Distinct electrophysiological and mechanical beating phenotypes of long QT syndrome type 1-specific cardiomyocytes carrying different mutations

IJC Heart and Vasculature

Volumn 8, Issue , 2015, Pages 19-31

  Kiviaho, Anna L ^a   Ahola, Antti ^b   Larsson, Kim ^a   Penttinen, Kirsi ^a   Swan, Heikki ^c   Pekkanen Mattila, Mari ^a   Venäläinen, Henna ^a   Paavola, Kiti ^a   Hyttinen, Jari ^b   Aalto Setälä, Katriina ^a,d  

^a TAMPERE UNIVERSITY OF TECHNOLOGY   (Finland)

^b TAMPERE UNIVERSITY OF TECHNOLOGY   (Finland)

^c HELSINKI UNIVERSITY CENTRAL HOSPITAL   (Finland)

^d TAMPERE UNIVERSITY HOSPITAL   (Finland)

Author keywords

Arrhythmia; Calcium imaging; Digital image correlation; Induced pluripotent stem cell; Long QT syndrome; Patch clamp

Indexed keywords

CALCIUM ION;

ADULT; ALLELIC IMBALANCE; ARTICLE; CASE REPORT; CELL DIFFERENTIATION; CELLULAR, SUBCELLULAR AND MOLECULAR BIOLOGICAL PHENOMENA AND FUNCTIONS; ELECTROPHYSIOLOGY; FEMALE; GENE; GENE MUTATION; HEART MUSCLE CELL; HEART MUSCLE FIBER MEMBRANE POTENTIAL; HUMAN; IMMUNOCYTOCHEMISTRY; KCNQ1 GENE; LONG QT SYNDROME 1; MECHANICAL BEATING; MIDDLE AGED; PHENOTYPE; PLURIPOTENT STEM CELL; REPOLARIZATION; VIDEORECORDING;

EID: 84934929449     PISSN: 23529067     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.ijcha.2015.04.008     Document Type: Article

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