X-linked Inhibitor of Apoptosis Protein Deficiency: More than an X-linked Lymphoproliferative Syndrome

Journal of Clinical Immunology

Volumn 35, Issue 4, 2015, Pages 331-338

  Aguilar, Claire ^a   Latour, Sylvain ^b  

^a INSERM   (France)

^b IMAGINE INSTITUTE   (France)

Author keywords

crohn s disease; hemophagocytic lymphohistiocytosis; inflammatory bowel disease; susceptibility to EBV infection; X linked lymphoproliferative syndrome

Indexed keywords

AZATHIOPRINE; CORTICOSTEROID; CYCLOSPORIN; ETOPOSIDE; NUCLEOTIDE BINDING OLIGOMERIZATION DOMAIN LIKE RECEPTOR; TUMOR NECROSIS FACTOR ALPHA INHIBITOR; X LINKED INHIBITOR OF APOPTOSIS;

ALLOGENEIC HEMATOPOIETIC STEM CELL TRANSPLANTATION; APOPTOSIS; CLINICAL FEATURE; CORTICOSTEROID THERAPY; CYTOTOXICITY; HUMAN; IMMUNE RESPONSE; IMMUNOGENETICS; IMMUNOPATHOGENESIS; IMMUNOSUPPRESSIVE TREATMENT; LYMPHOPROLIFERATIVE DISEASE; MOLECULAR PATHOLOGY; PATHOPHYSIOLOGY; PHENOTYPE; PRIORITY JOURNAL; PROGNOSIS; PROTEIN FUNCTION; REVIEW; SIGNAL TRANSDUCTION; X CHROMOSOME LINKED DISORDER; X LINKED INHIBITOR OF APOPTOSIS PROTEIN DEFICIENCY; GENETICS; LYMPHOPROLIFERATIVE DISORDERS; METABOLISM;

HUMANS; LYMPHOPROLIFERATIVE DISORDERS; PROGNOSIS; X-LINKED INHIBITOR OF APOPTOSIS PROTEIN;

EID: 84929840480     PISSN: 02719142     EISSN: 15732592     Source Type: Journal    
DOI: 10.1007/s10875-015-0141-9     Document Type: Review

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