Cardiomyocytes obtained from induced pluripotent stem cells with Long-QT syndrome 3 recapitulate typical disease-specific features in vitro

Circulation Research

Volumn 109, Issue 8, 2011, Pages 841-847

  Malan, Daniela ^a   Friedrichs, Stephanie ^a   Fleischmann, Bernd K ^a   Sasse, Philipp ^a  

^a UNIVERSITY OF BONN   (Germany)

Author keywords

cardiac electrophysiology; cell culture; induced pluripotent stem cells; long QT syndrome; SCN5A

Indexed keywords

SODIUM CHANNEL;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CONTROLLED STUDY; HEART DEPOLARIZATION; HEART MUSCLE CELL; HEART MUSCLE FIBER MEMBRANE POTENTIAL; IN VITRO STUDY; LONG QT SYNDROME; MOUSE; MUTATION; NONHUMAN; PATHOPHYSIOLOGY; PLURIPOTENT STEM CELL; PRIORITY JOURNAL;

ANIMALS; CELL DIFFERENTIATION; CELL LINE; HUMANS; INDUCED PLURIPOTENT STEM CELLS; LONG QT SYNDROME; MICE; MICE, SCID; MICE, TRANSGENIC; MYOCYTES, CARDIAC; SODIUM CHANNELS;

EID: 80053574096     PISSN: 00097330     EISSN: 15244571     Source Type: Journal    
DOI: 10.1161/CIRCRESAHA.111.243139     Document Type: Article

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