-
3
-
-
33750310849
-
Prions and their partners in crime
-
Caughey B., and Baron G.S. Prions and their partners in crime. Nature 443 (2006) 803-810
-
(2006)
Nature
, vol.443
, pp. 803-810
-
-
Caughey, B.1
Baron, G.S.2
-
4
-
-
36049020231
-
A general model of prion strains and their pathogenicity
-
Collinge J., and Clarke A.R. A general model of prion strains and their pathogenicity. Science 318 (2007) 930-936
-
(2007)
Science
, vol.318
, pp. 930-936
-
-
Collinge, J.1
Clarke, A.R.2
-
5
-
-
0027319326
-
Mice devoid of PrP are resistant to scrapie
-
Bueler H., Aguzzi A., Sailer A., Greiner R.A., Autenried P., Aguet M., and Weissmann C. Mice devoid of PrP are resistant to scrapie. Cell 73 (1993) 1339-1347
-
(1993)
Cell
, vol.73
, pp. 1339-1347
-
-
Bueler, H.1
Aguzzi, A.2
Sailer, A.3
Greiner, R.A.4
Autenried, P.5
Aguet, M.6
Weissmann, C.7
-
6
-
-
0030054010
-
Normal host prion protein necessary for scrapie-induced neurotoxicity
-
Brandner S., Isenmann S., Raeber A., Fischer M., Sailer A., Kobayashi Y., Marino S., Weissmann C., and Aguzzi A. Normal host prion protein necessary for scrapie-induced neurotoxicity. Nature 379 (1996) 339-343
-
(1996)
Nature
, vol.379
, pp. 339-343
-
-
Brandner, S.1
Isenmann, S.2
Raeber, A.3
Fischer, M.4
Sailer, A.5
Kobayashi, Y.6
Marino, S.7
Weissmann, C.8
Aguzzi, A.9
-
7
-
-
0242363656
-
Depleting neuronal PrP in prion infection prevents disease and reverses spongiosis
-
Mallucci G., Dickinson A., Linehan J., Klohn P.C., Brandner S., and Collinge J. Depleting neuronal PrP in prion infection prevents disease and reverses spongiosis. Science 302 (2003) 871-874
-
(2003)
Science
, vol.302
, pp. 871-874
-
-
Mallucci, G.1
Dickinson, A.2
Linehan, J.3
Klohn, P.C.4
Brandner, S.5
Collinge, J.6
-
8
-
-
0042855745
-
Cytosolic prion protein in neurons
-
Mironov Jr. A., Latawiec D., Wille H., Bouzamondo-Bernstein E., Legname G., Williamson R.A., Burton D., DeArmond S.J., Prusiner S.B., and Peters P.J. Cytosolic prion protein in neurons. J. Neurosci. 23 (2003) 7183-7193
-
(2003)
J. Neurosci.
, vol.23
, pp. 7183-7193
-
-
Mironov Jr., A.1
Latawiec, D.2
Wille, H.3
Bouzamondo-Bernstein, E.4
Legname, G.5
Williamson, R.A.6
Burton, D.7
DeArmond, S.J.8
Prusiner, S.B.9
Peters, P.J.10
-
9
-
-
0034623960
-
The chaperone protein BiP binds to a mutant prion protein and mediates its degradation by the proteasome
-
Jin T., Gu Y., Zanusso G., Sy M., Kumar A., Cohen M., Gambetti P., and Singh N. The chaperone protein BiP binds to a mutant prion protein and mediates its degradation by the proteasome. J. Biol. Chem. 275 (2000) 38699-38704
-
(2000)
J. Biol. Chem.
, vol.275
, pp. 38699-38704
-
-
Jin, T.1
Gu, Y.2
Zanusso, G.3
Sy, M.4
Kumar, A.5
Cohen, M.6
Gambetti, P.7
Singh, N.8
-
10
-
-
0035476688
-
Proteasomes and ubiquitin are involved in the turnover of the wild-type prion protein
-
Yedidia Y., Horonchik L., Tzaban S., Yanai A., and Taraboulos A. Proteasomes and ubiquitin are involved in the turnover of the wild-type prion protein. EMBO J. 20 (2001) 5383-5391
-
(2001)
EMBO J.
, vol.20
, pp. 5383-5391
-
-
Yedidia, Y.1
Horonchik, L.2
Tzaban, S.3
Yanai, A.4
Taraboulos, A.5
-
11
-
-
0035910069
-
Wild-type PrP and a mutant associated with prion disease are subject to retrograde transport and proteasome degradation
-
Ma J., and Lindquist S. Wild-type PrP and a mutant associated with prion disease are subject to retrograde transport and proteasome degradation. Proc. Natl. Acad. Sci. U. S. A. 98 (2001) 14955-14960
-
(2001)
Proc. Natl. Acad. Sci. U. S. A.
, vol.98
, pp. 14955-14960
-
-
Ma, J.1
Lindquist, S.2
-
12
-
-
10644267669
-
Protection from cytosolic prion protein toxicity by modulation of protein translocation
-
Rane N.S., Yonkovich J.L., and Hegde R.S. Protection from cytosolic prion protein toxicity by modulation of protein translocation. EMBO J. 23 (2004) 4550-4559
-
(2004)
EMBO J.
, vol.23
, pp. 4550-4559
-
-
Rane, N.S.1
Yonkovich, J.L.2
Hegde, R.S.3
-
13
-
-
33751333201
-
Substrate-specific translocational attenuation during ER stress defines a pre-emptive quality control pathway
-
Kang S.W., Rane N.S., Kim S.J., Garrison J.L., Taunton J., and Hegde R.S. Substrate-specific translocational attenuation during ER stress defines a pre-emptive quality control pathway. Cell 127 (2006) 999-1013
-
(2006)
Cell
, vol.127
, pp. 999-1013
-
-
Kang, S.W.1
Rane, N.S.2
Kim, S.J.3
Garrison, J.L.4
Taunton, J.5
Hegde, R.S.6
-
14
-
-
51449098355
-
Reduced translocation of nascent prion protein during ER stress contributes to neurodegeneration
-
Rane N.S., Kang S.W., Chakrabarti O., Feigenbaum L., and Hegde R.S. Reduced translocation of nascent prion protein during ER stress contributes to neurodegeneration. Dev. Cell 15 (2008) 359-370
-
(2008)
Dev. Cell
, vol.15
, pp. 359-370
-
-
Rane, N.S.1
Kang, S.W.2
Chakrabarti, O.3
Feigenbaum, L.4
Hegde, R.S.5
-
15
-
-
0037195647
-
Neurotoxicity and neurodegeneration when PrP accumulates in the cytosol
-
Ma J., Wollmann R., and Lindquist S. Neurotoxicity and neurodegeneration when PrP accumulates in the cytosol. Science 298 (2002) 1781-1785
-
(2002)
Science
, vol.298
, pp. 1781-1785
-
-
Ma, J.1
Wollmann, R.2
Lindquist, S.3
-
16
-
-
33746615107
-
Association of Bcl-2 with misfolded prion protein is linked to the toxic potential of cytosolic PrP
-
Rambold A.S., Miesbauer M., Rapaport D., Bartke T., Baier M., Winklhofer K.F., and Tatzelt J. Association of Bcl-2 with misfolded prion protein is linked to the toxic potential of cytosolic PrP. Mol. Biol. Cell 17 (2006) 3356-3368
-
(2006)
Mol. Biol. Cell
, vol.17
, pp. 3356-3368
-
-
Rambold, A.S.1
Miesbauer, M.2
Rapaport, D.3
Bartke, T.4
Baier, M.5
Winklhofer, K.F.6
Tatzelt, J.7
-
17
-
-
33646558563
-
Molecular morphology and toxicity of cytoplasmic prion protein aggregates in neuronal and non-neuronal cells
-
Grenier C., Bissonnette C., Volkov L., and Roucou X. Molecular morphology and toxicity of cytoplasmic prion protein aggregates in neuronal and non-neuronal cells. J. Neurochem. 97 (2006) 1456-1466
-
(2006)
J. Neurochem.
, vol.97
, pp. 1456-1466
-
-
Grenier, C.1
Bissonnette, C.2
Volkov, L.3
Roucou, X.4
-
18
-
-
15744395826
-
Cytosolic prion protein (PrP) is not toxic in N2a cells and primary neurons expressing pathogenic PrP mutations
-
Fioriti L., Dossena S., Stewart L.R., Stewart R.S., Harris D.A., Forloni G., and Chiesa R. Cytosolic prion protein (PrP) is not toxic in N2a cells and primary neurons expressing pathogenic PrP mutations. J. Biol. Chem. 280 (2005) 11320-11328
-
(2005)
J. Biol. Chem.
, vol.280
, pp. 11320-11328
-
-
Fioriti, L.1
Dossena, S.2
Stewart, L.R.3
Stewart, R.S.4
Harris, D.A.5
Forloni, G.6
Chiesa, R.7
-
19
-
-
33746770348
-
The truncated 23-230 form of the prion protein localizes to the nuclei of inducible cell lines independently of its nuclear localization signals and is not cytotoxic
-
Crozet C., Vezilier J., Delfieu V., Nishimura T., Onodera T., Casanova D., Lehmann S., and Beranger F. The truncated 23-230 form of the prion protein localizes to the nuclei of inducible cell lines independently of its nuclear localization signals and is not cytotoxic. Mol. Cell. Neurosci. 32 (2006) 315-323
-
(2006)
Mol. Cell. Neurosci.
, vol.32
, pp. 315-323
-
-
Crozet, C.1
Vezilier, J.2
Delfieu, V.3
Nishimura, T.4
Onodera, T.5
Casanova, D.6
Lehmann, S.7
Beranger, F.8
-
20
-
-
0142135128
-
Cytosolic prion protein is not toxic and protects against Bax-mediated cell death in human primary neurons
-
Roucou X., Guo Q., Zhang Y., Goodyer C.G., and LeBlanc A.C. Cytosolic prion protein is not toxic and protects against Bax-mediated cell death in human primary neurons. J. Biol. Chem. 278 (2003) 40877-40881
-
(2003)
J. Biol. Chem.
, vol.278
, pp. 40877-40881
-
-
Roucou, X.1
Guo, Q.2
Zhang, Y.3
Goodyer, C.G.4
LeBlanc, A.C.5
-
21
-
-
34248351522
-
Defective retrotranslocation causes loss of anti-Bax function in human familial prion protein mutants
-
Jodoin J., Laroche-Pierre S., Goodyer C.G., and LeBlanc A.C. Defective retrotranslocation causes loss of anti-Bax function in human familial prion protein mutants. J. Neurosci. 27 (2007) 5081-5091
-
(2007)
J. Neurosci.
, vol.27
, pp. 5081-5091
-
-
Jodoin, J.1
Laroche-Pierre, S.2
Goodyer, C.G.3
LeBlanc, A.C.4
-
23
-
-
0141514771
-
Sporadic and familial CJD: classification and characterisation
-
Gambetti P., Kong Q., Zou W., Parchi P., and Chen S.G. Sporadic and familial CJD: classification and characterisation. Br. Med. Bull. 66 (2003) 213-239
-
(2003)
Br. Med. Bull.
, vol.66
, pp. 213-239
-
-
Gambetti, P.1
Kong, Q.2
Zou, W.3
Parchi, P.4
Chen, S.G.5
-
24
-
-
0034856144
-
Gerstmann-Straussler-Scheinker syndrome, fatal familial insomnia, and kuru: a review of these less common human transmissible spongiform encephalopathies
-
Collins S., McLean C.A., and Masters C.L. Gerstmann-Straussler-Scheinker syndrome, fatal familial insomnia, and kuru: a review of these less common human transmissible spongiform encephalopathies. J. Clin. Neurosci. 8 (2001) 387-397
-
(2001)
J. Clin. Neurosci.
, vol.8
, pp. 387-397
-
-
Collins, S.1
McLean, C.A.2
Masters, C.L.3
-
25
-
-
0036459944
-
Mutations of the prion protein gene phenotypic spectrum
-
Kovacs G.G., Trabattoni G., Hainfellner J.A., Ironside J.W., Knight R.S., and Budka H. Mutations of the prion protein gene phenotypic spectrum. J. Neurol. 249 (2002) 1567-1582
-
(2002)
J. Neurol.
, vol.249
, pp. 1567-1582
-
-
Kovacs, G.G.1
Trabattoni, G.2
Hainfellner, J.A.3
Ironside, J.W.4
Knight, R.S.5
Budka, H.6
-
26
-
-
0032144128
-
Inducible and reversible gene expression with the rtTA system for the study of memory
-
Mansuy I.M., Winder D.G., Moallem T.M., Osman M., Mayford M., Hawkins R.D., and Kandel E.R. Inducible and reversible gene expression with the rtTA system for the study of memory. Neuron 21 (1998) 257-265
-
(1998)
Neuron
, vol.21
, pp. 257-265
-
-
Mansuy, I.M.1
Winder, D.G.2
Moallem, T.M.3
Osman, M.4
Mayford, M.5
Hawkins, R.D.6
Kandel, E.R.7
-
27
-
-
0037076496
-
Fierce: a new mouse deletion of Nr2e1; violent behaviour and ocular abnormalities are background-dependent
-
Young K.A., Berry M.L., Mahaffey C.L., Saionz J.R., Hawes N.L., Chang B., Zheng Q.Y., Smith R.S., Bronson R.T., Nelson R.J., and Simpson E.M. Fierce: a new mouse deletion of Nr2e1; violent behaviour and ocular abnormalities are background-dependent. Behav. Brain Res. 132 (2002) 145-158
-
(2002)
Behav. Brain Res.
, vol.132
, pp. 145-158
-
-
Young, K.A.1
Berry, M.L.2
Mahaffey, C.L.3
Saionz, J.R.4
Hawes, N.L.5
Chang, B.6
Zheng, Q.Y.7
Smith, R.S.8
Bronson, R.T.9
Nelson, R.J.10
Simpson, E.M.11
-
28
-
-
33744961080
-
The interaction between cytoplasmic prion protein and the hydrophobic lipid core of membrane correlates with neurotoxicity
-
Wang X., Wang F., Arterburn L., Wollmann R., and Ma J. The interaction between cytoplasmic prion protein and the hydrophobic lipid core of membrane correlates with neurotoxicity. J. Biol. Chem. 281 (2006) 13559-13565
-
(2006)
J. Biol. Chem.
, vol.281
, pp. 13559-13565
-
-
Wang, X.1
Wang, F.2
Arterburn, L.3
Wollmann, R.4
Ma, J.5
-
29
-
-
34250158426
-
Lipid interaction converts prion protein to a PrPSc-like proteinase K-resistant conformation under physiological conditions
-
Wang F., Yang F., Hu Y., Wang X., Jin C., and Ma J. Lipid interaction converts prion protein to a PrPSc-like proteinase K-resistant conformation under physiological conditions. Biochemistry 46 (2007) 7045-7053
-
(2007)
Biochemistry
, vol.46
, pp. 7045-7053
-
-
Wang, F.1
Yang, F.2
Hu, Y.3
Wang, X.4
Jin, C.5
Ma, J.6
-
30
-
-
2942567731
-
Identification and characterization of epsilon-sarcoglycans in the central nervous system
-
Nishiyama A., Endo T., Takeda S., and Imamura M. Identification and characterization of epsilon-sarcoglycans in the central nervous system. Brain Res. Mol. Brain Res. 125 (2004) 1-12
-
(2004)
Brain Res. Mol. Brain Res.
, vol.125
, pp. 1-12
-
-
Nishiyama, A.1
Endo, T.2
Takeda, S.3
Imamura, M.4
-
31
-
-
34250644988
-
Human prion proteins with pathogenic mutations share common conformational changes resulting in enhanced binding to glycosaminoglycans
-
Yin S., Pham N., Yu S., Li C., Wong P., Chang B., Kang S.C., Biasini E., Tien P., Harris D.A., and Sy M.S. Human prion proteins with pathogenic mutations share common conformational changes resulting in enhanced binding to glycosaminoglycans. Proc. Natl. Acad. Sci. U. S. A. 104 (2007) 7546-7551
-
(2007)
Proc. Natl. Acad. Sci. U. S. A.
, vol.104
, pp. 7546-7551
-
-
Yin, S.1
Pham, N.2
Yu, S.3
Li, C.4
Wong, P.5
Chang, B.6
Kang, S.C.7
Biasini, E.8
Tien, P.9
Harris, D.A.10
Sy, M.S.11
-
32
-
-
22344438508
-
Tau suppression in a neurodegenerative mouse model improves memory function
-
Santacruz K., Lewis J., Spires T., Paulson J., Kotilinek L., Ingelsson M., Guimaraes A., DeTure M., Ramsden M., McGowan E., Forster C., Yue M., Orne J., Janus C., Mariash A., Kuskowski M., Hyman B., Hutton M., and Ashe K.H. Tau suppression in a neurodegenerative mouse model improves memory function. Science 309 (2005) 476-481
-
(2005)
Science
, vol.309
, pp. 476-481
-
-
Santacruz, K.1
Lewis, J.2
Spires, T.3
Paulson, J.4
Kotilinek, L.5
Ingelsson, M.6
Guimaraes, A.7
DeTure, M.8
Ramsden, M.9
McGowan, E.10
Forster, C.11
Yue, M.12
Orne, J.13
Janus, C.14
Mariash, A.15
Kuskowski, M.16
Hyman, B.17
Hutton, M.18
Ashe, K.H.19
-
33
-
-
0035426211
-
Dopamine D1 receptor-dependent trafficking of striatal NMDA glutamate receptors to the postsynaptic membrane
-
Dunah A.W., and Standaert D.G. Dopamine D1 receptor-dependent trafficking of striatal NMDA glutamate receptors to the postsynaptic membrane. J. Neurosci. 21 (2001) 5546-5558
-
(2001)
J. Neurosci.
, vol.21
, pp. 5546-5558
-
-
Dunah, A.W.1
Standaert, D.G.2
-
34
-
-
0030720483
-
Synapsin I interacts with c-Src and stimulates its tyrosine kinase activity
-
Onofri F., Giovedi S., Vaccaro P., Czernik A.J., Valtorta F., De Camilli P., Greengard P., and Benfenati F. Synapsin I interacts with c-Src and stimulates its tyrosine kinase activity. Proc. Natl. Acad. Sci. U. S. A. 94 (1997) 12168-12173
-
(1997)
Proc. Natl. Acad. Sci. U. S. A.
, vol.94
, pp. 12168-12173
-
-
Onofri, F.1
Giovedi, S.2
Vaccaro, P.3
Czernik, A.J.4
Valtorta, F.5
De Camilli, P.6
Greengard, P.7
Benfenati, F.8
-
35
-
-
0242668337
-
Common structure of soluble amyloid oligomers implies common mechanism of pathogenesis
-
Kayed R., Head E., Thompson J.L., McIntire T.M., Milton S.C., Cotman C.W., and Glabe C.G. Common structure of soluble amyloid oligomers implies common mechanism of pathogenesis. Science 300 (2003) 486-489
-
(2003)
Science
, vol.300
, pp. 486-489
-
-
Kayed, R.1
Head, E.2
Thompson, J.L.3
McIntire, T.M.4
Milton, S.C.5
Cotman, C.W.6
Glabe, C.G.7
-
36
-
-
2942722444
-
Hsp104 catalyzes formation and elimination of self-replicating Sup35 prion conformers
-
Shorter J., and Lindquist S. Hsp104 catalyzes formation and elimination of self-replicating Sup35 prion conformers. Science 304 (2004) 1793-1797
-
(2004)
Science
, vol.304
, pp. 1793-1797
-
-
Shorter, J.1
Lindquist, S.2
-
37
-
-
8744220663
-
Permeabilization of lipid bilayers is a common conformation-dependent activity of soluble amyloid oligomers in protein misfolding diseases
-
Kayed R., Sokolov Y., Edmonds B., McIntire T.M., Milton S.C., Hall J.E., and Glabe C.G. Permeabilization of lipid bilayers is a common conformation-dependent activity of soluble amyloid oligomers in protein misfolding diseases. J. Biol. Chem. 279 (2004) 46363-46366
-
(2004)
J. Biol. Chem.
, vol.279
, pp. 46363-46366
-
-
Kayed, R.1
Sokolov, Y.2
Edmonds, B.3
McIntire, T.M.4
Milton, S.C.5
Hall, J.E.6
Glabe, C.G.7
-
38
-
-
20444496481
-
Calcium dysregulation and membrane disruption as a ubiquitous neurotoxic mechanism of soluble amyloid oligomers
-
Demuro A., Mina E., Kayed R., Milton S.C., Parker I., and Glabe C.G. Calcium dysregulation and membrane disruption as a ubiquitous neurotoxic mechanism of soluble amyloid oligomers. J. Biol. Chem. 280 (2005) 17294-17300
-
(2005)
J. Biol. Chem.
, vol.280
, pp. 17294-17300
-
-
Demuro, A.1
Mina, E.2
Kayed, R.3
Milton, S.C.4
Parker, I.5
Glabe, C.G.6
-
39
-
-
27744459883
-
Coexistence of multiple PrPSc types in individuals with Creutzfeldt-Jakob disease
-
Polymenidou M., Stoeck K., Glatzel M., Vey M., Bellon A., and Aguzzi A. Coexistence of multiple PrPSc types in individuals with Creutzfeldt-Jakob disease. Lancet Neurol. 4 (2005) 805-814
-
(2005)
Lancet Neurol.
, vol.4
, pp. 805-814
-
-
Polymenidou, M.1
Stoeck, K.2
Glatzel, M.3
Vey, M.4
Bellon, A.5
Aguzzi, A.6
-
40
-
-
33845723131
-
Neuron-specific conditional expression of a mitochondrially targeted fluorescent protein in mice
-
Chandrasekaran K., Hazelton J.L., Wang Y., Fiskum G., and Kristian T. Neuron-specific conditional expression of a mitochondrially targeted fluorescent protein in mice. J. Neurosci. 26 (2006) 13123-13127
-
(2006)
J. Neurosci.
, vol.26
, pp. 13123-13127
-
-
Chandrasekaran, K.1
Hazelton, J.L.2
Wang, Y.3
Fiskum, G.4
Kristian, T.5
-
41
-
-
51649103992
-
Prion pathogenesis is independent of caspase-12
-
Steele A.D., Hetz C.H., Yi C.H., Jackson W.S., Borkowski A.W., Yuan J., Wollmann R.H., and Lindquist S. Prion pathogenesis is independent of caspase-12. Prion 1 (2007) 1-5
-
(2007)
Prion
, vol.1
, pp. 1-5
-
-
Steele, A.D.1
Hetz, C.H.2
Yi, C.H.3
Jackson, W.S.4
Borkowski, A.W.5
Yuan, J.6
Wollmann, R.H.7
Lindquist, S.8
-
42
-
-
36348958583
-
Diminishing apoptosis by deletion of Bax or overexpression of Bcl-2 does not protect against infectious prion toxicity in vivo
-
Steele A.D., King O.D., Jackson W.S., Hetz C.A., Borkowski A.W., Thielen P., Wollmann R., and Lindquist S. Diminishing apoptosis by deletion of Bax or overexpression of Bcl-2 does not protect against infectious prion toxicity in vivo. J. Neurosci. 27 (2007) 13022-13027
-
(2007)
J. Neurosci.
, vol.27
, pp. 13022-13027
-
-
Steele, A.D.1
King, O.D.2
Jackson, W.S.3
Hetz, C.A.4
Borkowski, A.W.5
Thielen, P.6
Wollmann, R.7
Lindquist, S.8
-
43
-
-
33747200829
-
Bax deletion does not protect neurons from BSE-induced death
-
Coulpier M., Messiaen S., Hamel R., Fernandez de Marco M., Lilin T., and Eloit M. Bax deletion does not protect neurons from BSE-induced death. Neurobiol. Dis. 23 (2006) 603-611
-
(2006)
Neurobiol. Dis.
, vol.23
, pp. 603-611
-
-
Coulpier, M.1
Messiaen, S.2
Hamel, R.3
Fernandez de Marco, M.4
Lilin, T.5
Eloit, M.6
-
44
-
-
0037306746
-
Aggresome formation by mutant prion proteins: the unfolding role of proteasomes in familial prion disorders
-
Mishra R.S., Bose S., Gu Y., Li R., and Singh N. Aggresome formation by mutant prion proteins: the unfolding role of proteasomes in familial prion disorders. J. Alzheimers Dis. 5 (2003) 15-23
-
(2003)
J. Alzheimers Dis.
, vol.5
, pp. 15-23
-
-
Mishra, R.S.1
Bose, S.2
Gu, Y.3
Li, R.4
Singh, N.5
-
45
-
-
0033551776
-
Proteasomal degradation and N-terminal protease resistance of the codon 145 mutant prion protein
-
Zanusso G., Petersen R.B., Jin T., Jing Y., Kanoush R., Ferrari S., Gambetti P., and Singh N. Proteasomal degradation and N-terminal protease resistance of the codon 145 mutant prion protein. J. Biol. Chem. 274 (1999) 23396-23404
-
(1999)
J. Biol. Chem.
, vol.274
, pp. 23396-23404
-
-
Zanusso, G.1
Petersen, R.B.2
Jin, T.3
Jing, Y.4
Kanoush, R.5
Ferrari, S.6
Gambetti, P.7
Singh, N.8
-
46
-
-
0033551458
-
An inherited prion disease with a PrP P105L mutation: clinicopathologic and PrP heterogeneity
-
Yamada M., Itoh Y., Inaba A., Wada Y., Takashima M., Satoh S., Kamata T., Okeda R., Kayano T., Suematsu N., Kitamoto T., Otomo E., Matsushita M., and Mizusawa H. An inherited prion disease with a PrP P105L mutation: clinicopathologic and PrP heterogeneity. Neurology 53 (1999) 181-188
-
(1999)
Neurology
, vol.53
, pp. 181-188
-
-
Yamada, M.1
Itoh, Y.2
Inaba, A.3
Wada, Y.4
Takashima, M.5
Satoh, S.6
Kamata, T.7
Okeda, R.8
Kayano, T.9
Suematsu, N.10
Kitamoto, T.11
Otomo, E.12
Matsushita, M.13
Mizusawa, H.14
-
47
-
-
0025681138
-
Spontaneous neurodegeneration in transgenic mice with mutant prion protein
-
[see comments]
-
Hsiao K.K., Scott M., Foster D., Groth D.F., DeArmond S.J., and Prusiner S.B. Spontaneous neurodegeneration in transgenic mice with mutant prion protein. [see comments]. Science 250 (1990) 1587-1590
-
(1990)
Science
, vol.250
, pp. 1587-1590
-
-
Hsiao, K.K.1
Scott, M.2
Foster, D.3
Groth, D.F.4
DeArmond, S.J.5
Prusiner, S.B.6
-
48
-
-
0032427904
-
Neurological illness in transgenic mice expressing a prion protein with an insertional mutation
-
Chiesa R., Piccardo P., Ghetti B., and Harris D.A. Neurological illness in transgenic mice expressing a prion protein with an insertional mutation. Neuron 21 (1998) 1339-1351
-
(1998)
Neuron
, vol.21
, pp. 1339-1351
-
-
Chiesa, R.1
Piccardo, P.2
Ghetti, B.3
Harris, D.A.4
-
49
-
-
22744448690
-
Immunodetection of disease-associated mutant PrP, which accelerates disease in GSS transgenic mice
-
Nazor K.E., Kuhn F., Seward T., Green M., Zwald D., Purro M., Schmid J., Biffiger K., Power A.M., Oesch B., Raeber A.J., and Telling G.C. Immunodetection of disease-associated mutant PrP, which accelerates disease in GSS transgenic mice. EMBO J. 24 (2005) 2472-2480
-
(2005)
EMBO J.
, vol.24
, pp. 2472-2480
-
-
Nazor, K.E.1
Kuhn, F.2
Seward, T.3
Green, M.4
Zwald, D.5
Purro, M.6
Schmid, J.7
Biffiger, K.8
Power, A.M.9
Oesch, B.10
Raeber, A.J.11
Telling, G.C.12
-
50
-
-
34247185404
-
Disease-associated prion protein oligomers inhibit the 26S proteasome
-
Kristiansen M., Deriziotis P., Dimcheff D.E., Jackson G.S., Ovaa H., Naumann H., Clarke A.R., van Leeuwen F.W., Menendez-Benito V., Dantuma N.P., Portis J.L., Collinge J., and Tabrizi S.J. Disease-associated prion protein oligomers inhibit the 26S proteasome. Mol. Cell 26 (2007) 175-188
-
(2007)
Mol. Cell
, vol.26
, pp. 175-188
-
-
Kristiansen, M.1
Deriziotis, P.2
Dimcheff, D.E.3
Jackson, G.S.4
Ovaa, H.5
Naumann, H.6
Clarke, A.R.7
van Leeuwen, F.W.8
Menendez-Benito, V.9
Dantuma, N.P.10
Portis, J.L.11
Collinge, J.12
Tabrizi, S.J.13
-
51
-
-
0033046404
-
Studies on conditional gene expression in the brain
-
Jerecic J., Single F., Kruth U., Krestel H., Kolhekar R., Storck T., Kask K., Higuchi M., Sprengel R., and Seeburg P.H. Studies on conditional gene expression in the brain. Ann. N. Y. Acad. Sci. 868 (1999) 27-37
-
(1999)
Ann. N. Y. Acad. Sci.
, vol.868
, pp. 27-37
-
-
Jerecic, J.1
Single, F.2
Kruth, U.3
Krestel, H.4
Kolhekar, R.5
Storck, T.6
Kask, K.7
Higuchi, M.8
Sprengel, R.9
Seeburg, P.H.10
-
52
-
-
12844249401
-
Calpain and other cytosolic proteases can contribute to the degradation of retro-translocated prion protein in the cytosol
-
Wang X., Wang F., Sy M.S., and Ma J. Calpain and other cytosolic proteases can contribute to the degradation of retro-translocated prion protein in the cytosol. J. Biol. Chem. 280 (2005) 317-325
-
(2005)
J. Biol. Chem.
, vol.280
, pp. 317-325
-
-
Wang, X.1
Wang, F.2
Sy, M.S.3
Ma, J.4
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