Cerebellar Transcriptome Profiles of ATXN1 Transgenic Mice Reveal SCA1 Disease Progression and Protection Pathways

Neuron

Volumn 89, Issue 6, 2016, Pages 1194-1207

  Ingram, Melissa ^a,b   Wozniak, Emily A L ^a,b   Duvick, Lisa ^a   Yang, Rendong ^b   Bergmann, Paul ^c   Carson, Robert ^a   O'Callaghan, Brennon ^a   Zoghbi, Huda Y ^d   Henzler, Christine ^b   Orr, Harry T ^a  

^a UNIVERSITY OF MINNESOTA MEDICAL SCHOOL   (United States)

^b UNIVERSITY OF MINNESOTA   (United States)

^c Foresight Logic   (United States)

^d TEXAS CHILDREN S HOSPITAL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CHOLECYSTOKININ A RECEPTOR; ATAXIN 1; ATXN1 PROTEIN, MOUSE; BETA CHEMOKINE; CCL28 PROTEIN, MOUSE; CHOLECYSTOKININ; CHOLECYSTOKININ B RECEPTOR; GUANINE NUCLEOTIDE EXCHANGE FACTOR; NERVE PROTEIN; NEUROPEPTIDE; NUCLEAR PROTEIN; PCP2 PROTEIN, MOUSE; PEPTIDE; POLYGLUTAMINE; TRANSCRIPTOME;

ADULT; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; ATXN1 GENE; CONTROLLED STUDY; DISEASE COURSE; ENZYME ACTIVATION; FEMALE; GENE; GENE EXPRESSION PROFILING; MALE; MOUSE; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; PURKINJE CELL; RNA SEQUENCE; SPINOCEREBELLAR ATAXIA TYPE 1; SPINOCEREBELLAR DEGENERATION; UPREGULATION; ANIMAL; C57BL MOUSE; CEREBELLUM; DEFICIENCY; DISEASE MODEL; GENE REGULATORY NETWORK; GENETICS; METABOLISM; PATHOLOGY; TRANSGENIC MOUSE;

ANIMALS; ATAXIN-1; CEREBELLUM; CHEMOKINES, CC; CHOLECYSTOKININ; DISEASE MODELS, ANIMAL; DISEASE PROGRESSION; GENE REGULATORY NETWORKS; GUANINE NUCLEOTIDE EXCHANGE FACTORS; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; NERVE TISSUE PROTEINS; NEUROPEPTIDES; NUCLEAR PROTEINS; PEPTIDES; PURKINJE CELLS; RECEPTOR, CHOLECYSTOKININ B; SPINOCEREBELLAR ATAXIAS; TRANSCRIPTOME; UP-REGULATION;

EID: 84960813277     PISSN: 08966273     EISSN: 10974199     Source Type: Journal    
DOI: 10.1016/j.neuron.2016.02.011     Document Type: Article

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