Different structural stability and toxicity of PrPARR and PrPARQ sheep prion protein variants

Journal of Neurochemistry

Volumn 103, Issue 6, 2007, Pages 2291-2300

  Paludi, Domenico ^a   Thellung, Stefano ^b   Chiovitti, Katia ^c   Corsaro, Alessandro ^b   Villa, Valentina ^b   Russo, Claudio ^d   Ianieri, Adriana ^e   Bertsch, Uwe ^f   Kretzschmar, Hans A ^f   Aceto, Antonio ^c   Florio, Tullio ^b  

^a UNIVERSITY OF TERAMO   (Italy)

^b UNIVERSITY OF GENOA   (Italy)

^c UNIVERSITY OF CHIETI   (Italy)

^d UNIVERSITY OF MOLISE   (Italy)

^e UNIVERSITY OF PARMA   (Italy)

^f UNIVERSITY OF MUNICH   (Germany)

Author keywords

Cell death; Prion protein genetic polymorphism; Sheep prion protein

Indexed keywords

PRION PROTEIN; PRION PROTEIN ALANYLARGINYLARGININE; PRION PROTEIN ALANYLARGINYLGLUTAMINE; UNCLASSIFIED DRUG;

ARTICLE; CELL DEATH; CELL VIABILITY; CONTROLLED STUDY; CYTOTOXICITY; DRUG EFFECT; DRUG MECHANISM; HUMAN; HUMAN CELL; IN VITRO STUDY; NEUROBLASTOMA CELL; PRIORITY JOURNAL; PROTEIN INTERACTION; THERMOSTABILITY;

AMYLOID; ANIMALS; APOPTOSIS; BRAIN; GENETIC PREDISPOSITION TO DISEASE; HUMANS; NERVE DEGENERATION; NEURONS; PEPTIDES; PRIONS; PROTEIN ISOFORMS; PROTEIN STRUCTURE, SECONDARY; SCRAPIE; SHEEP, DOMESTIC; SPECTRUM ANALYSIS;

ANIMALIA; OVIS; OVIS ARIES;

EID: 36448986023     PISSN: 00223042     EISSN: 14714159     Source Type: Journal    
DOI: 10.1111/j.1471-4159.2007.04934.x     Document Type: Article

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