Aggresome formation by mutant prion proteins: The unfolding role of proteasomes in familial prion disorders

Journal of Alzheimer's Disease

Volumn 5, Issue 1, 2003, Pages 15-23

  Mishra, Ravi Shankar ^a   Bose, Sharmila ^a   Gu, Yaping ^a   Li, Ruliang ^a   Singh, Neena ^a  

^a CASE WESTERN RESERVE UNIVERSITY   (United States)

Author keywords

Aggresomes; CJD; Familial prion disorders; GSS; Proteasomes

Indexed keywords

MUTANT PROTEIN; PRION PROTEIN; PROTEASOME; UNCLASSIFIED DRUG;

AGGRESOME; ARTICLE; CONFORMATIONAL TRANSITION; CONTROLLED STUDY; CREUTZFELDT JAKOB DISEASE; CYTOSOL; FAMILIAL DISEASE; FLUORESCENCE; GENE MUTATION; GERSTMANN STRAUSSLER SCHEINKER SYNDROME; HUMAN; HUMAN CELL; IMMUNOPRECIPITATION; NERVE DEGENERATION; NEUROBLASTOMA CELL; NEUROTOXICITY; PRION DISEASE; PRIORITY JOURNAL; PROTEIN FOLDING; PROTEIN METABOLISM; WESTERN BLOTTING;

EID: 0037306746     PISSN: 13872877     EISSN: None     Source Type: Journal    
DOI: 10.3233/JAD-2003-5103     Document Type: Article

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