Isoform-specific dominant-negative effects associated with hERG1 G628S mutation in long QT syndrome

PLoS ONE

Volumn 7, Issue 8, 2012, Pages

  Stump, Matthew R ^a   Gong, Qiuming ^a   Zhou, Zhengfeng ^a  

^a OREGON HEALTH AND SCIENCE UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

POTASSIUM CHANNEL HERG;

ARTICLE; CONTROLLED STUDY; GENE; GENE FUNCTION; GENE MUTATION; GENE REPRESSION; GENETIC ASSOCIATION; HEART; HERG1A GENE; HERG1B GENE; HUMAN; HUMAN CELL; IMMUNOPRECIPITATION; LONG QT SYNDROME; MUTANT; PATCH CLAMP; STABLE EXPRESSION; WESTERN BLOTTING; WILD TYPE;

AMINO ACID SUBSTITUTION; CELL LINE; ETHER-A-GO-GO POTASSIUM CHANNELS; GENE EXPRESSION; GENE ORDER; GENES, DOMINANT; GENETIC VECTORS; HUMANS; LONG QT SYNDROME; MUTATION; MYOCARDIUM; PATCH-CLAMP TECHNIQUES; PROTEIN ISOFORMS; PROTEIN MULTIMERIZATION; PROTEIN TRANSPORT;

MAMMALIA;

EID: 84864465993     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0042552     Document Type: Article

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