S-palmitoylation regulates biogenesis of core glycosylated wild-type and F508del CFTR in a post-ER compartment

Biochemical Journal

Volumn 459, Issue 2, 2014, Pages 417-425

  Mcclure, Michelle L ^a,b   Wen, Hui ^a   Fortenberry, James ^a   Hong, Jeong S ^a,c   Sorscher, Eric J ^a,d  

^a UNIVERSITY OF ALABAMA AT BIRMINGHAM   (United States)

^b UNIVERSITY OF ALABAMA AT BIRMINGHAM   (United States)

^c UNIVERSITY OF ALABAMA AT BIRMINGHAM   (United States)

^d University of Alabama at Birmingham   (United States)

Author keywords

Cystic fibrosis; Palmitoylation; Post translational modification; Protein maturation; Protein trafficking

Indexed keywords

2 BROMOPALMITIC ACID; CORE PROTEIN; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; GLYCOSYLATED PROTEIN; ION CHANNEL; MUTANT PROTEIN;

ARTICLE; BIOGENESIS; CELL ASSAY; CELL COMPARTMENTALIZATION; CELL MATURATION; CELL SURFACE; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; HALIDE EFFLUX ASSAY; HUMAN; HUMAN CELL; IMMUNOFLUORESCENCE; IMMUNOPRECIPITATION; ISOTOPE LABELING; LOW TEMPERATURE; PALMITOYLATION; PRIORITY JOURNAL; PROTEIN DEFECT; S PALMITOYLATION; SHORT CIRCUIT CURRENT; STEADY STATE; WESTERN BLOTTING;

ACETYLTRANSFERASES; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; ENDOPLASMIC RETICULUM; GENE EXPRESSION REGULATION; HEK293 CELLS; HELA CELLS; HUMANS; INTRACELLULAR SIGNALING PEPTIDES AND PROTEINS; LIPOYLATION; MUTATION; PROTEIN PROCESSING, POST-TRANSLATIONAL; PROTEIN TRANSPORT; RECOMBINANT PROTEINS;

EID: 84897529001     PISSN: 02646021     EISSN: 14708728     Source Type: Journal    
DOI: 10.1042/BJ20131037     Document Type: Article

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