The angelman syndrome protein Ube3a/E6AP is required for golgi acidification and surface protein sialylation

Journal of Neuroscience

Volumn 33, Issue 9, 2013, Pages 3799-3814

  Condon, Kathryn H ^a   Ho, Jianghai ^a   Robinson, Camenzind G ^a,c   Hanus, Cyril ^a,d   Ehlers, Michael D ^a,b  

^a DUKE UNIVERSITY MEDICAL CENTER   (United States)

^b PFIZER INC   (United States)

^c UNITED STATES ARMY MEDICAL RESEARCH INSTITUTE OF INFECTIOUS DISEASES   (United States)

^d MAX PLANCK INSTITUTE FOR BRAIN RESEARCH   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

UBIQUITIN PROTEIN LIGASE E3; UBIQUITIN PROTEIN LIGASE E3A; UNCLASSIFIED DRUG;

ACIDIFICATION; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL MIGRATION; CONTROLLED STUDY; ELECTRON MICROSCOPY; ELECTROPHYSIOLOGY; GENOTYPING TECHNIQUE; GOLGI COMPLEX; HAPPY PUPPET SYNDROME; HOMEOSTASIS; IMMUNOBLOTTING; IMMUNOPRECIPITATION; IMMUNOREACTIVITY; MOUSE; MUTAGENESIS; NERVE CELL PLASTICITY; NONHUMAN; PATHOPHYSIOLOGY; PH; POLYMERASE CHAIN REACTION; PRIORITY JOURNAL; SIALYLATION;

ANALYSIS OF VARIANCE; ANGELMAN SYNDROME; ANIMALS; ANIMALS, NEWBORN; BACTERIAL PROTEINS; CELLS, CULTURED; CEREBRAL CORTEX; CYTOPLASMIC STRUCTURES; DISEASE MODELS, ANIMAL; EMBRYO, MAMMALIAN; FEMALE; GENE EXPRESSION REGULATION; GLYCINE; GOLGI APPARATUS; GREEN FLUORESCENT PROTEINS; HEK293 CELLS; HUMANS; HYDROGEN-ION CONCENTRATION; LECTINS; LUMINESCENT PROTEINS; MALE; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MICROSCOPY, ELECTRON, TRANSMISSION; MUTAGENESIS; N-ACETYLNEURAMINIC ACID; NEURONS; PROTEIN TRANSPORT; RNA, SMALL INTERFERING; SPERMINE; TRANSFECTION; UBIQUITIN-PROTEIN LIGASES; VESICLE-ASSOCIATED MEMBRANE PROTEIN 2; VIRAL PROTEINS;

EID: 84874586539     PISSN: 02706474     EISSN: 15292401     Source Type: Journal    
DOI: 10.1523/JNEUROSCI.1930-11.2013     Document Type: Article

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