-
1
-
-
0031043030
-
The mitochondrial carnitine palmitoyltransferase system. From concept to molecular analysis
-
McGarry J.D., Brown N.F. The mitochondrial carnitine palmitoyltransferase system. From concept to molecular analysis. Eur. J. Biochem. 1997, 244:1-14.
-
(1997)
Eur. J. Biochem.
, vol.244
, pp. 1-14
-
-
McGarry, J.D.1
Brown, N.F.2
-
2
-
-
0034717940
-
Fatty acid import into mitochondria
-
Kerner J., Hoppel C. Fatty acid import into mitochondria. Biochim. Biophys. Acta 2000, 1486:1-17.
-
(2000)
Biochim. Biophys. Acta
, vol.1486
, pp. 1-17
-
-
Kerner, J.1
Hoppel, C.2
-
3
-
-
0030865233
-
Regulation of mitochondrial outer-membrane carnitine palmitoyltransferase (CPT I): role of membrane-topology
-
Zammit V.A., Fraser F., Orstorphine C.G. Regulation of mitochondrial outer-membrane carnitine palmitoyltransferase (CPT I): role of membrane-topology. Adv. Enzyme Regul. 1997, 37:295-317.
-
(1997)
Adv. Enzyme Regul.
, vol.37
, pp. 295-317
-
-
Zammit, V.A.1
Fraser, F.2
Orstorphine, C.G.3
-
4
-
-
0018864840
-
Regulation of hepatic fatty acid oxidation and ketone body production
-
McGarry J.D., Foster D.W. Regulation of hepatic fatty acid oxidation and ketone body production. Annu. Rev. Biochem. 1980, 49:395-420.
-
(1980)
Annu. Rev. Biochem.
, vol.49
, pp. 395-420
-
-
McGarry, J.D.1
Foster, D.W.2
-
5
-
-
43649099634
-
Intertissue regulation of carnitine palmitoyltransferase I (CPT I): mitochondrial membrane properties and gene expression in rainbow trout (Oncorhynchus mykiss)
-
Morash A.J., Kajimura M., McClelland G.B. Intertissue regulation of carnitine palmitoyltransferase I (CPT I): mitochondrial membrane properties and gene expression in rainbow trout (Oncorhynchus mykiss). Biochim. Biophys. Acta 2008, 1778:1382-1389.
-
(2008)
Biochim. Biophys. Acta
, vol.1778
, pp. 1382-1389
-
-
Morash, A.J.1
Kajimura, M.2
McClelland, G.B.3
-
6
-
-
0028904122
-
Human liver mitochondrial carnitine palmitoyltransferase I: characterization of its cDNA and chromosomal localization and partial analysis of the gene
-
Britton C.H., Schultz R.A., Zhang B., Esser V., Foster D.W., McGarry J.D. Human liver mitochondrial carnitine palmitoyltransferase I: characterization of its cDNA and chromosomal localization and partial analysis of the gene. Proc. Natl. Acad. Sci. U. S. A. 1995, 92:1984-1988.
-
(1995)
Proc. Natl. Acad. Sci. U. S. A.
, vol.92
, pp. 1984-1988
-
-
Britton, C.H.1
Schultz, R.A.2
Zhang, B.3
Esser, V.4
Foster, D.W.5
McGarry, J.D.6
-
7
-
-
0029954776
-
Isolation and characterization of cDNA and genomic clones encoding human muscle type carnitine palmitoyltransferase I
-
Yamazaki N., Shinohara Y., Shima A., Yamanaka Y., Terada H. Isolation and characterization of cDNA and genomic clones encoding human muscle type carnitine palmitoyltransferase I. Biochim. Biophys. Acta 1996, 1307:157-161.
-
(1996)
Biochim. Biophys. Acta
, vol.1307
, pp. 157-161
-
-
Yamazaki, N.1
Shinohara, Y.2
Shima, A.3
Yamanaka, Y.4
Terada, H.5
-
8
-
-
0036421318
-
A novel brain-expressed protein related to carnitine palmitoyltransferase I
-
Price N., van der Leij F., Jackson V., Corstorphine C., Thomson R., Sorensen A., Zammit V. A novel brain-expressed protein related to carnitine palmitoyltransferase I. Genomics 2002, 80:433-442.
-
(2002)
Genomics
, vol.80
, pp. 433-442
-
-
Price, N.1
van der Leij, F.2
Jackson, V.3
Corstorphine, C.4
Thomson, R.5
Sorensen, A.6
Zammit, V.7
-
10
-
-
0037683658
-
Cloning and tissue distribution of a carnitine palmitoyltransferase I gene in rainbow trout (Oncorhynchus mykiss)
-
Gutieres S., Damon M., Panserat S., Kaushik S., Medale F. Cloning and tissue distribution of a carnitine palmitoyltransferase I gene in rainbow trout (Oncorhynchus mykiss). Comp. Biochem. Physiol. 2003, 135B:139-151.
-
(2003)
Comp. Biochem. Physiol.
, vol.135 B
, pp. 139-151
-
-
Gutieres, S.1
Damon, M.2
Panserat, S.3
Kaushik, S.4
Medale, F.5
-
11
-
-
77954864428
-
Molecular regulation of lipid metabolism in liver and muscle of rainbow trout subjected to acute and chronic insulin treatments
-
Polakof S., Medale F., Skiba-Cassy S., Corraze G., Panserat S. Molecular regulation of lipid metabolism in liver and muscle of rainbow trout subjected to acute and chronic insulin treatments. Domest. Anim. Endocrinol. 2010, 39:26-33.
-
(2010)
Domest. Anim. Endocrinol.
, vol.39
, pp. 26-33
-
-
Polakof, S.1
Medale, F.2
Skiba-Cassy, S.3
Corraze, G.4
Panserat, S.5
-
12
-
-
84861850750
-
Link between lipid metabolism and voluntary food intake in rainbow trout fed coconut oil rich in medium-chain TAG
-
Figueiredo-Silva A.C., Kaushik S., Terrier F., Schrama J.W., Medale F., Geurden I. Link between lipid metabolism and voluntary food intake in rainbow trout fed coconut oil rich in medium-chain TAG. Br. J. Nutr. 2012, 10.1017/S0007114511004739.
-
(2012)
Br. J. Nutr.
-
-
Figueiredo-Silva, A.C.1
Kaushik, S.2
Terrier, F.3
Schrama, J.W.4
Medale, F.5
Geurden, I.6
-
13
-
-
77955092147
-
Molecular characterization of a gilthead sea bream (Sparus aurata) muscle tissue cDNA for carnitine palmitoyltransferase 1B (CPT1B)
-
Boukouvala E., Leaver M.J., Favre-Krey L., Theodoridou M., Krey G. Molecular characterization of a gilthead sea bream (Sparus aurata) muscle tissue cDNA for carnitine palmitoyltransferase 1B (CPT1B). Comp. Biochem. Physiol. 2010, 157B:189-197.
-
(2010)
Comp. Biochem. Physiol.
, vol.157 B
, pp. 189-197
-
-
Boukouvala, E.1
Leaver, M.J.2
Favre-Krey, L.3
Theodoridou, M.4
Krey, G.5
-
14
-
-
17344392308
-
A new mathematical model for relative quantification in real-time RT-PCR
-
Pfaffl M.W. A new mathematical model for relative quantification in real-time RT-PCR. Nucleic Acids Res. 2001, 29:2003-2007.
-
(2001)
Nucleic Acids Res.
, vol.29
, pp. 2003-2007
-
-
Pfaffl, M.W.1
-
15
-
-
0011464758
-
Preparation and properties of rainbow trout liver mitochondria
-
Suarez R.K., Hochachka P.W. Preparation and properties of rainbow trout liver mitochondria. J. Comp. Physiol. 1981, 143B:269-273.
-
(1981)
J. Comp. Physiol.
, vol.143 B
, pp. 269-273
-
-
Suarez, R.K.1
Hochachka, P.W.2
-
16
-
-
0017184389
-
A rapid and sensitive method for the quantitation of microgram quantities of protein utilizing the principle of protein-dye binding
-
Bradford M.M. A rapid and sensitive method for the quantitation of microgram quantities of protein utilizing the principle of protein-dye binding. Anal. Biochem. 1976, 72:248-254.
-
(1976)
Anal. Biochem.
, vol.72
, pp. 248-254
-
-
Bradford, M.M.1
-
17
-
-
0020624753
-
Observations on the affinity for carnitine, and malonyl-CoA sensitivity, of carnitine palmitoyltransferase I in animal and human tissues. Demonstration of the presence of malonyl-CoA in non-hepatic tissues of the rat
-
McGarry J.D., Mills S.E., Long C.S., Foster D.W. Observations on the affinity for carnitine, and malonyl-CoA sensitivity, of carnitine palmitoyltransferase I in animal and human tissues. Demonstration of the presence of malonyl-CoA in non-hepatic tissues of the rat. Biochem. J. 1983, 214:21-28.
-
(1983)
Biochem. J.
, vol.214
, pp. 21-28
-
-
McGarry, J.D.1
Mills, S.E.2
Long, C.S.3
Foster, D.W.4
-
18
-
-
0022559002
-
Purification and assay of carnitine acyltransferases
-
Bieber L.L., Fiol C. Purification and assay of carnitine acyltransferases. Methods Enzymol. 1986, 123:276-284.
-
(1986)
Methods Enzymol.
, vol.123
, pp. 276-284
-
-
Bieber, L.L.1
Fiol, C.2
-
19
-
-
0034927508
-
Inhibition of mitochondrial carnitine palmitoyltransferase-1 by a trimetazidine derivative, S-15176
-
Hamdan M., Urien S., Le Louet H., Tillement J.P., Morin D. Inhibition of mitochondrial carnitine palmitoyltransferase-1 by a trimetazidine derivative, S-15176. Pharmacol. Res. 2001, 44:99-104.
-
(2001)
Pharmacol. Res.
, vol.44
, pp. 99-104
-
-
Hamdan, M.1
Urien, S.2
Le Louet, H.3
Tillement, J.P.4
Morin, D.5
-
20
-
-
5844225066
-
On the evaluation of the constants Vm and KM in enzyme reactions
-
Hofstee B. On the evaluation of the constants Vm and KM in enzyme reactions. Science 1952, 116:329-331.
-
(1952)
Science
, vol.116
, pp. 329-331
-
-
Hofstee, B.1
-
21
-
-
33751330608
-
The determination of enzyme dissociation constants
-
Lineweaver H., Burk D. The determination of enzyme dissociation constants. J. Am. Chem. Soc. 1934, 56:658-666.
-
(1934)
J. Am. Chem. Soc.
, vol.56
, pp. 658-666
-
-
Lineweaver, H.1
Burk, D.2
-
22
-
-
0035064946
-
Evolutionary rates of duplicate genes in fish and mammals
-
Robinson-Rechavi M., Laudet V. Evolutionary rates of duplicate genes in fish and mammals. Mol. Biol. Evol. 2001, 18:681-683.
-
(2001)
Mol. Biol. Evol.
, vol.18
, pp. 681-683
-
-
Robinson-Rechavi, M.1
Laudet, V.2
-
23
-
-
57649142833
-
A characteristic Glu17 residue of pig carnitine palmitoyltransferase 1 is responsible for the low Km for carnitine and the low sensitivity to malonyl-CoA inhibition of the enzyme
-
Relat J., Pujol-Vidal M., Haro D., Marrero P.F. A characteristic Glu17 residue of pig carnitine palmitoyltransferase 1 is responsible for the low Km for carnitine and the low sensitivity to malonyl-CoA inhibition of the enzyme. FEBS J. 2009, 276:210-218.
-
(2009)
FEBS J.
, vol.276
, pp. 210-218
-
-
Relat, J.1
Pujol-Vidal, M.2
Haro, D.3
Marrero, P.F.4
-
24
-
-
0022237772
-
Phosphorylation of carnitine palmitoyltransferase and activation by glucagon in isolated rat hepatocytes
-
Harano Y., Kashiwagi A., Kojima H., Suzuki M., Hashimoto T., Shigeta Y. Phosphorylation of carnitine palmitoyltransferase and activation by glucagon in isolated rat hepatocytes. FEBS Lett. 1985, 188:267-272.
-
(1985)
FEBS Lett.
, vol.188
, pp. 267-272
-
-
Harano, Y.1
Kashiwagi, A.2
Kojima, H.3
Suzuki, M.4
Hashimoto, T.5
Shigeta, Y.6
-
25
-
-
4444277089
-
Phosphorylation of rat liver mitochondrial carnitine palmitoyltransferase-I
-
Kerner J., Distler A.M., Minkler P., Parland W., Peterman S.M., Hoppel C.L. Phosphorylation of rat liver mitochondrial carnitine palmitoyltransferase-I. J. Biol. Chem. 2004, 279:41104-41113.
-
(2004)
J. Biol. Chem.
, vol.279
, pp. 41104-41113
-
-
Kerner, J.1
Distler, A.M.2
Minkler, P.3
Parland, W.4
Peterman, S.M.5
Hoppel, C.L.6
-
26
-
-
34247634168
-
Post-translational modifications of rat liver mitochondrial outer membrane proteins identified by mass spectrometry
-
Distler A.M., Kerner J., Hoppel C.L. Post-translational modifications of rat liver mitochondrial outer membrane proteins identified by mass spectrometry. Biochim. Biophys. Acta 2007, 1774:628-636.
-
(2007)
Biochim. Biophys. Acta
, vol.1774
, pp. 628-636
-
-
Distler, A.M.1
Kerner, J.2
Hoppel, C.L.3
-
27
-
-
0035895945
-
The N-terminal domain of rat liver carnitine palmitoyltransferase 1 contains an internal mitochondrial import signal and residues essential for folding of its C-terminal catalytic domain
-
Cohen I., Guillerault F., Girard J., Prip-Buus C. The N-terminal domain of rat liver carnitine palmitoyltransferase 1 contains an internal mitochondrial import signal and residues essential for folding of its C-terminal catalytic domain. J. Biol. Chem. 2001, 276:5403-5411.
-
(2001)
J. Biol. Chem.
, vol.276
, pp. 5403-5411
-
-
Cohen, I.1
Guillerault, F.2
Girard, J.3
Prip-Buus, C.4
-
28
-
-
0037436271
-
Leucine-764 near the extreme C-terminal end of carnitine palmitoyltransferase I is important for activity
-
Dai J., Zhu H., Woldegiorgis G. Leucine-764 near the extreme C-terminal end of carnitine palmitoyltransferase I is important for activity. Biochem. Biophys. Res. Commun. 2003, 301:758-763.
-
(2003)
Biochem. Biophys. Res. Commun.
, vol.301
, pp. 758-763
-
-
Dai, J.1
Zhu, H.2
Woldegiorgis, G.3
-
29
-
-
0032491604
-
The N-terminal domain of rat liver carnitine palmitoyltransferase 1 mediates import into the outer mitochondrial membrane and is essential for activity and malonyl-CoA sensitivity
-
Cohen I., Kohl C., McGarry J.D., Girard J., Prip-Buus C. The N-terminal domain of rat liver carnitine palmitoyltransferase 1 mediates import into the outer mitochondrial membrane and is essential for activity and malonyl-CoA sensitivity. J. Biol. Chem. 1998, 273:29896-29904.
-
(1998)
J. Biol. Chem.
, vol.273
, pp. 29896-29904
-
-
Cohen, I.1
Kohl, C.2
McGarry, J.D.3
Girard, J.4
Prip-Buus, C.5
-
30
-
-
0032511158
-
Topological and functional analysis of the rat liver carnitine palmitoyltransferase 1 expressed in Saccharomyces cerevisiae
-
Prip-Buus C., Cohen I., Kohl C., Esser V., McGarry J.D., Girard J. Topological and functional analysis of the rat liver carnitine palmitoyltransferase 1 expressed in Saccharomyces cerevisiae. FEBS Lett. 1998, 429:173-178.
-
(1998)
FEBS Lett.
, vol.429
, pp. 173-178
-
-
Prip-Buus, C.1
Cohen, I.2
Kohl, C.3
Esser, V.4
McGarry, J.D.5
Girard, J.6
-
31
-
-
33845964421
-
The mitochondrial intermembrane loop region of rat carnitine palmitoyltransferase 1A is a major determinant of its malonyl-CoA sensitivity
-
Borthwick K., Jackson V.N., Price N.T., Zammit V.A. The mitochondrial intermembrane loop region of rat carnitine palmitoyltransferase 1A is a major determinant of its malonyl-CoA sensitivity. J. Biol. Chem. 2006, 281:32946-32952.
-
(2006)
J. Biol. Chem.
, vol.281
, pp. 32946-32952
-
-
Borthwick, K.1
Jackson, V.N.2
Price, N.T.3
Zammit, V.A.4
-
32
-
-
56949093657
-
Effects of dietary fatty acid composition on the regulation of carnitine palmitoyltransferase (CPT) I in rainbow trout (Oncorhynchus mykiss)
-
Morash A.J., Bureau D.P., McClelland G.B. Effects of dietary fatty acid composition on the regulation of carnitine palmitoyltransferase (CPT) I in rainbow trout (Oncorhynchus mykiss). Comp. Biochem. Physiol. 2009, 152B:85-93.
-
(2009)
Comp. Biochem. Physiol.
, vol.152 B
, pp. 85-93
-
-
Morash, A.J.1
Bureau, D.P.2
McClelland, G.B.3
-
33
-
-
41749119661
-
Liver and muscle metabolic changes induced by dietary energy content and genetic selection in rainbow trout (Oncorhynchus mykiss)
-
Kolditz C., Borthaire M., Richard N., Corraze G., Panserat S., Vachot C., Lefevre F., Medale F. Liver and muscle metabolic changes induced by dietary energy content and genetic selection in rainbow trout (Oncorhynchus mykiss). Am. J. Physiol. 2008, 294:R1154-R1164.
-
(2008)
Am. J. Physiol.
, vol.294
-
-
Kolditz, C.1
Borthaire, M.2
Richard, N.3
Corraze, G.4
Panserat, S.5
Vachot, C.6
Lefevre, F.7
Medale, F.8
-
34
-
-
0033515467
-
A single amino acid change (substitution of glutamate 3 with alanine) in the N-terminal region of rat liver carnitine palmitoyltransferase I abolishes malonyl-CoA inhibition and high affinity binding
-
Shi J., Zhu H., Arvidson D.N., Woldegiorgis G. A single amino acid change (substitution of glutamate 3 with alanine) in the N-terminal region of rat liver carnitine palmitoyltransferase I abolishes malonyl-CoA inhibition and high affinity binding. J. Biol. Chem. 1999, 274:9421-9426.
-
(1999)
J. Biol. Chem.
, vol.274
, pp. 9421-9426
-
-
Shi, J.1
Zhu, H.2
Arvidson, D.N.3
Woldegiorgis, G.4
-
35
-
-
0034624069
-
Identification of positive and negative determinants of malonyl-CoA sensitivity and carnitine affinity within the amino termini of rat liver- and muscle-type carnitine palmitoyltransferase I
-
Jackson V.N., Zammit V.A., Pric N.T. Identification of positive and negative determinants of malonyl-CoA sensitivity and carnitine affinity within the amino termini of rat liver- and muscle-type carnitine palmitoyltransferase I. J. Biol. Chem. 2000, 275:38410-38416.
-
(2000)
J. Biol. Chem.
, vol.275
, pp. 38410-38416
-
-
Jackson, V.N.1
Zammit, V.A.2
Pric, N.T.3
-
36
-
-
0035807927
-
Specificity of the interactions between Glu-3, Ser-24, and Gln-30 within the N-terminal segment of rat liver mitochondrial overt carnitine palmitoyltransferase (L-CPT I) in determining the malonyl-CoA sensitivity of the enzyme
-
Jackson V.N., Price N.T., Zammit V.A. Specificity of the interactions between Glu-3, Ser-24, and Gln-30 within the N-terminal segment of rat liver mitochondrial overt carnitine palmitoyltransferase (L-CPT I) in determining the malonyl-CoA sensitivity of the enzyme. Biochemistry 2001, 40:14629-14634.
-
(2001)
Biochemistry
, vol.40
, pp. 14629-14634
-
-
Jackson, V.N.1
Price, N.T.2
Zammit, V.A.3
-
37
-
-
0037405394
-
Substitution of glutamate-3, valine-19, leucine-23, and serine-24 with alanine in the N-terminal region of human heart muscle carnitine palmitoyltransferase I abolishes malonyl CoA inhibition and binding
-
Zhu H., Shi J., Treber M., Dai J., Arvidson D.N., Woldegiorgis G. Substitution of glutamate-3, valine-19, leucine-23, and serine-24 with alanine in the N-terminal region of human heart muscle carnitine palmitoyltransferase I abolishes malonyl CoA inhibition and binding. Arch. Biochem. Biophys. 2003, 413:67-74.
-
(2003)
Arch. Biochem. Biophys.
, vol.413
, pp. 67-74
-
-
Zhu, H.1
Shi, J.2
Treber, M.3
Dai, J.4
Arvidson, D.N.5
Woldegiorgis, G.6
-
38
-
-
0032212886
-
Roles of the N-and C-terminal domains of carnitine palmitoyltransferase I isoforms in malonyl-CoA sensitivity of the enzymes: insights from expression of chimaeric proteins and mutation of conserved histidine residues
-
Swanson S.T., Foster D.W., McGarry J.D., Brown N.F. Roles of the N-and C-terminal domains of carnitine palmitoyltransferase I isoforms in malonyl-CoA sensitivity of the enzymes: insights from expression of chimaeric proteins and mutation of conserved histidine residues. Biochem. J. 1998, 335:513-519.
-
(1998)
Biochem. J.
, vol.335
, pp. 513-519
-
-
Swanson, S.T.1
Foster, D.W.2
McGarry, J.D.3
Brown, N.F.4
-
39
-
-
0346749506
-
Functional and structural basis of carnitine palmitoyltransferase 1A deficiency
-
Gobin S., Thuillier L., Jogl G., Faye A., Tong L., Chi M., Bonnefont J.P., Girard J., Prip-Buus C. Functional and structural basis of carnitine palmitoyltransferase 1A deficiency. J. Biol. Chem. 2003, 278:50428-50434.
-
(2003)
J. Biol. Chem.
, vol.278
, pp. 50428-50434
-
-
Gobin, S.1
Thuillier, L.2
Jogl, G.3
Faye, A.4
Tong, L.5
Chi, M.6
Bonnefont, J.P.7
Girard, J.8
Prip-Buus, C.9
-
40
-
-
0037192836
-
Structural model of a malonyl-CoA-binding site of carnitine octanoyltransferase and carnitine palmitoyltransferase I
-
Morillas M., Gomez-Puertas P., Rubi B., Clotet J., Ariño J., Valencia A., Hegardt F.G., Serra D., Asins G. Structural model of a malonyl-CoA-binding site of carnitine octanoyltransferase and carnitine palmitoyltransferase I. J. Biol. Chem. 2002, 277:11473-11480.
-
(2002)
J. Biol. Chem.
, vol.277
, pp. 11473-11480
-
-
Morillas, M.1
Gomez-Puertas, P.2
Rubi, B.3
Clotet, J.4
Ariño, J.5
Valencia, A.6
Hegardt, F.G.7
Serra, D.8
Asins, G.9
-
41
-
-
14244260908
-
Cysteine-scanning mutagenesis of muscle carnitine palmitoyltransferase I reveals a single cysteine residue (Cys-305) is important for catalysis
-
Liu H., Zheng G., Treber M., Dai J., Woldegiorgis G. Cysteine-scanning mutagenesis of muscle carnitine palmitoyltransferase I reveals a single cysteine residue (Cys-305) is important for catalysis. J. Biol. Chem. 2005, 280:4524-4531.
-
(2005)
J. Biol. Chem.
, vol.280
, pp. 4524-4531
-
-
Liu, H.1
Zheng, G.2
Treber, M.3
Dai, J.4
Woldegiorgis, G.5
-
42
-
-
0242286152
-
Mutations of penicillin acylase residue B71 extend substrate specificity by decreasing steric constraints for substrate binding
-
Morillas M., McVey C.E., Brannigan J.A., Ladurner A.G., Forney L.J., Virden R. Mutations of penicillin acylase residue B71 extend substrate specificity by decreasing steric constraints for substrate binding. Biochem. J. 2003, 371:143-150.
-
(2003)
Biochem. J.
, vol.371
, pp. 143-150
-
-
Morillas, M.1
McVey, C.E.2
Brannigan, J.A.3
Ladurner, A.G.4
Forney, L.J.5
Virden, R.6
-
43
-
-
0034698039
-
Identification by mutagenesis of conserved arginine and tryptophan residues in rat liver carnitine palmitoyltransferase I important for catalytic activity
-
Dai J., Zhu H., Shi J., Woldegiorgis G. Identification by mutagenesis of conserved arginine and tryptophan residues in rat liver carnitine palmitoyltransferase I important for catalytic activity. J. Biol. Chem. 2000, 275:22020-22024.
-
(2000)
J. Biol. Chem.
, vol.275
, pp. 22020-22024
-
-
Dai, J.1
Zhu, H.2
Shi, J.3
Woldegiorgis, G.4
-
44
-
-
0032145885
-
Molecular basis of hepatic carnitine palmitoyltransferase I deficiency
-
IJlst L., Mandel H., Oostheim W., Ruiter J., Gutman A., Wanders R. Molecular basis of hepatic carnitine palmitoyltransferase I deficiency. J. Clin. Invest. 1998, 102(1998):527-531.
-
(1998)
J. Clin. Invest.
, vol.102
, Issue.1998
, pp. 527-531
-
-
IJlst, L.1
Mandel, H.2
Oostheim, W.3
Ruiter, J.4
Gutman, A.5
Wanders, R.6
-
45
-
-
0034947983
-
Molecular characterization of L-CPT I deficiency in six patients: insights into function of the native enzyme
-
Brown N.F., Mullur R.S., Subramanian I., Esser V., Bennett M.J., Saudubray J.M., Feigenbaum A.S., Kobari J.A., Macleod P.M., McGarry J.D. Molecular characterization of L-CPT I deficiency in six patients: insights into function of the native enzyme. J. Lipid Res. 2001, 42:1134-1142.
-
(2001)
J. Lipid Res.
, vol.42
, pp. 1134-1142
-
-
Brown, N.F.1
Mullur, R.S.2
Subramanian, I.3
Esser, V.4
Bennett, M.J.5
Saudubray, J.M.6
Feigenbaum, A.S.7
Kobari, J.A.8
Macleod, P.M.9
McGarry, J.D.10
-
46
-
-
0141817917
-
A single amino acid change (substitution of the conserved Glu-590 with alanine) in the C-terminal domain of rat liver carnitine palmitoyltransferase I increases its malonyl-CoA sensitivity close to that observed with the muscle isoform of the enzyme
-
Napal L., Dai J., Treber M., Haro D., Marrero P.F., Woldegiorgis G. A single amino acid change (substitution of the conserved Glu-590 with alanine) in the C-terminal domain of rat liver carnitine palmitoyltransferase I increases its malonyl-CoA sensitivity close to that observed with the muscle isoform of the enzyme. J. Biol. Chem. 2003, 278:34084-34089.
-
(2003)
J. Biol. Chem.
, vol.278
, pp. 34084-34089
-
-
Napal, L.1
Dai, J.2
Treber, M.3
Haro, D.4
Marrero, P.F.5
Woldegiorgis, G.6
-
47
-
-
0037837797
-
Identification by mutagenesis of conserved arginine and glutamate residues in the C-terminal domain of rat liver carnitine palmitoyltransferase I that are important for catalytic activity and malonyl-CoA sensitivity
-
Treber M., Dai J., Woldegiorgis G. Identification by mutagenesis of conserved arginine and glutamate residues in the C-terminal domain of rat liver carnitine palmitoyltransferase I that are important for catalytic activity and malonyl-CoA sensitivity. J. Biol. Chem. 2003, 278:11145-11149.
-
(2003)
J. Biol. Chem.
, vol.278
, pp. 11145-11149
-
-
Treber, M.1
Dai, J.2
Woldegiorgis, G.3
-
48
-
-
0032544596
-
Redesign of choline acetyltransferase specificity by protein engineering
-
Cronin C.N. Redesign of choline acetyltransferase specificity by protein engineering. J. Biol. Chem. 1998, 273:24465-24469.
-
(1998)
J. Biol. Chem.
, vol.273
, pp. 24465-24469
-
-
Cronin, C.N.1
-
49
-
-
0034142251
-
The first 28 N-terminal amino acid residues of human heart muscle carnitine palmitoyltransferase I are essential for malonyl CoA sensitivity and high-affinity binding
-
Shi J., Zhu H., Arvidson D.N., Woldegiorgis G. The first 28 N-terminal amino acid residues of human heart muscle carnitine palmitoyltransferase I are essential for malonyl CoA sensitivity and high-affinity binding. Biochemistry 2000, 39:712-717.
-
(2000)
Biochemistry
, vol.39
, pp. 712-717
-
-
Shi, J.1
Zhu, H.2
Arvidson, D.N.3
Woldegiorgis, G.4
-
50
-
-
0037033090
-
The extreme C terminus of rat liver carnitine palmitoyltransferase I is not involved in malonyl-CoA sensitivity but in initial protein folding
-
Pan Y., Cohen I., Guillerault F., Feve B., Girard J., Prip-Buus C. The extreme C terminus of rat liver carnitine palmitoyltransferase I is not involved in malonyl-CoA sensitivity but in initial protein folding. J. Biol. Chem. 2002, 277:47184-47189.
-
(2002)
J. Biol. Chem.
, vol.277
, pp. 47184-47189
-
-
Pan, Y.1
Cohen, I.2
Guillerault, F.3
Feve, B.4
Girard, J.5
Prip-Buus, C.6
|