Human mitochondrial tRNA quality control in health and disease: A channeling mechanism?

RNA Biology

Volumn 9, Issue 1, 2012, Pages 33-39

  Belostotsky, Ruth ^a   Frishberg, Yaacov ^a,b   Entelis, Nina ^c  

^a SHAARE ZEDEK MEDICAL CENTER   (Israel)

^b HEBREW UNIVERSITY   (Israel)

^c UNIVERSITÉ DE STRASBOURG   (France)

Author keywords

Aminoacyl tRNA synthetases; Elongation factor Tu; Human diseases; Mitochondria; tRNA; tRNA channelling

Indexed keywords

AMINOACYL TRANSFER RNA SYTHETASE; ELONGATION FACTOR TU; RIBONUCLEASE P; SYNTHETASE; TRANSFER RNA; UNCLASSIFIED DRUG;

AMINO ACID SUBSTITUTION; AMINOACYLATION; GENE MUTATION; GENE OVEREXPRESSION; HUMAN; MITOCHONDRION; NUCLEAR PORE COMPLEX; PROTEIN FUNCTION; PROTEIN MODIFICATION; PROTEIN RNA BINDING; PROTEIN STRUCTURE; REVIEW; RIBOSOME; RNA DEGRADATION; RNA SEQUENCE; RNA STABILITY; RNA SYNTHESIS; RNA TRANSCRIPTION;

EID: 84856780095     PISSN: 15476286     EISSN: 15558584     Source Type: Journal    
DOI: 10.4161/rna.9.1.18009     Document Type: Review

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