Mechanisms of neurodegeneration in neuronal ceroid-lipofuscinoses

Acta Neuropathologica

Volumn 111, Issue 2, 2006, Pages 168-177

  Hachiya, Yasuo ^a   Hayashi, Masaharu ^b   Kumada, Satoko ^c   Uchiyama, Akira ^a   Tsuchiya, Kuniaki ^d   Kurata, Kiyoko ^a  

^a Metropolitan Fuchu Medical Center for Severe Motor and Intellectual Disabilities   (Japan)

^b TOKYO METROPOLITAN INSTITUTE OF MEDICAL SCIENCE   (Japan)

^c TOKYO METROPOLITAN NEUROLOGICAL HOSPITAL   (Japan)

^d TOKYO METROPOLITAN MATSUZAWA HOSPITAL   (Japan)

Author keywords

Calcium binding proteins; Immunohistochemistry; Neuronal ceroid lipofuscinosis; Oxidative stress; TUNEL

Indexed keywords

4 AMINOBUTYRIC ACID; 4 AMINOBUTYRIC ACID RECEPTOR STIMULATING AGENT; ANTIOXIDANT; CALBINDIN; CALCIUM BINDING PROTEIN; CALRETININ; DNA FRAGMENT; EXCITATORY AMINO ACID TRANSPORTER; GLUTAMATE TRANSPORTER; GLUTAMIC ACID; LIPID; PARVALBUMIN; PROTEIN; PROTEIN BCL 2; PROTEIN BCL X;

ADULT; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; BRAIN CORTEX; CASE REPORT; CELL NUCLEUS; CEREBELLUM CORTEX; CONTROLLED STUDY; CYTOPLASM; DEGENERATIVE DISEASE; EXCITOTOXICITY; FRONTAL CORTEX; GABAERGIC SYSTEM; HUMAN; HUMAN CELL; HUMAN TISSUE; HYPOGLOSSAL NUCLEUS; IMMUNOHISTOCHEMISTRY; IMMUNOREACTIVITY; INTERNEURON; LIPID OXIDATION; LYSOSOME STORAGE DISEASE; MALE; NERVE CELL NECROSIS; NERVE DEGENERATION; NEURONAL CEROID LIPOFUSCINOSIS; NICK END LABELING; ONSET AGE; OXIDATIVE STRESS; PRIORITY JOURNAL; PROTEIN EXPRESSION; SCHOOL CHILD;

ADOLESCENT; ADULT; APOPTOSIS; CALCIUM-BINDING PROTEINS; CHILD; EXCITATORY AMINO ACID TRANSPORTER 1; FEMALE; GLUTAMATE PLASMA MEMBRANE TRANSPORT PROTEINS; GLUTAMIC ACID; HUMANS; MALE; NERVE DEGENERATION; NEUROGLIA; NEURONAL CEROID-LIPOFUSCINOSES; NEUROTOXINS; OXIDATIVE STRESS;

EID: 33646202155     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00401-005-0024-x     Document Type: Article

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