Xpa deficiency reduces CAG trinucleotide repeat instability in neuronal tissues in a mouse model of SCA1

Human Molecular Genetics

Volumn 20, Issue 24, 2011, Pages 4822-4830

  Hubert Jr , Leroy ^a   Lin, Yunfu ^a   Dion, Vincent ^a,b   Wilson, John H ^a  

^a BAYLOR COLLEGE OF MEDICINE   (United States)

^b FRIEDRICH MIESCHER INSTITUTE FOR BIOMEDICAL RESEARCH   (Switzerland)

Author keywords

[No Author keywords available]

Indexed keywords

ATAXIN 1; XERODERMA PIGMENTOSUM GROUP A PROTEIN;

ALLELE; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN CORTEX; CORPUS STRIATUM; EXCISION REPAIR; FEMALE; GENE LOCUS; GENETIC STABILITY; GERMLINE MICRONUCLEUS; HIPPOCAMPUS; MALE; MOUSE; NONHUMAN; PRIORITY JOURNAL; SPINOCEREBELLAR ATAXIA TYPE 1; SPINOCEREBELLAR DEGENERATION; TRINUCLEOTIDE REPEAT;

ANIMALS; DISEASE MODELS, ANIMAL; FEMALE; GENE EXPRESSION REGULATION; GENETIC LOCI; GENOMIC INSTABILITY; GERM CELLS; HUMANS; KIDNEY; MALE; MICE; MICE, INBRED C57BL; NEOSTRIATUM; NERVE TISSUE PROTEINS; NEURONS; NUCLEAR PROTEINS; ORGAN SPECIFICITY; SPINOCEREBELLAR ATAXIAS; TRINUCLEOTIDE REPEAT EXPANSION; XERODERMA PIGMENTOSUM GROUP A PROTEIN;

EID: 81855206487     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddr421     Document Type: Article

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