-
1
-
-
0013911740
-
Ultrastructure of atrophic muscle in amyotrophic lateral sclerosis
-
Afifi A.K., Aleu F.P., Goodgold J., and MacKay B. Ultrastructure of atrophic muscle in amyotrophic lateral sclerosis. Neurology 16 (1966) 475-481
-
(1966)
Neurology
, vol.16
, pp. 475-481
-
-
Afifi, A.K.1
Aleu, F.P.2
Goodgold, J.3
MacKay, B.4
-
2
-
-
33646452761
-
Overloading of stable and exclusion of unstable human superoxide dismutase-1 variants in mitochondria of murine amyotrophic lateral sclerosis models
-
Bergemalm D., Jonsson P.A., Graffmo K.S., Andersen P.M., Brannstrom T., Rehnmark A., and Marklund S.L. Overloading of stable and exclusion of unstable human superoxide dismutase-1 variants in mitochondria of murine amyotrophic lateral sclerosis models. J. Neurosci. 26 (2006) 4147-4154
-
(2006)
J. Neurosci.
, vol.26
, pp. 4147-4154
-
-
Bergemalm, D.1
Jonsson, P.A.2
Graffmo, K.S.3
Andersen, P.M.4
Brannstrom, T.5
Rehnmark, A.6
Marklund, S.L.7
-
3
-
-
33749056809
-
ALS: a disease of motor neurons and their nonneuronal neighbors
-
Boillee S., Vande Velde C., and Cleveland D.W. ALS: a disease of motor neurons and their nonneuronal neighbors. Neuron 52 (2006) 39-59
-
(2006)
Neuron
, vol.52
, pp. 39-59
-
-
Boillee, S.1
Vande Velde, C.2
Cleveland, D.W.3
-
4
-
-
33744798774
-
Onset and progression in inherited ALS determined by motor neurons and microglia
-
Boillee S., Yamanaka K., Lobsiger C.S., Copeland N.G., Jenkins N.A., Kassiotis G., Kollias G., and Cleveland D.W. Onset and progression in inherited ALS determined by motor neurons and microglia. Science 312 (2006) 1389-1392
-
(2006)
Science
, vol.312
, pp. 1389-1392
-
-
Boillee, S.1
Yamanaka, K.2
Lobsiger, C.S.3
Copeland, N.G.4
Jenkins, N.A.5
Kassiotis, G.6
Kollias, G.7
Cleveland, D.W.8
-
5
-
-
33644832850
-
Motor neuron disease in a patient with a mitochondrial tRNAIle mutation
-
Borthwick G.M., Taylor R.W., Walls T.J., Tonska K., Taylor G.A., Shaw P.J., Ince P.G., and Turnbull D.M. Motor neuron disease in a patient with a mitochondrial tRNAIle mutation. Ann. Neurol. 59 (2006) 570-574
-
(2006)
Ann. Neurol.
, vol.59
, pp. 570-574
-
-
Borthwick, G.M.1
Taylor, R.W.2
Walls, T.J.3
Tonska, K.4
Taylor, G.A.5
Shaw, P.J.6
Ince, P.G.7
Turnbull, D.M.8
-
6
-
-
67349115326
-
Increased sensitivity of myoblasts to oxidative stress in amyotrophic lateral sclerosis peripheral tissues
-
Bradley L.J., Taanman J.W., Kallis C., and Orrell R.W. Increased sensitivity of myoblasts to oxidative stress in amyotrophic lateral sclerosis peripheral tissues. Exp. Neurol. 218 (2009) 92-97
-
(2009)
Exp. Neurol.
, vol.218
, pp. 92-97
-
-
Bradley, L.J.1
Taanman, J.W.2
Kallis, C.3
Orrell, R.W.4
-
7
-
-
0031051485
-
ALS-linked SOD1 mutant G85R mediates damage to astrocytes and promotes rapidly progressive disease with SOD1-containing inclusions
-
Bruijn L.I., Becher M.W., Lee M.K., Anderson K.L., Jenkins N.A., Copeland N.G., Sisodia S.S., Rothstein J.D., Borchelt D.R., Price D.L., and Cleveland D.W. ALS-linked SOD1 mutant G85R mediates damage to astrocytes and promotes rapidly progressive disease with SOD1-containing inclusions. Neuron 18 (1997) 327-338
-
(1997)
Neuron
, vol.18
, pp. 327-338
-
-
Bruijn, L.I.1
Becher, M.W.2
Lee, M.K.3
Anderson, K.L.4
Jenkins, N.A.5
Copeland, N.G.6
Sisodia, S.S.7
Rothstein, J.D.8
Borchelt, D.R.9
Price, D.L.10
Cleveland, D.W.11
-
8
-
-
0141642203
-
Wild-type nonneuronal cells extend survival of SOD1 mutant motor neurons in ALS mice
-
Clement A.M., Nguyen M.D., Roberts E.A., Garcia M.L., Boillee S., Rule M., McMahon A.P., Doucette W., Siwek D., Ferrante R.J., Brown Jr. R.H., Julien J.P., Goldstein L.S., and Cleveland D.W. Wild-type nonneuronal cells extend survival of SOD1 mutant motor neurons in ALS mice. Science 302 (2003) 113-117
-
(2003)
Science
, vol.302
, pp. 113-117
-
-
Clement, A.M.1
Nguyen, M.D.2
Roberts, E.A.3
Garcia, M.L.4
Boillee, S.5
Rule, M.6
McMahon, A.P.7
Doucette, W.8
Siwek, D.9
Ferrante, R.J.10
Brown Jr., R.H.11
Julien, J.P.12
Goldstein, L.S.13
Cleveland, D.W.14
-
9
-
-
0031915174
-
Cytochrome c oxidase subunit I microdeletion in a patient with motor neuron disease
-
Comi G.P., Bordoni A., Salani S., Franceschina L., Sciacco M., Prelle A., Fortunato F., Zeviani M., Napoli L., Bresolin N., Moggio M., Ausenda C.D., Taanman J.W., and Scarlato G. Cytochrome c oxidase subunit I microdeletion in a patient with motor neuron disease. Ann. Neurol. 43 (1998) 110-116
-
(1998)
Ann. Neurol.
, vol.43
, pp. 110-116
-
-
Comi, G.P.1
Bordoni, A.2
Salani, S.3
Franceschina, L.4
Sciacco, M.5
Prelle, A.6
Fortunato, F.7
Zeviani, M.8
Napoli, L.9
Bresolin, N.10
Moggio, M.11
Ausenda, C.D.12
Taanman, J.W.13
Scarlato, G.14
-
10
-
-
58149234264
-
Amyotrophic lateral sclerosis linked to a novel SOD1 mutation with muscle mitochondrial dysfunction
-
Corti S., Donadoni C., Ronchi D., Bordoni A., Fortunato F., Santoro D., Del Bo R., Lucchini V., Crugnola V., Papadimitriou D., Salani S., Moggio M., Bresolin N., and Comi G.P. Amyotrophic lateral sclerosis linked to a novel SOD1 mutation with muscle mitochondrial dysfunction. J. Neurol. Sci. 276 (2009) 170-174
-
(2009)
J. Neurol. Sci.
, vol.276
, pp. 170-174
-
-
Corti, S.1
Donadoni, C.2
Ronchi, D.3
Bordoni, A.4
Fortunato, F.5
Santoro, D.6
Del Bo, R.7
Lucchini, V.8
Crugnola, V.9
Papadimitriou, D.10
Salani, S.11
Moggio, M.12
Bresolin, N.13
Comi, G.P.14
-
11
-
-
0029809528
-
Amyotrophic lateral sclerosis: oxidative energy metabolism and calcium homeostasis in peripheral blood lymphocytes
-
Curti D., Malaspina A., Facchetti G., Camana C., Mazzini L., Tosca P., Zerbi F., and Ceroni M. Amyotrophic lateral sclerosis: oxidative energy metabolism and calcium homeostasis in peripheral blood lymphocytes. Neurology 47 (1996) 1060-1064
-
(1996)
Neurology
, vol.47
, pp. 1060-1064
-
-
Curti, D.1
Malaspina, A.2
Facchetti, G.3
Camana, C.4
Mazzini, L.5
Tosca, P.6
Zerbi, F.7
Ceroni, M.8
-
12
-
-
67651099064
-
Motor neuron survival is promoted by specific exercise in a mouse model of amyotrophic-lateral-sclerosis
-
Deforges S., Branchu J., Biondi O., Clement G., Pariset C., Lecolle S., Lopes P., Vidal P.P., Chanoine C., and Charbonnier F. Motor neuron survival is promoted by specific exercise in a mouse model of amyotrophic-lateral-sclerosis. J. Physiol. 587 Pt 14 (2009) 3561-3572
-
(2009)
J. Physiol.
, vol.587
, Issue.PART 14
, pp. 3561-3572
-
-
Deforges, S.1
Branchu, J.2
Biondi, O.3
Clement, G.4
Pariset, C.5
Lecolle, S.6
Lopes, P.7
Vidal, P.P.8
Chanoine, C.9
Charbonnier, F.10
-
13
-
-
34147131311
-
Inhibition of p38 mitogen activated protein kinase activation and mutant SOD1(G93A)-induced motor neuron death
-
Dewil M., dela Cruz V.F., Van Den Bosch L., and Robberecht W. Inhibition of p38 mitogen activated protein kinase activation and mutant SOD1(G93A)-induced motor neuron death. Neurobiol. Dis. 26 (2007) 332-341
-
(2007)
Neurobiol. Dis.
, vol.26
, pp. 332-341
-
-
Dewil, M.1
dela Cruz, V.F.2
Van Den Bosch, L.3
Robberecht, W.4
-
14
-
-
13844253540
-
Muscle expression of a local Igf-1 isoform protects motor neurons in an ALS mouse model
-
Dobrowolny G., Giacinti C., Pelosi L., Nicoletti C., Winn N., Barberi L., Molinaro M., Rosenthal N., and Musaro A. Muscle expression of a local Igf-1 isoform protects motor neurons in an ALS mouse model. J. Cell. Biol. 168 (2005) 193-199
-
(2005)
J. Cell. Biol.
, vol.168
, pp. 193-199
-
-
Dobrowolny, G.1
Giacinti, C.2
Pelosi, L.3
Nicoletti, C.4
Winn, N.5
Barberi, L.6
Molinaro, M.7
Rosenthal, N.8
Musaro, A.9
-
15
-
-
54849404282
-
Skeletal muscle is a primary target of SOD1G93A-mediated toxicity
-
Dobrowolny G., Aucello M., Rizzuto E., Beccafico S., Mammucari C., Bonconpagni S., Belia S., Wannenes F., Nicoletti C., Del Prete Z., Rosenthal N., Molinaro M., Protasi F., Fano G., Sandri M., and Musaro A. Skeletal muscle is a primary target of SOD1G93A-mediated toxicity. Cell. Metab. 8 (2008) 425-436
-
(2008)
Cell. Metab.
, vol.8
, pp. 425-436
-
-
Dobrowolny, G.1
Aucello, M.2
Rizzuto, E.3
Beccafico, S.4
Mammucari, C.5
Bonconpagni, S.6
Belia, S.7
Wannenes, F.8
Nicoletti, C.9
Del Prete, Z.10
Rosenthal, N.11
Molinaro, M.12
Protasi, F.13
Fano, G.14
Sandri, M.15
Musaro, A.16
-
16
-
-
65949094823
-
Neuromuscular junction destruction during amyotrophic lateral sclerosis: insights from transgenic models
-
Dupuis L., and Loeffler J.P. Neuromuscular junction destruction during amyotrophic lateral sclerosis: insights from transgenic models. Curr. Opin. Pharmacol. 9 (2009) 341-346
-
(2009)
Curr. Opin. Pharmacol.
, vol.9
, pp. 341-346
-
-
Dupuis, L.1
Loeffler, J.P.2
-
17
-
-
0036403767
-
Nogo provides a molecular marker for diagnosis of amyotrophic lateral sclerosis
-
Dupuis L., Gonzalez de Aguilar J.L., di Scala F., Rene F., de Tapia M., Pradat P.F., Lacomblez L., Seihlan D., Prinjha R., Walsh F.S., Meininger V., and Loeffler J.P. Nogo provides a molecular marker for diagnosis of amyotrophic lateral sclerosis. Neurobiol. Dis. 10 (2002) 358-365
-
(2002)
Neurobiol. Dis.
, vol.10
, pp. 358-365
-
-
Dupuis, L.1
Gonzalez de Aguilar, J.L.2
di Scala, F.3
Rene, F.4
de Tapia, M.5
Pradat, P.F.6
Lacomblez, L.7
Seihlan, D.8
Prinjha, R.9
Walsh, F.S.10
Meininger, V.11
Loeffler, J.P.12
-
18
-
-
0345426778
-
Up-regulation of mitochondrial uncoupling protein 3 reveals an early muscular metabolic defect in amyotrophic lateral sclerosis
-
Dupuis L., di Scala F., Rene F., de Tapia M., Oudart H., Pradat P.F., Meininger V., and Loeffler J.P. Up-regulation of mitochondrial uncoupling protein 3 reveals an early muscular metabolic defect in amyotrophic lateral sclerosis. FASEB J. 17 (2003) 2091-2093
-
(2003)
FASEB J.
, vol.17
, pp. 2091-2093
-
-
Dupuis, L.1
di Scala, F.2
Rene, F.3
de Tapia, M.4
Oudart, H.5
Pradat, P.F.6
Meininger, V.7
Loeffler, J.P.8
-
19
-
-
21844454460
-
Mitochondria in amyotrophic lateral sclerosis: a trigger and a target
-
Dupuis L., Gonzalez de Aguilar J.L., Oudart H., de Tapia M., Barbeito L., and Loeffler J.P. Mitochondria in amyotrophic lateral sclerosis: a trigger and a target. Neurodegener. Dis. 1 (2004) 245-254
-
(2004)
Neurodegener. Dis.
, vol.1
, pp. 245-254
-
-
Dupuis, L.1
Gonzalez de Aguilar, J.L.2
Oudart, H.3
de Tapia, M.4
Barbeito, L.5
Loeffler, J.P.6
-
20
-
-
3343020674
-
Evidence for defective energy homeostasis in amyotrophic lateral sclerosis: benefit of a high-energy diet in a transgenic mouse model
-
Dupuis L., Oudart H., Rene F., Gonzalez de Aguilar J.L., and Loeffler J.P. Evidence for defective energy homeostasis in amyotrophic lateral sclerosis: benefit of a high-energy diet in a transgenic mouse model. Proc. Natl. Acad. Sci. U. S. A. 101 (2004) 11159-11164
-
(2004)
Proc. Natl. Acad. Sci. U. S. A.
, vol.101
, pp. 11159-11164
-
-
Dupuis, L.1
Oudart, H.2
Rene, F.3
Gonzalez de Aguilar, J.L.4
Loeffler, J.P.5
-
21
-
-
65549128133
-
Muscle mitochondrial uncoupling dismantles neuromuscular junction and triggers distal degeneration of motor neurons
-
Dupuis L., Gonzalez de Aguilar J.L., Echaniz-Laguna A., Eschbach J., Rene F., Oudart H., Halter B., Huze C., Schaeffer L., Bouillaud F., and Loeffler J.P. Muscle mitochondrial uncoupling dismantles neuromuscular junction and triggers distal degeneration of motor neurons. PLoS One 4 (2009) e5390
-
(2009)
PLoS One
, vol.4
-
-
Dupuis, L.1
Gonzalez de Aguilar, J.L.2
Echaniz-Laguna, A.3
Eschbach, J.4
Rene, F.5
Oudart, H.6
Halter, B.7
Huze, C.8
Schaeffer, L.9
Bouillaud, F.10
Loeffler, J.P.11
-
22
-
-
0036828796
-
Mitochondrial respiratory chain function in skeletal muscle of ALS patients
-
Echaniz-Laguna A., Zoll J., Ribera F., Tranchant C., Warter J.M., Lonsdorfer J., and Lampert E. Mitochondrial respiratory chain function in skeletal muscle of ALS patients. Ann. Neurol. 52 (2002) 623-627
-
(2002)
Ann. Neurol.
, vol.52
, pp. 623-627
-
-
Echaniz-Laguna, A.1
Zoll, J.2
Ribera, F.3
Tranchant, C.4
Warter, J.M.5
Lonsdorfer, J.6
Lampert, E.7
-
23
-
-
32644434546
-
Muscular mitochondrial function in amyotrophic lateral sclerosis is progressively altered as the disease develops: a temporal study in man
-
Echaniz-Laguna A., Zoll J., Ponsot E., N'Guessan B., Tranchant C., Loeffler J.P., and Lampert E. Muscular mitochondrial function in amyotrophic lateral sclerosis is progressively altered as the disease develops: a temporal study in man. Exp. Neurol. 198 (2006) 25-30
-
(2006)
Exp. Neurol.
, vol.198
, pp. 25-30
-
-
Echaniz-Laguna, A.1
Zoll, J.2
Ponsot, E.3
N'Guessan, B.4
Tranchant, C.5
Loeffler, J.P.6
Lampert, E.7
-
25
-
-
0036992290
-
Mitochondriopathy as a differential diagnosis of amyotrophic lateral sclerosis
-
Finsterer J. Mitochondriopathy as a differential diagnosis of amyotrophic lateral sclerosis. Amyotroph. Lateral Scler. Other Motor Neuron. Disord. 3 (2002) 219-224
-
(2002)
Amyotroph. Lateral Scler. Other Motor Neuron. Disord.
, vol.3
, pp. 219-224
-
-
Finsterer, J.1
-
26
-
-
0037254203
-
Mitochondriopathy mimicking amyotrophic lateral sclerosis
-
Finsterer J. Mitochondriopathy mimicking amyotrophic lateral sclerosis. Neurologist 9 (2003) 45-48
-
(2003)
Neurologist
, vol.9
, pp. 45-48
-
-
Finsterer, J.1
-
27
-
-
16244363663
-
Lactate stress testing in sporadic amyotrophic lateral sclerosis
-
Finsterer J. Lactate stress testing in sporadic amyotrophic lateral sclerosis. Int. J. Neurosci. 115 (2005) 583-591
-
(2005)
Int. J. Neurosci.
, vol.115
, pp. 583-591
-
-
Finsterer, J.1
-
28
-
-
0345742771
-
Amyotrophic lateral sclerosis is a distal axonopathy: evidence in mice and man
-
Fischer L.R., Culver D.G., Tennant P., Davis A.A., Wang M., Castellano-Sanchez A., Khan J., Polak M.A., and Glass J.D. Amyotrophic lateral sclerosis is a distal axonopathy: evidence in mice and man. Exp. Neurol. 185 (2004) 232-240
-
(2004)
Exp. Neurol.
, vol.185
, pp. 232-240
-
-
Fischer, L.R.1
Culver, D.G.2
Tennant, P.3
Davis, A.A.4
Wang, M.5
Castellano-Sanchez, A.6
Khan, J.7
Polak, M.A.8
Glass, J.D.9
-
29
-
-
34248149517
-
Amyotrophic lateral sclerosis: all roads lead to Rome
-
Gonzalez de Aguilar J.L., Echaniz-Laguna A., Fergani A., Rene F., Meininger V., Loeffler J.P., and Dupuis L. Amyotrophic lateral sclerosis: all roads lead to Rome. J. Neurochem. 101 5 (2007) 1153-1160
-
(2007)
J. Neurochem.
, vol.101
, Issue.5
, pp. 1153-1160
-
-
Gonzalez de Aguilar, J.L.1
Echaniz-Laguna, A.2
Fergani, A.3
Rene, F.4
Meininger, V.5
Loeffler, J.P.6
Dupuis, L.7
-
30
-
-
33748261830
-
Complete dissociation of motor neuron death from motor dysfunction by Bax deletion in a mouse model of ALS
-
Gould T.W., Buss R.R., Vinsant S., Prevette D., Sun W., Knudson C.M., Milligan C.E., and Oppenheim R.W. Complete dissociation of motor neuron death from motor dysfunction by Bax deletion in a mouse model of ALS. J. Neurosci. 26 (2006) 8774-8786
-
(2006)
J. Neurosci.
, vol.26
, pp. 8774-8786
-
-
Gould, T.W.1
Buss, R.R.2
Vinsant, S.3
Prevette, D.4
Sun, W.5
Knudson, C.M.6
Milligan, C.E.7
Oppenheim, R.W.8
-
31
-
-
33847309054
-
A prospective study to evaluate the impact of 31P-MRS to determinate mitochondrial dysfunction in skeletal muscle of ALS patients
-
Grehl T., Fischer S., Muller K., Malin J.P., and Zange J. A prospective study to evaluate the impact of 31P-MRS to determinate mitochondrial dysfunction in skeletal muscle of ALS patients. Amyotroph. Lateral Scler. 8 (2007) 4-8
-
(2007)
Amyotroph. Lateral Scler.
, vol.8
, pp. 4-8
-
-
Grehl, T.1
Fischer, S.2
Muller, K.3
Malin, J.P.4
Zange, J.5
-
32
-
-
40849130169
-
Amyotrophic lateral sclerosis with ragged-red fibers
-
Hirano M., Angelini C., Montagna P., Hays A.P., Tanji K., Mitsumoto H., Gordon P.H., Naini A.B., DiMauro S., and Rowland L.P. Amyotrophic lateral sclerosis with ragged-red fibers. Arch. Neurol. 65 (2008) 403-406
-
(2008)
Arch. Neurol.
, vol.65
, pp. 403-406
-
-
Hirano, M.1
Angelini, C.2
Montagna, P.3
Hays, A.P.4
Tanji, K.5
Mitsumoto, H.6
Gordon, P.H.7
Naini, A.B.8
DiMauro, S.9
Rowland, L.P.10
-
33
-
-
62149094382
-
Cu/Zn superoxide dismutase typical for familial amyotrophic lateral sclerosis increases the vulnerability of mitochondria and perturbs Ca2+ homeostasis in SOD1G93A mice
-
Jaiswal M.K., and Keller B.U. Cu/Zn superoxide dismutase typical for familial amyotrophic lateral sclerosis increases the vulnerability of mitochondria and perturbs Ca2+ homeostasis in SOD1G93A mice. Mol. Pharmacol. 75 (2009) 478-489
-
(2009)
Mol. Pharmacol.
, vol.75
, pp. 478-489
-
-
Jaiswal, M.K.1
Keller, B.U.2
-
34
-
-
33750527780
-
The neurite outgrowth inhibitor Nogo-A promotes denervation in an amyotrophic lateral sclerosis model
-
Jokic N., Gonzalez de Aguilar J.L., Dimou L., Lin S., Fergani A., Ruegg M.A., Schwab M.E., Dupuis L., and Loeffler J.P. The neurite outgrowth inhibitor Nogo-A promotes denervation in an amyotrophic lateral sclerosis model. EMBO Rep. 7 (2006) 1162-1167
-
(2006)
EMBO Rep.
, vol.7
, pp. 1162-1167
-
-
Jokic, N.1
Gonzalez de Aguilar, J.L.2
Dimou, L.3
Lin, S.4
Fergani, A.5
Ruegg, M.A.6
Schwab, M.E.7
Dupuis, L.8
Loeffler, J.P.9
-
35
-
-
18244390714
-
Synergy of insulin-like growth factor-1 and exercise in amyotrophic lateral sclerosis
-
Kaspar B.K., Frost L.M., Christian L., Umapathi P., and Gage F.H. Synergy of insulin-like growth factor-1 and exercise in amyotrophic lateral sclerosis. Ann. Neurol. 57 (2005) 649-655
-
(2005)
Ann. Neurol.
, vol.57
, pp. 649-655
-
-
Kaspar, B.K.1
Frost, L.M.2
Christian, L.3
Umapathi, P.4
Gage, F.H.5
-
36
-
-
0038103806
-
Regular exercise is beneficial to a mouse model of amyotrophic lateral sclerosis
-
Kirkinezos I.G., Hernandez D., Bradley W.G., and Moraes C.T. Regular exercise is beneficial to a mouse model of amyotrophic lateral sclerosis. Ann. Neurol. 53 (2003) 804-807
-
(2003)
Ann. Neurol.
, vol.53
, pp. 804-807
-
-
Kirkinezos, I.G.1
Hernandez, D.2
Bradley, W.G.3
Moraes, C.T.4
-
37
-
-
0033051815
-
Neuroprotective effects of creatine in a transgenic animal model of amyotrophic lateral sclerosis
-
Klivenyi P., Ferrante R.J., Matthews R.T., Bogdanov M.B., Klein A.M., Andreassen O.A., Mueller G., Wermer M., Kaddurah-Daouk R., and Beal M.F. Neuroprotective effects of creatine in a transgenic animal model of amyotrophic lateral sclerosis. Nat. Med. 5 (1999) 347-350
-
(1999)
Nat. Med.
, vol.5
, pp. 347-350
-
-
Klivenyi, P.1
Ferrante, R.J.2
Matthews, R.T.3
Bogdanov, M.B.4
Klein, A.M.5
Andreassen, O.A.6
Mueller, G.7
Wermer, M.8
Kaddurah-Daouk, R.9
Beal, M.F.10
-
38
-
-
23444445882
-
Mitochondrial changes in skeletal muscle in amyotrophic lateral sclerosis and other neurogenic atrophies
-
Krasnianski A., Deschauer M., Neudecker S., Gellerich F.N., Muller T., Schoser B.G., Krasnianski M., and Zierz S. Mitochondrial changes in skeletal muscle in amyotrophic lateral sclerosis and other neurogenic atrophies. Brain 128 (2005) 1870-1876
-
(2005)
Brain
, vol.128
, pp. 1870-1876
-
-
Krasnianski, A.1
Deschauer, M.2
Neudecker, S.3
Gellerich, F.N.4
Muller, T.5
Schoser, B.G.6
Krasnianski, M.7
Zierz, S.8
-
39
-
-
0037119407
-
Mutated human SOD1 causes dysfunction of oxidative phosphorylation in mitochondria of transgenic mice
-
Mattiazzi M., D'Aurelio M., Gajewski C.D., Martushova K., Kiaei M., Beal M.F., and Manfredi G. Mutated human SOD1 causes dysfunction of oxidative phosphorylation in mitochondria of transgenic mice. J. Biol. Chem. 277 (2002) 29626-29633
-
(2002)
J. Biol. Chem.
, vol.277
, pp. 29626-29633
-
-
Mattiazzi, M.1
D'Aurelio, M.2
Gajewski, C.D.3
Martushova, K.4
Kiaei, M.5
Beal, M.F.6
Manfredi, G.7
-
40
-
-
0029793872
-
Quantitative immunocytochemical analysis of the spinal cord in G86R superoxide dismutase transgenic mice: neurochemical correlates of selective vulnerability
-
Morrison B.M., Gordon J.W., Ripps M.E., and Morrison J.H. Quantitative immunocytochemical analysis of the spinal cord in G86R superoxide dismutase transgenic mice: neurochemical correlates of selective vulnerability. J. Comp. Neurol. 373 (1996) 619-631
-
(1996)
J. Comp. Neurol.
, vol.373
, pp. 619-631
-
-
Morrison, B.M.1
Gordon, J.W.2
Ripps, M.E.3
Morrison, J.H.4
-
41
-
-
60549090787
-
The Psi(m) depolarization that accompanies mitochondrial Ca2+ uptake is greater in mutant SOD1 than in wild-type mouse motor terminals
-
Nguyen K.T., Garcia-Chacon L.E., Barrett J.N., Barrett E.F., and David G. The Psi(m) depolarization that accompanies mitochondrial Ca2+ uptake is greater in mutant SOD1 than in wild-type mouse motor terminals. Proc. Natl. Acad. Sci. U. S. A. 106 (2009) 2007-2011
-
(2009)
Proc. Natl. Acad. Sci. U. S. A.
, vol.106
, pp. 2007-2011
-
-
Nguyen, K.T.1
Garcia-Chacon, L.E.2
Barrett, J.N.3
Barrett, E.F.4
David, G.5
-
42
-
-
57649178442
-
Oxidative stress and energy crises in neuronal dysfunction
-
Nicholls D.G. Oxidative stress and energy crises in neuronal dysfunction. Ann. N.Y. Acad. Sci. 1147 (2008) 53-60
-
(2008)
Ann. N.Y. Acad. Sci.
, vol.1147
, pp. 53-60
-
-
Nicholls, D.G.1
-
43
-
-
48249103957
-
A systematic review of antioxidant treatment for amyotrophic lateral sclerosis/motor neuron disease
-
Orrell R.W., Lane R.J., and Ross M. A systematic review of antioxidant treatment for amyotrophic lateral sclerosis/motor neuron disease. Amyotroph. Lateral Scler. 9 (2008) 195-211
-
(2008)
Amyotroph. Lateral Scler.
, vol.9
, pp. 195-211
-
-
Orrell, R.W.1
Lane, R.J.2
Ross, M.3
-
44
-
-
0030970281
-
Oxidative stress mediates impairment of muscle function in transgenic mice with elevated level of wild-type Cu/Zn superoxide dismutase
-
Peled-Kamar M., Lotem J., Wirguin I., Weiner L., Hermalin A., and Groner Y. Oxidative stress mediates impairment of muscle function in transgenic mice with elevated level of wild-type Cu/Zn superoxide dismutase. Proc. Natl. Acad. Sci. U. S. A. 94 (1997) 3883-3887
-
(1997)
Proc. Natl. Acad. Sci. U. S. A.
, vol.94
, pp. 3883-3887
-
-
Peled-Kamar, M.1
Lotem, J.2
Wirguin, I.3
Weiner, L.4
Hermalin, A.5
Groner, Y.6
-
45
-
-
34547765317
-
Muscle Nogo-A expression is a prognostic marker in lower motor neuron syndromes
-
Pradat P.F., Bruneteau G., Gonzalez de Aguilar J.L., Dupuis L., Jokic N., Salachas F., Le Forestier N., Echaniz-Laguna A., Dubourg O., Hauw J.J., Tranchant C., Loeffler J.P., and Meininger V. Muscle Nogo-A expression is a prognostic marker in lower motor neuron syndromes. Ann. Neurol. 62 (2007) 15-20
-
(2007)
Ann. Neurol.
, vol.62
, pp. 15-20
-
-
Pradat, P.F.1
Bruneteau, G.2
Gonzalez de Aguilar, J.L.3
Dupuis, L.4
Jokic, N.5
Salachas, F.6
Le Forestier, N.7
Echaniz-Laguna, A.8
Dubourg, O.9
Hauw, J.J.10
Tranchant, C.11
Loeffler, J.P.12
Meininger, V.13
-
46
-
-
0028888945
-
Transgenic mice expressing an altered murine superoxide dismutase gene provide an animal model of amyotrophic lateral sclerosis
-
Ripps M.E., Huntley G.W., Hof P.R., Morrison J.H., and Gordon J.W. Transgenic mice expressing an altered murine superoxide dismutase gene provide an animal model of amyotrophic lateral sclerosis. Proc. Natl. Acad. Sci. U. S. A. 92 (1995) 689-693
-
(1995)
Proc. Natl. Acad. Sci. U. S. A.
, vol.92
, pp. 689-693
-
-
Ripps, M.E.1
Huntley, G.W.2
Hof, P.R.3
Morrison, J.H.4
Gordon, J.W.5
-
47
-
-
0344012223
-
Deleted 4977-bp mitochondrial DNA mutation is associated with sporadic amyotrophic lateral sclerosis: a hospital-based case-control study
-
Ro L.S., Lai S.L., Chen C.M., and Chen S.T. Deleted 4977-bp mitochondrial DNA mutation is associated with sporadic amyotrophic lateral sclerosis: a hospital-based case-control study. Muscle Nerve 28 (2003) 737-743
-
(2003)
Muscle Nerve
, vol.28
, pp. 737-743
-
-
Ro, L.S.1
Lai, S.L.2
Chen, C.M.3
Chen, S.T.4
-
48
-
-
34250612194
-
Sodium valproate exerts neuroprotective effects in vivo through CREB-binding protein-dependent mechanisms but does not improve survival in an amyotrophic lateral sclerosis mouse model
-
Rouaux C., Panteleeva I., Rene F., Gonzalez de Aguilar J.L., Echaniz-Laguna A., Dupuis L., Menger Y., Boutillier A.L., and Loeffler J.P. Sodium valproate exerts neuroprotective effects in vivo through CREB-binding protein-dependent mechanisms but does not improve survival in an amyotrophic lateral sclerosis mouse model. J. Neurosci. 27 (2007) 5535-5545
-
(2007)
J. Neurosci.
, vol.27
, pp. 5535-5545
-
-
Rouaux, C.1
Panteleeva, I.2
Rene, F.3
Gonzalez de Aguilar, J.L.4
Echaniz-Laguna, A.5
Dupuis, L.6
Menger, Y.7
Boutillier, A.L.8
Loeffler, J.P.9
-
49
-
-
33846087291
-
Mitochondrial alterations in the spinal cord of patients with sporadic amyotrophic lateral sclerosis
-
Sasaki S., and Iwata M. Mitochondrial alterations in the spinal cord of patients with sporadic amyotrophic lateral sclerosis. J. Neuropathol. Exp. Neurol. 66 (2007) 10-16
-
(2007)
J. Neuropathol. Exp. Neurol.
, vol.66
, pp. 10-16
-
-
Sasaki, S.1
Iwata, M.2
-
50
-
-
0035886521
-
Impaired oxidative metabolism in exercising muscle from ALS patients
-
Siciliano G., Pastorini E., Pasquali L., Manca M.L., Iudice A., and Murri L. Impaired oxidative metabolism in exercising muscle from ALS patients. J. Neurol. Sci. 191 (2001) 61-65
-
(2001)
J. Neurol. Sci.
, vol.191
, pp. 61-65
-
-
Siciliano, G.1
Pastorini, E.2
Pasquali, L.3
Manca, M.L.4
Iudice, A.5
Murri, L.6
-
51
-
-
0036388399
-
Impaired oxidative metabolism and lipid peroxidation in exercising muscle from ALS patients
-
Siciliano G., D'Avino C., Del Corona A., Barsacchi R., Kusmic C., Rocchi A., Pastorini E., and Murri L. Impaired oxidative metabolism and lipid peroxidation in exercising muscle from ALS patients. Amyotroph. Lateral Scler. Other Motor Neuron. Disord. 3 (2002) 57-62
-
(2002)
Amyotroph. Lateral Scler. Other Motor Neuron. Disord.
, vol.3
, pp. 57-62
-
-
Siciliano, G.1
D'Avino, C.2
Del Corona, A.3
Barsacchi, R.4
Kusmic, C.5
Rocchi, A.6
Pastorini, E.7
Murri, L.8
-
52
-
-
0141997900
-
Sexual differences in onset of disease and response to exercise in a transgenic model of ALS
-
Veldink J.H., Bar P.R., Joosten E.A., Otten M., Wokke J.H., and van den Berg L.H. Sexual differences in onset of disease and response to exercise in a transgenic model of ALS. Neuromuscul. Disord. 13 (2003) 737-743
-
(2003)
Neuromuscul. Disord.
, vol.13
, pp. 737-743
-
-
Veldink, J.H.1
Bar, P.R.2
Joosten, E.A.3
Otten, M.4
Wokke, J.H.5
van den Berg, L.H.6
-
53
-
-
0032716335
-
Visualization of defective mitochondrial function in skeletal muscle fibers of patients with sporadic amyotrophic lateral sclerosis
-
Vielhaber S., Winkler K., Kirches E., Kunz D., Buchner M., Feistner H., Elger C.E., Ludolph A.C., Riepe M.W., and Kunz W.S. Visualization of defective mitochondrial function in skeletal muscle fibers of patients with sporadic amyotrophic lateral sclerosis. J. Neurol. Sci. 169 (1999) 133-139
-
(1999)
J. Neurol. Sci.
, vol.169
, pp. 133-139
-
-
Vielhaber, S.1
Winkler, K.2
Kirches, E.3
Kunz, D.4
Buchner, M.5
Feistner, H.6
Elger, C.E.7
Ludolph, A.C.8
Riepe, M.W.9
Kunz, W.S.10
-
54
-
-
0033917463
-
Mitochondrial DNA abnormalities in skeletal muscle of patients with sporadic amyotrophic lateral sclerosis
-
Vielhaber S., Kunz D., Winkler K., Wiedemann F.R., Kirches E., Feistner H., Heinze H.J., Elger C.E., Schubert W., and Kunz W.S. Mitochondrial DNA abnormalities in skeletal muscle of patients with sporadic amyotrophic lateral sclerosis. Brain 123 Pt. 7 (2000) 1339-1348
-
(2000)
Brain
, vol.123
, Issue.PART 7
, pp. 1339-1348
-
-
Vielhaber, S.1
Kunz, D.2
Winkler, K.3
Wiedemann, F.R.4
Kirches, E.5
Feistner, H.6
Heinze, H.J.7
Elger, C.E.8
Schubert, W.9
Kunz, W.S.10
-
55
-
-
0032539791
-
Impairment of mitochondrial function in skeletal muscle of patients with amyotrophic lateral sclerosis
-
Wiedemann F.R., Winkler K., Kuznetsov A.V., Bartels C., Vielhaber S., Feistner H., and Kunz W.S. Impairment of mitochondrial function in skeletal muscle of patients with amyotrophic lateral sclerosis. J. Neurol. Sci. 156 (1998) 65-72
-
(1998)
J. Neurol. Sci.
, vol.156
, pp. 65-72
-
-
Wiedemann, F.R.1
Winkler, K.2
Kuznetsov, A.V.3
Bartels, C.4
Vielhaber, S.5
Feistner, H.6
Kunz, W.S.7
-
56
-
-
0029053881
-
An adverse property of a familial ALS-linked SOD1 mutation causes motor neuron disease characterized by vacuolar degeneration of mitochondria
-
Wong P.C., Pardo C.A., Borchelt D.R., Lee M.K., Copeland N.G., Jenkins N.A., Sisodia S.S., Cleveland D.W., and Price D.L. An adverse property of a familial ALS-linked SOD1 mutation causes motor neuron disease characterized by vacuolar degeneration of mitochondria. Neuron 14 (1995) 1105-1116
-
(1995)
Neuron
, vol.14
, pp. 1105-1116
-
-
Wong, P.C.1
Pardo, C.A.2
Borchelt, D.R.3
Lee, M.K.4
Copeland, N.G.5
Jenkins, N.A.6
Sisodia, S.S.7
Cleveland, D.W.8
Price, D.L.9
-
57
-
-
39749188753
-
Astrocytes as determinants of disease progression in inherited amyotrophic lateral sclerosis
-
Yamanaka K., Chun S.J., Boillee S., Fujimori-Tonou N., Yamashita H., Gutmann D.H., Takahashi R., Misawa H., and Cleveland D.W. Astrocytes as determinants of disease progression in inherited amyotrophic lateral sclerosis. Nat. Neurosci. 11 3 (2008) 251-253
-
(2008)
Nat. Neurosci.
, vol.11
, Issue.3
, pp. 251-253
-
-
Yamanaka, K.1
Chun, S.J.2
Boillee, S.3
Fujimori-Tonou, N.4
Yamashita, H.5
Gutmann, D.H.6
Takahashi, R.7
Misawa, H.8
Cleveland, D.W.9
|