-
1
-
-
0029346937
-
The relationship between infection and inflammation in the early stages of lung disease from cystic fibrosis
-
Balough, K., McCubbin, M., Weinberger, M., Smits, W., Ahrens, R., and Fick, R. (1995). The relationship between infection and inflammation in the early stages of lung disease from cystic fibrosis. Pediatr. Pulmonol. 20, 63-70.
-
(1995)
Pediatr. Pulmonol.
, vol.20
, pp. 63-70
-
-
Balough, K.1
McCubbin, M.2
Weinberger, M.3
Smits, W.4
Ahrens, R.5
Fick, R.6
-
2
-
-
0020657993
-
Epithelial dysfunction in cystic fibrosis lung disease
-
Boucher, R.C., Knowles, M.R., Stutts, M.J., and Gatzy, J.T. (1983). Epithelial dysfunction in cystic fibrosis lung disease. Lung 161, 1-17.
-
(1983)
Lung
, vol.161
, pp. 1-17
-
-
Boucher, R.C.1
Knowles, M.R.2
Stutts, M.J.3
Gatzy, J.T.4
-
4
-
-
0026523829
-
Cystic fibrosis: Molecular biology and therapeutic implications
-
Collins, F.S. (1992). Cystic fibrosis: molecular biology and therapeutic implications. Science 256, 774-779.
-
(1992)
Science
, vol.256
, pp. 774-779
-
-
Collins, F.S.1
-
5
-
-
0002497567
-
Pathophysiology of the lung disease in cystic fibrosis
-
P.B. Davis, ed. (New York: Marcel Dekker, Inc.)
-
Davis, P.B. (1993). Pathophysiology of the lung disease in cystic fibrosis. In Cystic Fibrosis, P.B. Davis, ed. (New York: Marcel Dekker, Inc.), pp. 193-218.
-
(1993)
Cystic Fibrosis
, pp. 193-218
-
-
Davis, P.B.1
-
6
-
-
0029061117
-
Bioaerosol concentrations in noncomplaint, complaint, and intervention homes in the Midwest
-
DeKoster, J.A., and Thorne, P.S. (1995). Bioaerosol concentrations in noncomplaint, complaint, and intervention homes in the Midwest. Am. Ind. Hyg. Assoc. J. 56, 573-580.
-
(1995)
Am. Ind. Hyg. Assoc. J.
, vol.56
, pp. 573-580
-
-
DeKoster, J.A.1
Thorne, P.S.2
-
7
-
-
0027298895
-
Airway epithelial cells are the site of expression of a mammalian antimicrobial peptide gene
-
Diamond, G., Jones, D.E., and Bevins, C.L. (1993). Airway epithelial cells are the site of expression of a mammalian antimicrobial peptide gene. Proc. Natl. Acad. Sci. USA 90, 4596-4600.
-
(1993)
Proc. Natl. Acad. Sci. USA
, vol.90
, pp. 4596-4600
-
-
Diamond, G.1
Jones, D.E.2
Bevins, C.L.3
-
8
-
-
0026951303
-
Submucosal glands are the predominant site of CFTR expression in the human bronchus
-
Engelhardt, J.F., Yankaskas, J.R., Ernst, S.A., Yang, Y., Marino, C.R., Boucher, B.C., Cohn, J.A., and Wilson, J.M. (1992). Submucosal glands are the predominant site of CFTR expression in the human bronchus. Nature Genet. 2, 240-248.
-
(1992)
Nature Genet.
, vol.2
, pp. 240-248
-
-
Engelhardt, J.F.1
Yankaskas, J.R.2
Ernst, S.A.3
Yang, Y.4
Marino, C.R.5
Boucher, B.C.6
Cohn, J.A.7
Wilson, J.M.8
-
9
-
-
0019521326
-
Cystic fibrosis pseudomonas opsonins: Inhibitory nature in an in vitro phagocytic assay
-
Fick, R.B., Jr., Naegel, G.P., Matthay, R.A., and Reynolds, H.Y. (1981). Cystic fibrosis pseudomonas opsonins: inhibitory nature in an in vitro phagocytic assay. J. Clin. Invest. 68, 899-914.
-
(1981)
J. Clin. Invest.
, vol.68
, pp. 899-914
-
-
Fick R.B., Jr.1
Naegel, G.P.2
Matthay, R.A.3
Reynolds, H.Y.4
-
10
-
-
0024523768
-
Increased bronchial chloride concentration in cystic fibrosis
-
Gilljam, H., Ellin, A., and Strandvik, B. (1989). Increased bronchial chloride concentration in cystic fibrosis. Scand. J. Clin. Lab. Invest. 49, 121-124.
-
(1989)
Scand. J. Clin. Lab. Invest.
, vol.49
, pp. 121-124
-
-
Gilljam, H.1
Ellin, A.2
Strandvik, B.3
-
11
-
-
0011940456
-
Host defenses in the lung: Neutrophils, complement, and other humoral mediators
-
J.F. Murray and J.A. Nadel, eds. (Philadelphia: W.B. Saunders)
-
Goldstein, I.M., and Shak, S. (1994). Host defenses in the lung: neutrophils, complement, and other humoral mediators. In Textbook of Respiratory Medicine, J.F. Murray and J.A. Nadel, eds. (Philadelphia: W.B. Saunders), pp. 402-418.
-
(1994)
Textbook of Respiratory Medicine
, pp. 402-418
-
-
Goldstein, I.M.1
Shak, S.2
-
12
-
-
0017872613
-
Pharyngeal aspiration in normal adults and patients with depressed consciousness
-
Huxley, E.J., Viroslav, J., Gray, W.R., and Pierce, A.K. (1978). Pharyngeal aspiration in normal adults and patients with depressed consciousness. Am. J. Med. 64, 564-568.
-
(1978)
Am. J. Med.
, vol.64
, pp. 564-568
-
-
Huxley, E.J.1
Viroslav, J.2
Gray, W.R.3
Pierce, A.K.4
-
13
-
-
0028920643
-
Cystic fibrosis epithelial cells have a receptor for pathogenic bacteria on their apical surface
-
Imundo, L., Barasch, J., Prince, A., and Al-Awqati, Q. (1995). Cystic fibrosis epithelial cells have a receptor for pathogenic bacteria on their apical surface. Proc. Natl. Acad. Sci. USA 92, 3019-3023.
-
(1995)
Proc. Natl. Acad. Sci. USA
, vol.92
, pp. 3019-3023
-
-
Imundo, L.1
Barasch, J.2
Prince, A.3
Al-Awqati, Q.4
-
14
-
-
0027363212
-
Altered fluid transport across airway epithelium in cystic fibrosis
-
Jiang, C., Finkbeiner, W.E., Widdicombe, J.H., McCray, P.B., Jr., and Miller, S.S. (1993). Altered fluid transport across airway epithelium in cystic fibrosis. Science 262, 424-427.
-
(1993)
Science
, vol.262
, pp. 424-427
-
-
Jiang, C.1
Finkbeiner, W.E.2
Widdicombe, J.H.3
McCray P.B., Jr.4
Miller, S.S.5
-
15
-
-
0027141851
-
Elemental composition of human airway surface fluid in healthy and diseased airways
-
Joris, L., Dab, I., and Quinton, P.M. (1993). Elemental composition of human airway surface fluid in healthy and diseased airways. Am. Rev. Respir. Dis. 148, 1633-1637.
-
(1993)
Am. Rev. Respir. Dis.
, vol.148
, pp. 1633-1637
-
-
Joris, L.1
Dab, I.2
Quinton, P.M.3
-
16
-
-
0028914085
-
Early pulmonary inflammation in infants with cystic fibrosis
-
Khan, T.Z., Wagener, J.S., Bost, T., Martinez, J., Accurso, F.J., and Riches, D.W.H. (1995). Early pulmonary inflammation in infants with cystic fibrosis. Am. J. Respir. Crit. Care Med. 151, 1075-1082.
-
(1995)
Am. J. Respir. Crit. Care Med.
, vol.151
, pp. 1075-1082
-
-
Khan, T.Z.1
Wagener, J.S.2
Bost, T.3
Martinez, J.4
Accurso, F.J.5
Riches, D.W.H.6
-
17
-
-
0025236867
-
A pilot study of aerosolized amiloride for the treatment of lung disease in cystic fibrosis
-
Knowles, M.R., Church, N.L., Waltner, W.E., Yankaskas, J.R., Gilligan, P., King, M., Edwards, L.J., Helms, R.W., and Boucher, R.C. (1990). A pilot study of aerosolized amiloride for the treatment of lung disease in cystic fibrosis. N. Engl. J. Med. 322, 1189-1194.
-
(1990)
N. Engl. J. Med.
, vol.322
, pp. 1189-1194
-
-
Knowles, M.R.1
Church, N.L.2
Waltner, W.E.3
Yankaskas, J.R.4
Gilligan, P.5
King, M.6
Edwards, L.J.7
Helms, R.W.8
Boucher, R.C.9
-
18
-
-
0025874599
-
Activation by extracellular nucleotides of chloride secretion in the airway epithelia of patients with cystic fibrosis
-
Knowles, M.R., Clarke, L.L., and Boucher, R.C. (1991). Activation by extracellular nucleotides of chloride secretion in the airway epithelia of patients with cystic fibrosis. N. Engl. J. Med. 325, 533-538.
-
(1991)
N. Engl. J. Med.
, vol.325
, pp. 533-538
-
-
Knowles, M.R.1
Clarke, L.L.2
Boucher, R.C.3
-
19
-
-
0001278692
-
Infection and inflammation of the lung in cystic fibrosis
-
P.B. Davis, ed. (New York: Marcel Dekker, Inc.)
-
Konstan, M.W., and Berger, M. (1993). Infection and inflammation of the lung in cystic fibrosis. In Cystic Fibrosis, P.B. Davis, ed. (New York: Marcel Dekker, Inc.), pp. 219-276.
-
(1993)
Cystic Fibrosis
, pp. 219-276
-
-
Konstan, M.W.1
Berger, M.2
-
20
-
-
0002054820
-
Airway inflammation and mucous hypersecretion
-
T. Takishima and S. Shimura, eds. (New York: Marcel Dekker, Inc.)
-
Larivée, P., Levine, S.J., Rieves, R.D., and Shelhamer, J.H. (1994). Airway inflammation and mucous hypersecretion. In Airway Secretion, T. Takishima and S. Shimura, eds. (New York: Marcel Dekker, Inc.), pp. 469-512.
-
(1994)
Airway Secretion
, pp. 469-512
-
-
Larivée, P.1
Levine, S.J.2
Rieves, R.D.3
Shelhamer, J.H.4
-
21
-
-
0027474382
-
Defensins: Anti-microbial and cytotoxic peptides of mammalian cells
-
Lehrer, R.I., Lichtenstein, A.K., and Ganz, T. (1993). Defensins: anti-microbial and cytotoxic peptides of mammalian cells. Annu. Rev. Immunol. 11, 105-128.
-
(1993)
Annu. Rev. Immunol.
, vol.11
, pp. 105-128
-
-
Lehrer, R.I.1
Lichtenstein, A.K.2
Ganz, T.3
-
22
-
-
0029242886
-
Tumor necrosis factor-α induces mucin hypersecretion and MUC-2 gene expression by human airway epithelial cells
-
Levine, S.J., Larivée, P., Logun, C., Angus, C.W., Ognibene, F.P., and Shelhamer, J.H. (1995). Tumor necrosis factor-α induces mucin hypersecretion and MUC-2 gene expression by human airway epithelial cells. Am. J. Respir. Cell Mol. Biol. 12, 196-204.
-
(1995)
Am. J. Respir. Cell Mol. Biol.
, vol.12
, pp. 196-204
-
-
Levine, S.J.1
Larivée, P.2
Logun, C.3
Angus, C.W.4
Ognibene, F.P.5
Shelhamer, J.H.6
-
23
-
-
0029051685
-
Defensins and other endogenous peptide antibiotics of vertebrates
-
Martin, E., Ganz, T., and Lehrer, R.I. (1995). Defensins and other endogenous peptide antibiotics of vertebrates. J. Leukoc. Biol. 58, 128-136.
-
(1995)
J. Leukoc. Biol.
, vol.58
, pp. 128-136
-
-
Martin, E.1
Ganz, T.2
Lehrer, R.I.3
-
24
-
-
0030021470
-
Role of mutant CFTR in hypersusceptibility of cystic fibrosis patients to lung infections
-
Pier, G.B., Grout, M., Zaidi, T.S., Olsen, J.C., Johnson, L.G., Yankaskas, J.R., and Goldberg, J.B. (1996). Role of mutant CFTR in hypersusceptibility of cystic fibrosis patients to lung infections. Science 271, 64-67.
-
(1996)
Science
, vol.271
, pp. 64-67
-
-
Pier, G.B.1
Grout, M.2
Zaidi, T.S.3
Olsen, J.C.4
Johnson, L.G.5
Yankaskas, J.R.6
Goldberg, J.B.7
-
25
-
-
0029395675
-
How do cystic fibrosis transmembrane conductance regulator mutations produce lung disease?
-
Pilewski, J.M., and Frizzell, R.A. (1995). How do cystic fibrosis transmembrane conductance regulator mutations produce lung disease? Curr. Opin. Pulm. Med. 1, 435-443.
-
(1995)
Curr. Opin. Pulm. Med.
, vol.1
, pp. 435-443
-
-
Pilewski, J.M.1
Frizzell, R.A.2
-
26
-
-
0343370211
-
Exocrine glands
-
L.M. Taussig, ed. (New York: Thieme-Statton, Inc.)
-
Quinton, P.M. (1984). Exocrine glands. In Cystic Fibrosis, L.M. Taussig, ed. (New York: Thieme-Statton, Inc.), pp 338-375.
-
(1984)
Cystic Fibrosis
, pp. 338-375
-
-
Quinton, P.M.1
-
27
-
-
0025349031
-
Cystic fibrosis: A disease in electrolyte transport
-
Quinton, P.M. (1990). Cystic fibrosis: a disease in electrolyte transport. FASEB J. 4, 2709-2717.
-
(1990)
FASEB J.
, vol.4
, pp. 2709-2717
-
-
Quinton, P.M.1
-
28
-
-
0028097887
-
Viscosity versus composition in airway pathology
-
Quinton, P.M. (1994). Viscosity versus composition in airway pathology. Am. J. Respir. Crit. Care Med. 149, 6-7.
-
(1994)
Am. J. Respir. Crit. Care Med.
, vol.149
, pp. 6-7
-
-
Quinton, P.M.1
-
29
-
-
0026377765
-
Predictive value of oropharyngeal cultures for identifying lower airway bacteria in cystic fibrosis patients
-
Ramsey, B.W., Wentz, K.R., Smith, A.L., Richardson, M., Williams-Warren, J., Hedges, D.L., Gibson, R., Redding, G.J., Lent, K., and Harris, K. (1991). Predictive value of oropharyngeal cultures for identifying lower airway bacteria in cystic fibrosis patients. Am. Rev. Respir. Dis. 144, 331-337.
-
(1991)
Am. Rev. Respir. Dis.
, vol.144
, pp. 331-337
-
-
Ramsey, B.W.1
Wentz, K.R.2
Smith, A.L.3
Richardson, M.4
Williams-Warren, J.5
Hedges, D.L.6
Gibson, R.7
Redding, G.J.8
Lent, K.9
Harris, K.10
-
30
-
-
0028343344
-
Mucociliary clearance in patients with cystic fibrosis and in normal subjects
-
Regnis, J.A., Robinson, M., Bailey, D.L., Cook, P., Hooper, P., Chan, H.-K., Gonda, I., Bautovich, G., and Bye, P.T.P. (1994). Mucociliary clearance in patients with cystic fibrosis and in normal subjects. Am. J. Respir. Grit. Care Med. 150, 66-71.
-
(1994)
Am. J. Respir. Grit. Care Med.
, vol.150
, pp. 66-71
-
-
Regnis, J.A.1
Robinson, M.2
Bailey, D.L.3
Cook, P.4
Hooper, P.5
Chan, H.-K.6
Gonda, I.7
Bautovich, G.8
Bye, P.T.P.9
-
31
-
-
0027481813
-
The cystic fibrosis transmembrane conductance regulator
-
Riordan, J.R. (1993). The cystic fibrosis transmembrane conductance regulator. Annu. Rev. Physiol. 55, 609-630.
-
(1993)
Annu. Rev. Physiol.
, vol.55
, pp. 609-630
-
-
Riordan, J.R.1
-
32
-
-
0027428606
-
Pseudomonas aeruginosa pili bind to asialoGM1 which is increased on the surface of cystic fibrosis epithelial cells
-
Saiman, L., and Prince, A. (1993). Pseudomonas aeruginosa pili bind to asialoGM1 which is increased on the surface of cystic fibrosis epithelial cells. J. Clin. Invest. 92, 1875-1880.
-
(1993)
J. Clin. Invest.
, vol.92
, pp. 1875-1880
-
-
Saiman, L.1
Prince, A.2
-
33
-
-
0015938912
-
Pulmonary mucociliary clearance in cystic fibrosis
-
Sanchis, J., Dolovich, M., Rossman, C., Wilson, W., and Newhouse, M. (1973). Pulmonary mucociliary clearance in cystic fibrosis. N. Engl. J. Med. 288, 651-654.
-
(1973)
N. Engl. J. Med.
, vol.288
, pp. 651-654
-
-
Sanchis, J.1
Dolovich, M.2
Rossman, C.3
Wilson, W.4
Newhouse, M.5
-
34
-
-
0028155017
-
Expression of cystic fibrosis transmembrane conductance regulator in a model epithelium
-
Sheppard, D.N., Carson, M.R., Ostedgaard, L.S., Denning, G.M., and Welsh, M.J. (1994). Expression of cystic fibrosis transmembrane conductance regulator in a model epithelium. Am. J. Physiol. 266, L405-L413.
-
(1994)
Am. J. Physiol.
, vol.266
-
-
Sheppard, D.N.1
Carson, M.R.2
Ostedgaard, L.S.3
Denning, G.M.4
Welsh, M.J.5
-
35
-
-
0027252125
-
Fluid and electrolyte transport by cultured human airway epithelia
-
Smith, J.J., and Welsh, M.J. (1993). Fluid and electrolyte transport by cultured human airway epithelia. J. Clin. Invest. 91, 1590-1597.
-
(1993)
J. Clin. Invest.
, vol.91
, pp. 1590-1597
-
-
Smith, J.J.1
Welsh, M.J.2
-
36
-
-
0028350324
-
Defective fluid transport by cystic fibrosis airway epithelia
-
Smith, J.J., Karp, P.H., and Welsh, M.J. (1994). Defective fluid transport by cystic fibrosis airway epithelia. J. Clin. Invest. 93, 1307-1311.
-
(1994)
J. Clin. Invest.
, vol.93
, pp. 1307-1311
-
-
Smith, J.J.1
Karp, P.H.2
Welsh, M.J.3
-
37
-
-
0000026508
-
Cystic fibrosis
-
C.R. Scriver, A.L. Beaudet, W.S. Sly, and D. Valle, eds. (New York: McGraw-Hill, Inc.)
-
Welsh, M.J., Tsui, L.-C., Boat, T.F., and Beaudet, A.L. (1995). Cystic fibrosis. In The Metabolic and Molecular Basis of Inherited Disease, C.R. Scriver, A.L. Beaudet, W.S. Sly, and D. Valle, eds. (New York: McGraw-Hill, Inc.), pp. 3799-3876.
-
(1995)
The Metabolic and Molecular Basis of Inherited Disease
, pp. 3799-3876
-
-
Welsh, M.J.1
Tsui, L.-C.2
Boat, T.F.3
Beaudet, A.L.4
-
38
-
-
0025281628
-
Increased levels of interleukin-1 in bronchoalveolar washings from children with bacterial pulmonary infections
-
Wilmott, R.W., Kassab, J.T., Kilian, P.L., Benjamin, W.R., Douglas, S.D., and Wood, R.E. (1990). Increased levels of interleukin-1 in bronchoalveolar washings from children with bacterial pulmonary infections. Am. Rev. Respir. Dis. 142, 365-368.
-
(1990)
Am. Rev. Respir. Dis.
, vol.142
, pp. 365-368
-
-
Wilmott, R.W.1
Kassab, J.T.2
Kilian, P.L.3
Benjamin, W.R.4
Douglas, S.D.5
Wood, R.E.6
-
39
-
-
0029424334
-
How do CFTR mutations cause cystic fibrosis?
-
Wine, J.J. (1995). How do CFTR mutations cause cystic fibrosis? Curr. Biol. 5, 1357-1359.
-
(1995)
Curr. Biol.
, vol.5
, pp. 1357-1359
-
-
Wine, J.J.1
-
40
-
-
0026636673
-
Differentiated structure and function of cultures from human tracheal epithelium
-
Yamaya, M., Finkbeiner, W.E., Chun, S.Y., and Widdicombe, J.H. (1992). Differentiated structure and function of cultures from human tracheal epithelium. Am. J. Physiol. 262, L713-L724.
-
(1992)
Am. J. Physiol.
, vol.262
-
-
Yamaya, M.1
Finkbeiner, W.E.2
Chun, S.Y.3
Widdicombe, J.H.4
-
41
-
-
0017251117
-
Mucociliary transport in trachea of patients with cystic fibrosis
-
Yeates, D.B., Sturgess, J.M., Kahn, S.R., Levison, H., and Aspin, N. (1976). Mucociliary transport in trachea of patients with cystic fibrosis. Arch. Dis. Child. 51, 28-33.
-
(1976)
Arch. Dis. Child.
, vol.51
, pp. 28-33
-
-
Yeates, D.B.1
Sturgess, J.M.2
Kahn, S.R.3
Levison, H.4
Aspin, N.5
-
42
-
-
0028170353
-
Correction of cAMP-stimulated fluid secretion in cystic fibrosis airway epithelia: Efficiency of adenovirus-mediated gene transfer in vitro
-
Zabner, J., Couture, L.A., Smith, A.E., and Welsh, M.J. (1994). Correction of cAMP-stimulated fluid secretion in cystic fibrosis airway epithelia: efficiency of adenovirus-mediated gene transfer in vitro. Hum. Gene Ther. 5, 585-593.
-
(1994)
Hum. Gene Ther.
, vol.5
, pp. 585-593
-
-
Zabner, J.1
Couture, L.A.2
Smith, A.E.3
Welsh, M.J.4
|