Familial and sporadic fatal insomnia

Lancet Neurology

Volumn 2, Issue 3, 2003, Pages 167-176

  Montagna, Pasquale ^a   Gambetti, Pierluigi ^c   Cortelli, Pietro ^b   Lugaresi, Elio ^a  

^a UNIVERSITY OF BOLOGNA   (Italy)

^b UNIVERSITY OF MODENA AND REGGIO EMILIA   (Italy)

^c CASE WESTERN RESERVE UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

PRION PROTEIN; AMYLOID; INFECTIOUS AMYLOID PRECURSOR PROTEIN; PRNP PROTEIN, HUMAN; PROTEIN PRECURSOR;

ASTROCYTOSIS; ATAXIA; BIOACCUMULATION; BRAIN CORTEX; CIRCADIAN RHYTHM; CLINICAL FEATURE; CREUTZFELDT JAKOB DISEASE; DREAM; DYSARTHRIA; DYSPHAGIA; FAMILIAL FATAL INSOMNIA; GENE MUTATION; HUMAN; HYPERACTIVITY; INSOMNIA; MOLECULAR BIOLOGY; MOLECULAR GENETICS; MYOCLONUS; NERVE CELL LESION; NEUROPATHOLOGY; PATHOGENESIS; PHENOTYPE; PRION DISEASE; PRIORITY JOURNAL; PYRAMIDAL SIGN; REM SLEEP; REVIEW; SLOW WAVE SLEEP; SPORADIC FATAL INSOMNIA; THALAMUS; BRAIN; DIAGNOSTIC IMAGING; DIFFERENTIAL DIAGNOSIS; ELECTROENCEPHALOGRAPHY; FATAL FAMILIAL INSOMNIA; GENETICS; NERVE DEGENERATION; NUCLEOTIDE SEQUENCE; PATHOLOGY; PRION;

AMYLOID; BRAIN; DIAGNOSIS, DIFFERENTIAL; DIAGNOSTIC IMAGING; DNA MUTATIONAL ANALYSIS; ELECTROENCEPHALOGRAPHY; HUMANS; INSOMNIA, FATAL FAMILIAL; NERVE DEGENERATION; PRIONS; PROTEIN PRECURSORS; THALAMUS;

EID: 0041851001     PISSN: 14744422     EISSN: None     Source Type: Journal    
DOI: 10.1016/S1474-4422(03)00323-5     Document Type: Review

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