Nuclear-encoded factors involved in post-transcriptional processing and modification of mitochondrial tRNAs in human disease

Frontiers in Genetics

Volumn 5, Issue FEB, 2015, Pages

  Powell, Christopher A ^a   Nicholls, Thomas J ^a,b   Minczuk, Michal ^a  

^a UNIVERSITY OF CAMBRIDGE   (United Kingdom)

^b UNIVERSITY OF GOTHENBURG   (Sweden)

Author keywords

Mitochondria; Mitochondrial disease; Post transcriptional regulation; RNA modification; RNA processing; TRNA

Indexed keywords

GTP BINDING PROTEIN 3; MESSENGER RNA; METHIONINE TRANSFER RNA FORMYLTRANSFERASE; METHYLTRANSFERASE; MITOCHONDRIAL PROTEIN; MITOCHONDRIAL RNA; MTO1 PROTEIN; POLYRIBONUCLEOTIDE NUCLEOTIDYLTRANSFERASE; PROTEIN; RIBOSOME RNA; TRANSFER RNA; TRMT1 PROTEIN; TRMT10C PROTEIN; TRMT5 PROTEIN; TRMT61B PROTEIN; TRNT1 PROTEIN; UNCLASSIFIED DRUG;

CHOREOATHETOSIS; DISEASE COURSE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME ACTIVITY; GENE MUTATION; GENETIC CODE; GENETIC TRANSCRIPTION; HUMAN; MITOCHONDRIAL ENCEPHALOMYOPATHY; MITOCHONDRIAL GENOME; MITOCHONDRIAL RESPIRATION; PROTEIN POLYMERIZATION; REVIEW; RNA PROCESSING; RNA TRANSLATION; TISSUE SPECIFICITY;

MAMMALIA;

EID: 84923531787     PISSN: None     EISSN: 16648021     Source Type: Journal    
DOI: 10.3389/fgene.2015.00079     Document Type: Review

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