Calpain 3 deficiency is associated with myonuclear apoptosis and profound perturbation of the IκBα/NF-κB pathway in limb-girdle muscular dystrophy type 2A

Nature Medicine

Volumn 5, Issue 5, 1999, Pages 503-511

  Baghdiguian, Stephen ^a   Martin, Marianne ^a   Richard, Isabelle ^b   Pons, Françoise ^a   Astier, Catherine ^a   Bourg, Nathalie ^b   Hay, Ronald T ^c   Chemaly, Raymond ^d   Halaby, Georges ^d   Loiselet, Jacques ^d   Anderson, Louise V B ^e   De Munain, Adolfo Lopez ^f   Fardeau, Michel ^b   Mangeat, Paul ^a   Beckmann, Jacques S ^b   Lefranc, Gérard ^g  

^a UNIV MONTPELLIER   (France)

^b CNRS   (France)

^c UNIVERSITY OF ST ANDREWS   (United Kingdom)

^d SAINT JOSEPH UNIVERSITY   (Lebanon)

^e NEWCASTLE UNIVERSITY   (United Kingdom)

^f Hospital Nuestra Senora de Aranzazu   (Spain)

^g INSTITUTE OF HUMAN GENETICS   (France)

Author keywords

[No Author keywords available]

Indexed keywords

CALPAIN; IMMUNOGLOBULIN ENHANCER BINDING PROTEIN;

ADOLESCENT; ADULT; APOPTOSIS; ARTICLE; CELLULAR DISTRIBUTION; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; FEMALE; FETUS; GENE OVEREXPRESSION; HUMAN; HUMAN CELL; HUMAN TISSUE; LIMB GIRDLE MUSCULAR DYSTROPHY; MALE; MUSCLE BIOPSY; PRIORITY JOURNAL; PROTEIN DEFICIENCY; PROTEIN LOCALIZATION;

EID: 0032941594     PISSN: 10788956     EISSN: None     Source Type: Journal    
DOI: 10.1038/8385     Document Type: Article

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