Liver transplantation for aHUS: still needed in the eculizumab era?

Pediatric Nephrology

Volumn 31, Issue 5, 2016, Pages 759-768

  Coppo, Rosanna ^a   Bonaudo, Roberto ^a   Peruzzi, R Licia ^a   Amore, Alessandro ^a   Brunati, Andrea ^b   Romagnoli, Renato ^b   Salizzoni, Mauro ^b   Galbusera, Miriam ^c   Gotti, Eliana ^d   Daina, Erica ^c   Noris, Marina ^c   Remuzzi, Giuseppe ^c,d,e  

^a REGINA MARGHERITA CHILDREN S HOSPITAL   (Italy)

^b UNIVERSITY OF TURIN   (Italy)

^c MARIO NEGRI INSTITUTE FOR PHARMACOLOGICAL RESEARCH   (Italy)

^d Azienda Ospedaliera Papa Giovanni XXIII   (Italy)

^e UNIVERSITY OF MILAN   (Italy)

Author keywords

Alternative; Atypical hemolytic uremic syndrome; Complement pathway; Eculizumab; Kidney transplantation; Liver transplantation; Rare diseases

Indexed keywords

5,10 METHYLENETETRAHYDROFOLATE REDUCTASE (FADH2); AMLODIPINE; AZATHIOPRINE; BASILIXIMAB; CALCIUM ANTAGONIST; CREATININE; CYCLOSPORIN; ECULIZUMAB; FRESH FROZEN PLASMA; LACTATE DEHYDROGENASE; MEPREDNISONE; MYCOPHENOLATE MOFETIL; PREDNISONE; STEROID; THYMOCYTE ANTIBODY; COMPLEMENT FACTOR H; COMPLEMENT FACTOR H, HUMAN; COMPLEMENT INHIBITOR; MONOCLONAL ANTIBODY;

ACUTE KIDNEY FAILURE; ARTICLE; CAPILLARY ENDOTHELIAL CELL; CASE REPORT; COMPLEMENT ACTIVATION; CREATININE BLOOD LEVEL; DISEASE ACTIVITY; DRUG SUBSTITUTION; DRUG TREATMENT FAILURE; END STAGE RENAL DISEASE; FOLLOW UP; GENETIC VARIABILITY; GLOMERULUS FILTRATION RATE; HAPLOTYPE; HEMATURIA; HEMOLYTIC UREMIC SYNDROME; HUMAN; HUMAN CELL; IMMUNOSUPPRESSIVE TREATMENT; INFANT; KIDNEY GRAFT; LACTATE DEHYDROGENASE BLOOD LEVEL; LIVER GRAFT; LIVER GRAFT REJECTION; LOW DRUG DOSE; MALE; PALLOR; PERITONEAL DIALYSIS; PLASMAPHERESIS; PRIORITY JOURNAL; RECURRENT DISEASE; SINGLE NUCLEOTIDE POLYMORPHISM; THROMBOCYTE COUNT; THROMBOCYTOPENIA; TREATMENT DURATION; UPPER RESPIRATORY TRACT INFECTION; URINARY TRACT INFECTION; ATYPICAL HEMOLYTIC UREMIC SYNDROME; CELL CULTURE; DNA MUTATIONAL ANALYSIS; DRUG EFFECTS; GENETIC PREDISPOSITION; GENETICS; HEREDITY; KIDNEY TRANSPLANTATION; LIVER TRANSPLANTATION; MUTATION; PEDIGREE; PHENOTYPE; TREATMENT OUTCOME;

ANTIBODIES, MONOCLONAL, HUMANIZED; ATYPICAL HEMOLYTIC UREMIC SYNDROME; CELLS, CULTURED; COMPLEMENT ACTIVATION; COMPLEMENT FACTOR H; COMPLEMENT INACTIVATING AGENTS; DNA MUTATIONAL ANALYSIS; GENETIC PREDISPOSITION TO DISEASE; HEREDITY; HUMANS; INFANT; KIDNEY TRANSPLANTATION; LIVER TRANSPLANTATION; MALE; MUTATION; PEDIGREE; PHENOTYPE; TREATMENT OUTCOME;

EID: 84948138781     PISSN: 0931041X     EISSN: 1432198X     Source Type: Journal    
DOI: 10.1007/s00467-015-3278-0     Document Type: Article

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