Altered cofactor regulation with disease-associated p97/VCP mutations

Proceedings of the National Academy of Sciences of the United States of America

Volumn 112, Issue 14, 2015, Pages E1705-E1714

  Zhang, Xiaoyi ^a,b   Gui, Lin ^a,b   Zhang, Xiaoyan ^c   Bulfer, Stacie L ^d   Sanghez, Valentina ^a   Wong, Daniel E ^a   Lee, YouJin ^e   Lehmann, Lynn ^f   Lee, James Siho ^g   Shih, Pei Yin ^g   Lin, Henry J ^a   Iacovino, Michelina ^a   Weihl, Conrad C ^e   Arkin, Michelle R ^d   Wang, Yanzhuang ^c   Chou, Tsui Fen ^a  

^a HARBOR UCLA MEDICAL CENTER   (United States)

^b CAPITAL MEDICAL UNIVERSITY   (China)

^c UNIVERSITY OF MICHIGAN   (United States)

^d UNIVERSITY OF CALIFORNIA   (United States)

^e WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

^f NanoTemper Technologies GmbH   (Germany)

^g California Institute of Technology   (United States)

Author keywords

AAA ATPase; MSP1; P47; P97NCP; Steady state kinetics

Indexed keywords

ADENOSINE DIPHOSPHATE; ADENOSINE TRIPHOSPHATASE; ADENOSINE TRIPHOSPHATE; PROTEIN P37; PROTEIN P47; PROTEIN P97; VALOSIN CONTAINING PROTEIN; CDC48 PROTEIN; CELL CYCLE PROTEIN; P37 PROTEIN, HUMAN; SIGNAL TRANSDUCING ADAPTOR PROTEIN;

AMINO ACID SEQUENCE; ANIMAL CELL; ARTICLE; AUTOPHAGOSOME; AUTOPHAGY; CONFORMATIONAL TRANSITION; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; ENZYME ACTIVITY; ENZYME BINDING; ENZYME CONFORMATION; ENZYME REGULATION; GENE MUTATION; IN VITRO STUDY; MITOSIS; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN DOMAIN; PROTEIN PROTEIN INTERACTION; RAT; STEADY STATE; STOICHIOMETRY; BONE DISEASE; DEGENERATIVE DISEASE; GOLGI COMPLEX; HOMEOSTASIS; HUMAN; METABOLISM; MUSCLE DISEASE; MUTATION; PHENOTYPE; PROTEIN TERTIARY STRUCTURE; SIZE EXCLUSION CHROMATOGRAPHY; SURFACE PLASMON RESONANCE; TUMOR CELL LINE;

ADAPTOR PROTEINS, SIGNAL TRANSDUCING; ADENOSINE TRIPHOSPHATASES; ADENOSINE TRIPHOSPHATE; AUTOPHAGY; BONE DISEASES; CELL CYCLE PROTEINS; CELL LINE, TUMOR; CHROMATOGRAPHY, GEL; GOLGI APPARATUS; HOMEOSTASIS; HUMANS; MUSCULAR DISEASES; MUTATION; NEURODEGENERATIVE DISEASES; PHENOTYPE; PROTEIN STRUCTURE, TERTIARY; SURFACE PLASMON RESONANCE;

EID: 84929657116     PISSN: 00278424     EISSN: 10916490     Source Type: Journal    
DOI: 10.1073/pnas.1418820112     Document Type: Article

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