Von Willebrand factor cleaving protease (ADAMTS13) is deficient in recurrent and familial thrombotic thrombocytopenic purpura and hemolytic uremic syndrome

Blood

Volumn 100, Issue 3, 2002, Pages 778-785

  Remuzzi, Giuseppe ^a,b,c   Galbusera, Miriam ^a,b,c   Noris, Marina ^a,b,c   Canciani, Maria Teresa ^a,b,c   Daina, Erica ^a,b,c   Bresin, Elena ^a,b,c   Contaretti, Silvia ^a,b,c   Caprioli, Jessica ^a,b,c   Gamba, Sara ^a,b,c   Ruggenenti, Piero ^a,b,c   Perico, Norberto ^a,b,c   Mannucci, Pier O ^a,b,c  

^a MARIO NEGRI INSTITUTE FOR PHARMACOLOGICAL RESEARCH   (Italy)

^b OSPEDALI RIUNITI   (Italy)

^c UNIVERSITY OF MILAN   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

PROTEINASE; UNCLASSIFIED DRUG; VON WILLEBRAND FACTOR; VON WILLEBRAND FACTOR CLEAVING PROTEINASE;

ADOLESCENT; ADULT; ARTICLE; BLOOD SAMPLING; CLINICAL ARTICLE; ENZYME ACTIVITY; FAMILIAL DISEASE; FEMALE; HEMOLYTIC ANEMIA; HEMOLYTIC UREMIC SYNDROME; HUMAN; MALE; PRIORITY JOURNAL; RECURRENT DISEASE; THROMBOSIS; THROMBOTIC THROMBOCYTOPENIC PURPURA;

EID: 0036683408     PISSN: 00064971     EISSN: None     Source Type: Journal    
DOI: 10.1182/blood-2001-12-0166     Document Type: Article

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