATI. Defective acidification of the biosynthetic pathway in cystic fibrosis. J. Cell Sci. 17, Suppl.: 229-233, 1993.
-
(1993)
J. Cell Sci.
, vol.17
, Issue.SUPPL.
, pp. 229-233
-
-
Barasch, J.1
Al-Awqati, Q.2
-
20
-
-
0025784535
-
Defective acidification of intracellular organelles in cystic fibrosis
-
BARASCH, J., B. KISS, A. PRINCE, L. SAIMAN, D. GRUENERT, AND Q. AL-AWQATI. Defective acidification of intracellular organelles in cystic fibrosis. Nature 352: 70-73, 1991.
-
(1991)
Nature
, vol.352
, pp. 70-73
-
-
Barasch, J.1
Kiss, B.2
Prince, A.3
Saiman, L.4
Gruenert, D.5
Al-Awqati, Q.6
-
22
-
-
0344436345
-
The lung in cystic fibrosis
-
BEDROSSIAN, C. W. M., S. D. GREENBERG, D. B. SINGER, J. J. HANSEN, AND H. S. ROSENBERG. The lung in cystic fibrosis. Hum. Pathol. 7: 196-220, 1976.
-
(1976)
Hum. Pathol.
, vol.7
, pp. 196-220
-
-
Bedrossian, C.W.M.1
Greenberg, S.D.2
Singer, D.B.3
Hansen, J.J.4
Rosenberg, H.S.5
-
23
-
-
0029887172
-
Effect of uridine 5'-triphosphate plus amiloride on mucociliary clearance in adult cystic fibrosis
-
BENNETT, W. D., K. N. OLIVIER, K. L. ZEMAN, K. W. HOHNEKER, R. C. BOUCHER, AND M. R. KNOWLES. Effect of uridine 5'-triphosphate plus amiloride on mucociliary clearance in adult cystic fibrosis. Am. J. Respir Crit. Care Med. 153: 1796-1801, 1996.
-
(1996)
Am. J. Respir Crit. Care Med.
, vol.153
, pp. 1796-1801
-
-
Bennett, W.D.1
Olivier, K.N.2
Zeman, K.L.3
Hohneker, K.W.4
Boucher, R.C.5
Knowles, M.R.6
-
24
-
-
0024459145
-
Complement receptor expression on neutrophils at an inflammatory site, the Pseudomonas-infected lung in cystic fibrosis
-
BERGER, J., R. U. SORENSEN, M. F. TOSI, D. G. DEARBORN, AND G. DORING. Complement receptor expression on neutrophils at an inflammatory site, the Pseudomonas-infected lung in cystic fibrosis. J. Clin. Invest. 84: 1302-1313, 1989.
-
(1989)
J. Clin. Invest.
, vol.84
, pp. 1302-1313
-
-
Berger, J.1
Sorensen, R.U.2
Tosi, M.F.3
Dearborn, D.G.4
Doring, G.5
-
26
-
-
0028045712
-
Functional CFTR in endosomal compartment of CFTR expressing fibroblasts and T84 crlls
-
BIWERSI, J., AND A. S. VERKMAN. Functional CFTR in endosomal compartment of CFTR expressing fibroblasts and T84 crlls. Am. J. Physiol 266 (Cell Physiol. 35): C149-C156, 1994.
-
(1994)
Am. J. Physiol 266 (Cell Physiol. 35)
, vol.266
-
-
Biwersi, J.1
Verkman, A.S.2
-
28
-
-
0026578165
-
Developmental changes in lung epithelial ion transport and liquid movement
-
BLAND, R. D., AND D. W. NIELSON. Developmental changes in lung epithelial ion transport and liquid movement. Annu. Rev. Physiol. 54: 373-394, 1992.
-
(1992)
Annu. Rev. Physiol.
, vol.54
, pp. 373-394
-
-
Bland, R.D.1
Nielson, D.W.2
-
29
-
-
0344868183
-
Chemical composition of human tracheobronchial secretions
-
edited by M. J. Dulfano. Springfield, IL: Thomas
-
BOAT, T. F., AND L. W. MATTHEWS. Chemical composition of human tracheobronchial secretions. In: Sputum: Fundamentals and Clinical Pathology, edited by M. J. Dulfano. Springfield, IL: Thomas, 1973, p. 243-274.
-
(1973)
Sputum: Fundamentals and Clinical Pathology
, pp. 243-274
-
-
Boat, T.F.1
Matthews, L.W.2
-
30
-
-
0029372481
-
Normal bronchial epithelial cells constitutively produce the anti-inflammatory cytokine interleukin-10, which is downregulated in cystic fibrosis
-
BONFIELD, T. L., M. W. KONSTAN, P. BURFEIND, J. R. PANUSKA, J. B. HILLIARD, AND M. BERGER. Normal bronchial epithelial cells constitutively produce the anti-inflammatory cytokine interleukin-10, which is downregulated in cystic fibrosis. Am. J. Respir. Cell Mol. Biol. 13: 257-261, 1995.
-
(1995)
Am. J. Respir. Cell Mol. Biol.
, vol.13
, pp. 257-261
-
-
Bonfield, T.L.1
Konstan, M.W.2
Burfeind, P.3
Panuska, J.R.4
Hilliard, J.B.5
Berger, M.6
-
31
-
-
0028784322
-
Inflammatory cyokines in cystic fibrosis lungs
-
BONFIELD, T. L., J. R. PANUSKA, M. W. KONSTAN, K. A. HILLIARD, J. B. HILLIARD, H. GHNAIM, AND M. BERGER. Inflammatory cyokines in cystic fibrosis lungs. Am. J. Respir. Crit. Care Med. 152: 2111-2118, 1995.
-
(1995)
Am. J. Respir. Crit. Care Med.
, vol.152
, pp. 2111-2118
-
-
Bonfield, T.L.1
Panuska, J.R.2
Konstan, M.W.3
Hilliard, K.A.4
Hilliard, J.B.5
Ghnaim, H.6
Berger, M.7
-
34
-
-
0024465128
-
Cl secretory response of cystic fibrosis human airway epithelia: Preservation of calcium but not protein kinase C-and A-dependent mechanisms
-
BOUCHER, R. C., E. H. C. CHENG, A. M. PARADISO, M. J. STUTTS, M. R. KNOWLES, AND H. S. EARP. Cl secretory response of cystic fibrosis human airway epithelia: preservation of calcium but not protein kinase C-and A-dependent mechanisms. J. Clin. Invest. 84: 1424-1431, 1989.
-
(1989)
J. Clin. Invest.
, vol.84
, pp. 1424-1431
-
-
Boucher, R.C.1
Cheng, E.H.C.2
Paradiso, A.M.3
Stutts, M.J.4
Knowles, M.R.5
Earp, H.S.6
-
35
-
-
0022973473
-
+ transport in cystic fibrosis respiratory epithelia. Abnormal basal rate and response to adenylate cyclase activation
-
+ transport in cystic fibrosis respiratory epithelia. Abnormal basal rate and response to adenylate cyclase activation. J. Clin. Invest. 78: 1245-1252, 1986.
-
(1986)
J. Clin. Invest.
, vol.78
, pp. 1245-1252
-
-
Boucher, R.C.1
Stutts, M.J.2
Knowles, M.R.3
Cantley, L.4
Gatzy, J.T.5
-
37
-
-
0028322331
-
Biochemical and biophysical identification of cystic fibrosis transmembrane conductance Cl channels as components of endocytic clathrin coated vesicles
-
BRADBURY, N. A., J. A. COHN, C. J. VENGLARIK, AND R. J. BRIDGES. Biochemical and biophysical identification of cystic fibrosis transmembrane conductance Cl channels as components of endocytic clathrin coated vesicles. J. Biol. Chem, 269: 8296-8302, 1994.
-
(1994)
J. Biol. Chem
, vol.269
, pp. 8296-8302
-
-
Bradbury, N.A.1
Cohn, J.A.2
Venglarik, C.J.3
Bridges, R.J.4
-
38
-
-
0026581842
-
Regulation of plasma membrane recycling by CFTR
-
BRADBURY, N. A., T. JILLING, G. BERTA, E. J. SORSCHER, R. J. BRIDGES, AND K. L. KIRK. Regulation of plasma membrane recycling by CFTR. Science 256: 530-532, 1992.
-
(1992)
Science
, vol.256
, pp. 530-532
-
-
Bradbury, N.A.1
Jilling, T.2
Berta, G.3
Sorscher, E.J.4
Bridges, R.J.5
Kirk, K.L.6
-
40
-
-
0027997410
-
Role of free radicals in the pathogenesis of cystic fibrosis
-
BROWN, R. K., AND F. J. KELLY. Role of free radicals in the pathogenesis of cystic fibrosis. Thorax 49: 738-742, 1994.
-
(1994)
Thorax
, vol.49
, pp. 738-742
-
-
Brown, R.K.1
Kelly, F.J.2
-
43
-
-
0026632470
-
Production of the Pseudomonas aeruginosa neuraminidase in increased under hyperosmolar conditions and is regulated by genes involved in alginate expression
-
CACALANO, G., M. KAZYS, L. SAIMAN, AND A. PRINCE. Production of the Pseudomonas aeruginosa neuraminidase in increased under hyperosmolar conditions and is regulated by genes involved in alginate expression. J. Clin. Invest. 89: 1866-1874, 1992.
-
(1992)
J. Clin. Invest.
, vol.89
, pp. 1866-1874
-
-
Cacalano, G.1
Kazys, M.2
Saiman, L.3
Prince, A.4
-
44
-
-
0029286816
-
Cystic fibrosis lung inflammation: Early, sustained, and severe
-
CANTIN, A. Cystic fibrosis lung inflammation: early, sustained, and severe. Am. J. Respir. Crit. Care Med. 151: 939-940, 1995.
-
(1995)
Am. J. Respir. Crit. Care Med.
, vol.151
, pp. 939-940
-
-
Cantin, A.1
-
45
-
-
0023263523
-
Normal alveolar epithelial lining fluid contains high levels of glutathione
-
CANTIN, A. M., S. L. NORTH, R. C. HUBBARD, AND R. G. CRYSTAL. Normal alveolar epithelial lining fluid contains high levels of glutathione. J. Appl. Physiol. 63: 152-157, 1987.
-
(1987)
J. Appl. Physiol.
, vol.63
, pp. 152-157
-
-
Cantin, A.M.1
North, S.L.2
Hubbard, R.C.3
Crystal, R.G.4
-
46
-
-
0027670252
-
Altered carbohydrate composition of salivary mucins from patients with cystic fibrosis and the adhesion of Pseudomonas aeruginosa
-
CARNOY, C., R. RAMPHAL, A. SCHARFMAN, J. M. LO-GUIDICE, N. HOUDRET, A. KLEIN, C. GALABERT, G. LAMBLIN, AND P. ROUSSEL. Altered carbohydrate composition of salivary mucins from patients with cystic fibrosis and the adhesion of Pseudomonas aeruginosa. Am. J. Respir. Cell Mol. Biol. 9: 323-334, 1993.
-
(1993)
Am. J. Respir. Cell Mol. Biol.
, vol.9
, pp. 323-334
-
-
Carnoy, C.1
Ramphal, R.2
Scharfman, A.3
Lo-Guidice, J.M.4
Houdret, N.5
Klein, A.6
Galabert, C.7
Lamblin, G.8
Roussel, P.9
-
47
-
-
0025287964
-
Ultrastructure of airway epithelial cell membranes among patients with cystic fibrosis
-
CARSON, J. L., A. M. COLLIER, T. M. GAMBLING, M. R. KNOWLES, AND R. C. BOUCHER. Ultrastructure of airway epithelial cell membranes among patients with cystic fibrosis. Hum. Pathol. 21: 640-647, 1990.
-
(1990)
Hum. Pathol.
, vol.21
, pp. 640-647
-
-
Carson, J.L.1
Collier, A.M.2
Gambling, T.M.3
Knowles, M.R.4
Boucher, R.C.5
-
48
-
-
13344295074
-
Mutations in subunits of the epithelial Na channel cause salt wasting with hyperkalaemic acidosis, pseudohypoaldosteronism type 1
-
CHANG, S. S., S. GRUNDER, A. HANUKOGLU, A. ROSLER, P. M. MATHEW, I. HANUKOGLU, L. SCHILD, Y. LU, R. A. SHIMKETS, C. NELSON-WILLIAMS, B. C. ROSSIER, AND R. P. LIFTON. Mutations in subunits of the epithelial Na channel cause salt wasting with hyperkalaemic acidosis, pseudohypoaldosteronism type 1. Nature Genet, 12: 248-253, 1996.
-
(1996)
Nature Genet
, vol.12
, pp. 248-253
-
-
Chang, S.S.1
Grunder, S.2
Hanukoglu, A.3
Rosler, A.4
Mathew, P.M.5
Hanukoglu, I.6
Schild, L.7
Lu, Y.8
Shimkets, R.A.9
Nelson-Williams, C.10
Rossier, B.C.11
Lifton, R.P.12
-
49
-
-
0024345843
-
Increased sulfation of glycoconjugates by cultured nasal epithelial cells from patients with cystic fibrosis
-
CHENG, P. W., T. F. BOAT, K. CRANFILL, J. R. YANKASKAS, AND R. C. BOUCHER. Increased sulfation of glycoconjugates by cultured nasal epithelial cells from patients with cystic fibrosis. J. Clin. Invest. 84: 68-72, 1989.
-
(1989)
J. Clin. Invest.
, vol.84
, pp. 68-72
-
-
Cheng, P.W.1
Boat, T.F.2
Cranfill, K.3
Yankaskas, J.R.4
Boucher, R.C.5
-
50
-
-
0028944377
-
Functional activation of the cystic fibrosis trafficking mutant delta F508-CFTR by overexpression
-
CHENG, S. H., S. L. FANG, J. ZABNER J. MARSHALL, S. PIRAINO, S. C. SCHIAVI D. M. JEFFERSON, M. J. WELSH, AND A. E. SMITH. Functional activation of the cystic fibrosis trafficking mutant delta F508-CFTR by overexpression. Am. J. Physiol. 268 (Lung Cell. Mol. Physiol. 12): L615-L624, 1995.
-
(1995)
Am. J. Physiol. 268 (Lung Cell. Mol. Physiol. 12)
, vol.268
-
-
Cheng, S.H.1
Fang, S.L.2
Zabner, J.3
Marshall, J.4
Piraino, S.5
Schiavi, S.C.6
Jefferson, D.M.7
Welsh, M.J.8
Smith, A.E.9
-
51
-
-
0025242929
-
Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis
-
CHENG, S. H., R. J. GREGORY, J. MARSHALL, S. PAUL, D. W. SOUZA, G. A. WHITE, C. R. O'RIORDAN, AND A. E. SMITH. Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis. Cell 63: 827-834, 1990.
-
(1990)
Cell
, vol.63
, pp. 827-834
-
-
Cheng, S.H.1
Gregory, R.J.2
Marshall, J.3
Paul, S.4
Souza, D.W.5
White, G.A.6
O'Riordan, C.R.7
Smith, A.E.8
-
52
-
-
0029025333
-
Mutations in the cystic fibrosis gene in patients with congenital absence of the vas deferens
-
CHILLON, M., T. CASALS, B. MERCIER, L. BASSAS, W. LISSENS, S. SILBER, M. C. ROMEY, J. RUIZ ROMERO, C. VERLINGUE, AND M. CLAUSTRES. Mutations in the cystic fibrosis gene in patients with congenital absence of the vas deferens. N. Engl. J. Med. 332: 1475-1480, 1995.
-
(1995)
N. Engl. J. Med.
, vol.332
, pp. 1475-1480
-
-
Chillon, M.1
Casals, T.2
Mercier, B.3
Bassas, L.4
Lissens, W.5
Silber, S.6
Romey, M.C.7
Romero, J.R.8
Verlingue, C.9
Claustres, M.10
-
53
-
-
0019353003
-
Ultrastructural localization of endogenous peroxidase in the lower respiratory tract of the guinea pig
-
CHRISTENSEN, T. G., G. C. BLANCHARD, G. NOLLEY, AND J. A. HAYES. Ultrastructural localization of endogenous peroxidase in the lower respiratory tract of the guinea pig. Cell Tissue Res. 214: 407-415, 1981.
-
(1981)
Cell Tissue Res.
, vol.214
, pp. 407-415
-
-
Christensen, T.G.1
Blanchard, G.C.2
Nolley, G.3
Hayes, J.A.4
-
54
-
-
0020362785
-
Bronchial mucous glands in the newborn with cystic fibrosis
-
CHOW, C. W., L. I. LANDAU, AND L. M. TAUSSIG. Bronchial mucous glands in the newborn with cystic fibrosis. Eur. J. Pediatr. 139: 240-243, 1982.
-
(1982)
Eur. J. Pediatr.
, vol.139
, pp. 240-243
-
-
Chow, C.W.1
Landau, L.I.2
Taussig, L.M.3
-
55
-
-
0027502580
-
Genetic basis of variable exon 9 skipping in cystic fibrosis transmembrane conductance regulator mRNA
-
CHU, C. S., AND G. R. CUTTING. Genetic basis of variable exon 9 skipping in cystic fibrosis transmembrane conductance regulator mRNA. Nature Genet. 3: 151-156, 1993.
-
(1993)
Nature Genet.
, vol.3
, pp. 151-156
-
-
Chu, C.S.1
Cutting, G.R.2
-
56
-
-
0026603095
-
Effects of bradykinin on Na and Cl transport in human nasal epithelium
-
CLARKE, L. L., A. M. PARADISO, S. J. MASON, AND R. C. BOUCHER. Effects of bradykinin on Na and Cl transport in human nasal epithelium. Am. J. Physiol. 262 (Cell Physiol. 31): C644-C655, 1992.
-
(1992)
Am. J. Physiol. 262 (Cell Physiol. 31)
, vol.262
-
-
Clarke, L.L.1
Paradiso, A.M.2
Mason, S.J.3
Boucher, R.C.4
-
57
-
-
0030934353
-
Ciliary beat frequency in human bronchi and bronchioles
-
CLARY-MEINESZ, C., J. MOUROUX, P. HUITOREL, J. COSSON, D. SCHOEVAERT, AND B. BLAIVE. Ciliary beat frequency in human bronchi and bronchioles. Chest 111: 692-697, 1997.
-
(1997)
Chest
, vol.111
, pp. 692-697
-
-
Clary-Meinesz, C.1
Mouroux, J.2
Huitorel, P.3
Cosson, J.4
Schoevaert, D.5
Blaive, B.6
-
59
-
-
0021731128
-
Airway mucus: Composition and regulation of its secretion by neuropeptides in vitro
-
edited by J. Nugent and M. O'Connor. London: Pitman, (Ciba Found. Symp. 109)
-
COLES, S. J., K. R. BHASKAR, D. D. O'SULLIVAN, K. H. NEILL, AND L. M. REID. Airway mucus: composition and regulation of its secretion by neuropeptides in vitro. In: Mucus and Mucosa, edited by J. Nugent and M. O'Connor. London: Pitman, 1984, p. 40-60. (Ciba Found. Symp. 109)
-
(1984)
Mucus and Mucosa
, pp. 40-60
-
-
Coles, S.J.1
Bhaskar, K.R.2
O'Sullivan, D.D.3
Neill, K.H.4
Reid, L.M.5
-
60
-
-
0031471090
-
Longitudinal analysis of pulmonary function decline in patients with cystic fibrosis
-
COREY, M., L. EDWARDS, H. LEVISON, AND M. KNOWLES. Longitudinal analysis of pulmonary function decline in patients with cystic fibrosis. J. Pediatr. 131: 809-814, 1997.
-
(1997)
J. Pediatr.
, vol.131
, pp. 809-814
-
-
Corey, M.1
Edwards, L.2
Levison, H.3
Knowles, M.4
-
61
-
-
0023150501
-
Abnormal apical cell membrane in cystic fibrosis respiratory epithelium. An in vitro electrophysiologic analysis
-
COTTON, C. U., M. J. STUTTS, M. R. KNOWLES, J. T. GATZY, AND R. C. BOUCHER. Abnormal apical cell membrane in cystic fibrosis respiratory epithelium. An in vitro electrophysiologic analysis. J. Clin. Invest. 79: 80-85, 1987.
-
(1987)
J. Clin. Invest.
, vol.79
, pp. 80-85
-
-
Cotton, C.U.1
Stutts, M.J.2
Knowles, M.R.3
Gatzy, J.T.4
Boucher, R.C.5
-
62
-
-
0032518518
-
m locus explains the partial penetrance of the T5 polymorphism as a disease mutation
-
m locus explains the partial penetrance of the T5 polymorphism as a disease mutation. J. Clin. Invest. 101: 487-496, 1998.
-
(1998)
J. Clin. Invest.
, vol.101
, pp. 487-496
-
-
Cuppens, H.1
Lin, W.2
Jaspers, M.3
Costes, B.4
Teng, H.5
Vankeerberghen, A.6
Jorissen, M.7
Droogmans, G.8
Reynaert, I.9
Goossens, M.10
Nilium, B.11
Cassiman, J.-M.12
-
63
-
-
0029044546
-
Binding of Haemophilus influenzae to purified mucins from the human respiratory tract
-
DAVIES, J., I. CARLSTEDT, A. K. NILSSON, A. HAKANSSON, H. SABHARWAL, L. VAN ALPHEN, M. VAN HAM, AND C. SVANBORG. Binding of Haemophilus influenzae to purified mucins from the human respiratory tract. Infect. Immun. 63: 2485-2492, 1995.
-
(1995)
Infect. Immun.
, vol.63
, pp. 2485-2492
-
-
Davies, J.1
Carlstedt, I.2
Nilsson, A.K.3
Hakansson, A.4
Sabharwal, H.5
Van Alphen, L.6
Van Ham, M.7
Svanborg, C.8
-
65
-
-
0025312731
-
Multiple mutations in highly conserved residues are found in mildly affected cystic fibrosis patients
-
DEAN M., M. B. WHITE, J. AMOS, B. GERRARD, C. STEWART, K. T. KHAW, AND M. LEPPERT. Multiple mutations in highly conserved residues are found in mildly affected cystic fibrosis patients. Cell 61: 863-870, 1990.
-
(1990)
Cell
, vol.61
, pp. 863-870
-
-
Dean, M.1
White, M.B.2
Amos, J.3
Gerrard, B.4
Stewart, C.5
Khaw, K.T.6
Leppert, M.7
-
66
-
-
0029767885
-
Pseudomonas aeruginosa adherence to remodelling respiratory epithelium
-
DE BENTZMANN, S., P. ROGER, AND E. PUCHELLE. Pseudomonas aeruginosa adherence to remodelling respiratory epithelium. Eur. Respir. J. 9: 2145-2150, 1996.
-
(1996)
Eur. Respir. J.
, vol.9
, pp. 2145-2150
-
-
De Bentzmann, S.1
Roger, P.2
Puchelle, E.3
-
67
-
-
0028142615
-
Exogenous surfactant enhances mucociliary clearance in the anaesthetized dog
-
DE SANCTIS, G. T., R. P. TOMKIEWICZ, B. K. RUBIN, S. SCHURCH, AND M. KING. Exogenous surfactant enhances mucociliary clearance in the anaesthetized dog. Eur. Respir. J. 7: 1616-1621, 1994.
-
(1994)
Eur. Respir. J.
, vol.7
, pp. 1616-1621
-
-
De Sanctis, G.T.1
Tomkiewicz, R.P.2
Rubin, B.K.3
Schurch, S.4
King, M.5
-
68
-
-
0030498716
-
Mechanisms of airway inflammation in cystic fibrosis. Pediatr
-
DORING, G. Mechanisms of airway inflammation in cystic fibrosis. Pediatr. Allergy Immunol. 7: 63-66, 1996.
-
(1996)
Allergy Immunol.
, vol.7
, pp. 63-66
-
-
Doring, G.1
-
69
-
-
0029082368
-
CFTR and differentiation markers expression in non-CF and delta F508 homozygous CF nasal epithelium
-
DUPUIT, F., N. KALIN, S. BREZILLON, J. HINNRASKY, B. TUMMLER, AND E. PUCHELLE. CFTR and differentiation markers expression in non-CF and delta F508 homozygous CF nasal epithelium. J. Clin. Invest. 96: 1601-1611, 1995.
-
(1995)
J. Clin. Invest.
, vol.96
, pp. 1601-1611
-
-
Dupuit, F.1
Kalin, N.2
Brezillon, S.3
Hinnrasky, J.4
Tummler, B.5
Puchelle, E.6
-
70
-
-
0028795401
-
Diagnositic criteria for cystic fibrosis in men with congenital absence of the vas deferens
-
DURIEU, I., F. BEY-OMAR, J. ROLLET, L. CALEMARD, D. BOGGIO, H. LEJEUNE, R. GILLY, Y. MOREL, AND D. V. DURAND. Diagnositic criteria for cystic fibrosis in men with congenital absence of the vas deferens. Medicine 74: 42-47, 1996.
-
(1996)
Medicine
, vol.74
, pp. 42-47
-
-
Durieu, I.1
Bey-Omar, F.2
Rollet, J.3
Calemard, L.4
Boggio, D.5
Lejeune, H.6
Gilly, R.7
Morel, Y.8
Durand, D.V.9
-
71
-
-
0025732775
-
Intracellular Cl in submucosal gland cells
-
DWYER, T. M., AND J. M. FARLEY. Intracellular Cl in submucosal gland cells. Life Sci. 48: 2119-2127, 1991.
-
(1991)
Life Sci.
, vol.48
, pp. 2119-2127
-
-
Dwyer, T.M.1
Farley, J.M.2
-
72
-
-
0028896289
-
Differential expression of ORCC and CFTR induced by low temperature in CF airway epithelial cells
-
EGAN, M. E., E. M. SCHWIEBERT, AND W. B. GUGGINO. Differential expression of ORCC and CFTR induced by low temperature in CF airway epithelial cells. Am. J. Physiol 268 (Cell Physiol 37): C243-C251, 1995.
-
(1995)
Am. J. Physiol 268 (Cell Physiol 37)
, vol.268
-
-
Egan, M.E.1
Schwiebert, E.M.2
Guggino, W.B.3
-
73
-
-
0026095436
-
Killing of gram-negative bacteria by lactoferrin and lysozyme
-
ELLISON, R. T., AND T. J. GIEHL. Killing of gram-negative bacteria by lactoferrin and lysozyme. J. Clin. Invest. 88: 1080-1091, 1991.
-
(1991)
J. Clin. Invest.
, vol.88
, pp. 1080-1091
-
-
Ellison, R.T.1
Giehl, T.J.2
-
74
-
-
0026951303
-
Submucosal glands are the predominant site of CFTR expression in the human bronchus
-
ENGELHARDT, J. F., J. R. YANKASKAS, S. A. ERNST, Y. YANG, C. R. MARINO, R. C. BOUCHER, J. A. COHN, AND J. M. WILSON. Submucosal glands are the predominant site of CFTR expression in the human bronchus. Nature Genet. 2: 240-248, 1992.
-
(1992)
Nature Genet.
, vol.2
, pp. 240-248
-
-
Engelhardt, J.F.1
Yankaskas, J.R.2
Ernst, S.A.3
Yang, Y.4
Marino, C.R.5
Boucher, R.C.6
Cohn, J.A.7
Wilson, J.M.8
-
75
-
-
25044431575
-
Chondroitin sulfate is a secretory product of trachea gland serous cells in vivo as well as in culture
-
ESCUDIER, E., L. S. FORSBERG, AND C. B. BASBAUM. Chondroitin sulfate is a secretory product of trachea gland serous cells in vivo as well as in culture (Abstract). J. Cell Biol. 105: 330A, 1988.
-
(1988)
J. Cell Biol.
, vol.105
-
-
Escudier, E.1
Forsberg, L.S.2
Basbaum, C.B.3
-
76
-
-
0014353524
-
Cystic fibrosis of the pancreas: Structural changes in peripheral airways
-
ESTERLY, J., AND E. H. OPPENHEIMER. Cystic fibrosis of the pancreas: structural changes in peripheral airways. Thorax 23: 670-675, 1968.
-
(1968)
Thorax
, vol.23
, pp. 670-675
-
-
Esterly, J.1
Oppenheimer, E.H.2
-
77
-
-
0014249867
-
Observations in cystic fibrosis of the pancreas. III. Pulmonary lesions
-
ESTERLY, J. R., AND E. H. OPPENHEIMER. Observations in cystic fibrosis of the pancreas. III. Pulmonary lesions. Johns Hopkins Med. J. 122: 94-104, 1968.
-
(1968)
Johns Hopkins Med. J.
, vol.122
, pp. 94-104
-
-
Esterly, J.R.1
Oppenheimer, E.H.2
-
78
-
-
0029761031
-
Lung function in bronchiectasis: The influence of Pseudomonas aeruginosa
-
EVANS, S. A., S. M. TURNER, B. J. BOSCH, C. C. HARDY, AND M. A. WOODHEAD. Lung function in bronchiectasis: the influence of Pseudomonas aeruginosa. Eur. Respir. J. 9: 1601-1604, 1996.
-
(1996)
Eur. Respir. J.
, vol.9
, pp. 1601-1604
-
-
Evans, S.A.1
Turner, S.M.2
Bosch, B.J.3
Hardy, C.C.4
Woodhead, M.A.5
-
79
-
-
84984082362
-
Study of the fine structure of ciliated epithelia
-
FAWCETT, D. W., AND K. R. PORTER. Study of the fine structure of ciliated epithelia. J. Morphol 94: 221-281, 1954.
-
(1954)
J. Morphol
, vol.94
, pp. 221-281
-
-
Fawcett, D.W.1
Porter, K.R.2
-
80
-
-
0021239746
-
Proteins of the cystic fibrosis respiratory tract: Fragmented immunoglobulin G opsonic antibody causing defective opsonophagocytosis
-
FICK, R. B., JR., G. P. NAEGEL, S. U. SQUIER, R. E. WOOD, J. B. C. GEE, AND H. Y. REYNOLDS. Proteins of the cystic fibrosis respiratory tract: fragmented immunoglobulin G opsonic antibody causing defective opsonophagocytosis. J. Clin. Invest. 74: 236-248, 1984.
-
(1984)
J. Clin. Invest.
, vol.74
, pp. 236-248
-
-
Fick R.B., Jr.1
Naegel, G.P.2
Squier, S.U.3
Wood, R.E.4
Gee, J.B.C.5
Reynolds, H.Y.6
-
81
-
-
0023932725
-
Alveolar liquid pressures in newborn and adult rabbit lungs
-
FIKE, C. D., S. J. LAI-FOOK, AND R. D. BLAND. Alveolar liquid pressures in newborn and adult rabbit lungs. J. Appl. Physiol. 64: 1629-1635, 1988.
-
(1988)
J. Appl. Physiol.
, vol.64
, pp. 1629-1635
-
-
Fike, C.D.1
Lai-Fook, S.J.2
Bland, R.D.3
-
83
-
-
0030022103
-
Transepithelial water permeability in microperfused distal airways. Evidence for channel-mediated water transport
-
FOLKESSON, H. G., M. A. MATTHAY, A. FRIGERI, AND A. S. VERKMAN. Transepithelial water permeability in microperfused distal airways. Evidence for channel-mediated water transport. J. Clin. Invest. 97: 664-671, 1996.
-
(1996)
J. Clin. Invest.
, vol.97
, pp. 664-671
-
-
Folkesson, H.G.1
Matthay, M.A.2
Frigeri, A.3
Verkman, A.S.4
-
86
-
-
0022516747
-
Altered regulation of airway epithelial cell Cl channels in cystic fibrosis
-
FRIZZELL, R. A., G. RECHKEMMER, AND R. L. SHOEMAKER. Altered regulation of airway epithelial cell Cl channels in cystic fibrosis. Science 233: 558-560, 1986.
-
(1986)
Science
, vol.233
, pp. 558-560
-
-
Frizzell, R.A.1
Rechkemmer, G.2
Shoemaker, R.L.3
-
87
-
-
0019732315
-
Hormonal control of Cl secretion by canine tracheal epithelium: An electrophysiologic analysis
-
FRIZZELL, R. A., M. J. WELSH, AND P. L. SMITH. Hormonal control of Cl secretion by canine tracheal epithelium: an electrophysiologic analysis. Ann. NY Acad. Sci. 372: 558-570, 1981.
-
(1981)
Ann. NY Acad. Sci.
, vol.372
, pp. 558-570
-
-
Frizzell, R.A.1
Welsh, M.J.2
Smith, P.L.3
-
88
-
-
0029003982
-
A cystic fibrosis mutation associated with mild lung disease
-
GAN, K.-H., H. J. VEEZE, A. M. W. VAN DEN OUWELAND, D. J. J. HALLEY, H. SCHEFFER, A. VAN DER HOUT, S. E. OVERBEEK, H. C. DEJONGSTE, W. BARKER, AND H. G. M. HEIJERMAN. A cystic fibrosis mutation associated with mild lung disease. N. Engl. J. Med. 333: 95-99, 1995.
-
(1995)
N. Engl. J. Med.
, vol.333
, pp. 95-99
-
-
Gan, K.-H.1
Veeze, H.J.2
Van Den Ouweland, A.M.W.3
Halley, D.J.J.4
Scheffer, H.5
Van Der Hout, A.6
Overbeek, S.E.7
Dejongste, H.C.8
Barker, W.9
Heijerman, H.G.M.10
-
89
-
-
0030945484
-
Epithelial Na channels: Function, structure, and regulation
-
GARTY, H., AND L. G. PALMER. Epithelial Na channels: function, structure, and regulation. Physiol. Rev. 77: 359-396, 1997.
-
(1997)
Physiol. Rev.
, vol.77
, pp. 359-396
-
-
Garty, H.1
Palmer, L.G.2
-
90
-
-
0025762972
-
The search for South European cystic fibrosis mutations: Identification of two new mutations, four variants, and intronic sequences
-
GASPARINI P., V. NUNES, A. SAVOIA, M. DOGNINI, N. MORRAL, A. GAONA, A. BONIZZATO, M. CHILLON, F. SANGIUOLO, G. NOVELLI, B. DALLAPICCOLA, P. F. PIGNATTI, AND X. ESTIVILL. The search for South European cystic fibrosis mutations: identification of two new mutations, four variants, and intronic sequences. Genomics 10: 193-200, 1991.
-
(1991)
Genomics
, vol.10
, pp. 193-200
-
-
Gasparini, P.1
Nunes, V.2
Savoia, A.3
Dognini, M.4
Morral, N.5
Gaona, A.6
Bonizzato, A.7
Chillon, M.8
Sangiuolo, F.9
Novelli, G.10
Dallapiccola, B.11
Pignatti, P.F.12
Estivill, X.13
-
91
-
-
0027258526
-
Cholinergic and adrenergic stimulation of mucociliary transport in the rat trachea
-
GATTO, L. A. Cholinergic and adrenergic stimulation of mucociliary transport in the rat trachea. Respir. Physiol. 92: 209-217, 1993.
-
(1993)
Respir. Physiol.
, vol.92
, pp. 209-217
-
-
Gatto, L.A.1
-
92
-
-
0024523768
-
Increased bronchial chloride concentration in cystic fibrosis
-
GILLJAM, H., A. ELLIN, AND B. STRANDVIK. Increased bronchial chloride concentration in cystic fibrosis. Scand. J. Clin. Lab. Invest. 49: 121-124, 1989.
-
(1989)
Scand. J. Clin. Lab. Invest.
, vol.49
, pp. 121-124
-
-
Gilljam, H.1
Ellin, A.2
Strandvik, B.3
-
93
-
-
0030949875
-
Human beta-defensin-1 is a salt-sensitive antibiotic in lung that is inactivated in cystic fibrosis
-
GOLDMAN, M. J., G. M. ANDERSON, E. D. STOLZENBERG, U. P. KARI, M. ZASLOFF, AND J. M. WILSON. Human beta-defensin-1 is a salt-sensitive antibiotic in lung that is inactivated in cystic fibrosis. Cell 88: 553-560, 1997.
-
(1997)
Cell
, vol.88
, pp. 553-560
-
-
Goldman, M.J.1
Anderson, G.M.2
Stolzenberg, E.D.3
Kari, U.P.4
Zasloff, M.5
Wilson, J.M.6
-
95
-
-
0029983188
-
Mutant cystic fibrosis transmembrane conductance regulator inhibits acidification and apoptosis in C127 cells: Possible relevance to cystic fibrosis
-
GOTTLIEB, R. A., AND A. DOSANJH. Mutant cystic fibrosis transmembrane conductance regulator inhibits acidification and apoptosis in C127 cells: possible relevance to cystic fibrosis. Proc. Natl. Acad. Sci. USA 93: 3587-3591, 1996.
-
(1996)
Proc. Natl. Acad. Sci. USA
, vol.93
, pp. 3587-3591
-
-
Gottlieb, R.A.1
Dosanjh, A.2
-
96
-
-
0020045045
-
Granulocyte chemiluminescence in patients with cystic fibrosis
-
GRAFT, D. R., E. MISCHLER, P. M. FARRELL, AND W. BUSSE. Granulocyte chemiluminescence in patients with cystic fibrosis. Am. Rev. Respir. Dis. 125: 540-543, 1982.
-
(1982)
Am. Rev. Respir. Dis.
, vol.125
, pp. 540-543
-
-
Graft, D.R.1
Mischler, E.2
Farrell, P.M.3
Busse, W.4
-
97
-
-
0023782863
-
Secretion-regulated chloride channel on the apical plasma membrane of pancreatic duct cells
-
GRAY, M. A., J. R. GREENWELL, AND B. E. ARGENT. Secretion-regulated chloride channel on the apical plasma membrane of pancreatic duct cells. J. Membr. Biol. 105: 131-142, 1988.
-
(1988)
J. Membr. Biol.
, vol.105
, pp. 131-142
-
-
Gray, M.A.1
Greenwell, J.R.2
Argent, B.E.3
-
99
-
-
0344743590
-
A mutation causing pseudohypoaldosteronism type 1 identifies a conserved glycine that is involved in the gating of the epithelial Na channel
-
GRUNDER, S., D. FIRSOV, S. S. CHANG, N. FOWLER JAEGER, I. GAUTSCHI, L. SCHILD, R. P. LIFTON, AND B. C. ROSSIER. A mutation causing pseudohypoaldosteronism type 1 identifies a conserved glycine that is involved in the gating of the epithelial Na channel. EMBO J. 16: 899-907, 1997.
-
(1997)
EMBO J.
, vol.16
, pp. 899-907
-
-
Grunder, S.1
Firsov, D.2
Chang, S.S.3
Jaeger, N.F.4
Gautschi, I.5
Schild, L.6
Lifton, R.P.7
Rossier, B.C.8
-
100
-
-
0031000174
-
The type-4 pilus is the major virulence-associated adhesin of Pseudomonas aeruginosa: A review
-
HAHN, H. P. The type-4 pilus is the major virulence-associated adhesin of Pseudomonas aeruginosa: a review. Gene 192: 99-108, 1997.
-
(1997)
Gene
, vol.192
, pp. 99-108
-
-
Hahn, H.P.1
-
101
-
-
0027517995
-
Cystic fibrosis genotype-phenotype consortium. Correlation between genotype and phenotype in patients with cystic fibrosis
-
HAMOSH, A., AND M. COREY. Cystic fibrosis genotype-phenotype consortium. Correlation between genotype and phenotype in patients with cystic fibrosis. N. Engl. J. Med. 329: 1308-1313, 1993.
-
(1993)
N. Engl. J. Med.
, vol.329
, pp. 1308-1313
-
-
Hamosh, A.1
Corey, M.2
-
102
-
-
0026725724
-
Cystic fibrosis patients bearing both the common missense Gly→Asp at codon 551 and the delta F508 mutation are clinically indistinguishable from delta F508 homozygotes, except for decreased risk of meconium ileus
-
HAMOSH, A., T. M. KING, B. J. ROSENSTEIN, M. MACEK, JR., D. ZEMKOVA, H. KRASNICANOVA, V. VAVROVA, M. MACEK, SR., N. GOLDER, M. J. SCHWARZ, M. SUPER, E. K. WATSON, C. WILLIAMS, A. BUSH, S. M. O'MAHONEY, P. HUMPHRIES, M. A. DE ARCE, A. REIS, J. BURGER, M. STUHRMANN, J. SCHMIDTKE, V. WULBRAND, T. DORK, B. TUMMLER, AND G. R. CUTTING. Cystic fibrosis patients bearing both the common missense Gly→Asp at codon 551 and the delta F508 mutation are clinically indistinguishable from delta F508 homozygotes, except for decreased risk of meconium ileus. Am. J. Hum. Genet. 51: 249-250, 1992.
-
(1992)
Am. J. Hum. Genet.
, vol.51
, pp. 249-250
-
-
Hamosh, A.1
King, T.M.2
Rosenstein, B.J.3
Macek M., Jr.4
Zemkova, D.5
Krasnicanova, H.6
Vavrova, V.7
Macek M., Sr.8
Golder, N.9
Schwarz, M.J.10
Super, M.11
Watson, E.K.12
Williams, C.13
Bush, A.14
O'Mahoney, S.M.15
Humphries, P.16
De Arce, M.A.17
Reis, A.18
Burger, J.19
Stuhrmann, M.20
Schmidtke, J.21
Wulbrand, V.22
Dork, T.23
Tummler, B.24
Cutting, G.R.25
more..
-
104
-
-
0029092801
-
Hypertension caused by a truncated epithelial Na channel subunit: Genetic heterogeneity of Liddle's syndrome
-
HANSSON, J. H., C. NELSON-WILLIAMS, H. SUZUKI, L. SCHILD, R. SHIMKETS, Y. LU, C. CANESSA, T. IWASAKI, B. ROSSIER, AND R. P. LIFTON. Hypertension caused by a truncated epithelial Na channel subunit: genetic heterogeneity of Liddle's syndrome. Nature Genet. 11: 76-82, 1995.
-
(1995)
Nature Genet.
, vol.11
, pp. 76-82
-
-
Hansson, J.H.1
Nelson-Williams, C.2
Suzuki, H.3
Schild, L.4
Shimkets, R.5
Lu, Y.6
Canessa, C.7
Iwasaki, T.8
Rossier, B.9
Lifton, R.P.10
-
105
-
-
0028143993
-
Pseudohypoaldosteronism with increases sweat and saliva electrolyte values and frequent lower respiratory tract infections mimicking cystic fibrosis
-
HANUKOGLU, A., T. BISTRITZER, Y. RAKOVER, AND A. MANDELBERG. Pseudohypoaldosteronism with increases sweat and saliva electrolyte values and frequent lower respiratory tract infections mimicking cystic fibrosis. J. Pediatr. 125: 752-755, 1994.
-
(1994)
J. Pediatr.
, vol.125
, pp. 752-755
-
-
Hanukoglu, A.1
Bistritzer, T.2
Rakover, Y.3
Mandelberg, A.4
-
106
-
-
0021013640
-
Polyelectrolyte behaviour in mucus glycoproteins
-
HARDING, S. E., AND M. CREETH. Polyelectrolyte behaviour in mucus glycoproteins. Biochim. Biophys. Acta 746: 114-119, 1983.
-
(1983)
Biochim. Biophys. Acta
, vol.746
, pp. 114-119
-
-
Harding, S.E.1
Creeth, M.2
-
107
-
-
0025883051
-
Expression of the cystic fibrosis gene in human development
-
HARRIS, A., G. CHALKLEY, S. GOODMAN, AND L. COLEMAN. Expression of the cystic fibrosis gene in human development. Development 113: 305-310, 1991.
-
(1991)
Development
, vol.113
, pp. 305-310
-
-
Harris, A.1
Chalkley, G.2
Goodman, S.3
Coleman, L.4
-
108
-
-
0028292615
-
CFTR in Calu-3 human airway cells: Channel properties and role in cAMP-activated Cl conductance
-
HAWS, C., W. E. FINKBEINER, J. H. WIDDICOMBE, AND J. J. WINE. CFTR in Calu-3 human airway cells: channel properties and role in cAMP-activated Cl conductance. Am. J. Physiol. 266 (Lung Cell. Mol. Physiol. 10): L502-L512, 1994.
-
(1994)
Am. J. Physiol. 266 (Lung Cell. Mol. Physiol. 10)
, vol.266
-
-
Haws, C.1
Finkbeiner, W.E.2
Widdicombe, J.H.3
Wine, J.J.4
-
109
-
-
0028086056
-
A novel mutation in the cystic fibrosis gene in patients with pulmonary disease and normal sweat electrolytes
-
HIGHSMITH, W. E., L. H. BURCH, Z. ZHOU, J. C. OLSEN, T. E. BOAT, A. SPOCK, J. D. GORVOY, L. QUITTELL, K. J. FRIEDMAN, L. M. SILVERMAN, R. C. BOUCHER, AND M. R. KNOWLES. A novel mutation in the cystic fibrosis gene in patients with pulmonary disease and normal sweat electrolytes. N. Engl. J. Med. 331: 974-980, 1994.
-
(1994)
N. Engl. J. Med.
, vol.331
, pp. 974-980
-
-
Highsmith, W.E.1
Burch, L.H.2
Zhou, Z.3
Olsen, J.C.4
Boat, T.E.5
Spock, A.6
Gorvoy, J.D.7
Quittell, L.8
Friedman, K.J.9
Silverman, L.M.10
Boucher, R.C.11
Knowles, M.R.12
-
110
-
-
0031259163
-
Organ-specific over-sulfation of glycosaminoglycans and altered extracellular matrix in a mouse model of cystic fibrosis
-
HILL, W. G., G. S. HARPER, T. ROZAKLIS, R. C. BOUCHER, AND J. J. HOPWOOD. Organ-specific over-sulfation of glycosaminoglycans and altered extracellular matrix in a mouse model of cystic fibrosis. Biochem. Mol. Med. 62: 113-122, 1997.
-
(1997)
Biochem. Mol. Med.
, vol.62
, pp. 113-122
-
-
Hill, W.G.1
Harper, G.S.2
Rozaklis, T.3
Boucher, R.C.4
Hopwood, J.J.5
-
111
-
-
0030924036
-
Correlation between nasal potential difference measurements, genotype, and clinical condition in patients with cystic fibrosis
-
HO, L. P., J. M. SAMWAYS, D. J. PORTEOUS, J. R. DORIN, A. CAROTHERS, A P. GREENING, AND J. A. INNES. Correlation between nasal potential difference measurements, genotype, and clinical condition in patients with cystic fibrosis. Eur. Respir. J. 10: 2018-2022, 1997.
-
(1997)
Eur. Respir. J.
, vol.10
, pp. 2018-2022
-
-
Ho, L.P.1
Samways, J.M.2
Porteous, D.J.3
Dorin, J.R.4
Carothers, A.5
Greening, A.P.6
Innes, J.A.7
-
112
-
-
0029860775
-
Genotype-phenotype relationships in a cohort of adult cystic fibrosis patients
-
HUBERT, D., T. BIENVENU, N. DESMAZES-DUFEU, I. FAJAC, J. LACRONIQUE, R. MATRAN, J. C. KAPLAN, AND D. J. DUSSER. Genotype-phenotype relationships in a cohort of adult cystic fibrosis patients. Eur. Respir. J. 9: 2207-2214, 1996.
-
(1996)
Eur. Respir. J.
, vol.9
, pp. 2207-2214
-
-
Hubert, D.1
Bienvenu, T.2
Desmazes-Dufeu, N.3
Fajac, I.4
Lacronique, J.5
Matran, R.6
Kaplan, J.C.7
Dusser, D.J.8
-
113
-
-
0019916574
-
An improved method for fixation of the respiratory epithelial surface with the mucous and surfaciant layers
-
HULBERT, W. C., B. B. FORSTER, W. LAIRD, C. E. LIHL, AND D. C. WALKER. An improved method for fixation of the respiratory epithelial surface with the mucous and surfaciant layers. Acta Otolaryngol. (Stockh.) 47: 354-363, 1982.
-
(1982)
Acta Otolaryngol. (Stockh.)
, vol.47
, pp. 354-363
-
-
Hulbert, W.C.1
Forster, B.B.2
Laird, W.3
Lihl, C.E.4
Walker, D.C.5
-
114
-
-
0031918382
-
Elemental content of airway surface liquid from infants with cystic fibrosis
-
HULL, J., W. SKINNER, C. ROBERTSON, AND P. PHELAN. Elemental content of airway surface liquid from infants with cystic fibrosis. Am. J. Respir. Crit. Care Med. 157: 10-14, 1998.
-
(1998)
Am. J. Respir. Crit. Care Med.
, vol.157
, pp. 10-14
-
-
Hull, J.1
Skinner, W.2
Robertson, C.3
Phelan, P.4
-
115
-
-
12644300654
-
A mouse model for the renal salt-wasting syndrome pseudohypoaldosteronism
-
HUMMLER, E., P. BARKER, C. TALBOT, Q. WANG, C. VERDUMO, B. GRUBB, J. GATZY, M. BURNIER, J. D, HORISBERGER, F. BEERMANN, R. BOUCHER, AND B. C. ROSSIER. A mouse model for the renal salt-wasting syndrome pseudohypoaldosteronism. Proc. Natl. Acad. Sci. USA 94: 11710-11715, 1997.
-
(1997)
Proc. Natl. Acad. Sci. USA
, vol.94
, pp. 11710-11715
-
-
Hummler, E.1
Barker, P.2
Talbot, C.3
Wang, Q.4
Verdumo, C.5
Grubb, B.6
Gatzy, J.7
Burnier, M.8
J, D.9
Beermann, F.10
Boucher, R.11
Rossier, B.C.12
-
116
-
-
0028920643
-
Cystic fibrosis epithelial cells have a receptor for pathogenic bacteria on their apical surface
-
IMUNDO, L., J. BARASCH, A. PRINCE, AND Q. AL-AWQATI. Cystic fibrosis epithelial cells have a receptor for pathogenic bacteria on their apical surface. Proc. Natl. Acad. Sci. USA 92: 3019-3023, 1995.
-
(1995)
Proc. Natl. Acad. Sci. USA
, vol.92
, pp. 3019-3023
-
-
Imundo, L.1
Barasch, J.2
Prince, A.3
Al-Awqati, Q.4
-
117
-
-
0030946640
-
In situ visualization of bronchial submucosal glands and their secretory response to acetylcholine
-
INGLIS, S. K., M. R. CORBOZ, A. E. TAYLOR, AND S. T. BALLARD. In situ visualization of bronchial submucosal glands and their secretory response to acetylcholine. Am. J. Physiol. 272 (Lung Cell. Mol. Physiol. 16): L203-L210, 1997.
-
(1997)
Am. J. Physiol. 272 (Lung Cell. Mol. Physiol. 16)
, vol.272
-
-
Inglis, S.K.1
Corboz, M.R.2
Taylor, A.E.3
Ballard, S.T.4
-
118
-
-
0030909697
-
Effect of anion secretion inhibition on mucus secretion by airway submucosal glands
-
INGLIS, S. K., M. R. CORBOZ, A. E. TAYLOR, AND S. T. BALLARD. Effect of anion secretion inhibition on mucus secretion by airway submucosal glands. Am. J. Physiol. 272 (Lung Cell. Mol. Physiol. 16): L372-L377, 1997.
-
(1997)
Am. J. Physiol. 272 (Lung Cell. Mol. Physiol. 16)
, vol.272
-
-
Inglis, S.K.1
Corboz, M.R.2
Taylor, A.E.3
Ballard, S.T.4
-
120
-
-
0029802579
-
Bicarbonate secretion in interlobular ducts from guinea-pig pancreas
-
ISHIGURO, H., M. C. STEWARD, R. W. WILSON, AND R. M. CASE. Bicarbonate secretion in interlobular ducts from guinea-pig pancreas. J. Physiol. (Lond.) 495: 179-191, 1996.
-
(1996)
J. Physiol. (Lond.)
, vol.495
, pp. 179-191
-
-
Ishiguro, H.1
Steward, M.C.2
Wilson, R.W.3
Case, R.M.4
-
121
-
-
0027402791
-
Localization of the cystic fibrosis transmembrane conductance regulator in airway secretory glands
-
JACQUOT, J., E. PUCHELLE, J. HINNRASKY, C. FUCHEY, C. BETTINGER, C. SPILMONT, N. BONNET, A. DIETERLE, D. DREYER, AND A. PAVIRANI. Localization of the cystic fibrosis transmembrane conductance regulator in airway secretory glands. Eur. Respir. J. 6: 169-176, 1993.
-
(1993)
Eur. Respir. J.
, vol.6
, pp. 169-176
-
-
Jacquot, J.1
Puchelle, E.2
Hinnrasky, J.3
Fuchey, C.4
Bettinger, C.5
Spilmont, C.6
Bonnet, N.7
Dieterle, A.8
Dreyer, D.9
Pavirani, A.10
-
122
-
-
0026575049
-
Human airway secretory cells during development and in mature airway epithelium
-
JEFFERY, P. K., D. GAILLARD, AND S. MORET. Human airway secretory cells during development and in mature airway epithelium. Eur. Respir. J. 5: 93-104, 1992.
-
(1992)
Eur. Respir. J.
, vol.5
, pp. 93-104
-
-
Jeffery, P.K.1
Gaillard, D.2
Moret, S.3
-
123
-
-
0016765571
-
New observations of rat airway epithelium: A quantitative electron microscopic study
-
JEFFERY, P. K., AND L. REID. New observations of rat airway epithelium: a quantitative electron microscopic study. J. Anat. 120: 295-320, 1975.
-
(1975)
J. Anat.
, vol.120
, pp. 295-320
-
-
Jeffery, P.K.1
Reid, L.2
-
124
-
-
0027363212
-
Altered fluid transport across airway epithelium in cystic fibrosis
-
JIANG, C., W. E. FINKBEINER, J. H. WIDDICOMBE, P. B. McCRAY, JR., AND S. S. MILLER. Altered fluid transport across airway epithelium in cystic fibrosis. Science 262: 424-427, 1993.
-
(1993)
Science
, vol.262
, pp. 424-427
-
-
Jiang, C.1
Finkbeiner, W.E.2
Widdicombe, J.H.3
McCray P.B., Jr.4
Miller, S.S.5
-
125
-
-
0030797257
-
Fluid transport across cultures of human tracheal glands is altered in cystic fibrosis
-
JIANG, C., W. E. FINKBEINER, J. H. WIDDICOMBE, AND S. S. MILLER. Fluid transport across cultures of human tracheal glands is altered in cystic fibrosis. J. Physiol. (Lond.) 501: 637-647, 1997.
-
(1997)
J. Physiol. (Lond.)
, vol.501
, pp. 637-647
-
-
Jiang, C.1
Finkbeiner, W.E.2
Widdicombe, J.H.3
Miller, S.S.4
-
126
-
-
0030029836
-
Cyclic AMP and Cl-dependent regulation of the apical constitutive secretory pathway in colonic epithelial cells
-
JILLING, T., AND K. L. KIRK. Cyclic AMP and Cl-dependent regulation of the apical constitutive secretory pathway in colonic epithelial cells. J. Biol. Chem. 271: 4381-4387, 1996.
-
(1996)
J. Biol. Chem.
, vol.271
, pp. 4381-4387
-
-
Jilling, T.1
Kirk, K.L.2
-
127
-
-
0027141851
-
Elemental composition of human airway surface fluid in healthy and diseased airways
-
JORIS, L., I. DAB, AND P. M. QUINTON. Elemental composition of human airway surface fluid in healthy and diseased airways. Am. Rev. Respir. Dis. 148: 1633-1637, 1993.
-
(1993)
Am. Rev. Respir. Dis.
, vol.148
, pp. 1633-1637
-
-
Joris, L.1
Dab, I.2
Quinton, P.M.3
-
128
-
-
0024443417
-
Evidence for electrogenic Na-glucose co-transport in tracheal epithelium
-
JORIS, L., AND P. M. QUINTON. Evidence for electrogenic Na-glucose co-transport in tracheal epithelium. Eur. J. Physiol. 415:118-120, 1989.
-
(1989)
Eur. J. Physiol.
, vol.415
, pp. 118-120
-
-
Joris, L.1
Quinton, P.M.2
-
129
-
-
0028047077
-
Involvement of protein kinase C in mucus secretion by hamster tracheal epithelial cells in culture
-
KAI, H., K. YOSHITAKE, Y. ISOHAMA, I. HAMAMURA, K. TAKAHAMA, AND T. MIYATA. Involvement of protein kinase C in mucus secretion by hamster tracheal epithelial cells in culture. Am. J. Physiol. 267 (Lung Cell. Mol. Physiol. 11): L526-L530, 1994.
-
(1994)
Am. J. Physiol. 267 (Lung Cell. Mol. Physiol. 11)
, vol.267
-
-
Kai, H.1
Yoshitake, K.2
Isohama, Y.3
Hamamura, I.4
Takahama, K.5
Miyata, T.6
-
130
-
-
0026073070
-
Expression of the cystic fibrosis gene in non-epithelial invertebrate cells produce a regulated anion conductance
-
KARTNER, N., J. W. HANRAHAN, T. J. JENSEN, A. L. NAISMITH, S. SUN, C. A. ACKERLEY, E. F. REYES, L. C. TSUI, J. M. ROMMENS, C. E. BEAR, AND J. R. RIORDAN. Expression of the cystic fibrosis gene in non-epithelial invertebrate cells produce a regulated anion conductance. Cell 64: 681-691, 1991.
-
(1991)
Cell
, vol.64
, pp. 681-691
-
-
Kartner, N.1
Hanrahan, J.W.2
Jensen, T.J.3
Naismith, A.L.4
S, S.U.N.5
Ackerley, C.A.6
Reyes, E.F.7
Tsui, L.C.8
Rommens, J.M.9
Bear, C.E.10
Riordan, J.R.11
-
131
-
-
0345299477
-
Respiratory disease in patients with systemic pseudohypoaldosteronism: A disorder of excess airway surface liquid
-
In press
-
KEREM, E., T. BISTRITZER, A. HANUKOGLU, T. HOFMANNKHAIR, Z. ZHOU, W. BENNETT, V. HOMOLYA, E. MACLAUGHLIN, P. BARKER, B. KEENAN, M. NASH, L. QUITTELL, R. BOUCHER, AND M. R. KNOWLES. Respiratory disease in patients with systemic pseudohypoaldosteronism: a disorder of excess airway surface liquid. N. Engl. J. Med. In press.
-
N. Engl. J. Med.
-
-
Kerem, E.1
Bistritzer, T.2
Hanukoglu, A.3
Hofmannkhair, T.4
Zhou, Z.5
Bennett, W.6
Homolya, V.7
Maclaughlin, E.8
Barker, P.9
Keenan, B.10
Nash, M.11
Quittell, L.12
Boucher, R.13
Knowles, M.R.14
-
132
-
-
0025355607
-
Pulmonary function and clinical course in patients with cystic fibrosis after pulmonary colonization with Pseudomonas aeruginosa
-
KEREM, E., M. COREY, R. GOLD, AND H. LEVISON. Pulmonary function and clinical course in patients with cystic fibrosis after pulmonary colonization with Pseudomonas aeruginosa. J. Pediatr. 16: 714-719, 1990.
-
(1990)
J. Pediatr.
, vol.16
, pp. 714-719
-
-
Kerem, E.1
Corey, M.2
Gold, R.3
Levison, H.4
-
133
-
-
0025313244
-
Risk factors for P. Aeruginosa colonization in CF patients. Pediatr
-
KEREM, E., M. COREY, R. STEIN, R. GOLD, AND H. LEVISON. Risk factors for P. aeruginosa colonization in CF patients. Pediatr. Infect. Dis. J. 9: 494-498, 1990.
-
(1990)
Infect. Dis. J.
, vol.9
, pp. 494-498
-
-
Kerem, E.1
Corey, M.2
Stein, R.3
Gold, R.4
Levison, H.5
-
134
-
-
8244257360
-
A cystic fibrosis transmembrane conductance regulator splice variant with partial penetrance associated with variable cystic fibrosis presentations
-
KEREM, E., N. RAVE-HAREL, A. AUGARTEN, I. MADGAR, M. NISSIM-RAFINIA, Y. YAHEV, R. GOSHEN, L. BENTUR, J. RIVLIN, M. AVIRAM, A. GENEM, O. CHIBA-FALEK, M. R. KRAEMER, A. SIMON, D. BRANSKI, AND B. KEREM. A cystic fibrosis transmembrane conductance regulator splice variant with partial penetrance associated with variable cystic fibrosis presentations. Am. J. Respir. Crit. Care Med. 155: 1914-1920, 1997.
-
(1997)
Am. J. Respir. Crit. Care Med.
, vol.155
, pp. 1914-1920
-
-
Kerem, E.1
Rave-Harel, N.2
Augarten, A.3
Madgar, I.4
Nissim-Rafinia, M.5
Yahev, Y.6
Goshen, R.7
Bentur, L.8
Rivlin, J.9
Aviram, M.10
Genem, A.11
Chiba-Falek, O.12
Kraemer, M.R.13
Simon, A.14
Branski, D.15
Kerem, B.16
-
135
-
-
0029812466
-
Bacterial-induced release of inflammatory mediators by bronchial epithelial cells
-
KHAIR, O. A., R. J. DAVIES, AND J. L. DEVALIA. Bacterial-induced release of inflammatory mediators by bronchial epithelial cells. Eur. Respir. J. 9: 1913-1922, 1996.
-
(1996)
Eur. Respir. J.
, vol.9
, pp. 1913-1922
-
-
Khair, O.A.1
Davies, R.J.2
Devalia, J.L.3
-
136
-
-
0028914085
-
Early pulmonary inflammation in infants with cystic fibrosis
-
KHAN, T. Z., J. S. WAGENER, T. BOST, J. MARINEZ, F. J. ACCURSO, AND D. W. H. RICHES. Early pulmonary inflammation in infants with cystic fibrosis. Am. J. Respir. Crit. Care Med. 151: 1075-1082, 1995.
-
(1995)
Am. J. Respir. Crit. Care Med.
, vol.151
, pp. 1075-1082
-
-
Khan, T.Z.1
Wagener, J.S.2
Bost, T.3
Marinez, J.4
Accurso, F.J.5
Riches, D.W.H.6
-
137
-
-
0027521663
-
A mutation in CFTR produces different phenotypes depending on chromosomal background
-
KIESEWETTEH, S., M. MACEK, JR., C. DAVIS, S. M. CURRISTIN, C.-S. CHU, C. GRAHAM, A. E. SHRIMPTON, S. M. CASHMAN, L.-C. TSUI, J. MICKLE, J. AMOS, W. E. HIGHSMITH, A. SHUBER, D. R. WITT, R. G. CRYSTAL, AND G. R. CUTTING. A mutation in CFTR produces different phenotypes depending on chromosomal background. Nature Genet. 5: 274-278, 1993.
-
(1993)
Nature Genet.
, vol.5
, pp. 274-278
-
-
Kiesewetteh, S.1
Macek M., Jr.2
Davis, C.3
Curristin, S.M.4
C-S, C.H.U.5
Graham, C.6
Shrimpton, A.E.7
Cashman, S.M.8
Tsui, L.-C.9
Mickle, J.10
Amos, J.11
Highsmith, W.E.12
Shuber, A.13
Witt, D.R.14
Crystal, R.G.15
Cutting, G.R.16
-
138
-
-
0014335205
-
A hypothesis for pulmonary clearance and its implications
-
KILBURN, K. H. A hypothesis for pulmonary clearance and its implications. Am. Rev. Respir. Dis. 98: 449-463, 1968.
-
(1968)
Am. Rev. Respir. Dis.
, vol.98
, pp. 449-463
-
-
Kilburn, K.H.1
-
139
-
-
0025922842
-
2 purinoceptor regulation of mucin release by airway goblet cells in primary culture
-
2 purinoceptor regulation of mucin release by airway goblet cells in primary culture. Br. J. Pharmacol. 103: 1053-1056, 1991.
-
(1991)
Br. J. Pharmacol.
, vol.103
, pp. 1053-1056
-
-
Kim, K.C.1
Lee, B.C.2
-
140
-
-
0030666976
-
Aquaporins in complex tissues. I. Developmental patterns in respiratory and glandular tissues of rat
-
KING, L. S., S. NIELSEN, AND P. AGRE. Aquaporins in complex tissues. I. Developmental patterns in respiratory and glandular tissues of rat Am. J. Physiol. 273 (Cell Physiol. 42): C1541-C1548, 1997.
-
(1997)
Am. J. Physiol. 273 (Cell Physiol. 42)
, vol.273
-
-
King, L.S.1
Nielsen, S.2
Agre, P.3
-
141
-
-
0023611276
-
The role of mucus viscoelasticity in cough clearance
-
KING, M. The role of mucus viscoelasticity in cough clearance. Biorheology 24: 589-597, 1987.
-
(1987)
Biorheology
, vol.24
, pp. 589-597
-
-
King, M.1
-
142
-
-
0027299375
-
A planar model for mucociliary transport: Effect of mucus viscoelasticity
-
KING, M., M. AGARWAL, AND J. B. SHUKLA. A planar model for mucociliary transport: effect of mucus viscoelasticity. Biorheology 30: 49-61, 1993.
-
(1993)
Biorheology
, vol.30
, pp. 49-61
-
-
King, M.1
Agarwal, M.2
Shukla, J.B.3
-
143
-
-
0002833685
-
Rheology of airway mucus. Relationship with clearance function
-
edited by T. Takishima and S. Shimura. New York: Dekker
-
KING, M., AND B. K. RUBIN. Rheology of airway mucus. Relationship with clearance function. In: Airway Secretion. Physiological Bases for the Control of Mucus Hypersecretion, edited by T. Takishima and S. Shimura. New York: Dekker, 1994, p. 283-314.
-
(1994)
Airway Secretion. Physiological Bases for the Control of Mucus Hypersecretion
, pp. 283-314
-
-
King, M.1
Rubin, B.K.2
-
144
-
-
0019985202
-
Measurements of transepithelial electric potential differences in the trachea and bronchi of human subjects in vivo
-
KNOWLES, M. R., W. H. BUNTIN, P. BROMBER, J. T. GATZY, AND R. C. BOUCHER. Measurements of transepithelial electric potential differences in the trachea and bronchi of human subjects in vivo. Am. Rev. Respir. Dis. 126: 108-112, 1982.
-
(1982)
Am. Rev. Respir. Dis.
, vol.126
, pp. 108-112
-
-
Knowles, M.R.1
Buntin, W.H.2
Bromber, P.3
Gatzy, J.T.4
Boucher, R.C.5
-
145
-
-
0019490443
-
Measurements of nasal transepithelial electric potential differences in normal human subjects in vivo
-
KNOWLES, M. R., J. L. CARSON, A. M. COLLIER, J. T. GATZY, AND R. C. BOUCHER. Measurements of nasal transepithelial electric potential differences in normal human subjects in vivo. Am. Rev. Respir. Dis. 124: 484-490, 1981.
-
(1981)
Am. Rev. Respir. Dis.
, vol.124
, pp. 484-490
-
-
Knowles, M.R.1
Carson, J.L.2
Collier, A.M.3
Gatzy, J.T.4
Boucher, R.C.5
-
146
-
-
0019809960
-
Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis
-
KNOWLES, M. R., J. GATZY, AND R. BOUCHER. Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis. N. Engl. J. Med. 305: 1489-1495, 1981.
-
(1981)
N. Engl. J. Med.
, vol.305
, pp. 1489-1495
-
-
Knowles, M.R.1
Gatzy, J.2
Boucher, R.3
-
147
-
-
0021823866
-
Aldosterone metabolism and transepithelial potential difference in normal and cystic fibrosis subjects
-
KNOWLES, M. R., J. T. GATZY, AND R. C. BOUCHER. Aldosterone metabolism and transepithelial potential difference in normal and cystic fibrosis subjects. Pediatr. Res. 19: 676-679, 1985.
-
(1985)
Pediatr. Res.
, vol.19
, pp. 676-679
-
-
Knowles, M.R.1
Gatzy, J.T.2
Boucher, R.C.3
-
148
-
-
0021352368
-
Bioelectric properties and ion flow across excised human bronchi
-
KNOWLES, M., G. MURRAY, J. SHALLAL, F. ASKIN, V. RANGA, J. GATZY, AND R. BOUCHER. Bioelectric properties and ion flow across excised human bronchi. J. Appl. Physiol. 56: 868-877, 1984.
-
(1984)
J. Appl. Physiol.
, vol.56
, pp. 868-877
-
-
Knowles, M.1
Murray, G.2
Shallal, J.3
Askin, F.4
Ranga, V.5
Gatzy, J.6
Boucher, R.7
-
149
-
-
0028991826
-
In vivo nasal potential difference: Techniques and protocols for assessing efficacy of gene transfer in cystic fibrosis
-
KNOWLES, M. R., A. M. PARADISO, AND R. C. BOUCHER. In vivo nasal potential difference: techniques and protocols for assessing efficacy of gene transfer in cystic fibrosis. Hum. Gene Ther. 6:445-455, 1995.
-
(1995)
Hum. Gene Ther.
, vol.6
, pp. 445-455
-
-
Knowles, M.R.1
Paradiso, A.M.2
Boucher, R.C.3
-
150
-
-
0030814886
-
Ion composition of airway surface liquid of patients with cystic fibrosis as compared with normal and disease-control subjects
-
KNOWLES, M. R., J. M. ROBINSON, R. E. WOOD, C. A. PUE, W. M. MENTZ, G. C. WAGER, J. T. GATSY, AND R. C. BOUCHER. Ion composition of airway surface liquid of patients with cystic fibrosis as compared with normal and disease-control subjects. J. Clin. Invest. 100: 2588-2595, 1997.
-
(1997)
J. Clin. Invest.
, vol.100
, pp. 2588-2595
-
-
Knowles, M.R.1
Robinson, J.M.2
Wood, R.E.3
Pue, C.A.4
Mentz, W.M.5
Wager, G.C.6
Gatsy, J.T.7
Boucher, R.C.8
-
151
-
-
0020610435
-
Abnormal ion permeation through cystic fibrosis respiratory epithelium
-
KNOWLES, M. R., M. J. STUTTS, A. SPOCK, N. FISCHER, J. T. GATZY, AND R. C. BOUCHER. Abnormal ion permeation through cystic fibrosis respiratory epithelium. Science 221: 1067-1070, 1983.
-
(1983)
Science
, vol.221
, pp. 1067-1070
-
-
Knowles, M.R.1
Stutts, M.J.2
Spock, A.3
Fischer, N.4
Gatzy, J.T.5
Boucher, R.C.6
-
153
-
-
0018216627
-
Cystic fibrosis compared with the immotile-cilia syndrome. A study of mucociliary clearance, ciliary ultrastructure, clinical picture, and ventilatory function
-
KOLLBERG, H., B. MOSSBERG, B. A AFZELIUS, K. PHILIPSON, AND P. CAMNER. Cystic fibrosis compared with the immotile-cilia syndrome. A study of mucociliary clearance, ciliary ultrastructure, clinical picture, and ventilatory function. Scand. J. Respir. Dis. 59: 297-306, 1978.
-
(1978)
Scand. J. Respir. Dis.
, vol.59
, pp. 297-306
-
-
Kollberg, H.1
Mossberg, B.2
Afzelius, B.A.3
Philipson, K.4
Camner, P.5
-
154
-
-
0023185422
-
Role of sialic acid in saliva-mediated aggregation of Pseudomonas aeruginosa isolated from cystic fibrosis patients
-
KOMIYAMA, K., B. F. HABBICK, AND S. K. TUMBER. Role of sialic acid in saliva-mediated aggregation of Pseudomonas aeruginosa isolated from cystic fibrosis patients. Infect. Immun. 55: 2364-2369, 1987.
-
(1987)
Infect. Immun.
, vol.55
, pp. 2364-2369
-
-
Komiyama, K.1
Habbick, B.F.2
Tumber, S.K.3
-
155
-
-
0001278692
-
Infection and inflammation of the lung in cystic fibrosis
-
edited by P. B. Davis. New York: Dekker
-
KONSTAN, M. W., AND M. BERGER. Infection and inflammation of the lung in cystic fibrosis. In: Cystic Fibrosis. Lung Biology in Health and Disease, edited by P. B. Davis. New York: Dekker, 1993, p. 219-275.
-
(1993)
Cystic Fibrosis. Lung Biology in Health and Disease
, pp. 219-275
-
-
Konstan, M.W.1
Berger, M.2
-
156
-
-
0028015883
-
Bronchoalveolar lavage findings in cystic fibrosis patients with stable, clinically mild lung disease suggest ongoing infection and inflammation
-
KONSTAN, M. W., K. A. HILLIARD, T. M. NORVELL, AND M. BERGER. Bronchoalveolar lavage findings in cystic fibrosis patients with stable, clinically mild lung disease suggest ongoing infection and inflammation. Am. J. Respir. Crit. Care Med. 150: 448-454, 1994.
-
(1994)
Am. J. Respir. Crit. Care Med.
, vol.150
, pp. 448-454
-
-
Konstan, M.W.1
Hilliard, K.A.2
Norvell, T.M.3
Berger, M.4
-
157
-
-
0023856867
-
Pseudomonas aeruginosa and Pseudamonas cepacia isolated from cystic fibrosis patients bind specifically to gangliotetraosylceramide (asialo GM1) and gangliotriaosylceramide (asialo GM2)
-
KRIVAN, H. B., V. GINSBURG, AND D. D. ROBERTS. Pseudomonas aeruginosa and Pseudamonas cepacia isolated from cystic fibrosis patients bind specifically to gangliotetraosylceramide (asialo GM1) and gangliotriaosylceramide (asialo GM2). Arch. Biochem. Biophys. 260: 493-496, 1988.
-
(1988)
Arch. Biochem. Biophys.
, vol.260
, pp. 493-496
-
-
Krivan, H.B.1
Ginsburg, V.2
Roberts, D.D.3
-
158
-
-
0011680902
-
Many pulmonary pathogenic bacteria bind specifically to the carbohydrate sequence GalNAcb1-4Gal found in some glycolipids
-
KRIVAN, H. C., D. D. ROBERTS, AND V. GINSBURG. Many pulmonary pathogenic bacteria bind specifically to the carbohydrate sequence GalNAcb1-4Gal found in some glycolipids. Proc. Natl. Acad. Sci. USA 85: 6157-6161, 1988.
-
(1988)
Proc. Natl. Acad. Sci. USA
, vol.85
, pp. 6157-6161
-
-
Krivan, H.C.1
Roberts, D.D.2
Ginsburg, V.3
-
159
-
-
0027409808
-
Genetic determinants of airways colonization with Pseudomonas aeruginosa in cystic fibrosis
-
KUBESCH, P., T. DORK, U. WULBRAND, N. KALIN, T. NEUMANN, B. WULF, H. GEERLINGS, H. WEIBRODT, H. VON DER HARDT, AND B. TUMMLER. Genetic determinants of airways colonization with Pseudomonas aeruginosa in cystic fibrosis. Lancet 341: 189-193, 1993.
-
(1993)
Lancet
, vol.341
, pp. 189-193
-
-
Kubesch, P.1
Dork, T.2
Wulbrand, U.3
Kalin, N.4
Neumann, T.5
Wulf, B.6
Geerlings, H.7
Weibrodt, H.8
Von Der Hardt, H.9
Tummler, B.10
-
160
-
-
0024352013
-
Characterization of K channels in respiratory cells. I. General properties
-
KUNZELMANN, K., H. PAVENSTAEDT, C. BECK, O. UENAL, P. EMMRICH, H. J. ARNDT, AND R. GREGER. Characterization of K channels in respiratory cells. I. General properties. Pflügers Arch. 414: 291-296, 1989.
-
(1989)
Pflügers Arch.
, vol.414
, pp. 291-296
-
-
Kunzelmann, K.1
Pavenstaedt, H.2
Beck, C.3
Uenal, O.4
Emmrich, P.5
Arndt, H.J.6
Greger, R.7
-
161
-
-
0342579142
-
Characterization of K channels in respiratory cells. II. Inhibitors and regulation
-
KUNZELMANN, K., H. PAVENSTAEDT, AND R. GREGER. Characterization of K channels in respiratory cells. II. Inhibitors and regulation. Pflügers Arch. 414: 297-303, 1989.
-
(1989)
Pflügers Arch.
, vol.414
, pp. 297-303
-
-
Kunzelmann, K.1
Pavenstaedt, H.2
Greger, R.3
-
162
-
-
0028061411
-
Constitutive mucin secretion linked to CFTR expression
-
KUVER, R., N. RAMESH, S. LAU, C. SAVARD, S. P. LEE, AND W. R. A. OSBORNE. Constitutive mucin secretion linked to CFTR expression. Biochem. Biophys. Res. Commun. 203: 1457-1462, 1994.
-
(1994)
Biochem. Biophys. Res. Commun.
, vol.203
, pp. 1457-1462
-
-
Kuver, R.1
Ramesh, N.2
Lau, S.3
Savard, C.4
Lee, S.P.5
Osborne, W.R.A.6
-
163
-
-
0028317428
-
PGE generates intracellular cAMP and accelerates mucin secretion by cultured dog gallbladder epithelial cells
-
KUVER, R., C. SAVARD, D. ODA, AND S. P. LEE. PGE generates intracellular cAMP and accelerates mucin secretion by cultured dog gallbladder epithelial cells. Am. J. Physiol. 267 (Gastrointest. Liver Physiol. 30): G998-G1003, 1994.
-
(1994)
Am. J. Physiol. 267 (Gastrointest. Liver Physiol. 30)
, vol.267
-
-
Kuver, R.1
Savard, C.2
Oda, D.3
Lee, S.P.4
-
164
-
-
0022416735
-
Possible function of bronchial surfactant
-
LACHMANN, B. Possible function of bronchial surfactant. Eur. J. Respir. Dis. 67: 49-60, 1985.
-
(1985)
Eur. J. Respir. Dis.
, vol.67
, pp. 49-60
-
-
Lachmann, B.1
-
165
-
-
0022526266
-
Mechanics of lung fluid balance
-
LAI-FOOK, S. J. Mechanics of lung fluid balance. Crit. Rev. Biomed. Eng. 13: 171-200, 1986.
-
(1986)
Crit. Rev. Biomed. Eng.
, vol.13
, pp. 171-200
-
-
Lai-Fook, S.J.1
-
167
-
-
0031943230
-
Evidence that Calu-3 human airway cells secrete bicarbonate
-
LEE, M. C., C. M. PENLAND, J. H. WIDDICOMBE, AND J. J. WINE, Evidence that Calu-3 human airway cells secrete bicarbonate. Am. J. Physiol. 274 (Lung Cell. Mol. Physiol. 18): L450-L453, 1998.
-
(1998)
Am. J. Physiol. 274 (Lung Cell. Mol. Physiol. 18)
, vol.274
-
-
Lee, M.C.1
Penland, C.M.2
Widdicombe, J.H.3
Wine, J.J.4
-
168
-
-
0030973385
-
Genomic organization and developmental expression of aquaporin-5 in lung
-
LEE, M. D., L. S. KING, S. NIELSEN, AND P. AGRE. Genomic organization and developmental expression of aquaporin-5 in lung. Chest 111, Suppl.: 111S-113S, 1997.
-
(1997)
Chest
, vol.111
, Issue.SUPPL.
-
-
Lee, M.D.1
King, L.S.2
Nielsen, S.3
Agre, P.4
-
169
-
-
0026787649
-
Secretion stimulates bile ductular secretory activity through the cAMP system
-
LENZEN, R., G. ALPINI, AND N. TAVALONI. Secretion stimulates bile ductular secretory activity through the cAMP system. Am. J. Physiol. 263 (Gastrointest, Liver Physiol. 26): G527-G532, 1992.
-
(1992)
Am. J. Physiol. 263 (Gastrointest, Liver Physiol. 26)
, vol.263
-
-
Lenzen, R.1
Alpini, G.2
Tavaloni, N.3
-
170
-
-
0024990329
-
The role of mucous glycoproteins in the rhelogic properties of cystic fibrosis sputum
-
LETHEM, M. I., S. L. JAMES, AND C. MARRIOTT. The role of mucous glycoproteins in the rhelogic properties of cystic fibrosis sputum. Am. Rev. Respir. Dis. 142: 1053-1058, 1990.
-
(1990)
Am. Rev. Respir. Dis.
, vol.142
, pp. 1053-1058
-
-
Lethem, M.I.1
James, S.L.2
Marriott, C.3
-
171
-
-
0027483610
-
The cystic fibrosis mutation delta F508 does not influence Cl channel activity of CFTR
-
LI, C. L., M. RAMJEESING, E. REYES, T. JENSEN, X. CHANG, J. M. ROMMENS, AND C. E. BEAR. The cystic fibrosis mutation delta F508 does not influence Cl channel activity of CFTR. Nature Genet. 3: 311-316, 1993.
-
(1993)
Nature Genet.
, vol.3
, pp. 311-316
-
-
Li, C.L.1
Ramjeesing, M.2
Reyes, E.3
Jensen, T.4
Chang, X.5
Rommens, J.M.6
Bear, C.E.7
-
173
-
-
0028264035
-
Cystic fibrosis transmembrane conductance regulator mutations that disrupt nucleotide binding
-
LOGAN, J., D. HIESTAND, P. DARAM, Z. HUANG, D. D. MUCCIO, J. HARTMAN, B. HALEY, W. J. COOK, AND E. J. SORSCHER. Cystic fibrosis transmembrane conductance regulator mutations that disrupt nucleotide binding. J. Clin. Invest. 94: 228-236, 1994.
-
(1994)
J. Clin. Invest.
, vol.94
, pp. 228-236
-
-
Logan, J.1
Hiestand, D.2
Daram, P.3
Huang, Z.4
Muccio, D.D.5
Hartman, J.6
Haley, B.7
Cook, W.J.8
Sorscher, E.J.9
-
174
-
-
0001634030
-
Principles underlying ciliary activity in the respiratory tract. II. A comparison of nasal clearance in man, monkey and other mammals
-
LUCAS, A. M., AND L. C. DOUGLAS. Principles underlying ciliary activity in the respiratory tract. II. A comparison of nasal clearance in man, monkey and other mammals. Arch. Otolaryngol. 230: 518-541, 1994.
-
(1994)
Arch. Otolaryngol.
, vol.230
, pp. 518-541
-
-
Lucas, A.M.1
Douglas, L.C.2
-
175
-
-
0026777811
-
The cystic fibrosis transmembrane conductance regulator is present and functional in endosomes: Role as a determinant of endosomal pH
-
LUKACS, G. L., X. B. CHANG, N. KARTNER, O. D. ROTSTEIN, J. R. RIORDAN, AND S. GRINSTEIN. The cystic fibrosis transmembrane conductance regulator is present and functional in endosomes: role as a determinant of endosomal pH. J. Biol. Chem. 267: 14568-14572, 1992.
-
(1992)
J. Biol. Chem.
, vol.267
, pp. 14568-14572
-
-
Lukacs, G.L.1
Chang, X.B.2
Kartner, N.3
Rotstein, O.D.4
Riordan, J.R.5
Grinstein, S.6
-
176
-
-
0024518394
-
Characterization of beta-adrenergic receptors in cultured bovine tracheal gland cells
-
MADISON, J. M., C. B. BASBAUM, J. K. BROWN, AND W. E. FINKBEINER. Characterization of beta-adrenergic receptors in cultured bovine tracheal gland cells. Am. J. Physiol. 256 (Cell Physiol. 25): C310-C314, 1989.
-
(1989)
Am. J. Physiol. 256 (Cell Physiol. 25)
, vol.256
-
-
Madison, J.M.1
Basbaum, C.B.2
Brown, J.K.3
Finkbeiner, W.E.4
-
177
-
-
0018622980
-
Changes in the gel properties of tracheal mucus induced by divalent cations
-
MARRIOTT, C., C. K. SHIH, AND M. LITT. Changes in the gel properties of tracheal mucus induced by divalent cations. Biorheology 16: 331-337 1979.
-
(1979)
Biorheology
, vol.16
, pp. 331-337
-
-
Marriott, C.1
Shih, C.K.2
Litt, M.3
-
178
-
-
0020463366
-
Transepithelial transport by pulmonary alveolar type II cells in primary culture
-
MASON, R. J., M. C. WILLIAMS, J. H. WIDDICOMBE, M. J. SANDERS, D. S. MISFELDT, AND L. C. BERRY. Transepithelial transport by pulmonary alveolar type II cells in primary culture. Proc. Natl. Acad. Sci. USA 79: 6033-6037, 1982.
-
(1982)
Proc. Natl. Acad. Sci. USA
, vol.79
, pp. 6033-6037
-
-
Mason, R.J.1
Williams, M.C.2
Widdicombe, J.H.3
Sanders, M.J.4
Misfeldt, D.S.5
Berry, L.C.6
-
179
-
-
0025845558
-
Regulation of transepithelial ion transport and intracellular calcium by extra-cellular adenosine triphosphate in human normal and cystic fibrosis airway epithelium
-
MASON, S. J., A. M. PARADISO, AND R. C. BOUCHER. Regulation of transepithelial ion transport and intracellular calcium by extra-cellular adenosine triphosphate in human normal and cystic fibrosis airway epithelium. J. Pharmacol. 103: 1649-1656, 1991.
-
(1991)
J. Pharmacol.
, vol.103
, pp. 1649-1656
-
-
Mason, S.J.1
Paradiso, A.M.2
Boucher, R.C.3
-
180
-
-
0032530370
-
Coordinated clearance of periciliary liquid and mucus from airway surfaces
-
MATSUI, H., S. H. RANDELL, S. W. PERETTI, C. W. DAVIS, AND R. C. BOUCHER. Coordinated clearance of periciliary liquid and mucus from airway surfaces. J. Clin. Invest. 102:1125-1131, 1998.
-
(1998)
J. Clin. Invest.
, vol.102
, pp. 1125-1131
-
-
Matsui, H.1
Randell, S.H.2
Peretti, S.W.3
Davis, C.W.4
Boucher, R.C.5
-
182
-
-
75549102827
-
Studies on pulmonary secretions. I. The overall chemical composition of pulmonary secretions from patients with cystic fibrosis, bronchiectasis, and laryngectomy
-
MATTHEWS, L. W., S. SPECTOR, J. LEMM, AND J. L. POTTER. Studies on pulmonary secretions. I. The overall chemical composition of pulmonary secretions from patients with cystic fibrosis, bronchiectasis, and laryngectomy. Am. Rev. Respir. Dis. 88: 199-204, 1963.
-
(1963)
Am. Rev. Respir. Dis.
, vol.88
, pp. 199-204
-
-
Matthews, L.W.1
Spector, S.2
Lemm, J.3
Potter, J.L.4
-
183
-
-
0025345720
-
+ channels in airway epithelia. II. Role in Cl secretion and evidence for two types of K channel
-
+ channels in airway epithelia. II. Role in Cl secretion and evidence for two types of K channel. Am. J. Physiol. 258 (Lung Cell. Mol. Physiol. 2): L343-L348, 1990.
-
(1990)
Am. J. Physiol. 258 (Lung Cell. Mol. Physiol. 2)
, vol.258
-
-
McCann, J.D.1
Welsh, M.J.2
-
184
-
-
0026628384
-
Expression of CFTR and presence of cAMP-mediated fluid secretion in human fetal lung
-
McCRAY, P. B., W. W. REENSTRA, E. LOUIE, J. JOHNSON, J. D. BETTENCOURT, AND J. BASTACKY. Expression of CFTR and presence of cAMP-mediated fluid secretion in human fetal lung. Am. J. Physiol. 262 (Lung Cell. Mol. Physiol. 6): L472-L481, 1992.
-
(1992)
Am. J. Physiol. 262 (Lung Cell. Mol. Physiol. 6)
, vol.262
-
-
McCray, P.B.1
Reenstra, W.W.2
Louie, E.3
Johnson, J.4
Bettencourt, J.D.5
Bastacky, J.6
-
185
-
-
0028831875
-
Viscoelastic properties of human tracheobronchial mucin in aqueous solution
-
McCULLAGH, C. M., A. M. JAMIESON, J. BLACKWELL, AND R. GUPTA. Viscoelastic properties of human tracheobronchial mucin in aqueous solution. Biopolymers 35: 149-159, 1995.
-
(1995)
Biopolymers
, vol.35
, pp. 149-159
-
-
McCullagh, C.M.1
Jamieson, A.M.2
Blackwell, J.3
Gupta, R.4
-
186
-
-
0027546872
-
Cystic fibrosis gene and protein expression during fetal lung development
-
McGRATH, S. A., A. BASU, AND P. L. ZEITLIN. Cystic fibrosis gene and protein expression during fetal lung development. Am. J. Respir. Cell. Mol. Biol. 8: 201-208, 1993.
-
(1993)
Am. J. Respir. Cell. Mol. Biol.
, vol.8
, pp. 201-208
-
-
McGrath, S.A.1
Basu, A.2
Zeitlin, P.L.3
-
187
-
-
0028456277
-
Cell number and distribution in human and rat airways
-
MERCER, R. R., M. L. RUSSELL, V. L. ROGGLI, AND J. D. CRAPO. Cell number and distribution in human and rat airways. Am. J. Respir. Cell Mol. Biol. 10: 613-624, 1994.
-
(1994)
Am. J. Respir. Cell Mol. Biol.
, vol.10
, pp. 613-624
-
-
Mercer, R.R.1
Russell, M.L.2
Roggli, V.L.3
Crapo, J.D.4
-
188
-
-
0029621143
-
CFTR gene transfer corrects defective glycoconjugate secretion in human CF epithelial tracheal cells
-
MERGEY, M., M. LEMNAOUAR, D. VEISSIERE, M. PERRICAUDET, D. C. GRUENERT, J. PICARD, J. CAPEAU, M.-C. BRAHIMI-HORN, AND A. PAUL. CFTR gene transfer corrects defective glycoconjugate secretion in human CF epithelial tracheal cells. Am. J. Physiol. 269 (Lung Cell. Mol. Physiol. 13): L855-L864, 1995.
-
(1995)
Am. J. Physiol. 269 (Lung Cell. Mol. Physiol. 13)
, vol.269
-
-
Mergey, M.1
Lemnaouar, M.2
Veissiere, D.3
Perricaudet, M.4
Gruenert, D.C.5
Picard, J.6
Capeau, J.7
Brahimi-Horn, M.-C.8
Paul, A.9
-
189
-
-
0014840076
-
Ultrastructure of celss in human bronchial submucosal glands
-
MEYRICK, B., AND L. REID. Ultrastructure of celss in human bronchial submucosal glands. J. Anat. 107: 291-299, 1970.
-
(1970)
J. Anat.
, vol.107
, pp. 291-299
-
-
Meyrick, B.1
Reid, L.2
-
190
-
-
0014599770
-
A reconstruction of the duct system and secretory tubules of the human bronchial submucosal gland
-
MEYRICK, B., J. M. STURGESS, AND L. REID. A reconstruction of the duct system and secretory tubules of the human bronchial submucosal gland. Thorax 24: 729-736, 1969.
-
(1969)
Thorax
, vol.24
, pp. 729-736
-
-
Meyrick, B.1
Sturgess, J.M.2
Reid, L.3
-
191
-
-
0020485130
-
Factors influencing the viscous properties of chicken tracheal mucins
-
MIAN, N., A. J. POPE, C. E. ANDERSON, AND P. W. KENT. Factors influencing the viscous properties of chicken tracheal mucins. Biochim. Biophys. Acta 717: 41-48, 1982.
-
(1982)
Biochim. Biophys. Acta
, vol.717
, pp. 41-48
-
-
Mian, N.1
Pope, A.J.2
Anderson, C.E.3
Kent, P.W.4
-
192
-
-
0026473068
-
An antibody against a CFTR-derived synthetic peptide, incorporated into living submandibular cells, inhibits beta-adrenergic stimulation of mucin secretion
-
MILLS, C. L., M. M. C. PEREIRA, R. L. DORMER, AND M. A. McPHERSON. An antibody against a CFTR-derived synthetic peptide, incorporated into living submandibular cells, inhibits beta-adrenergic stimulation of mucin secretion. Biochem. Biophys. Res. Commun. 188: 1146-1152, 1992.
-
(1992)
Biochem. Biophys. Res. Commun.
, vol.188
, pp. 1146-1152
-
-
Mills, C.L.1
Pereira, M.M.C.2
Dormer, R.L.3
McPherson, M.A.4
-
193
-
-
0029016145
-
Alteration of sulfation of glycoconjugates, but not sulfate transport and intracellular inorganic sulfate content, in cystic fibrosis airway epithelial cells
-
MOHAPATRA, N. K., P.-W. CHENG, J. C. PARKER, A. M. PARADISO, J. R. YANKASKAS, R. C. BOUCHER, AND T. F. BOAT. Alteration of sulfation of glycoconjugates, but not sulfate transport and intracellular inorganic sulfate content, in cystic fibrosis airway epithelial cells. Pediatr. Res. 38: 42-48, 1995.
-
(1995)
Pediatr. Res.
, vol.38
, pp. 42-48
-
-
Mohapatra, N.K.1
Cheng, P.-W.2
Parker, J.C.3
Paradiso, A.M.4
Yankaskas, J.R.5
Boucher, R.C.6
Boat, T.F.7
-
194
-
-
0031416788
-
Calcium-stimulated Cl-secretion in Calu-3 human airway cells requires CFTR
-
MOON, S., M. SINGH, M. E. KROUSE, AND J. J. WINE. Calcium-stimulated Cl-secretion in Calu-3 human airway cells requires CFTR. Am. J. Physiol. 273 (Lung Cell. Mol. Physiol. 17): L1208-L1219, 1997.
-
(1997)
Am. J. Physiol. 273 (Lung Cell. Mol. Physiol. 17)
, vol.273
-
-
Moon, S.1
Singh, M.2
Krouse, M.E.3
Wine, J.J.4
-
195
-
-
0014162745
-
Observations on the basophilia of amyloids
-
MOWRY, R. W., AND J. E. SCOTT. Observations on the basophilia of amyloids. Histochemie 10: 8-32, 1967.
-
(1967)
Histochemie
, vol.10
, pp. 8-32
-
-
Mowry, R.W.1
Scott, J.E.2
-
196
-
-
0025887417
-
Modulation of coated vesicle Cl channel activity and acidification by reversible protein kinase A-dependent phosphorylation
-
MULBERG, A. E., B. M. TULK, AND M. FORGAC. Modulation of coated vesicle Cl channel activity and acidification by reversible protein kinase A-dependent phosphorylation. J. Biol. Chem. 266: 20590-20593, 1991.
-
(1991)
J. Biol. Chem.
, vol.266
, pp. 20590-20593
-
-
Mulberg, A.E.1
Tulk, B.M.2
Forgac, M.3
-
197
-
-
0029316542
-
ClC-2: A developmentally regulated Cl channel expressed in fetal lung and downregulated after birth
-
MURRAY, C. B., M. M. MORALES, T. R. FLOTTE, S. A. McGRATH-MORROW, W. B. GUGGINO, AND P. L. ZEITLIN. ClC-2: a developmentally regulated Cl channel expressed in fetal lung and downregulated after birth. Am. J. Respir. Cell Mol. Biol. 12: 597-604, 1995.
-
(1995)
Am. J. Respir. Cell Mol. Biol.
, vol.12
, pp. 597-604
-
-
Murray, C.B.1
Morales, M.M.2
Flotte, T.R.3
McGrath-Morrow, S.A.4
Guggino, W.B.5
Zeitlin, P.L.6
-
198
-
-
0030657804
-
Aquaporins in complex tissues. II. Subcellular distribution in respiratory and glandular tissues of rat
-
NIELSEN, S., L. S. KING, B. M. CHRISTENSEN, AND P. AGRE. Aquaporins in complex tissues. II. Subcellular distribution in respiratory and glandular tissues of rat. Am. J. Physiol. 273 (Cell Physiol. 42): C1549-C1561, 1997.
-
(1997)
Am. J. Physiol. 273 (Cell Physiol. 42)
, vol.273
-
-
Nielsen, S.1
King, L.S.2
Christensen, B.M.3
Agre, P.4
-
199
-
-
0023920052
-
Properties of the luminal membrane of isolated perfused rat pancretic ducts: Effect of cyclic AMP and blockers of chloride transport
-
NOVAK, I., AND R. GREGER. Properties of the luminal membrane of isolated perfused rat pancretic ducts: effect of cyclic AMP and blockers of chloride transport. Pflügers Arch. 411: 546-553, 1988.
-
(1988)
Pflügers Arch.
, vol.411
, pp. 546-553
-
-
Novak, I.1
Greger, R.2
-
200
-
-
0031964259
-
Destruction and loss of bronchial cartilage in cystic fibrosis
-
OGRINC, G., B. KAMPALATH, AND J. F. TOMASHEFSKI, JR. Destruction and loss of bronchial cartilage in cystic fibrosis. Hum. Pathol. 29: 65-73, 1998.
-
(1998)
Hum. Pathol.
, vol.29
, pp. 65-73
-
-
Ogrinc, G.1
Kampalath, B.2
Tomashefski J.F., Jr.3
-
201
-
-
0019811260
-
Similarity of the tracheobronchial mucous glands and epithelium in infants with and without cystic fibrosis
-
OPPENHEIMER, E. H. Similarity of the tracheobronchial mucous glands and epithelium in infants with and without cystic fibrosis. Hum. Pathol. 12: 36-48, 1981.
-
(1981)
Hum. Pathol.
, vol.12
, pp. 36-48
-
-
Oppenheimer, E.H.1
-
202
-
-
0016417460
-
Pathology of cystic fibrosis: Review of the literature and comparison with 146 autopsied cases
-
OPPENHEIMER, E. H., AND J. R. ESTERLY. Pathology of cystic fibrosis: review of the literature and comparison with 146 autopsied cases. Perspect. Pediatr. Pathol. 2: 241-278, 1975.
-
(1975)
Perspect. Pediatr. Pathol.
, vol.2
, pp. 241-278
-
-
Oppenheimer, E.H.1
Esterly, J.R.2
-
203
-
-
0023629643
-
Pathological confirmation of cystic fibrosis in the fetus following prenatal diagnosis
-
ORNOY, A., J. ARNON, D. KATZNELSON, M. GRANAT, B. SACPI, AND J. CHEMKE. Pathological confirmation of cystic fibrosis in the fetus following prenatal diagnosis. Am. J. Med. Genet. 28: 935-947, 1987.
-
(1987)
Am. J. Med. Genet.
, vol.28
, pp. 935-947
-
-
Ornoy, A.1
Arnon, J.2
Katznelson, D.3
Granat, M.4
Sacpi, B.5
Chemke, J.6
-
204
-
-
0027313337
-
In vitro study of the bronchial mucosa during Pseudomonas aeruginosa infection
-
PHILIPPON, S., H. J. STRECKERT, AND K. MORGENROTH. In vitro study of the bronchial mucosa during Pseudomonas aeruginosa infection. Virchows Arch. A Pathol. Anal. 423: 39-43, 1993.
-
(1993)
Virchows Arch. A Pathol. Anal.
, vol.423
, pp. 39-43
-
-
Philippon, S.1
Streckert, H.J.2
Morgenroth, K.3
-
205
-
-
0017892815
-
Pus, deoxyribonucleic acid, and sputum viscosity
-
PICOT, R., L. DAS, AND L. REID. Pus, deoxyribonucleic acid, and sputum viscosity. Thorax 33: 235-242, 1978.
-
(1978)
Thorax
, vol.33
, pp. 235-242
-
-
Picot, R.1
Das, L.2
Reid, L.3
-
206
-
-
0026589342
-
Work of adhesion of respiratory tract mucus
-
PILLAI, R. S., T. CHANDRA, I. F. MILER, J. LLOYD-STILL, AND D. B. YEATES. Work of adhesion of respiratory tract mucus. J. Appl. Physiol 72: 1604-1610, 1992.
-
(1992)
J. Appl. Physiol
, vol.72
, pp. 1604-1610
-
-
Pillai, R.S.1
Chandra, T.2
Miler, I.F.3
Lloyd-Still, J.4
Yeates, D.B.5
-
207
-
-
0026543277
-
Epithelial respiratory cells from cystic fibrosis patients do not possess specific Pseudomonas aeruginosa-adhesive properties
-
PLOTKOWSKI, M. C., M. CHEVILLARD, D. PIERROT, D. ALTEMAYER, AND E. PUCHELLE. Epithelial respiratory cells from cystic fibrosis patients do not possess specific Pseudomonas aeruginosa-adhesive properties. J. Med. Microbiol. 36: 104-111, 1992.
-
(1992)
J. Med. Microbiol.
, vol.36
, pp. 104-111
-
-
Plotkowski, M.C.1
Chevillard, M.2
Pierrot, D.3
Altemayer, D.4
Puchelle, E.5
-
208
-
-
0026006325
-
Differential adhesion of Pseudomonas aeruginosa to human respiratory epithelial cells in primary culture
-
PLOTKOWSKI, M. C., M. CHEVILLARD, D. PIERROT, D. ALTERNMAYER, J. M. ZAHM, G. COLLIOT, AND E. PUCHELLE. Differential adhesion of Pseudomonas aeruginosa to human respiratory epithelial cells in primary culture. J. Clin. Invest. 87: 2018-2028, 1991.
-
(1991)
J. Clin. Invest.
, vol.87
, pp. 2018-2028
-
-
Plotkowski, M.C.1
Chevillard, M.2
Pierrot, D.3
Alternmayer, D.4
Zahm, J.M.5
Colliot, G.6
Puchelle, E.7
-
209
-
-
0023901499
-
Familial psuedohypoaldosteronism
-
POPOW, C., A. POLLAK, K. HERKNER, S. SCHEIBENREITER, AND W. SWOBADA. Familial psuedohypoaldosteronism. Acta Paediatr. Scand. 77: 136-141, 1988.
-
(1988)
Acta Paediatr. Scand.
, vol.77
, pp. 136-141
-
-
Popow, C.1
Pollak, A.2
Herkner, K.3
Scheibenreiter, S.4
Swobada, W.5
-
210
-
-
0014108774
-
Studies on pulmonary secretions. II. Osmolality and the ionic environment of pulmonary secretions from patients with cystic fibrosis, bronchiectasis, and laryngectomy
-
POTTER, J. L., L. W. MATTHEWS, S. SPECTOR, AND J. LEMM. Studies on pulmonary secretions. II. Osmolality and the ionic environment of pulmonary secretions from patients with cystic fibrosis, bronchiectasis, and laryngectomy. Am. Rev. Respir. Dis. 96: 83-87, 1967.
-
(1967)
Am. Rev. Respir. Dis.
, vol.96
, pp. 83-87
-
-
Potter, J.L.1
Matthews, L.W.2
Spector, S.3
Lemm, J.4
-
211
-
-
0026935273
-
Adhesins and receptors of Pseudomonas aeruginosa associated with infection of the respiratory tract
-
PRINCE, A. Adhesins and receptors of Pseudomonas aeruginosa associated with infection of the respiratory tract. Microbial Pathogenesis 13: 251-260, 1992.
-
(1992)
Microbial Pathogenesis
, vol.13
, pp. 251-260
-
-
Prince, A.1
-
213
-
-
0028236014
-
Rapid endocytosis of the cystic fibrosis transmembrane conductance regulator Cl channel
-
PRINCE, L. S., R. B. WORKMAN, AND R. B. MARCHASE. Rapid endocytosis of the cystic fibrosis transmembrane conductance regulator Cl channel. Cell Biol. 91: 5192-5196, 1994.
-
(1994)
Cell Biol.
, vol.91
, pp. 5192-5196
-
-
Prince, L.S.1
Workman, R.B.2
Marchase, R.B.3
-
214
-
-
0017610710
-
The upper airways. I. Nasal physiology and defense of the lungs
-
PROCTOR, D. F. The upper airways. I. Nasal physiology and defense of the lungs. Am. Rev. Respir. Dis. 115: 97-130, 1977.
-
(1977)
Am. Rev. Respir. Dis.
, vol.115
, pp. 97-130
-
-
Proctor, D.F.1
-
215
-
-
0022380149
-
Rheological and transport properties of airway secretions in cystic fibrosis relationships with the degree of infection and severity of the disease
-
PUCHELLE, E., J. JACQUOT, G. BECK, J. M. ZAHM, AND C. GALABERT. Rheological and transport properties of airway secretions in cystic fibrosis relationships with the degree of infection and severity of the disease. Eur. J. Clin. Invest. 15: 389-394, 1985.
-
(1985)
Eur. J. Clin. Invest.
, vol.15
, pp. 389-394
-
-
Puchelle, E.1
Jacquot, J.2
Beck, G.3
Zahm, J.M.4
Galabert, C.5
-
216
-
-
0020619697
-
The frog palate for studying mucociliary transport and velocity and mucociliary frequency
-
PUCHELLE, E., J. M. TOURNIER, AND A. PETIT. The frog palate for studying mucociliary transport and velocity and mucociliary frequency. Eur. J. Respir. Dis. 64: 293-303, 1983.
-
(1983)
Eur. J. Respir. Dis.
, vol.64
, pp. 293-303
-
-
Puchelle, E.1
Tournier, J.M.2
Petit, A.3
-
217
-
-
0018704394
-
Composition and control of secretions from tracheal bronchial submucosal glands
-
QUINTON, P. M. Composition and control of secretions from tracheal bronchial submucosal glands. Nature 279: 551-552, 1979.
-
(1979)
Nature
, vol.279
, pp. 551-552
-
-
Quinton, P.M.1
-
218
-
-
0025349031
-
Cystic fibrosis: A disease in electrolyte transport
-
QUINTON, P. M. Cystic fibrosis: a disease in electrolyte transport. FASEB J. 4: 2709-2717, 1990.
-
(1990)
FASEB J.
, vol.4
, pp. 2709-2717
-
-
Quinton, P.M.1
-
219
-
-
0028097887
-
Viscosity versus composition in airway pathology
-
QUINTON, P. M. Viscosity versus composition in airway pathology. Am. J. Respir. Crit. Care Med. 149: 6-7, 1994.
-
(1994)
Am. J. Respir. Crit. Care Med.
, vol.149
, pp. 6-7
-
-
Quinton, P.M.1
-
220
-
-
0025976345
-
Pseudomonas aeruginosa recognizes carbohydrate chains containing type 1 (Gal beta 1-3GlcNAc) or type 2 (Gal beta 1-4GlcNAc) disaccharide units
-
RAMPHAL, R., C. CARNOY, S. FIEVRE, J. C. MICHALSKI, N. HOUDRET, G. LAMBLIN, G. STRECKER, AND P. ROUSSEL. Pseudomonas aeruginosa recognizes carbohydrate chains containing type 1 (Gal beta 1-3GlcNAc) or type 2 (Gal beta 1-4GlcNAc) disaccharide units. Infect. Immun. 59: 700-704, 1991.
-
(1991)
Infect. Immun.
, vol.59
, pp. 700-704
-
-
Ramphal, R.1
Carnoy, C.2
Fievre, S.3
Michalski, J.C.4
Houdret, N.5
Lamblin, G.6
Strecker, G.7
Roussel, P.8
-
221
-
-
0024417494
-
Differences in adhesion of Pseudomonas aeruginosa to mucin glycopeptides from sputa of patients with cystic fibrosis and chronic bronchitis
-
RAMPHAL, R., N. HOUDRET, L. KOO, G. LAMBLIN, AND P. ROUSSEL Differences in adhesion of Pseudomonas aeruginosa to mucin glycopeptides from sputa of patients with cystic fibrosis and chronic bronchitis. Infect. Immun. 57: 3066-3071, 1989.
-
(1989)
Infect. Immun.
, vol.57
, pp. 3066-3071
-
-
Ramphal, R.1
Houdret, N.2
Koo, L.3
Lamblin, G.4
Roussel, P.5
-
222
-
-
0026082010
-
Adhesion of Pseudomonas aeruginosa pilin-deficient mutants to mucin
-
RAMPHAL, R., L. KOO, K. S. ISHIMOTO, P. A. TOTTEN, J. C. LARA, AND S. LORY. Adhesion of Pseudomonas aeruginosa pilin-deficient mutants to mucin. Infect. Immun. 59: 1307-1311, 1991.
-
(1991)
Infect. Immun.
, vol.59
, pp. 1307-1311
-
-
Ramphal, R.1
Koo, L.2
Ishimoto, K.S.3
Totten, P.A.4
Lara, J.C.5
Lory, S.6
-
223
-
-
0020631367
-
Evidence for mucins and sialic acid as receptors for Pseudomonas aeruginosa in the lower respiratory tract
-
RAMPHAL, R., AND M. PYLE. Evidence for mucins and sialic acid as receptors for Pseudomonas aeruginosa in the lower respiratory tract. Infect. Immun. 41: 339-344, 1983.
-
(1983)
Infect. Immun.
, vol.41
, pp. 339-344
-
-
Ramphal, R.1
Pyle, M.2
-
224
-
-
34249767036
-
Rapid regulation of electrolyte absorption in sweat duct
-
REDDY, M. M., AND P. M. QUINTON. Rapid regulation of electrolyte absorption in sweat duct. J. Membr. Biol. 140: 57-67, 1994.
-
(1994)
J. Membr. Biol.
, vol.140
, pp. 57-67
-
-
Reddy, M.M.1
Quinton, P.M.2
-
225
-
-
0022612677
-
Increased monocyte chemiluminescence in cystic fibrosis patients and in their parents
-
REGELMAN, W. E., N. M. LUNDE, P. T. PORTER, AND T. G. QUIE. Increased monocyte chemiluminescence in cystic fibrosis patients and in their parents. Pediatr. Res. 20: 619-622, 1986.
-
(1986)
Pediatr. Res.
, vol.20
, pp. 619-622
-
-
Regelman, W.E.1
Lunde, N.M.2
Porter, P.T.3
Quie, T.G.4
-
226
-
-
0017808680
-
Sulfated compounds in the zymogen granules of the guinea pig pancreas
-
REGGIO, H. A., AND G. E. PALADE. Sulfated compounds in the zymogen granules of the guinea pig pancreas. J. Cell Biol. 77: 288-314, 1978.
-
(1978)
J. Cell Biol.
, vol.77
, pp. 288-314
-
-
Reggio, H.A.1
Palade, G.E.2
-
227
-
-
0028343344
-
Mucociliary clearance in patients with cystic fibrosis and in normal subjects
-
REGNIS, J. A., M. ROBINSON, D. L. BAILEY, P. COOK, P. HOOPER, H.-K. CHAN, I. GONDA, G. BAUTOVICH, AND P. T. P. BYE. Mucociliary clearance in patients with cystic fibrosis and in normal subjects. Am. J. Respir. Crit. Care Med. 150: 66-71, 1994.
-
(1994)
Am. J. Respir. Crit. Care Med.
, vol.150
, pp. 66-71
-
-
Regnis, J.A.1
Robinson, M.2
Bailey, D.L.3
Cook, P.4
Hooper, P.5
Chan, H.-K.6
Gonda, I.7
Bautovich, G.8
Bye, P.T.P.9
-
228
-
-
0000385474
-
Measurement of the brochial mucous gland layer: A diagnostic yardstick in chronic bronchitis
-
REID, L. Measurement of the brochial mucous gland layer: a diagnostic yardstick in chronic bronchitis. Thorax 15: 132-141, 1960.
-
(1960)
Thorax
, vol.15
, pp. 132-141
-
-
Reid, L.1
-
229
-
-
0017143494
-
Sputum and mucociliary clearance mechanisms
-
REID, L. Sputum and mucociliary clearance mechanisms. Postgrad. Med. J. 606: 183-189, 1976.
-
(1976)
Postgrad. Med. J.
, vol.606
, pp. 183-189
-
-
Reid, L.1
-
230
-
-
0013884664
-
Ultrastructure and function of the human tracheal mucosa
-
RHODIN, J. A. G. Ultrastructure and function of the human tracheal mucosa. Am. Rev. Respir. Dis. 93: 101, 1966.
-
(1966)
Am. Rev. Respir. Dis.
, vol.93
, pp. 101
-
-
Rhodin, J.A.G.1
-
231
-
-
0025485377
-
Interactions of respiratory pathogens with host cell surface and extracellular matrix components
-
ROBERTS, D. D. Interactions of respiratory pathogens with host cell surface and extracellular matrix components. Am. J. Respir. Cell. Mol. Biol. 3: 181-186, 1990.
-
(1990)
Am. J. Respir. Cell. Mol. Biol.
, vol.3
, pp. 181-186
-
-
Roberts, D.D.1
-
232
-
-
0024338753
-
Increased phagocytic cell chemiluminscence in patients with cystic fibrosis
-
ROBERTS, R. L., AND R. STIEHM. Increased phagocytic cell chemiluminscence in patients with cystic fibrosis. Am. J. Dis. Child. 143: 944-950, 1989.
-
(1989)
Am. J. Dis. Child.
, vol.143
, pp. 944-950
-
-
Roberts, R.L.1
Stiehm, R.2
-
234
-
-
0028029443
-
CFTR does not alter acidification of L cell endosomes
-
ROOT, K. V., J. F. ENGELHARDT, M. POST, J. W. WILSON, AND R. W. VAN DYKE. CFTR does not alter acidification of L cell endosomes. Biochem. Biophys. Res. Commun. 205: 396-401, 1994.
-
(1994)
Biochem. Biophys. Res. Commun.
, vol.205
, pp. 396-401
-
-
Root, K.V.1
Engelhardt, J.F.2
Post, M.3
Wilson, J.W.4
Van Dyke, R.W.5
-
235
-
-
0020618019
-
Nasal cilia in normal man, primary ciliary dyskinesia and other respiratory diseases: Analysis of motility and ultrastructure
-
ROSSMAN, C. M., R. M. LEE, J. B. FORREST, AND M. T. NEWHOUSE. Nasal cilia in normal man, primary ciliary dyskinesia and other respiratory diseases: analysis of motility and ultrastructure. Eur. J. Respir. Dis. 127: 64-70, 1983.
-
(1983)
Eur. J. Respir. Dis.
, vol.127
, pp. 64-70
-
-
Rossman, C.M.1
Lee, R.M.2
Forrest, J.B.3
Newhouse, M.T.4
-
236
-
-
0027742895
-
Systemic deficiency of glutathione in cystic fibrosis
-
ROUM, J. H., R. BUHL, N. G. McELVANEY, Z. BOROK, AND R. G. CRYSTAL. Systemic deficiency of glutathione in cystic fibrosis. J. Appl. Physiol 75: 2419-2424, 1993.
-
(1993)
J. Appl. Physiol
, vol.75
, pp. 2419-2424
-
-
Roum, J.H.1
Buhl, R.2
McElvaney, N.G.3
Borok, Z.4
Crystal, R.G.5
-
237
-
-
0019824013
-
Nasal mucociliary clearance and ciliary beat frequency in cystic fibrosis compared with sinusitis and bronchiectasis
-
RUTLAND, J., AND P. J. COLE. Nasal mucociliary clearance and ciliary beat frequency in cystic fibrosis compared with sinusitis and bronchiectasis. Thorax 36: 654-658, 1981.
-
(1981)
Thorax
, vol.36
, pp. 654-658
-
-
Rutland, J.1
Cole, P.J.2
-
238
-
-
0014816714
-
The role of mucus in transport by cilia
-
SADE, J., N. ELIEZER, A. SILBERBERG, AND A. C. NERVO. The role of mucus in transport by cilia. Am. Rev. Respir. Dis. 102: 48-52, 1970.
-
(1970)
Am. Rev. Respir. Dis.
, vol.102
, pp. 48-52
-
-
Sade, J.1
Eliezer, N.2
Silberberg, A.3
Nervo, A.C.4
-
239
-
-
0026572283
-
Identification of the mucin-binding adhesin of Pseudomonas cepacia isolated from patients with cystic fibrosis
-
SAJJAN, S. U., AND J. F. FORSTNER. Identification of the mucin-binding adhesin of Pseudomonas cepacia isolated from patients with cystic fibrosis. Infect. Immun. 60: 1434-1440, 1992.
-
(1992)
Infect. Immun.
, vol.60
, pp. 1434-1440
-
-
Sajjan, S.U.1
Forstner, J.F.2
-
240
-
-
0026604399
-
Binding of nonmucoid Pseudomonas aeruginosa to normal human intestinal mucin and respiratory mucin from patients with cystic fibrosis
-
SAJJAN, U., J. REISMAN, P. DOIG, R. T. IRVIN, G. FORSTNER, AND J. FORSTNER. Binding of nonmucoid Pseudomonas aeruginosa to normal human intestinal mucin and respiratory mucin from patients with cystic fibrosis. J. Clin. Invest. 89: 657-665, 1992.
-
(1992)
J. Clin. Invest.
, vol.89
, pp. 657-665
-
-
Sajjan, U.1
Reisman, J.2
Doig, P.3
Irvin, R.T.4
Forstner, G.5
Forstner, J.6
-
241
-
-
0026753576
-
Comparison of adherence of Pseudomonas aeruginosa to respiratory epithelial cells from cystic fibrosis patients and healthy subjects
-
SAIMAN, L., G. CACALANO, D. GRUENERT, AND A. PRINCE. Comparison of adherence of Pseudomonas aeruginosa to respiratory epithelial cells from cystic fibrosis patients and healthy subjects. Infect. Immun. 60: 2808-2814, 1992.
-
(1992)
Infect. Immun.
, vol.60
, pp. 2808-2814
-
-
Saiman, L.1
Cacalano, G.2
Gruenert, D.3
Prince, A.4
-
242
-
-
0027428606
-
Pseudomonas aeruginosa pili bind to asialoGM1 which is increased on the surface of cystic fibrosis epithelial cells
-
SAIMAN, L., AND A. PRINCE. Pseudomonas aeruginosa pili bind to asialoGM1 which is increased on the surface of cystic fibrosis epithelial cells. J. Clin. Invest. 92: 1875-1880, 1993.
-
(1993)
J. Clin. Invest.
, vol.92
, pp. 1875-1880
-
-
Saiman, L.1
Prince, A.2
-
243
-
-
0015938912
-
Pulmonary mucociliary clearance in cystic fibrosis
-
SANCHIS, J., M. DOLOVICH, C. ROSSMAN, W. WILSON, AND M. NEWHOUSE. Pulmonary mucociliary clearance in cystic fibrosis. N. Engl. J. Med. 288: 651-654, 1973.
-
(1973)
N. Engl. J. Med.
, vol.288
, pp. 651-654
-
-
Sanchis, J.1
Dolovich, M.2
Rossman, C.3
Wilson, W.4
Newhouse, M.5
-
244
-
-
0024407968
-
Binding of Staphylococci to mucus in vivo and in vitro
-
SANFORD, B. A., V. L. THOMAS, AND M. A. RAMSAY. Binding of Staphylococci to mucus in vivo and in vitro. Infect. Immun. 57: 3735-3742, 1989.
-
(1989)
Infect. Immun.
, vol.57
, pp. 3735-3742
-
-
Sanford, B.A.1
Thomas, V.L.2
Ramsay, M.A.3
-
245
-
-
0029973935
-
Interactions between glycoconjugates from human respiratory airways and Pseudomonas aeruginosa
-
SCHARFMAN, A., E. VAN BRUSSEL, N. HOUDRET, G. LAMBLIN, AND P. ROUSSEL Interactions between glycoconjugates from human respiratory airways and Pseudomonas aeruginosa. Am. J. Respir. Crit. Care Med. 154, Suppl: S163-S169, 1996.
-
(1996)
Am. J. Respir. Crit. Care Med.
, vol.154
, Issue.SUPPL.
-
-
Scharfman, A.1
Van Brussel, E.2
Houdret, N.3
Lamblin, G.4
Roussel, P.5
-
246
-
-
0025307779
-
Surfactant displaces particles toward the epithelium in airways and alveoli
-
SCHURCH, S., P. GEHR, V. IM HOF, M. GEISER, AND F. GREEN. Surfactant displaces particles toward the epithelium in airways and alveoli. Respir. Physiol. 80: 17-32, 1990.
-
(1990)
Respir. Physiol.
, vol.80
, pp. 17-32
-
-
Schurch, S.1
Gehr, P.2
Im Hof, V.3
Geiser, M.4
Green, F.5
-
247
-
-
0030859292
-
CpG motifs in bacterial DNA cause inflammation in the lower respiratory tract
-
SCHWARTZ, D. A., T. J. QUINN, P. S. THORNE, S. SAYEED, A. K. YI, AND A. M. KRIEG. CpG motifs in bacterial DNA cause inflammation in the lower respiratory tract. J. Clin. Invest. 100: 68-73, 1997.
-
(1997)
J. Clin. Invest.
, vol.100
, pp. 68-73
-
-
Schwartz, D.A.1
Quinn, T.J.2
Thorne, P.S.3
Sayeed, S.4
A K, Y.I.5
Krieg, A.M.6
-
248
-
-
0028140935
-
Heterotrimeric G proteins, vesicle trafficking, and CFTR Cl channels
-
SCHWIEBERT, E. M., F. GESEK, L. ERCOLANI, C. WJASOW, D. C. GRUENERT, K. KARLSON, AND B. A. STANTON. Heterotrimeric G proteins, vesicle trafficking, and CFTR Cl channels. Am. J. Physiol. 267 (Cell Physiol. 36): C272-C281, 1994.
-
(1994)
Am. J. Physiol. 267 (Cell Physiol. 36)
, vol.267
-
-
Schwiebert, E.M.1
Gesek, F.2
Ercolani, L.3
Wjasow, C.4
Gruenert, D.C.5
Karlson, K.6
Stanton, B.A.7
-
249
-
-
0017649337
-
Length and distribution of cilia in human and canine airways
-
SERAFINI, S. M., AND E. D. MICHAELSON. Length and distribution of cilia in human and canine airways. Bull. Eur. Physiopathol. Respir. 13: 551-559, 1977.
-
(1977)
Bull. Eur. Physiopathol. Respir.
, vol.13
, pp. 551-559
-
-
Serafini, S.M.1
Michaelson, E.D.2
-
250
-
-
0028868212
-
Aerosolized recombinant human DNase I for the treatment of cystic fibrosis
-
SHAK, S. Aerosolized recombinant human DNase I for the treatment of cystic fibrosis. Chest 107, Suppl.: 65S-70S, 1995.
-
(1995)
Chest
, vol.107
, Issue.SUPPL.
-
-
Shak, S.1
-
251
-
-
0025647882
-
Recombinant human DNase I reduces the viscosity of cystic fibrosis sputum
-
SHAK, S., D. J. CAPON, R. HELLMISS, S. A. MARSTERS, AND C. L. BAKER. Recombinant human DNase I reduces the viscosity of cystic fibrosis sputum. Proc. Natl. Acad. Sci. USA 87: 9188-9192, 1990.
-
(1990)
Proc. Natl. Acad. Sci. USA
, vol.87
, pp. 9188-9192
-
-
Shak, S.1
Capon, D.J.2
Hellmiss, R.3
Marsters, S.A.4
Baker, C.L.5
-
252
-
-
0028307695
-
Calu-3: A human airway epithelial cell line that shows cAMP-dependent Cl secretion
-
SHEN, B. Q., W. E. FINKBEINER, J. J. WINE, R. J. MRSNY, AND J. H. WIDDICOMBE. Calu-3: a human airway epithelial cell line that shows cAMP-dependent Cl secretion. Am. J. Physiol. 266 (Lung Cell. Mol. Physiol. 10): L493-L501, 1994.
-
(1994)
Am. J. Physiol. 266 (Lung Cell. Mol. Physiol. 10)
, vol.266
-
-
Shen, B.Q.1
Finkbeiner, W.E.2
Wine, J.J.3
Mrsny, R.J.4
Widdicombe, J.H.5
-
253
-
-
0028929909
-
Mechanism of dysfunction of two nucleotide binding domain mutations in cystic fibrosis transmembrane conductance regulator that are associated with pancreatic sufficiency
-
SHEPPARD, D. N., L. S. OSTEDGAARD, M. C. WINTER, AND M. J. WELSH. Mechanism of dysfunction of two nucleotide binding domain mutations in cystic fibrosis transmembrane conductance regulator that are associated with pancreatic sufficiency. EMBO J. 14: 876-883, 1995.
-
(1995)
Embo J.
, vol.14
, pp. 876-883
-
-
Sheppard, D.N.1
Ostedgaard, L.S.2
Winter, M.C.3
Welsh, M.J.4
-
254
-
-
0027408231
-
Mutations in CFTR associated with mild disease form Cl channels with altered pore properties
-
SHEPPARD, D. N., D. P. RICH, L. S. OSTEDGAARD, R. J. GREGORY, A. E. SMITH, AND M. J. WELSH. Mutations in CFTR associated with mild disease form Cl channels with altered pore properties. Nature 362: 160-164, 1993.
-
(1993)
Nature
, vol.362
, pp. 160-164
-
-
Sheppard, D.N.1
Rich, D.P.2
Ostedgaard, L.S.3
Gregory, R.J.4
Smith, A.E.5
Welsh, M.J.6
-
255
-
-
0000963297
-
The pathology of cystic fibrosis
-
edited by M. E. Hodson and D. M. Geddes. London: Chapman & Hall
-
SHEPPARD, M. N. The pathology of cystic fibrosis. In: Cystic Fibrosis, edited by M. E. Hodson and D. M. Geddes. London: Chapman & Hall, 1995, p. 131-149.
-
(1995)
Cystic Fibrosis
, pp. 131-149
-
-
Sheppard, M.N.1
-
256
-
-
0027946089
-
Liddle's syndrome: Heritable human hypertension caused by mutation in the β subunit of the epithelial Na channel
-
SHIMKETS, R. A., D. G. WARNOCK, C. M. BOSITIS, C. NELSON-WILLIAMS, J. H. HANSSON, M. SCHAMBELAN, H. R. GILL, JR., S. ULICK, R. V. MILORA, J. W. FINDLING, C. M. CANESSA, B. C. ROSSIER, AND R. P. LIFTON. Liddle's syndrome: heritable human hypertension caused by mutation in the β subunit of the epithelial Na channel. Cell 79: 407-414, 1994.
-
(1994)
Cell
, vol.79
, pp. 407-414
-
-
Shimkets, R.A.1
Warnock, D.G.2
Bositis, C.M.3
Nelson-Williams, C.4
Hansson, J.H.5
Schambelan, M.6
Gill H.R., Jr.7
Ulick, S.8
Milora, R.V.9
Findling, J.W.10
Canessa, C.M.11
Rossier, B.C.12
Lifton, R.P.13
-
257
-
-
0030052451
-
Slaphylococcus aureus binding to human nasal mucin
-
SHUTER, J., V. B. HATCHER, AND F. D. LOWY. Slaphylococcus aureus binding to human nasal mucin. Infect. Immun. 64: 310-318, 1996.
-
(1996)
Infect. Immun.
, vol.64
, pp. 310-318
-
-
Shuter, J.1
Hatcher, V.B.2
Lowy, F.D.3
-
260
-
-
0028350324
-
Defective fluid transport by cystic fibrosis airway epithelia
-
SMITH, J. J., P. H. KARP, AND M. J. WELSH. Defective fluid transport by cystic fibrosis airway epithelia J. Clin. Invest. 93: 1307-1311, 1994.
-
(1994)
J. Clin. Invest.
, vol.93
, pp. 1307-1311
-
-
Smith, J.J.1
Karp, P.H.2
Welsh, M.J.3
-
261
-
-
0029870085
-
Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid
-
SMITH, J. J., S. M. TRAVIS, E. P. GREENBERG, AND M. J. WELSH. Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid. Cell 85: 229-236, 1996.
-
(1996)
Cell
, vol.85
, pp. 229-236
-
-
Smith, J.J.1
Travis, S.M.2
Greenberg, E.P.3
Welsh, M.J.4
-
262
-
-
0026645366
-
Bicarbonate secretion across normal, but not cystic fibrosis airway epithelia
-
SMITH, J. J., AND M. J. WELSH. Bicarbonate secretion across normal, but not cystic fibrosis airway epithelia. J. Clin. Invest. 89: 1148-1153, 1992.
-
(1992)
J. Clin. Invest.
, vol.89
, pp. 1148-1153
-
-
J, J.1
Welsh, M.J.2
-
263
-
-
0027252125
-
Fluid and electrolyte transport by cultured human airway epithelia
-
SMITH, J. J., AND M. J. WELSH. Fluid and electrolyte transport by cultured human airway epithelia. J. Clin. Invest. 91: 1590-1597, 1993.
-
(1993)
J. Clin. Invest.
, vol.91
, pp. 1590-1597
-
-
Smith, J.J.1
Welsh, M.J.2
-
264
-
-
0021369751
-
Cl secretion by canine tracheal epithelium. IV. Basolateral membrane K permeability parallels secretion rate
-
SMITH, P. L., AND R. A. FRIZZELL. Cl secretion by canine tracheal epithelium. IV. Basolateral membrane K permeability parallels secretion rate. J. Membr. Biol. 77: 187-199, 1984.
-
(1984)
J. Membr. Biol.
, vol.77
, pp. 187-199
-
-
Smith, P.L.1
Frizzell, R.A.2
-
265
-
-
0026649122
-
An animal model for cystic fibrosis made by gene targeting
-
SNOUWAERT, J. N., K. K. BRIGMAN, A. M. LATOUR, N. N. MALOUF, R. C. BOUCHER, O. SMITHIES, AND B. H. KOLLER. An animal model for cystic fibrosis made by gene targeting. Science 257: 1083-1088, 1992.
-
(1992)
Science
, vol.257
, pp. 1083-1088
-
-
Snouwaert, J.N.1
Brigman, K.K.2
Latour, A.M.3
Malouf, N.N.4
Boucher, R.C.5
Smithies, O.6
Koller, B.H.7
-
266
-
-
0029591506
-
+ channel
-
+ channel. Cell 83: 969-978, 1995.
-
(1995)
Cell
, vol.83
, pp. 969-978
-
-
Snyder, P.M.1
Price, M.P.2
McDonald, F.J.3
Adams, C.M.4
Volk, K.A.5
Zeiher, B.G.6
Stokes, J.B.7
Welsh, M.J.8
-
267
-
-
0022462591
-
Quantitative aspects of lung pathology in cystic fibrosis
-
SOBONYA, R. E., AND L. M. TAUSSIG. Quantitative aspects of lung pathology in cystic fibrosis. Am. Rev. Respir. Dis. 134: 290-295, 1986.
-
(1986)
Am. Rev. Respir. Dis.
, vol.134
, pp. 290-295
-
-
Sobonya, R.E.1
Taussig, L.M.2
-
268
-
-
0029097956
-
3849-10 kb C to T mutation and disease severity in cystic fibrosis
-
STERN, R. C., C. F. DOERSHUK, AND M. L. DRUMM. 3849-10 kb C to T mutation and disease severity in cystic fibrosis. Lancet 346: 274-276, 1995.
-
(1995)
Lancet
, vol.346
, pp. 274-276
-
-
Stern, R.C.1
Doershuk, C.F.2
Drumm, M.L.3
-
269
-
-
0026054929
-
Fetal lung liquid: Secretion and reabsorption
-
STRANG, L. B. Fetal lung liquid: secretion and reabsorption. Physiol. Rev. 71: 991-1016, 1991.
-
(1991)
Physiol. Rev.
, vol.71
, pp. 991-1016
-
-
Strang, L.B.1
-
270
-
-
0030068042
-
A novel splice-site mutation in the gamma subunit of the epithelial Na channel gene in three pseuodohypoaldosteronism type 1 families
-
STRAUTNIEKS, S. S., R. J. THOMPSON, R. M. GARDINER, AND E. CHUNG. A novel splice-site mutation in the gamma subunit of the epithelial Na channel gene in three pseuodohypoaldosteronism type 1 families. Nature Genet. 13: 248-250, 1996.
-
(1996)
Nature Genet.
, vol.13
, pp. 248-250
-
-
Strautnieks, S.S.1
Thompson, R.J.2
Gardiner, R.M.3
Chung, E.4
-
271
-
-
0027310434
-
Expression of an abundantly alternatively spliced form of the cystic fibrosis transmembrane conductance regulator (CFTR) gene is not associated with a cAMP-activated Cl conductance
-
STRONG, T. V., D. J. WILKINSON, M. K. MANSOURA, D. C. DEVOR, K. HENZE, Y. YANG, J. M. WILSON, J. A. COHN, D. C. DAWSON, R. A. FRIZZELL, AND F. S. COLLINS. Expression of an abundantly alternatively spliced form of the cystic fibrosis transmembrane conductance regulator (CFTR) gene is not associated with a cAMP-activated Cl conductance. Hum. Mol. Genet. 2: 225-230, 1993.
-
(1993)
Hum. Mol. Genet.
, vol.2
, pp. 225-230
-
-
Strong, T.V.1
Wilkinson, D.J.2
Mansoura, M.K.3
Devor, D.C.4
Henze, K.5
Yang, Y.6
Wilson, J.M.7
Cohn, J.A.8
Dawson, D.C.9
Frizzell, R.A.10
Collins, F.S.11
-
272
-
-
0020082418
-
Quantitative evaluation of the development of tracheal submucosal glands in infants with cystic fibrosis and control infants
-
STURGESS, J., AND J. IMRIE. Quantitative evaluation of the development of tracheal submucosal glands in infants with cystic fibrosis and control infants. Am. J. Pathol. 106: 303-311, 1982.
-
(1982)
Am. J. Pathol.
, vol.106
, pp. 303-311
-
-
Sturgess, J.1
Imrie, J.2
-
273
-
-
0028982894
-
CFTR as a cAMP-dependent regulator of sodium channels
-
STUTTS, M. J., C. M. CANESSA, J. C. OLSEN, M. HAMRICK, J. A. COHN, B. C. ROSSIER, AND R. C. BOUCHER. CFTR as a cAMP-dependent regulator of sodium channels. Science 269: 847-850, 1995.
-
(1995)
Science
, vol.269
, pp. 847-850
-
-
Stutts, M.J.1
Canessa, C.M.2
Olsen, J.C.3
Hamrick, M.4
Cohn, J.A.5
Rossier, B.C.6
Boucher, R.C.7
-
274
-
-
0026530524
-
Regulation of Cl channels in normal and cystic fibrosis airway epithelial cells by extracellular ATP
-
STUTTS, M. J., T. C. CHINET, S. J. MASON, J. M. FULLTON, L. L. CLARKE, AND R. C. BOUCHER. Regulation of Cl channels in normal and cystic fibrosis airway epithelial cells by extracellular ATP. Proc. Natl. Acad. Sci. USA 89: 1621-1625, 1992.
-
(1992)
Proc. Natl. Acad. Sci. USA
, vol.89
, pp. 1621-1625
-
-
Stutts, M.J.1
Chinet, T.C.2
Mason, S.J.3
Fullton, J.M.4
Clarke, L.L.5
Boucher, R.C.6
-
275
-
-
0023039339
-
Oxygen consumption and ouabain binding sites in cystic fibrosis nasal epithelium
-
STUTTS, M. J., M. R. KNOWLES, J. T. GATZY, AND R. C. BOUCHER. Oxygen consumption and ouabain binding sites in cystic fibrosis nasal epithelium. Pediatr. Res. 20: 1316-1320, 1986.
-
(1986)
Pediatr. Res.
, vol.20
, pp. 1316-1320
-
-
Stutts, M.J.1
Knowles, M.R.2
Gatzy, J.T.3
Boucher, R.C.4
-
276
-
-
0030970422
-
Cystic fibrosis transmembrane conductance regulator inverts protein kinase A-mediated regulation of epithelial Na channel single channel kinetics
-
STUTTS, M. J., B. C. ROSSIER, AND R. C. BOUCHER. Cystic fibrosis transmembrane conductance regulator inverts protein kinase A-mediated regulation of epithelial Na channel single channel kinetics. J. Biol. Chem. 272: 14037-14040, 1997.
-
(1997)
J. Biol. Chem.
, vol.272
, pp. 14037-14040
-
-
Stutts, M.J.1
Rossier, B.C.2
Boucher, R.C.3
-
278
-
-
0030460582
-
CFTR-dependent membrane insertion is linked to stimulation of the CFTR Cl conductance
-
TAKAHASHI, A., S. C. WATKINS, M. E. HOWARD, AND R. A. FRIZZELL. CFTR-dependent membrane insertion is linked to stimulation of the CFTR Cl conductance. Am. J. Physiol 271 (Cell Physiol. 40): C1887-C1894, 1996.
-
(1996)
Am. J. Physiol 271 (Cell Physiol. 40)
, vol.271
-
-
Takahashi, A.1
Watkins, S.C.2
Howard, M.E.3
Frizzell, R.A.4
-
279
-
-
0015074482
-
A comparative study of four methods of assessing the morphologic changes in chronic bronchitis
-
TAKIZAWA, T., AND W. M. THURLBECK. A comparative study of four methods of assessing the morphologic changes in chronic bronchitis. Am. Rev. Respir. Dis. 103: 774-783, 1971.
-
(1971)
Am. Rev. Respir. Dis.
, vol.103
, pp. 774-783
-
-
Takizawa, T.1
Thurlbeck, W.M.2
-
281
-
-
0031023970
-
Increased proportion of exon 9 alternatively spliced CFTR transcripts in vas deferens compared with nasal epithelial cells
-
TENG, H., M. JORISSEN, H. V. POPPEL, E. LEGIUS, J.-J., CASSIMAN, AND H. CUPPENS. Increased proportion of exon 9 alternatively spliced CFTR transcripts in vas deferens compared with nasal epithelial cells. Hum. Mol. Genet. 6: 85-90, 1997.
-
(1997)
Hum. Mol. Genet.
, vol.6
, pp. 85-90
-
-
Teng, H.1
Jorissen, M.2
Poppel, H.V.3
Legius, E.4
J-J, C.5
Cuppens, H.6
-
282
-
-
0015914223
-
Lung clearance in two patients with cystic fibrosis
-
THOMSON, M. L., D. PAVIA, M. D. SHORT, AND A. P. NORMAN. Lung clearance in two patients with cystic fibrosis. N. Engl. J. Med. 289: 749-750, 1974.
-
(1974)
N. Engl. J. Med.
, vol.289
, pp. 749-750
-
-
Thomson, M.L.1
Pavia, D.2
Short, M.D.3
Norman, A.P.4
-
283
-
-
0028418099
-
Regional expression of CFTR in developing respiratory tissues
-
TIZZANO, E. F., H. OBRODOVICH, D. CHITAYAT, J.-C. BENICHOU, AND M. BUCHWALD. Regional expression of CFTR in developing respiratory tissues. Am. J. Respir. Crit. Care Med. 10: 355-362, 1994.
-
(1994)
Am. J. Respir. Crit. Care Med.
, vol.10
, pp. 355-362
-
-
Tizzano, E.F.1
Obrodovich, H.2
Chitayat, D.3
Benichou, J.-C.4
Buchwald, M.5
-
284
-
-
0027520191
-
Amiloride inhalation therapy in cystic fibrosis. Influence on ion content, hydration, and rheology of sputum
-
TOMKIEWICZ, R. P., E. M. APP, J. G. ZAYAS, O. RAMIREZ, N. CHURCH, R. C. BOUCHER, M. R. KNOWLES, AND M. KING. Amiloride inhalation therapy in cystic fibrosis. Influence on ion content, hydration, and rheology of sputum. Am. Rev. Respir. Dis. 148: 1002-1007, 1993.
-
(1993)
Am. Rev. Respir. Dis.
, vol.148
, pp. 1002-1007
-
-
Tomkiewicz, R.P.1
E M, A.P.P.2
Zayas, J.G.3
Ramirez, O.4
Church, N.5
Boucher, R.C.6
Knowles, M.R.7
King, M.8
-
285
-
-
0001934613
-
The daily amount of tracheo-bronchial secretions in man
-
TOREMALM, N. G. The daily amount of tracheo-bronchial secretions in man. Acta Oto-Laryngol. Suppl. 158: 43-53, 1960.
-
(1960)
Acta Oto-laryngol. Suppl.
, vol.158
, pp. 43-53
-
-
Toremalm, N.G.1
-
286
-
-
0014909786
-
Mucous glands of the trachea in children
-
TOS, M. Mucous glands of the trachea in children. Anat. Am. 126: 146-160, 1970.
-
(1970)
Anat. Am.
, vol.126
, pp. 146-160
-
-
Tos, M.1
-
287
-
-
0023766047
-
Functional differences between the 40kDa and 50 to 60 kDa IgG Fc receptors on human neutrophils revealed by elastase treatment and anti-receptor antibodies
-
TOSI, M., AND M. BERGER. Functional differences between the 40kDa and 50 to 60 kDa IgG Fc receptors on human neutrophils revealed by elastase treatment and anti-receptor antibodies. J. Immunol. 141: 2097-2103, 1988.
-
(1988)
J. Immunol.
, vol.141
, pp. 2097-2103
-
-
Berger, M.1
-
288
-
-
0025374923
-
Neutrophil elastase cleaves C3bi on opsorazed Pseudomonas as well as CRl on neutrophils to create a functionally important opsonin receptor mismatch
-
TOSI, M. F., H. ZAKEM, AND M. BERGER. Neutrophil elastase cleaves C3bi on opsorazed Pseudomonas as well as CRl on neutrophils to create a functionally important opsonin receptor mismatch. J. Clin. Invest. 86: 300-308, 1990.
-
(1990)
J. Clin. Invest.
, vol.86
, pp. 300-308
-
-
Tosi, M.F.1
Zakem, H.2
Berger, M.3
-
290
-
-
0026043883
-
Expression of the cystic fibrosis transmembrane conductance regulator gene in the respiratory tract of normal individuals and individuals with cystic fibrosis
-
TRAPNELL, B. C., C. S. CHU, P. K. PAAKKO, T. C. BANKS, K. YOSHIMURA, V. J. FERRANS, M. S. CHERNICK, AND R. G. CRYSTAL. Expression of the cystic fibrosis transmembrane conductance regulator gene in the respiratory tract of normal individuals and individuals with cystic fibrosis. Proc. Natl. Acad. Sci. USA 88:6565-6569, 1991.
-
(1991)
Proc. Natl. Acad. Sci. USA
, vol.88
, pp. 6565-6569
-
-
Trapnell, B.C.1
Chu, C.S.2
Paakko, P.K.3
Banks, T.C.4
Yoshimura, K.5
Ferrans, V.J.6
Chernick, M.S.7
Crystal, R.G.8
-
291
-
-
0025787393
-
In vivo cell-specific expression of the cystic fibrosis transmembrane conductance regulator
-
TREZISE, A. E., AND M. BUCHWALD. In vivo cell-specific expression of the cystic fibrosis transmembrane conductance regulator. Nature 353: 434-437, 1991.
-
(1991)
Nature
, vol.353
, pp. 434-437
-
-
Trezise, A.E.1
Buchwald, M.2
-
292
-
-
0031913234
-
Inhibition of airway liquid secretion and its effect on the physical properties of airway mucus
-
TROUT, L., M. KING, W. FENG, S. K. INGLIS, AND S. T. BALLARD. Inhibition of airway liquid secretion and its effect on the physical properties of airway mucus. Am. J. Physiol. 274 (Lung Cell. Mol. Physiol. 18): L258-L263, 1998.
-
(1998)
Am. J. Physiol. 274 (Lung Cell. Mol. Physiol. 18)
, vol.274
-
-
Trout, L.1
King, M.2
Feng, W.3
Inglis, S.K.4
Ballard, S.T.5
-
293
-
-
0027986953
-
Interaction of Pseudomonas aeruginosa with human respiratory mucosa in vitro
-
TSANG, K. W. T., A. RUTMAN, E. TANAKA, V. LUND, A. DEWAR, P. J. COLE, AND R. WILSON. Interaction of Pseudomonas aeruginosa with human respiratory mucosa in vitro. Eur. Respir. J. 7: 1746-1753, 1994.
-
(1994)
Eur. Respir. J.
, vol.7
, pp. 1746-1753
-
-
Tsang, K.W.T.1
Rutman, A.2
Tanaka, E.3
Lund, V.4
Dewar, A.5
Cole, P.J.6
Wilson, R.7
-
294
-
-
0026641782
-
The spectrum of cystic fibrosis mutations
-
TSUI, L.-C. The spectrum of cystic fibrosis mutations. Trends Genet. 8: 392-398, 1992.
-
(1992)
Trends Genet.
, vol.8
, pp. 392-398
-
-
Tsui, L.-C.1
-
295
-
-
0018823482
-
Micropipette measurement of airway submucosal gland secretion: Autonomic effects
-
UEKI, I., V. F. GERMAN, AND J. NADEL. Micropipette measurement of airway submucosal gland secretion: autonomic effects. Am. Rev. Respir. Dis. 121: 351-357, 1980.
-
(1980)
Am. Rev. Respir. Dis.
, vol.121
, pp. 351-357
-
-
Ueki, I.1
German, V.F.2
Nadel, J.3
-
296
-
-
0029758488
-
Engineering actin-resistant human DNase I for treatment of cystic fibrosis
-
ULMER, J. S., A. HERZKA, K. J. TOY, D. L. BAKER, A. H. DODGE, D. SINICROPI, S. SHAK, AND R. A. LAZARUS. Engineering actin-resistant human DNase I for treatment of cystic fibrosis. Proc. Natl. Acad. Sci. USA 93: 8225-8229, 1996.
-
(1996)
Proc. Natl. Acad. Sci. USA
, vol.93
, pp. 8225-8229
-
-
Ulmer, J.S.1
Herzka, A.2
Toy, K.J.3
Baker, D.L.4
Dodge, A.H.5
Sinicropi, D.6
Shak, S.7
Lazarus, R.A.8
-
297
-
-
0032113268
-
Localization of Staphylococcus aureus in infected airways of patients with cystic fibrosis and in a cell culture model of S. Aureus adherence
-
ULRICH, M., S. HERBERT, J. BERGER, G. BELLON, D. LOUIS, G. MUNDER, AND G. DORING. Localization of Staphylococcus aureus in infected airways of patients with cystic fibrosis and in a cell culture model of S. aureus adherence. Am. J. Respir. Cell Mol. Biol. 19: 83-91, 1998.
-
(1998)
Am. J. Respir. Cell Mol. Biol.
, vol.19
, pp. 83-91
-
-
Ulrich, M.1
Herbert, S.2
Berger, J.3
Bellon, G.4
Louis, D.5
Munder, G.6
Doring, G.7
-
298
-
-
0017647606
-
Pulmonary airway clearance mechanisms: A reappraisal
-
VAN AS, A. Pulmonary airway clearance mechanisms: a reappraisal. Am. Rev. Respir. Dis. 115: 721-726, 1977.
-
(1977)
Am. Rev. Respir. Dis.
, vol.115
, pp. 721-726
-
-
Van As, A.1
-
299
-
-
0030337835
-
Acidification of lysosomes and endosomes
-
VAN DYKE, R. W. Acidification of lysosomes and endosomes. Subcell. Biochem. 27: 331-360, 1996.
-
(1996)
Subcell. Biochem.
, vol.27
, pp. 331-360
-
-
Van Dyke, R.W.1
-
300
-
-
0030585371
-
cAMP and protein kinase A stimulate acidification of rat liver endosomes in the absence of chloride
-
VAN DYKE, R. W., K. V. ROOT, AND R. A. HSI. cAMP and protein kinase A stimulate acidification of rat liver endosomes in the absence of chloride. Biochem. Biophys. Res. Commun. 222:312-316, 1996.
-
(1996)
Biochem. Biophys. Res. Commun.
, vol.222
, pp. 312-316
-
-
Van Dyke, R.W.1
Root, K.V.2
Hsi, R.A.3
-
301
-
-
0023392080
-
Ion transport by rabbit nonciliated bronchiolar epithelial cells (Clara cells) in culture
-
VAN SCOTT, M. R., S. HESTER, AND R. C. BOUCHER. Ion transport by rabbit nonciliated bronchiolar epithelial cells (Clara cells) in culture. Proc. Natl. Acad. Sci. USA 84: 5496-5500, 1987.
-
(1987)
Proc. Natl. Acad. Sci. USA
, vol.84
, pp. 5496-5500
-
-
Van Scott, M.R.1
Hester, S.2
Boucher, R.C.3
-
302
-
-
0005684427
-
-
Cell Physiol. 24
-
VAN SCOTT, M. R., N. P. LEE, J. R. YANKASKAS, AND R. C. BOUCHER. Effect of hormones on growth and function of cultured canine tracheal epithelial cells. Am. J. Physiol. 255 (Cell Physiol. 24): C237-C245, 1988.
-
(1988)
Effect of hormones on growth and function of cultured canine tracheal epithelial cells
, vol.255
-
-
Van Scott, M.R.1
Lee, N.P.2
Yankaskas, J.R.3
Boucher, R.C.4
-
303
-
-
0028212809
-
Reduction in viscosity of cystic fibrosis sputum in vitro by gelsolin
-
VASCONCELLOS, C. A., P. G. ALLEN, M. E. WOHL, J. M. DRAZEN, P. A. JANMEY, AND T. P. STOSSEL. Reduction in viscosity of cystic fibrosis sputum in vitro by gelsolin. Science 263: 969-971, 1994.
-
(1994)
Science
, vol.263
, pp. 969-971
-
-
Vasconcellos, C.A.1
Allen, P.G.2
Wohl, M.E.3
Drazen, J.M.4
Janmey, P.A.5
Stossel, T.P.6
-
304
-
-
0028218460
-
Determinants of mild clinical symptoms in cystic fibrosis patients. Residual Cl secretion measured in rectal biopsies in relation to genotype
-
VEEZE, H. J., D. J. HALLEY, J. BIJMAN, J. C. DE JONGSTE, H. R. DE JONGE, AND M. SINAASAPPEL. Determinants of mild clinical symptoms in cystic fibrosis patients. Residual Cl secretion measured in rectal biopsies in relation to genotype. J. Clin. Invest. 93: 461-466, 1994.
-
(1994)
J. Clin. Invest.
, vol.93
, pp. 461-466
-
-
Veeze, H.J.1
Halley, D.J.2
Bijman, J.3
De Jongste, J.C.4
De Jonge, H.R.5
Sinaasappel, M.6
-
305
-
-
84872076320
-
-
edited by G. L. Baum, Z. Priel, Y. Roth, N. Liron, and E. Ostfeld. New York: Dekker
-
VERDUGO, P. Cilia, Mucus, and Mucociliary Interactions, edited by G. L. Baum, Z. Priel, Y. Roth, N. Liron, and E. Ostfeld. New York: Dekker, 1988, p. 167-189.
-
(1988)
Cilia, Mucus, and Mucociliary Interactions
, pp. 167-189
-
-
Verdugo, P.1
-
306
-
-
0023283053
-
Molecular mechanism of mucin secretion. I. The role of intragranular charge shielding
-
VERDUGO, P., I. DEYRUP-OLSEN, M. AITKEN, M. VILLALON, AND D. JOHNSON. Molecular mechanism of mucin secretion. I. The role of intragranular charge shielding. J. Dent. Res. 66: 506-508, 1987.
-
(1987)
J. Dent. Res.
, vol.66
, pp. 506-508
-
-
Verdugo, P.1
Deyrup-Olsen, I.2
Aitken, M.3
Villalon, M.4
Johnson, D.5
-
307
-
-
0021986142
-
Tracheobronchial mucin receptor for Pseudomonas aeruginosa: Predominance of amino sugars in binding sites
-
VISHWANATH, S., AND R. RAMPHAL. Tracheobronchial mucin receptor for Pseudomonas aeruginosa: predominance of amino sugars in binding sites. Infect. Immun. 48: 331-335, 1985.
-
(1985)
Infect. Immun.
, vol.48
, pp. 331-335
-
-
Vishwanath, S.1
Ramphal, R.2
-
308
-
-
0030960151
-
Relationship between airway ion transport and a mild pulmonary disease mutation in CFTR
-
WALKER, L. C., C. J. VENGLARIK, G. AUBIN, M. R. WEATHERLY, N. A. McCARTY, B. LESNICK, F. RUIZ, J. P. CLANCY, AND E. J. SORSCHER. Relationship between airway ion transport and a mild pulmonary disease mutation in CFTR. Am. J. Respir. Crit. Care Med. 155: 1684-1689, 1997.
-
(1997)
Am. J. Respir. Crit. Care Med.
, vol.155
, pp. 1684-1689
-
-
Walker, L.C.1
Venglarik, C.J.2
Aubin, G.3
Weatherly, M.R.4
McCarty, N.A.5
Lesnick, B.6
Ruiz, F.7
Clancy, J.P.8
Sorscher, E.J.9
-
310
-
-
0027998367
-
Subcellular localization of CFTR to endosomes in a ductal epithelium
-
WEBSTER, P., L. VANACORE, A. C. NAIRN, AND C. K. MARINO. Subcellular localization of CFTR to endosomes in a ductal epithelium. Am. J. Physiol. 267 (Cell Physiol. 36): C340-C348, 1994.
-
(1994)
Am. J. Physiol. 267 (Cell Physiol. 36)
, vol.267
-
-
Webster, P.1
Vanacore, L.2
Nairn, A.C.3
Marino, C.K.4
-
311
-
-
0020261597
-
Cl secretion by canine trachea epithelium. II. The cellular electrical potential profile
-
WELSH, M. J., P. L. SMITH, AND R. A. FRIZZELL. Cl secretion by canine trachea epithelium. II. The cellular electrical potential profile. J. Membr. Biol. 70: 227-238, 1982.
-
(1982)
J. Membr. Biol.
, vol.70
, pp. 227-238
-
-
Welsh, M.J.1
Smith, P.L.2
Frizzell, R.A.3
-
312
-
-
0020585873
-
Chloride secretion by canine tracheal epithelium. III. Membrane resistances and electromotive forces
-
WELSH, M. J., P. L. SMITH, AND R. A. FRIZZELL. Chloride secretion by canine tracheal epithelium. III. Membrane resistances and electromotive forces. J. Membr. Biol. 71: 209-218, 1983.
-
(1983)
J. Membr. Biol.
, vol.71
, pp. 209-218
-
-
Welsh, M.J.1
Smith, P.L.2
Frizzell, R.A.3
-
313
-
-
0027162649
-
Molecular mechanisms of CFTR chloride channel dysfunction in cystic fibrosis
-
WELSH, M. J., AND A. E. SMITH. Molecular mechanisms of CFTR chloride channel dysfunction in cystic fibrosis. Cell 73: 1251-1254, 1993.
-
(1993)
Cell
, vol.73
, pp. 1251-1254
-
-
Welsh, M.J.1
Smith, A.E.2
-
314
-
-
0023462429
-
Role of lipids in airway function
-
WIDDICOME, J. G. Role of lipids in airway function. Eur. J. Respir. Dis. 71: 197-204, 1987.
-
(1987)
Eur. J. Respir. Dis.
, vol.71
, pp. 197-204
-
-
Widdicome, J.G.1
-
315
-
-
0028630758
-
Accumulation of airway mucus in cystic fibrosis
-
WIDDICOMBE, J. H. Accumulation of airway mucus in cystic fibrosis. Pulm. Pharmacol. 7: 225-233, 1994.
-
(1994)
Pulm. Pharmacol.
, vol.7
, pp. 225-233
-
-
Widdicombe, J.H.1
-
316
-
-
0001177927
-
Structure and function of human airway mucous glands in health and disease
-
WIDDICOMBE, J. H., B.-Q. SHEN, AND W. E. FINKBEINER. Structure and function of human airway mucous glands in health and disease. Adv. Struct. Biol. 3: 225-241, 1994.
-
(1994)
Adv. Struct. Biol.
, vol.3
, pp. 225-241
-
-
Widdicombe, J.H.1
Shen, B.-Q.2
Finkbeiner, W.E.3
-
318
-
-
0028904520
-
The ciliary transportability of sputum is slow on the mucus-depleted bovine trachea
-
WILLS, P. J., M. J. GARCIA SUAREZ, A. RUTMAN, R. WILSON, AND P. J. COLE. The ciliary transportability of sputum is slow on the mucus-depleted bovine trachea. Am. J. Respir. Crit. Care Med. 151: 1255-1258, 1995.
-
(1995)
Am. J. Respir. Crit. Care Med.
, vol.151
, pp. 1255-1258
-
-
Wills, P.J.1
Suarez, M.J.G.2
Rutman, A.3
Wilson, R.4
Cole, P.J.5
-
319
-
-
0031018453
-
NaCl increases the ciliary transportability of cystic fibrosis and bronchiectasis sputum on the mucus-depleted bovine trachea
-
WILLS, P. J., R. L. HALL, W. CHAN, AND P. J. COLE. NaCl increases the ciliary transportability of cystic fibrosis and bronchiectasis sputum on the mucus-depleted bovine trachea. J. Clin. Invest. 99: 9-13, 1997.
-
(1997)
J. Clin. Invest.
, vol.99
, pp. 9-13
-
-
Wills, P.J.1
Hall, R.L.2
Chan, W.3
Cole, P.J.4
-
320
-
-
0024547744
-
Shunt resistance and ion permeabilities in normal and cystic fibrosis airway epithelium
-
WILLUMSEN, N. J., AND R. C. BOUCHER. Shunt resistance and ion permeabilities in normal and cystic fibrosis airway epithelium. Am. J. Physiol. 256 (Cell Physiol. 25): C1054-C1063, 1989.
-
(1989)
Am. J. Physiol. 256 (Cell Physiol. 25)
, vol.256
-
-
Willumsen, N.J.1
Boucher, R.C.2
-
321
-
-
0025995248
-
Transcellular Na transport in cultured cystic fibrosis human nasal epithelium
-
WILLUMSEN, N. J., AND R. C. BOUCHER. Transcellular Na transport in cultured cystic fibrosis human nasal epithelium. Am. J. Physiol. 261 (Cell Physiol. 30): C332-C341, 1991.
-
(1991)
Am. J. Physiol. 261 (Cell Physiol. 30)
, vol.261
-
-
Willumsen, N.J.1
Boucher, R.C.2
-
324
-
-
0025281628
-
Increased levels of interleukin-1 in bronchoalveolar washings from children with bacterial pulmonary infections
-
WILMOTT, R. W., J. T. KASSAB, P. L. KILIAN, W. R. BENJAMIN, S. D. DOUGLAS, AND R. E. WOOD. Increased levels of interleukin-1 in bronchoalveolar washings from children with bacterial pulmonary infections. Am. Rev. Respir. Dis. 142: 365-368, 1990.
-
(1990)
Am. Rev. Respir. Dis.
, vol.142
, pp. 365-368
-
-
Wilmott, R.W.1
Kassab, J.T.2
Kilian, P.L.3
Benjamin, W.R.4
Douglas, S.D.5
Wood, R.E.6
-
325
-
-
0030861594
-
Interaction between ion transporters and the mucociliary transport system in dog and baboon
-
WINTERS, S. L., AND D. B. YEATES. Interaction between ion transporters and the mucociliary transport system in dog and baboon. J. Appl. Physiol. 83: 1348-1359, 1997.
-
(1997)
J. Appl. Physiol.
, vol.83
, pp. 1348-1359
-
-
Winters, S.L.1
Yeates, D.B.2
-
326
-
-
0030863028
-
Roles of hydration, Na, and Cl in regulation of canine mucociliary transport system
-
WINTERS, S. L., AND D. B. YEATES. Roles of hydration, Na, and Cl in regulation of canine mucociliary transport system. J. Appl. Physiol. 83: 1360-1369, 1997.
-
(1997)
J. Appl. Physiol.
, vol.83
, pp. 1360-1369
-
-
Winters, S.L.1
Yeates, D.B.2
-
327
-
-
0030587191
-
Disturbed myeloperoxidase-dependent activity of neutrophils in cystic fibrosis homozygotes and heterozygotes, and its correction by amiloride
-
WITKO-SARSAT, V., R. C. CALLEN, M. PAULAIS, A. T. NGUYEN, G. BESSOU, G. LENOIR, AND B. DESCAMPS-LATSCHA. Disturbed myeloperoxidase-dependent activity of neutrophils in cystic fibrosis homozygotes and heterozygotes, and its correction by amiloride. J. Immunol. 157: 2728-2735, 1996.
-
(1996)
J. Immunol.
, vol.157
, pp. 2728-2735
-
-
Witko-Sarsat, V.1
Callen, R.C.2
Paulais, M.3
Nguyen, A.T.4
Bessou, G.5
Lenoir, G.6
Descamps-Latscha, B.7
-
328
-
-
0016793255
-
Tracheal mucociliary transport in patients with cystic fibrosis and its stimulation by terbutaline
-
WOOD, R. E., A. WANNER, J. HIRSCH, AND P. M. FARRELL. Tracheal mucociliary transport in patients with cystic fibrosis and its stimulation by terbutaline. Am. Rev. Respir. Dis. 111: 733-738, 1975.
-
(1975)
Am. Rev. Respir. Dis.
, vol.111
, pp. 733-738
-
-
Wood, R.E.1
Wanner, A.2
Hirsch, J.3
Farrell, P.M.4
-
331
-
-
0026636673
-
Differentiated structure and function of cultures from human tracheal epithelium
-
YAMAYA, M., W. E. FINKBEINER, S. Y. CHUN, AND J. H. WIDDICOMBE. Differentiated structure and function of cultures from human tracheal epithelium. Am. J. Physiol. 262 (Cell Physiol. 31): C713-C724, 1992.
-
(1992)
Am. J. Physiol. 262 (Cell Physiol. 31)
, vol.262
-
-
Yamaya, M.1
Finkbeiner, W.E.2
Chun, S.Y.3
Widdicombe, J.H.4
-
332
-
-
0022396481
-
Culture of human nasal epithelial cells on collagen matrix supports
-
YANKASKAS, J. R., C. U. COTTON, M. R. KNOWLES, J. T. GATZY, AND R. C. BOUCHER. Culture of human nasal epithelial cells on collagen matrix supports. Am. Rev. Respir. Dis. 132: 1281-1287, 1985.
-
(1985)
Am. Rev. Respir. Dis.
, vol.132
, pp. 1281-1287
-
-
Yankaskas, J.R.1
Cotton, C.U.2
Knowles, M.R.3
Gatzy, J.T.4
Boucher, R.C.5
-
333
-
-
0016724570
-
Mucociliary tracheal transport rates in man
-
YEATES, D. B., N. ASPIN, H. LEVISON, M. T. JONES, AND A. C. BRYAN. Mucociliary tracheal transport rates in man. J. Appl. Physiol. 39: 487-495, 1975.
-
(1975)
J. Appl. Physiol.
, vol.39
, pp. 487-495
-
-
Yeates, D.B.1
Aspin, N.2
Levison, H.3
Jones, M.T.4
Bryan, A.C.5
-
334
-
-
0008162268
-
Physicochemical properties of mucus and its propulsion
-
edited by R. G. Crystal and J. B. West. Philadelphia, PA: Lippincott-Raven
-
YEATES, D. B., G. J. BESSERIS, AND L. B. WONG. Physicochemical properties of mucus and its propulsion. In: The Lung: Scientific Foundations (2nd ed.), edited by R. G. Crystal and J. B. West. Philadelphia, PA: Lippincott-Raven, 1997, p. 487-503.
-
(1997)
The Lung: Scientific Foundations (2nd Ed.)
, pp. 487-503
-
-
Yeates, D.B.1
Besseris, G.J.2
Wong, L.B.3
-
335
-
-
0017251117
-
Mucociliary transport in trachea of patients with cystic fibrosis
-
YEATES, D. B., J. M. STURGESS, S. R. KAHN, H. LEVISON, AND N. ASPIN. Mucociliary transport in trachea of patients with cystic fibrosis. Arch. Dis. Childh. 51: 28-33, 1976.
-
(1976)
Arch. Dis. Childh.
, vol.51
, pp. 28-33
-
-
Yeates, D.B.1
Sturgess, J.M.2
Kahn, S.R.3
Levison, H.4
Aspin, N.5
-
337
-
-
0017109266
-
Mucous blanket of rat bronchus: An ultrastructural study
-
YONEDA, K. Mucous blanket of rat bronchus: an ultrastructural study. Am. Rev. Respir. Dis. 114: 837-842, 1976.
-
(1976)
Am. Rev. Respir. Dis.
, vol.114
, pp. 837-842
-
-
Yoneda, K.1
-
338
-
-
0025949558
-
Expression of the cystic fibrosis transmembrane conductance regulator gene in cells of non-epithelial origin
-
YOSHIMURA, K., H. NAKAMURA, B. C. TRAPNELL, C. S. CHU, W. DALEMANS, A. PAVIRANI, J. P. LECOCQ, AND R. G. CRYSTAL. Expression of the cystic fibrosis transmembrane conductance regulator gene in cells of non-epithelial origin. Nucleic Acids Res. 19: 5417-5423, 1991.
-
(1991)
Nucleic Acids Res.
, vol.19
, pp. 5417-5423
-
-
Yoshimura, K.1
Nakamura, H.2
Trapnell, B.C.3
Chu, C.S.4
Dalemans, W.5
Pavirani, A.6
Lecocq, J.P.7
Crystal, R.G.8
-
339
-
-
0001361078
-
Secretion by the major salivary glands
-
edited by L. R. Johnson. New York: Raven
-
YOUNG, J. A., D. I. COOK, E. W. VAN LENNEP, AND M. ROBERTS. Secretion by the major salivary glands. In: Physiology of the Gastrointestinal Tract (2nd ed.), edited by L. R. Johnson. New York: Raven, 1987, vol. 1 p. 773-816.
-
(1987)
Physiology of the Gastrointestinal Tract (2nd Ed.)
, vol.1
, pp. 773-816
-
-
Young, J.A.1
Cook, D.I.2
Van Lennep, E.W.3
Roberts, M.4
-
340
-
-
0028847778
-
Binding of Pseudomonas aeruginosa to respiratory epithelial cells from patients with various mutations in the cystic fibrosis transmembrane regulator
-
ZAR, H., L. SAIMAN, L. QUITTELL, AND A. PRINCE. Binding of Pseudomonas aeruginosa to respiratory epithelial cells from patients with various mutations in the cystic fibrosis transmembrane regulator. J. Pediatr. 126: 230-233, 1995.
-
(1995)
J. Pediatr.
, vol.126
, pp. 230-233
-
-
Zar, H.1
Saiman, L.2
Quittell, L.3
Prince, A.4
-
341
-
-
0028804840
-
Genotypic analysis of respiratory mucous sulfation defects in cystic fibrosis
-
ZHANG, Y., B. DORANZ, J. R. YANKASKAS, AND J. F. ENGELHARDT. Genotypic analysis of respiratory mucous sulfation defects in cystic fibrosis. J. Clin. Invest. 96: 2997-3004, 1995.
-
(1995)
J. Clin. Invest.
, vol.96
, pp. 2997-3004
-
-
Zhang, Y.1
Doranz, B.2
Yankaskas, J.R.3
Engelhardt, J.F.4
-
342
-
-
0030569343
-
Widespread expression of beta-defensin hBD-1 in human secretory glands and epithelial cells
-
ZHAO, C., I. WANG, AND R. I. LEHRER. Widespread expression of beta-defensin hBD-1 in human secretory glands and epithelial cells. FEBS Lett. 396: 319-22, 1996.
-
(1996)
FEBS Lett.
, vol.396
, pp. 319-322
-
-
Wang, I.1
Lehrer, R.I.2
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