Structural basis of protein complex formation and reconfiguration by polyglutamine disease protein ataxin-1 and Capicua

Genes and Development

Volumn 27, Issue 6, 2013, Pages 590-595

  Kim, Eunji ^a   Lu, Hsiang Chih ^b,c   Zoghbi, Huda Y ^b,c,d   Song, Ji Joon ^a  

^a Korea Advanced Institute of Science and Technology (KAIST)   (South Korea)

^b BAYLOR COLLEGE OF MEDICINE   (United States)

^c TEXAS CHILDREN S HOSPITAL   (United States)

^d HOWARD HUGHES MEDICAL INSTITUTE   (United States)

Author keywords

Complex; Neurodegenerative disease; SCA1

Indexed keywords

ATAXIN 1; POLYGLUTAMINE;

ARTICLE; ATAXIA; CRYSTAL STRUCTURE; DEGENERATIVE DISEASE; DIMERIZATION; HUMAN; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN PROTEIN INTERACTION; PROTEIN STRUCTURE; SPINOCEREBELLAR ATAXIA TYPE 1;

DIMERIZATION; HUMANS; MODELS, MOLECULAR; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; PROTEIN BINDING; PROTEIN STRUCTURE, QUATERNARY; REPRESSOR PROTEINS;

EID: 84875324689     PISSN: 08909369     EISSN: 15495477     Source Type: Journal    
DOI: 10.1101/gad.212068.112     Document Type: Article

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