A deafness-associated tRNAHis mutation alters the mitochondrial function, ROS production and membrane potential

Nucleic Acids Research

Volumn 42, Issue 12, 2014, Pages 8039-8048

  Gong, Shasha ^a   Peng, Yanyan ^a,b   Jiang, Pingping ^a   Wang, Meng ^a   Fan, Mingjie ^a   Wang, Xinjian ^b   Zhou, Hong ^a   Li, Huawei ^c   Yan, Qingfeng ^a   Huang, Taosheng ^b   Guan, Min Xin ^a,b  

^a Zhejiang University   (China)

^b CINCINNATI CHILDREN'S HOSPITAL MEDICAL CENTER   (United States)

^c FUDAN UNIVERSITY   (China)

Author keywords

[No Author keywords available]

Indexed keywords

ADENOSINE TRIPHOSPHATE; HISTIDINE; MITOCHONDRIAL DNA; MITOCHONDRIAL RNA; REACTIVE OXYGEN METABOLITE; TRANSFER RNA; HISTIDINE TRANSFER RNA; MITOCHONDRIAL PROTEIN;

ARTICLE; BASE PAIRING; CONFORMATIONAL TRANSITION; CONTROLLED STUDY; ELECTROPHORETIC MOBILITY; GENE MUTATION; GENETIC ASSOCIATION; HEARING IMPAIRMENT; HUMAN; HUMAN CELL; MITOCHONDRIAL MEMBRANE POTENTIAL; MITOCHONDRIAL RESPIRATION; MOLECULAR PATHOLOGY; OXIDATIVE PHOSPHORYLATION; PRIORITY JOURNAL; RNA CONFORMATION; RNA METABOLISM; TRANSFER RNA GENE; AMINOACYLATION; BIOSYNTHESIS; CELL LINE; CELL RESPIRATION; CHEMISTRY; GENETICS; METABOLISM; MITOCHONDRION; MUTATION;

ADENOSINE TRIPHOSPHATE; CELL LINE; CELL RESPIRATION; DEAFNESS; HUMANS; MEMBRANE POTENTIAL, MITOCHONDRIAL; MITOCHONDRIA; MITOCHONDRIAL PROTEINS; MUTATION; REACTIVE OXYGEN SPECIES; RNA, TRANSFER, HIS; TRANSFER RNA AMINOACYLATION;

EID: 84904016403     PISSN: 03051048     EISSN: 13624962     Source Type: Journal    
DOI: 10.1093/nar/gku466     Document Type: Article

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