The Effect of SOD1 Mutation on Cellular Bioenergetic Profile and Viability in Response to Oxidative Stress and Influence of Mutation-Type

PLoS ONE

Volumn 8, Issue 6, 2013, Pages

  Richardson, Katie ^a   Allen, Scott P ^a   Mortiboys, Heather ^a   Grierson, Andrew J ^a   Wharton, Stephen B ^a   Ince, Paul G ^a   Shaw, Pamela J ^a   Heath, Paul R ^a  

^a UNIVERSITY OF SHEFFIELD   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE; HYDROGEN PEROXIDE; LACTATE DEHYDROGENASE; REACTIVE OXYGEN METABOLITE;

AMYOTROPHIC LATERAL SCLEROSIS; ANAEROBIC GLYCOLYSIS; ANIMAL CELL; ARTICLE; BIOENERGY; CELL DEATH; CELL VIABILITY; CONTROLLED STUDY; ENZYME RELEASE; GENE ACTIVITY; GENE FUNCTION; GENE MUTATION; GENETIC ANALYSIS; GENETIC SUSCEPTIBILITY; GENETIC TRANSFECTION; MITOCHONDRIAL MEMBRANE POTENTIAL; MITOCHONDRIAL RESPIRATION; MOUSE; NEUROBLASTOMA CELL; NONHUMAN; OXIDATIVE STRESS; OXYGEN CONSUMPTION; SOD1 GENE; TRANSGENE;

ANIMALS; CELL DEATH; CELL LINE; CELL RESPIRATION; CELL SURVIVAL; ENERGY METABOLISM; GLYCOLYSIS; HUMANS; HYDROGEN PEROXIDE; MICE; MOTOR NEURONS; MUTATION; OXIDATIVE STRESS; OXYGEN CONSUMPTION; REACTIVE OXYGEN SPECIES; SUPEROXIDE DISMUTASE;

EID: 84879536538     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0068256     Document Type: Article

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