Wiskott-Aldrich Syndrome protein deficiency perturbs the homeostasis of B-cell compartment in humans

Journal of Autoimmunity

Volumn 50, Issue , 2014, Pages 42-50

  Castiello, Maria Carmina ^a,b   Bosticardo, Marita ^a   Pala, Francesca ^a   Catucci, Marco ^a   Chamberlain, Nicolas ^c   Van Zelm, Menno C ^d   Driessen, Gertjan J ^d   Pac, Malgorzata ^e   Bernatowska, Ewa ^e   Scaramuzza, Samantha ^a   Aiuti, Alessandro ^a,f   Sauer, Aisha V ^a   Traggiai, Elisabetta ^g   Meffre, Eric ^c   Villa, Anna ^a,h   Van der Burg, Mirjam ^d  

^a SAN RAFFAELE SCIENTIFIC INSTITUTE   (Italy)

^b VITA SALUTE SAN RAFFAELE UNIVERSITY   (Italy)

^c YALE UNIVERSITY SCHOOL OF MEDICINE   (United States)

^d ERASMUS MEDICAL CENTER   (Netherlands)

^e CHILDREN'S MEMORIAL HEALTH INSTITUTE   (Poland)

^f UNIVERSITY OF ROME TOR VERGATA   (Italy)

^g NOVARTIS PHARMA AG   (Switzerland)

^h CNR   (Italy)

Author keywords

Autoimmunity; B lymphocyte; B cell activating factor (BAFF); Immunoglobulin repertoire; Primary immunodeficiency; Wiskott aldrich syndrome

Indexed keywords

B CELL ACTIVATING FACTOR; COMPLEMENT COMPONENT C3D RECEPTOR; IMMUNOGLOBULIN HEAVY CHAIN; STROMAL CELL DERIVED FACTOR 1; TNFSF13B PROTEIN, HUMAN; WISKOTT ALDRICH SYNDROME PROTEIN;

AUTOIMMUNITY; B LYMPHOCYTE; BLOOD; BONE MARROW; CELL DIFFERENTIATION; CELL MOTION; DEFICIENCY; DISEASE PREDISPOSITION; GENE EXPRESSION; GENETICS; HOMEOSTASIS; HUMAN; IMMUNOLOGICAL MEMORY; IMMUNOLOGY; PATHOLOGY; WISKOTT ALDRICH SYNDROME;

AUTOIMMUNITY; B-CELL ACTIVATING FACTOR; B-LYMPHOCYTES; BONE MARROW; CELL DIFFERENTIATION; CELL MOVEMENT; CHEMOKINE CXCL12; DISEASE SUSCEPTIBILITY; GENE EXPRESSION; HOMEOSTASIS; HUMANS; IMMUNOGLOBULIN HEAVY CHAINS; IMMUNOLOGIC MEMORY; RECEPTORS, COMPLEMENT 3D; WISKOTT-ALDRICH SYNDROME; WISKOTT-ALDRICH SYNDROME PROTEIN;

EID: 84898802787     PISSN: 08968411     EISSN: 10959157     Source Type: Journal    
DOI: 10.1016/j.jaut.2013.10.006     Document Type: Article

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