The unfolded protein response has a protective role in yeast models of classic galactosemia

DMM Disease Models and Mechanisms

Volumn 7, Issue 1, 2014, Pages 55-61

  De Souza, Evandro A ^a   Pimentel, Felipe S A ^a   Machado, Caio M ^a   Martins, Larissa S ^a   Da Silva, Wagner S ^a   Montero Lomelí, Mónica ^a   Masuda, Claudio A ^a  

^a FEDERAL UNIVERSITY OF RIO DE JANEIRO   (Brazil)

Author keywords

Galactose; Galactosemia; Lithium; UPR; Yeast

Indexed keywords

GALACTOSE; GALACTOSE 1 PHOSPHATE URIDYLYLTRANSFERASE; LITHIUM; MEMBRANE PROTEIN; PHOSPHATE; TRANSCRIPTION FACTOR; TRANSCRIPTION FACTOR HAC1P; UNCLASSIFIED DRUG;

ARTICLE; CARBOHYDRATE METABOLISM; CARBON SOURCE; CELL GROWTH; CELL SURVIVAL; CELL VIABILITY ASSAY; CONTROLLED STUDY; CYTOTOXICITY; ENDOPLASMIC RETICULUM; ENDOPLASMIC RETICULUM STRESS; ENZYME SYNTHESIS; GALACTOSEMIA; NONHUMAN; PRIORITY JOURNAL; SACCHAROMYCES CEREVISIAE; UNFOLDED PROTEIN RESPONSE; YEAST; YEAST CELL;

GALACTOSE; GALACTOSEMIA; LITHIUM; UPR; YEAST;

ALTERNATIVE SPLICING; BASIC-LEUCINE ZIPPER TRANSCRIPTION FACTORS; ENDOPLASMIC RETICULUM; FUNGAL PROTEINS; GALACTOKINASE; GALACTOSE; GALACTOSEMIAS; GALACTOSEPHOSPHATES; GENE EXPRESSION REGULATION, FUNGAL; GLYCOPROTEINS; HSP70 HEAT-SHOCK PROTEINS; HUMANS; MUTATION; OXIDOREDUCTASES ACTING ON SULFUR GROUP DONORS; PROTEIN FOLDING; REPRESSOR PROTEINS; RNA, MESSENGER; SACCHAROMYCES CEREVISIAE; SACCHAROMYCES CEREVISIAE PROTEINS; UNFOLDED PROTEIN RESPONSE;

EID: 84892387872     PISSN: 17548403     EISSN: 17548411     Source Type: Journal    
DOI: 10.1242/dmm.012641     Document Type: Article

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