Coupling cystic fibrosis to endoplasmic reticulum stress: Differential role of Grp78 and ATF6

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1772, Issue 11-12, 2007, Pages 1236-1249

  Kerbiriou, Mathieu ^a,b,c   Le Drévo, Marie Anne ^a,b,c   Férec, Claude ^a,b,c,d   Trouvé, Pascal ^a,b,c  

^a INSERM   (France)

^b FACULTÉ DE MÉDECINE ET DES SCIENCES DE LA SANTÉ   (France)

^c ETABLISSEMENT FRANÇAIS DU SANG   (France)

^d CHU MORVAN   (France)

Author keywords

ATF6; Cystic fibrosis; Endoplasmic reticulum; Grp78; Unfolded protein response

Indexed keywords

ACTIVATING TRANSCRIPTION FACTOR 6; CYCLIC AMP; GLUCOSE REGULATED PROTEIN 78; THAPSIGARGIN; TRANSMEMBRANE CONDUCTANCE REGULATOR; TUNICAMYCIN;

ARTICLE; CONTROLLED STUDY; CYSTIC FIBROSIS; ENDOPLASMIC RETICULUM STRESS; EPITHELIUM CELL; FUNCTIONAL PROTEOMICS; GENE MUTATION; GENETIC TRANSFECTION; HUMAN; HUMAN CELL; IMMUNOPRECIPITATION; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FOLDING; PROTEIN FUNCTION; RNA INTERFERENCE;

ACTIVATING TRANSCRIPTION FACTOR 6; CELL LINE; CELL MEMBRANE; CYCLIC AMP; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; ENDOPLASMIC RETICULUM; GENETIC VECTORS; HEAT-SHOCK PROTEINS; HUMANS; MOLECULAR CHAPERONES; PROTEIN BINDING; PROTEIN FOLDING; PROTEIN ISOFORMS; PROTEIN TRANSPORT; RNA, SMALL INTERFERING; THAPSIGARGIN; TRANSFECTION; TUNICAMYCIN;

EID: 36849077205     PISSN: 09254439     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbadis.2007.10.004     Document Type: Article

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