Defective interactions of protein partner with ion channels and transporters as alternative mechanisms of membrane channelopathies

Biochimica et Biophysica Acta - Biomembranes

Volumn 1838, Issue 2, 2014, Pages 723-730

  Kline, Crystal F ^a   Mohler, Peter J ^a  

^a OHIO STATE UNIVERSITY   (United States)

Author keywords

Ankyrin B syndrome; Auxiliary subunit; Cardiac arrhythmia; Catecholaminergic polymorphic ventricular tachycardia; Ion channel

Indexed keywords

ADENOSINE TRIPHOSPHATE SENSITIVE POTASSIUM CHANNEL; ALPHA NSYNTROPHIN; ANKYRIN; ANKYRIN B; ANKYRIN G; CARRIER PROTEIN; CASPASE 2; CAVEOLIN 3; CYCLIC AMP DEPENDENT PROTEIN KINASE; EPITHELIAL SODIUM CHANNEL; POTASSIUM CHANNEL; POTASSIUM CHANNEL KCNQ1; RYANODINE RECEPTOR; SODIUM CHANNEL; SODIUM CHANNEL NAV1.5; SYNTROPHIN; UBIQUITIN PROTEIN LIGASE NEDD4; UNCLASSIFIED DRUG;

ANKYRIN B SYNDROME; ARRHYTHMOGENESIS; BRUGADA SYNDROME; CATECHOLAMINERGIC POLYMORPHIC VENTRICULAR TACHYCARDIA; CELL DAMAGE; CELL STIMULATION; CHANNELOPATHY; DISEASE COURSE; GLUCOSE HOMEOSTASIS; HUMAN; HYPERTENSION; LIDDLE SYNDROME; LONG QT SYNDROME; MACROMOLECULE; NONHUMAN; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN DEFECT; PROTEIN PHOSPHORYLATION; PROTEIN PROTEIN INTERACTION; REVIEW; SYNDROME;

ANKYRIN-B SYNDROME; AUXILIARY SUBUNIT; CARDIAC ARRHYTHMIA; CATECHOLAMINERGIC POLYMORPHIC VENTRICULAR TACHYCARDIA; ION CHANNEL;

ANIMALS; BIOLOGICAL TRANSPORT; CHANNELOPATHIES; HUMANS; ION CHANNELS; PROTEIN INTERACTION DOMAINS AND MOTIFS;

EID: 84892144999     PISSN: 00052736     EISSN: 18792642     Source Type: Journal    
DOI: 10.1016/j.bbamem.2013.05.024     Document Type: Review

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