The mitochondrial myopathy, encephalopathy, lactic acidosis, and stroke- like episode syndrome-associated human mitochondrial tRNA(Leu(UUR)) mutation causes aminoacylation deficiency and concomitant reduced association of mRNA with ribosomes

Journal of Biological Chemistry

Volumn 275, Issue 25, 2000, Pages 19198-19209

  Chomyn, Anne ^a   Enriquez, José Antonio ^a,b   Micol, Vicente ^a,c   Fernandez Silva, Patricio ^a,b   Attardi, Giuseppe ^a  

^a CALIFORNIA INSTITUTE OF TECHNOLOGY   (United States)

^b UNIVERSITY OF ZARAGOZA   (Spain)

^c MIGUEL HERNÁNDEZ UNIVERSITY   (Spain)

Author keywords

[No Author keywords available]

Indexed keywords

MESSENGER RNA; TRANSFER RNA;

AMINOACYLATION; ARTICLE; BINDING SITE; BRAIN DISEASE; CONTROLLED STUDY; GENE MUTATION; GENETIC ASSOCIATION; GENETIC TRANSCRIPTION; HUMAN; HUMAN CELL; LACTIC ACIDOSIS; MELAS SYNDROME; MITOCHONDRIAL MYOPATHY; PRIORITY JOURNAL; PROTEIN SYNTHESIS; RIBOSOME; RNA STRUCTURE; RNA TRANSLATION;

ACYLATION; BASE SEQUENCE; CELL LINE; DNA FOOTPRINTING; DNA, MITOCHONDRIAL; DNA, RIBOSOMAL; HUMANS; MELAS SYNDROME; MITOCHONDRIA; MUTATION; PROTEIN BIOSYNTHESIS; RIBOSOMES; RNA, MESSENGER; RNA, TRANSFER, LEU;

EID: 0034705419     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M908734199     Document Type: Article

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