Frataxin deficiency leads to reduced expression and impaired translocation of NF-E2-Related factor (Nrf2) in cultured motor neurons

International Journal of Molecular Sciences

Volumn 14, Issue 4, 2013, Pages 7853-7865

  D'Oria, Valentina ^a   Petrini, Stefania ^a   Travaglini, Lorena ^a   Priori, Chiara ^a   Piermarini, Emanuela ^a   Petrillo, Sara ^a   Carletti, Barbara ^a   Bertini, Enrico ^a   Piemonte, Fiorella ^a  

^a BAMBINO GESÙ CHILDREN S HOSPITAL   (Italy)

Author keywords

Frataxin; FRDA; GSSG; Nrf2; NSC34 neurons; Oxidative stress

Indexed keywords

FRATAXIN; MESSENGER RNA; TRANSCRIPTION FACTOR NRF2; IRON BINDING PROTEIN; NFE2L2 PROTEIN, HUMAN;

ANIMAL CELL; ARTICLE; CELLULAR DISTRIBUTION; CONFOCAL MICROSCOPY; CONTROLLED STUDY; DOWN REGULATION; FRATAXIN GENE; FRIEDREICH ATAXIA; GENE EXPRESSION REGULATION; GENE LOCATION; GENE SILENCING; MOTONEURON; MOUSE; NERVE CELL CULTURE; NEUROPATHOLOGY; NF E2 RELATED FACTOR GENE; NONHUMAN; OXIDATIVE STRESS; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; ANIMAL; BIOSYNTHESIS; GENETICS; HUMAN; METABOLISM; PATHOLOGY; TUMOR CELL LINE;

ANIMALS; CELL LINE, TUMOR; FRIEDREICH ATAXIA; GENE EXPRESSION REGULATION; HUMANS; IRON-BINDING PROTEINS; MICE; MOTOR NEURONS; NF-E2-RELATED FACTOR 2; OXIDATIVE STRESS;

EID: 84876310656     PISSN: 16616596     EISSN: 14220067     Source Type: Journal    
DOI: 10.3390/ijms14047853     Document Type: Article

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