Increased aggregation of polyleucine compared with that of polyglutamine in dentatorubral-pallidoluysian atrophy protein

Neuroscience Letters

Volumn 552, Issue , 2013, Pages 156-161

  Suzuki, Yasuyo ^a   Jin, Chenghua ^a   Yazawa, Ikuru ^a  

^a NATIONAL CENTER FOR GERIATRICS AND GERONTOLOGY   (Japan)

Author keywords

Atrophin 1; Dentatorubral pallidoluysian atrophy; Neurodegeneration; Polyglutamine; Polyleucine

Indexed keywords

ATROPHIN 1; CELL PROTEIN; DENTATORUBRAL PALLIDOLUYSIAN ATROPHY PROTEIN; NERVE PROTEIN; POLYGLUTAMINE; POLYLEUCINE; POLYPEPTIDE; UNCLASSIFIED DRUG;

ANIMAL CELL; ARTICLE; CAG REPEAT; CELL STRAIN COS7; CELLULAR DISTRIBUTION; CONTROLLED STUDY; CYTOPLASM; CYTOTOXICITY; IMMUNOCYTOCHEMISTRY; NONHUMAN; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN ANALYSIS; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN LOCALIZATION;

ATN1; ATROPHIN-1; BENZYLOXYCARBONYL-VAL-ALA-ASP(OME)-FLUOROMETHYL KETONE.; CENTRAL NERVOUS SYSTEM; CNS; DENTATORUBRAL-PALLIDOLUYSIAN ATROPHY; DRPLA; HD; HUNTINGTON'S DISEASE; N,N,N′,N′-TETRAKIS (2-PYRIDYLMETHYL) ETHYLENEDIAMINE; NEURODEGENERATION; POLYGLUTAMINE; POLYL; POLYLEUCINE; POLYQ; SCA; SPINOCEREBELLAR ATAXIA; TPEN; Z-VAD-FMK;

ANIMALS; CELLS, CULTURED; CERCOPITHECUS AETHIOPS; COS CELLS; MUTANT PROTEINS; MYOCLONIC EPILEPSIES, PROGRESSIVE; NERVE DEGENERATION; NERVE TISSUE PROTEINS; PEPTIDES; TRINUCLEOTIDE REPEATS;

EID: 84884214974     PISSN: 03043940     EISSN: 18727972     Source Type: Journal    
DOI: 10.1016/j.neulet.2013.07.043     Document Type: Article

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