Impaired genomic stability and increased oxidative stress exacerbate different features of Ataxia-telangiectasia

Human Molecular Genetics

Volumn 14, Issue 19, 2005, Pages 2929-2943

  Ziv, Shelly ^a   Brenner, Ori ^b   Amariglio, Ninette ^a,c   Smorodinsky, Nechama I ^a   Galron, Ronit ^a   Carrion, Danaise V ^d   Zhang, Weijia ^d   Sharma, Girdhar G ^e   Pandita, Raj K ^e   Agarwal, Manjula ^e   Elkon, Ran ^a   Katzin, Nirit ^f   Bar Am, Irit ^f   Pandita, Tej K ^e   Kucherlapati, Raju ^d   Rechavi, Gideon ^c   Shiloh, Yosef ^a   Barzilai, Ari ^a  

^a TEL AVIV UNIVERSITY   (Israel)

^b WEIZMANN INSTITUTE OF SCIENCE   (Israel)

^c SHEBA MEDICAL CENTER   (Israel)

^d HARVARD MEDICAL SCHOOL   (United States)

^e WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

^f Applied Spectral Imaging   (Israel)

Author keywords

[No Author keywords available]

Indexed keywords

ATM PROTEIN; COPPER ZINC SUPEROXIDE DISMUTASE; MYC PROTEIN; ONCOPROTEIN; PROTEIN MLH1;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; ATAXIA TELANGIECTASIA; CANCER SUSCEPTIBILITY; CHROMOSOME 12; CHROMOSOME 15; CHROMOSOME ABERRATION; CLINICAL FEATURE; CLONAL VARIATION; CONTROLLED STUDY; DISEASE EXACERBATION; FEMALE; GENE AMPLIFICATION; GENETIC PREDISPOSITION; GENOMIC INSTABILITY; GENOTYPE; GROWTH RETARDATION; HETEROZYGOSITY; IONIZING RADIATION; KNOCKOUT MOUSE; LIFESPAN; MALE; MISMATCH REPAIR; MOUSE; MOUSE STRAIN; NONHUMAN; NULL ALLELE; OXIDATIVE STRESS; PHENOTYPE; PRIORITY JOURNAL; RADIOSENSITIVITY; SURVIVAL TIME; THYMOCYTE; THYMUS LYMPHOMA; TUMOR LOCALIZATION;

ANIMALS; ATAXIA TELANGIECTASIA; CELL CYCLE PROTEINS; CHROMOSOME ABERRATIONS; DNA-BINDING PROTEINS; GENE AMPLIFICATION; GENETIC PREDISPOSITION TO DISEASE; GENOMIC INSTABILITY; GENOTYPE; LYMPHOMA; MICE; MICE, KNOCKOUT; MICROSATELLITE REPEATS; MUTATION; OXIDATIVE STRESS; PROTEIN-SERINE-THREONINE KINASES; RADIATION TOLERANCE; SUPEROXIDE DISMUTASE; THYMUS NEOPLASMS; TUMOR SUPPRESSOR PROTEINS;

ATAXIA TELANGIECTASIA;

EID: 26444513273     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddi324     Document Type: Article

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