Defective fluid shear stress mechanotransduction mediates hereditary hemorrhagic telangiectasia

Journal of Cell Biology

Volumn 214, Issue 7, 2016, Pages

  Baeyens, Nicolas ^a   Larrivée, Bruno ^a,b   Ola, Roxana ^a   Hayward Piatkowskyi, Brielle ^a   Dubrac, Alexandre ^a   Huang, Billy ^a   Ross, Tyler D ^a   Coon, Brian G ^a   Min, Elizabeth ^a   Tsarfati, Maya ^a   Tong, Haibin ^a,c   Eichmann, Anne ^a,d   Schwartz, Martin A ^a,e  

^a YALE UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF MONTREAL   (Canada)

^c BEIHUA UNIVERSITY   (China)

^d PARIS CARDIOVASCULAR RESEARCH CENTER   (France)

^e Yale University   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ACTIVIN RECEPTOR LIKE KINASE 1; BONE MORPHOGENETIC PROTEIN 10; BONE MORPHOGENETIC PROTEIN 9; ENDOGLIN; UNCLASSIFIED DRUG; ACTIVIN RECEPTOR 2; ACVRL1 PROTEIN, HUMAN; BONE MORPHOGENETIC PROTEIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CELL PROLIFERATION; CONTROLLED STUDY; ENDOTHELIUM CELL; ENZYME ACTIVATION; ENZYME INHIBITION; HUMAN; HUMAN CELL; MECHANOTRANSDUCTION; MOUSE; NONHUMAN; PERICYTE; PRIORITY JOURNAL; RENDU OSLER WEBER DISEASE; SHEAR STRESS; SIGNAL TRANSDUCTION; ARTERIOVENOUS MALFORMATION; ARTERIOVENOUS SHUNT; BLOOD FLOW; BLOOD RHEOLOGY; GENE DELETION; HEK293 CELL LINE; MECHANICAL STRESS; METABOLISM; PATHOLOGY; RETINA; SOLUBILITY; UMBILICAL VEIN ENDOTHELIAL CELL;

ACTIVIN RECEPTORS, TYPE II; ARTERIOVENOUS MALFORMATIONS; ARTERIOVENOUS SHUNT, SURGICAL; BONE MORPHOGENETIC PROTEINS; CELL PROLIFERATION; ENDOGLIN; ENDOTHELIAL CELLS; GENE DELETION; HEK293 CELLS; HEMORHEOLOGY; HUMAN UMBILICAL VEIN ENDOTHELIAL CELLS; HUMANS; MECHANOTRANSDUCTION, CELLULAR; PERICYTES; REGIONAL BLOOD FLOW; RETINA; SIGNAL TRANSDUCTION; SOLUBILITY; STRESS, MECHANICAL; TELANGIECTASIA, HEREDITARY HEMORRHAGIC;

EID: 84991238142     PISSN: 00219525     EISSN: 15408140     Source Type: Journal    
DOI: 10.1083/jcb.201603106     Document Type: Article

References (35)

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