Muscle atrophy in Limb Girdle Muscular Dystrophy 2A: A morphometric and molecular study

Neuropathology and Applied Neurobiology

Volumn 39, Issue 7, 2013, Pages 762-771

  Fanin, M ^a   Nascimbeni, A C ^a   Angelini, C ^a,b  

^a UNIVERSITY OF PADOVA   (Italy)

^b IRCCS SAN CAMILLO HOSPITAL   (Italy)

Author keywords

Autophagic lysosomal degradation; Calpain 3; Limb girdle muscular dystrophy; Muscle atrophy; Ubiquitin proteasome system

Indexed keywords

MUSCLE RING FINGER 1 PROTEIN; MYOSIN; PROTEASOME; UBIQUITIN;

ADULT; ANTIBODY LABELING; ARTICLE; ATROGIN1 GENE; AUTOPHAGY; BNIP3 GENE; CLINICAL ARTICLE; CONTROLLED STUDY; GENE; GENE EXPRESSION; HUMAN; HUMAN TISSUE; LIMB GIRDLE MUSCULAR DYSTROPHY; LIMB GIRDLE MUSCULAR DYSTROPHY 2A; LYSOSOME; MALE; MICROTUBULE ASSOCIATED PROTEIN LIGHT CHAIN 3 GENE; MORPHOMETRICS; MUSCLE ATROPHY; MUSCLE CELL; MUSCLE REGENERATION; P62 GENE; PRIORITY JOURNAL; UPREGULATION;

AUTOPHAGIC-LYSOSOMAL DEGRADATION; CALPAIN-3; LIMB GIRDLE MUSCULAR DYSTROPHY; MUSCLE ATROPHY; UBIQUITIN-PROTEASOME SYSTEM;

ADOLESCENT; ADULT; CALPAIN; HUMANS; MALE; MIDDLE AGED; MUSCLE PROTEINS; MUSCULAR ATROPHY; MUSCULAR DYSTROPHIES, LIMB-GIRDLE; PROTEASOME ENDOPEPTIDASE COMPLEX; REGENERATION; UBIQUITIN; UP-REGULATION; YOUNG ADULT;

EID: 84886775213     PISSN: 03051846     EISSN: 13652990     Source Type: Journal    
DOI: 10.1111/nan.12034     Document Type: Article

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