Biochemical analysis of respiratory function in cybrid cell lines harbouring mitochondrial DNA mutations

Biochemical Journal

Volumn 384, Issue 2, 2004, Pages 287-293

  Pallotti, Francesco ^a,b   Baracca, Alessandra ^c   Hernandez Rosa, Evelyn ^a   Walker, Winsome F ^a   Solaini, Giancarlo ^d   Lenaz, Giorgio ^c   Melzi D'Eril, Gian Vico ^b   Dimauro, Salvatore ^a   Schon, Eric A ^a   Davidson, Mercy M ^a  

^a New York Presbyterian Columbia University Medical Center   (United States)

^b UNIVERSITY OF INSUBRIA   (Italy)

^c UNIVERSITY OF BOLOGNA   (Italy)

^d UNIVERSITY OF PISA   (Italy)

Author keywords

ATP synthesis; Cybrid; Lactate; Mitochondrial DNA mutation; Oxygen consumption; Pyruvate

Indexed keywords

CELLS; DNA; GLYCOLS;

GLUCOSE OXIDATION; RESPIRATORY FUNCTIONS;

BIOCHEMISTRY;

ADENOSINE TRIPHOSPHATASE; ADENOSINE TRIPHOSPHATE; DNA; PYRUVIC ACID;

ARTICLE; CELL COUNT; CLINICAL FEATURE; CONTROLLED STUDY; CORRELATION ANALYSIS; CYBRID; DISEASE ASSOCIATION; GENE DELETION; GENE MUTATION; GENOME; GLUCOSE OXIDATION; GLYCOLYSIS; HUMAN; HUMAN CELL; MITOCHONDRION; OXIDATION; OXYGEN CONSUMPTION; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN PHOSPHORYLATION; RESPIRATORY FUNCTION; WILD TYPE;

ADENOSINE TRIPHOSPHATE; BLOOD PLATELETS; CELL LINE; CELL RESPIRATION; CITRIC ACID; CYTOPLASM; DNA, MITOCHONDRIAL; EXTRACELLULAR MATRIX; FIBROBLASTS; HUMANS; HYBRID CELLS; INTRACELLULAR SPACE; LACTIC ACID; MUTATION; MYOBLASTS; OXYGEN CONSUMPTION; PYRUVIC ACID;

EID: 10644245921     PISSN: 02646021     EISSN: None     Source Type: Journal    
DOI: 10.1042/BJ20040561     Document Type: Article

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