Biochemical features of ceruloplasmin gene mutations linked to aceruloplasminemia

NeuroMolecular Medicine

Volumn 8, Issue 3, 2006, Pages 361-373

  Kono, Satoshi ^a   Suzuki, Hitoshi ^a   Oda, Toshiaki ^a   Miyajima, Hiroaki ^a   Takahashi, Yoshitomo ^a   Shirakawa, Kentaro ^a   Ishikawa, Kuniko ^b   Kitagawa, Masatoshi ^a  

^a HAMAMATSU UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^b National Hospital Organization   (Japan)

Author keywords

Aceruloplasminemia; Aggresomes; Ceruloplasmin; ER stress; GPI; GRP78; Inclusion; Mutation; Ubiquitin

Indexed keywords

CERULOPLASMIN; GAMMA TUBULIN; GLUCOSE REGULATED PROTEIN 78; GLYCOSYLPHOSPHATIDYLINOSITOL; IRON; MUTANT PROTEIN; NOCODAZOLE; PROTEASOME; PROTEASOME INHIBITOR; UBIQUITIN;

ACERULOPLASMINEMIA; AGGRESOME; ANIMAL CELL; ARTICLE; ASTROCYTE; CELL DEATH; CELL VIABILITY; CHO CELL; CONTROLLED STUDY; DEGENERATIVE DISEASE; ENDOPLASMIC RETICULUM; GENE MUTATION; GENE OVEREXPRESSION; GENETIC TRANSFECTION; HUMAN; IMMUNOFLUORESCENCE; IRON STORAGE; MICROTUBULE ORGANIZING CENTER; NONHUMAN; PRIORITY JOURNAL; PROMOTER REGION; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN TRANSPORT;

CRICETULUS GRISEUS;

EID: 33745225581     PISSN: 15351084     EISSN: None     Source Type: Journal    
DOI: 10.1385/NMM:8:3:361     Document Type: Article

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