Mammalian Fe-S cluster biogenesis and its implication in disease

Biochimie

Volumn 100, Issue 1, 2014, Pages 48-60

  Beilschmidt, Lena K ^a,b,c,d,e   Puccio, Hélène M ^a,b,c,d,e  

^a INSTITUT DE GÉNÉTIQUE ET DE BIOLOGIE MOLÉCULAIRE ET CELLULAIRE   (France)

^b INSERM   (France)

^c CNRS   (France)

^d UNIVERSITÉ DE STRASBOURG   (France)

^e Paris Sciences et Lettres   (France)

Author keywords

Genetic disease; Iron sulfur cluster; Mitochondria; Mutation

Indexed keywords

IRON; SULFUR;

BIOGENESIS; CATARACT; FRIEDREICH ATAXIA; GENE CLUSTER; GENE MUTATION; GENETIC CODE; GENETIC DISORDER; GENETIC REGULATION; IN VIVO STUDY; IRON OVERLOAD; MACHINE; MAMMAL; MICROCYTIC ANEMIA; MITOCHONDRIAL ENCEPHALOMYOPATHY; MITOCHONDRIAL MYOPATHY; MITOCHONDRION; MURINE MODEL; NONHUMAN; PROTEIN FUNCTION; RESPIRATORY CHAIN; RESPIRATORY CHAIN DEFICIENCY; RESPIRATORY FAILURE; REVIEW; SIDEROBLASTIC ANEMIA; X LINKED SIDEROBLASTIC ANEMIA;

EUKARYOTA; MAMMALIA; MURINAE;

GENETIC DISEASE; IRON-SULFUR CLUSTER; MITOCHONDRIA; MUTATION;

ANIMALS; ESCHERICHIA COLI; GENE EXPRESSION REGULATION; HUMANS; IRON-SULFUR PROTEINS; MICE; MITOCHONDRIA; MITOCHONDRIAL DISEASES; MITOCHONDRIAL PROTEINS; MUTATION; OXIDATIVE PHOSPHORYLATION; OXYGEN;

EID: 84897099325     PISSN: 03009084     EISSN: 61831638     Source Type: Journal    
DOI: 10.1016/j.biochi.2014.01.009     Document Type: Review

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