Rapid and progressive pulmonary fibrosis in 2 families with DNA repair deficiencies of undetermined etiology

Journal of Pediatrics

Volumn 160, Issue 4, 2012, Pages

  Vece, Timothy J ^a   Schecter, Marc G ^a   Gatti, Richard A ^b   Tunuguntla, Rashmi ^b   Garcia, Christine Kim ^c   Langston, Claire ^a   Dishop, Megan K ^d   Moore, Robert H ^a   Fan, Leland L ^e  

^a BAYLOR COLLEGE OF MEDICINE   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c UNIVERSITY OF TEXAS SOUTHWESTERN MEDICAL CENTER   (United States)

^d UNIVERSITY OF COLORADO SCHOOL OF MEDICINE   (United States)

^e University of Colorado Denver and Children s Hospital Colorado   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ATM PROTEIN; IMMUNOGLOBULIN; METHYLPREDNISOLONE;

ARTICLE; CASE REPORT; DISORDERS OF DNA SYNTHESIS AND REPAIR; DNA REPAIR; DRUG TREATMENT FAILURE; FAMILY STUDY; FEMALE; GENETIC SCREENING; HUMAN; HUMAN TISSUE; INFANT; LUNG BIOPSY; LUNG FIBROSIS; LUNG TRANSPLANTATION; MALE; PICORNAVIRUS INFECTION; PRIORITY JOURNAL;

EID: 84858340689     PISSN: 00223476     EISSN: 10976833     Source Type: Journal    
DOI: 10.1016/j.jpeds.2011.12.001     Document Type: Article

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