The interrelationship between mitochondrial dysfunction and transcriptional dysregulation in Huntington disease

Journal of Bioenergetics and Biomembranes

Volumn 42, Issue 3, 2010, Pages 199-205

  Jin, Youngnam N ^a   Johnson, Gail V W ^a  

^a UNIVERSITY OF ROCHESTER   (United States)

Author keywords

Ca2+; Huntingtin; Mitochondria; PGC 1 PPAR ; Respiration

Indexed keywords

CALCIUM; HUNTINGTIN; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA COACTIVATOR 1ALPHA; REACTIVE OXYGEN METABOLITE; THAPSIGARGIN; HEAT SHOCK PROTEIN; MUTANT PROTEIN; PPARGC1A PROTEIN, HUMAN; TRANSCRIPTION FACTOR;

BIOGENESIS; BRAIN CELL; CALCIUM TRANSPORT; CORPUS STRIATUM; DISEASE ASSOCIATION; HUMAN; HUNTINGTON CHOREA; MEMBRANE DEPOLARIZATION; MITOCHONDRIAL MEMBRANE POTENTIAL; MITOCHONDRIAL PERMEABILITY; MITOCHONDRION; NONHUMAN; PROTEIN EXPRESSION; REVIEW; SIGNAL TRANSDUCTION; TRANSCRIPTION REGULATION; CELL RESPIRATION; GENETIC TRANSCRIPTION; GENETICS; METABOLISM; PATHOLOGY;

CALCIUM; CELL RESPIRATION; HEAT-SHOCK PROTEINS; HUMANS; HUNTINGTON DISEASE; MITOCHONDRIA; MUTANT PROTEINS; PPAR GAMMA; TRANSCRIPTION FACTORS; TRANSCRIPTION, GENETIC;

EID: 77954424991     PISSN: 0145479X     EISSN: 15736881     Source Type: Journal    
DOI: 10.1007/s10863-010-9286-7     Document Type: Review

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